Abstract：
:With the advent of prenatal diagnosis and the feasibility of intrauterine treatment, non-immune hydrops fetalis (NHIF) is gaining increasing importance. 14 patients are reported 10 of whom having been diagnosed prenatally. 13 were born prematurely severe asphyxia being a frequent occurrence. 7 out of 14 infants survived. In 5 cases no definite etiology could be established. In 7 patients NHIF was attributable to cardiovascular diseases, predominantly associated with brady- or tachycardia. A survey of the literature reveals that etiology remains unidentified in about 40%. For the rest fetal, maternal or placental diseases are the primary causes. The abundance of underlying diseases are operative via three pathophysiological pathways: hemodynamic disturbances, decreased oncotic pressure and increased capillary permeability. By ultrasound examination, NHIF can be detected prenatally permitting intrauterine treatment in selected cases. In combination with improved postnatal management, this might contribute to a better outcome of NIHF which is still associated with a high mortality rate. Meticulous diagnostic work-up facilitates genetic counseling and the pursuit of prenatal diagnosis in subsequent pregnancies.
journal_name
Klin Padiatrjournal_title
Klinische Padiatrieauthors
Kühl PG,Ulmer HE,Schmidt W,Wille Ldoi
10.1055/s-2008-1033984subject
Has Abstractpub_date
1985-07-01 00:00:00pages
282-7issue
4eissn
0300-8630issn
1439-3824journal_volume
197pub_type
杂志文章abstract：BACKGROUND:In study AML-BFM 87 the relapse rate was lower in patients receiving cranial irradiation (CRT). However, CRT has always been associated with adverse cognitive side effects. Therefore, the impact of CRT on neuropsychological function in children with AML was retrospectively evaluated. PATIENTS:We tested 53 c...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-2002-19861
更新日期：2002-01-01 00:00:00
abstract：:A case of true hermaphroditism was described. The patient had an uterus, a fallopian tube, a testide on the left in the position of the ovary and an ovary on the right side. The chromosome picture corresponded to a 47, XXY/46, XX/46 XXY mosaic. The phenotype of the patient was male so the decision for male sex seemed ...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：
更新日期：1976-09-01 00:00:00
abstract：:A two month old boy with Fournier's Gangrene of the scrotum as a result of unnecessary needle puncture of the hydrocele is being reported. The importance of appropriate diagnosis operation and drug-therapy is also described. ...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-2008-1034104
更新日期：1984-11-01 00:00:00
abstract：:In approximately 10% of the children suffering from juvenile chronic arthritis (JCA), rheumatic iridocyclitis was also diagnosed. In 90 JCA and iridocyclitis patients we studied relative risk, clinical course and prognosis by means of several clinical and immunological parameters. Antinuclear antibodies (ANA), selecti...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-2008-1033783
更新日期：1982-03-01 00:00:00
abstract：:An unbalanced structural chromosome aberration was found in a 6-year-old girl. Mother and maternal grandmother were shown to be carriers of a complex balanced translocation involving chromosomes 1, 5 and 15 and are of normal phenotype. The unbalanced status in the proband was defined as a partial trisomy 1p21-1p31. Pa...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-2008-1026754
更新日期：1987-01-01 00:00:00
abstract：:Neurofibromatosis type 1 is the most common of the phakomatoses and the clinical follow-up is an interdisciplinary challenge. The data of 27 patients with NF1 were systematically reviewed and compared to data from the literature. All of our patients had clinical signs of NF1. Besides the classic criteria café-au-lait ...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-2007-973086
更新日期：2007-11-01 00:00:00
abstract：:Centralized treatment of critically ill pediatric patients and related problems are presented. Pediatric intensive care allows to overbridge deranged or interrupted organ functions while simultaneously treating the disease causing the disturbance. Its efficiency depends on continuity of medical care. Medical and nursi...
journal_title：Klinische Padiatrie
pub_type： 杂志文章,评审
doi：10.1055/s-2008-1035616
更新日期：1980-09-01 00:00:00
abstract：:The aetiology and pathogenesis of the Duchenne-type muscular dystrophy (pseudohypertrophic muscular dystrophy) are still largely unknown. The possibilities of treating the disease are rather limited. Treatment is the more successful, the earlier diagnosis was possible, and the earlier treatment is initiated. The CK-Sc...
journal_title：Klinische Padiatrie
pub_type： 杂志文章,评审
doi：
更新日期：1978-11-01 00:00:00
abstract：BACKGROUND:The considerable increase of obesity in children and adolescents poses a major challenge to the health care system. METHODS:In an observation study of the Bundeszentrale für gesundheitliche Aufklärung (BZgA) somatic data of 1916 overweight and obese children and adolescents aged 8-17 years were compared to ...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-0031-1280766
更新日期：2011-12-01 00:00:00
abstract：:16 patients of studies AML-BFM-83 and -87 with allogeneic bone marrow transplantation (BMT) in first complete remission (CR) were compared with matched controls with postremission chemotherapy (CT-MC). CT-MC were selected from 250 non-grafted patients with a minimum of remission duration corresponding to the median in...
journal_title：Klinische Padiatrie
pub_type： 临床试验,杂志文章,随机对照试验
doi：10.1055/s-2007-1025355
更新日期：1992-07-01 00:00:00
abstract：:23 children with acute spinal syndromes are presented. The clinical signs were caused by trauma in 11 patients, by extramedullary tumors in 6, by operations (coarctation of the aorta, scoliosis) in 4 and by encephalomyelitis in 2. Motor signs (flaccid paraplegia or paraparesis, monoplegia, bilateral weakness) and chan...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-2007-1025246
更新日期：1993-09-01 00:00:00
abstract：:A case of a severe heroin withdrawal syndrom in a newborn infant is reported. Diagnostic and therapeutic aspects of the disease are reviewed. ...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：
更新日期：1976-11-01 00:00:00
abstract：BACKGROUND:Late effects become progressively more important for the evaluation of therapeutic success in paediatric oncology. Thus, in 1998, the Late Effects Surveillance System (LESS) started to register and assess multicentrally, prospectively and longitudinally late effects of treatment for the group of Ewing's, sof...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-2005-836503
更新日期：2005-05-01 00:00:00
abstract：:Scoring systems for evaluation of the degree of severity in patients with cystic fibrosis are critically evaluated. Cross-sectional comparison of Shwachman's score, Cooperman's score, Taussig-NIH score, Bernese score and Huang score reveals that advantages and disadvantages of each score exist. In early days used as a...
journal_title：Klinische Padiatrie
pub_type： 杂志文章,评审
doi：10.1055/s-2007-1025188
更新日期：1993-01-01 00:00:00
abstract：:Bacteriologic cultures of the vagina and the cervix of 38 praepubertal children, aged 3 months to 16 years (average age 9 years) from the outpatient department for infants and juveniles of the 1st Department of Obstetrics and Gynecology of the University of Vienna were obtained vaginascopically using anaerobic transpo...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-2008-1033769
更新日期：1982-01-01 00:00:00
abstract：:The GPOH-MAHO trials designed in 3/82 and 7/88 for treatment of childhood testicular germ cell tumors registered 3/92 105 pts. In MAHO 82 study 57 pts. and in MAHO 88 study 48 pts. were treated. Histologically 60% of the tumors revealed yolk sac tumors (YST), 22% teratomas (TD) and 18% malignant teratomas (MTI, MTU, M...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-2007-1025231
更新日期：1993-07-01 00:00:00
abstract：BACKGROUND:A fast and comprehensive diagnostic by means of whole-body CT has been shown to reduce mortality in the adult trauma population. Therefore whole-body CT seems to be the standard in adult trauma-patients. Due to the higher radiation exposure of whole-body CT the use of this diagnostic toll in pediatric trauma...
journal_title：Klinische Padiatrie
pub_type： 杂志文章,多中心研究
doi：10.1055/s-0035-1547311
更新日期：2015-07-01 00:00:00
abstract：:A familial cerebral malformation combined with chronic hypernatremia is reported. We found three children of a Moroccan family with microcephaly and hypoplasia of the frontal brain. The frontal parts of the lateral ventricles were absent. Two of the children had a defect of the midline structures with fusion of the la...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-2008-1033901
更新日期：1986-09-01 00:00:00
abstract：BACKGROUND:Children suffering from life limiting diseases are frequently cared for by adult palliative care teams due to missing paediatric structures in that field. However it is questionable whether palliative care curricula for physicians comprehensively cover issues of paediatric palliative care (PaedPC). AIM:To i...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-0035-1569266
更新日期：2016-01-01 00:00:00
abstract：:Bacterial endocarditis belongs to the rare diseases in childhood. It occurs usually as a single episode and almost exclusively in children with congenital heart disease. In recent years, however, an increased number of renewed endocarditis after the first episode were reported, especially in drug addicts. We present a...
journal_title：Klinische Padiatrie
pub_type： 杂志文章,评审
doi：10.1055/s-2008-1046498
更新日期：1995-01-01 00:00:00
abstract：:A multi-center retrospective survey was conducted to evaluate the incidence and types of hemostatic complications occurring in children with acute lymphoblastic leukemia (ALL) during treatment according to the ALL-BFM-90 treatment protocol. All of the BFM-treatment centers (n = 77) were approached and a 95% response r...
journal_title：Klinische Padiatrie
pub_type： 杂志文章,多中心研究
doi：10.1055/s-2008-1043788
更新日期：1999-07-01 00:00:00
abstract：:Iron concentration was determined by the aid of the ESA Ferrochem 3050 analyzer and the bathophenanthroline method with deproteinization. Both methods showed a good precision and accuracy. The investigation was carried out in 505 sera with an iron concentration between 9 and 333 micrograms/dl. The comparison of the tw...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-2008-1033773
更新日期：1982-01-01 00:00:00
abstract：:In 20 children with mumps and mumps meningitis thrombocyte functions, the thrombopoiesis and the platelet count were examinated over a four week period. The spontaneous, standardized platelet adhesion and aggregation on silikonized glass surface showed a statistically significant increase from the 5th to the 15th day ...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：
更新日期：1977-09-01 00:00:00
abstract：BACKGROUND:17beta hydroxysteroid dehydrogenase deficiency is a presumable rare cause for a severe virilization disorder in children with 46,XY karyotype due to a defect in the testicular testosterone biosynthesis from androstenedione. PATIENT:We report on a 14 year old child with 46,XY karyotype with a predominantly f...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-2002-34015
更新日期：2002-09-01 00:00:00
abstract：:The case of a newborn with duplications of rectum, presenting as a tumor of the labia majora, and duplication of bladder and urethra is reported. In addition malformations from the VACTERL-association (sacral malformation, anal atresia with vestibulum fistula, renal dysplasia, only eleven pairs of ribs with hypoplasia...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-2008-1026776
更新日期：1987-03-01 00:00:00
abstract：:Glutaracidemia/glutaraciduria type I is an acute or subacute neuropathic disorder of infancy or early childhood. The following symptoms characterize the clinical course: macrocephalus present at birth, cerebral atrophy revealed by CT or MRI scans, most striking in the frontal and temporal lobes, choreoathetosis and dy...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-2007-1025211
更新日期：1993-03-01 00:00:00
abstract：BACKGROUND:Drug handling in paediatric intensive care units (PICU) is prone to medication errors. We aimed to identify type and prevalence of those errors and to assess preventative interventions. METHODS:Prospective intervention study investigating a 3-step intervention for preventing errors in drug handling in a 10-...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-0033-1364030
更新日期：2014-04-01 00:00:00
abstract：BACKGROUND:Thyroglossal duct cysts arise from mucus production in an incomplete regressed thyroglossal duct. Often they are only noticed in case of infection or secondary fistulation. The operative management is a Sistrunk procedure. METHOD AND PATIENTS:In a retrospective study we analyse 26 patients aged 0,3 - 10 yea...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-2001-17223
更新日期：2001-09-01 00:00:00
abstract：:630 neonates with risk factors of perinatal hearing impairment were screened of hearing loss by means of registration of transient otoacoustic emissions before discharge from the newborn nursery. Neonates were screened additionally by means of brainstem evoked response audiometry, if they had bilateral negative emissi...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-2008-1043853
更新日期：1998-03-01 00:00:00
abstract：:In 24 patients at risk for SIDS (12 infants with a near miss event and 12 infants with apnea and perioral cyanosis during sleep) respiratory and esophageal function were investigated by impedance pneumography (IP) and esophageal manometry combined with simultaneous pH-monitoring (EMPH). Both groups had ad early pathol...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-2007-1025483
更新日期：1990-01-01 00:00:00
