[Hyperammonemia due to ornithine transcarbamylase deficiency--a cause of lethal metabolic crisis during the newborn period and infancy (author's transl)].

abstract：:About 2% of the general population and up to 6% of children suffer from food allergy. Cow's milk is charged with a important role in infancy after weaning, since conventional formula are based on its procession. IgE-mediated and Non-IgE- mediated allergic reactions, which are different in manifestation and pathogenesi...

journal_title：Klinische Padiatrie

authors： Kirchlechner V,Dehlink E,Szepfalusi Z

更新日期：2007-07-01 00:00:00

abstract：BACKGROUND:Gender differences in overall neonatal survival and in short term pulmonary outcome have been reported. Furthermore gender differences in childhood chronic lung disorders have been described all in favor of females. METHODS:A typical survey on published data regarding gender differences in lung development ...

journal_title：Klinische Padiatrie

authors： Gortner L,Shen J,Tutdibi E

更新日期：2013-03-01 00:00:00

abstract：:The article reports on the case history of a 8 month old baby who fell ill of a ileocolic intussusception. The barium enema demonstrated the typical cupping in the head of the barium. The successful reposition by hydrostatic pressure was manifest by barium reflux in the small intestine. ...

journal_title：Klinische Padiatrie

authors： Klingmüller V

更新日期：1983-07-01 00:00:00

abstract：:Growing teratoma is still an often unsolved problem especially in male with mixed malignant GCTs of the testis or the mediastinum. This specific situation with progressive tumor growth and simultaneous normalization of tumor markers during or after treatment of malignant GCTs with teratomatous elements is judged as a ...

journal_title：Klinische Padiatrie

authors： Calaminus G,Schneider DT,Weissbach L,Schönberger S,Okpanyi V,Leuschner I,Poremba C,Göbel U

更新日期：2009-05-01 00:00:00

abstract：:Within the scope of an observation study 40 premature low birth weight infants requiring parenteral nutrition received either 10% or 20% lipid emulsions (Lipovenös) for 7 days. The 10% lipid emulsion differs from the 20% lipid emulsion in the higher phospholipid/triglyceride-ratio (0.06 resp. 0.12). Lipid infusion was...

journal_title：Klinische Padiatrie

authors： Hanssler L,Schlotzer E,Blenkers B,Roll C,Zhou C,Kordass U

更新日期：1992-01-01 00:00:00

abstract：:The synchronous occurrence of blasts of the lymphatic and myelogenous lineage in acute leukemia has been rarely observed. Reviewing individual case reports it is suggested that malignant transformation already starts at the level of the stem cell. We are reporting a case of a 13-year old boy who initially showed morph...

journal_title：Klinische Padiatrie

authors： Creutzig U,Eschenbach C,Ritter J,Schellong G

更新日期：1981-05-01 00:00:00

abstract：:In 20 children with mumps and mumps meningitis thrombocyte functions, the thrombopoiesis and the platelet count were examinated over a four week period. The spontaneous, standardized platelet adhesion and aggregation on silikonized glass surface showed a statistically significant increase from the 5th to the 15th day ...

journal_title：Klinische Padiatrie

authors： Lemanczyk S,Podolsak B

更新日期：1977-09-01 00:00:00

abstract：:Bacterial endocarditis belongs to the rare diseases in childhood. It occurs usually as a single episode and almost exclusively in children with congenital heart disease. In recent years, however, an increased number of renewed endocarditis after the first episode were reported, especially in drug addicts. We present a...

journal_title：Klinische Padiatrie

authors： Hunkert F,Handrick W,Kinzel P,Schneider P,Spencker FB,Günther E

更新日期：1995-01-01 00:00:00

abstract：BACKGROUND:Reimbursement of inpatient treatment by daily constant charges is replaced by diagnosis- and procedure-related group system (G-DRG) in German acute care hospitals excerpt for psychiatry since 2004. Re-designs of G-DRG system were undertaken in 2005 and 2006. Parallel to implementation requirement- and resour...

journal_title：Klinische Padiatrie

authors： Christaras A,Schaper J,Strelow H,Laws HJ,Göbel U

更新日期：2006-11-01 00:00:00

abstract：:Report of accidental ingestion and aspiration of lamp oil of a boy aged 16 months. He develops in a few hours a severe pneumonitis with tachycardia. Echocardiography shows diminished contractability. After losing his symptoms, the chest x-rays on the 13th day show bilateral pneumatoceles. The course remains asymptomat...

journal_title：Klinische Padiatrie

authors： Leuchter D,Stübecke W,Oberschulte-Beckmann D

更新日期：1998-11-01 00:00:00

abstract：BACKGROUND:One of the strongest predictive factors for therapy outcome in childhood acute lymphoblastic leukaemia (ALL), treated according to ALL-BFM protocols, is the response to initial prednisone treatment. Prednisone response is characterized by the peripheral leukaemic blast count. The threshold value for the char...

journal_title：Klinische Padiatrie

authors： Lauten M,Stanulla M,Zimmermann M,Welte K,Riehm H,Schrappe M

更新日期：2001-07-01 00:00:00

abstract：BACKGROUND:The aim of the present study was to evaluate paediatric reference values for platelet function using a point-of-care whole blood impedance aggregometry. METHODS, RESULTS & CONCLUSION: In 265 healthy infants and children aged

journal_title：Klinische Padiatrie

authors： Halimeh S,Angelis Gd,Sander A,Edelbusch C,Rott H,Thedieck S,Mesters R,Schlegel N,Nowak-Göttl U

更新日期：2010-05-01 00:00:00

abstract：:Prolactin levels were measured immediately after the seizure in some, and 15 to 20 minutes later in all of 67 children aged between 6 months and 17 years. Values were determined after grand mal, complex partial and petit mal seizures and psychogen seizures. A more than 2 to 3 fold prolactin increase over the baseline ...

journal_title：Klinische Padiatrie

authors： Kurlemann G,Heyen P,Menges EM,Palm DG

更新日期：1992-05-01 00:00:00

abstract：:The Austrian Screening Program performed during the last 12 years 5,833.381 tests in 1,003.841 newborns to detect at last 10 different disorders. 225 cases were uncovered: 81 PKU, 1 Dihydropteridine-Reductase-Deficiency, 37 Hyperphenylalaninemias of long duration, 23 Galactosemias by Transferase deficiency, 6 by Kinas...

journal_title：Klinische Padiatrie

authors： Thalhammer O,Scheibenreiter S,Knoll E,Wehle E,Schön R

更新日期：1980-11-01 00:00:00

abstract：:The investigation of Immunoglobulins-and Total protein concentrations in saliva of healthy children shows an agreement with literature, a maturation in individual development of the saliva-producing organs in the mouth. ...

journal_title：Klinische Padiatrie

authors： Tympner KD,Dörfler S

更新日期：1980-09-01 00:00:00

abstract：:While many aspects related to the etiology and pathogenesis of sudden infant death remain unclear, the ultimate trigger event appears to be an acute regulatory disturbance of the cardiorespiratory neurons of the reticular formation of the brain stem. Retrospective studies have demonstrated that SIDS often occurs after...

journal_title：Klinische Padiatrie

authors： Sterniste W,Bock W

更新日期：1992-03-01 00:00:00

abstract：:A familial cerebral malformation combined with chronic hypernatremia is reported. We found three children of a Moroccan family with microcephaly and hypoplasia of the frontal brain. The frontal parts of the lateral ventricles were absent. Two of the children had a defect of the midline structures with fusion of the la...

journal_title：Klinische Padiatrie

authors： Franek A,Böcker H,Kahlen T

更新日期：1986-09-01 00:00:00

abstract：:The secretory IgA system is common to all mucosal membranes and is presumably of great importance for their defense. In addition to the secretory IgA antibodies produced in a mucosa in response to a local antigenic stimulus there is a spread of this type of IgA response via committed lymphocytes. They originate from c...

journal_title：Klinische Padiatrie

authors： Hanson LA,Andersson B,Carlsson B,Dahlgren U,Mellander L,Porras O,Svanborg Edén C,Söderström T

更新日期：1985-07-01 00:00:00

abstract：:Evoked otoacoustic emissions (EOAE) and brainstem acoustic evoked potentials (BAEP) were recorded from 78 children following neonatal intensive care. In 23% no EOAE could be obtained. Hearing impairment in the BAEP was found in 9%. In 22% negative EOAE were found in spite of normal BAEP. According to the latency-inten...

journal_title：Klinische Padiatrie

authors： Lauffer H,Pröschel U,Gerling S,Wenzel D

更新日期：1994-03-01 00:00:00

abstract：:Members of the histone deacetylase (HDAC) family exhibit great promise as potential drug targets in pediatric tumors including neuroblastoma, medulloblastoma, ependymoma and Ewing's sarcoma. HDAC inhibitors of various structural classes have shown anti-tumoral effects in pre-clinical pediatric tumor models as single a...

journal_title：Klinische Padiatrie

authors： Witt O,Milde T,Deubzer HE,Oehme I,Witt R,Kulozik A,Eisenmenger A,Abel U,Karapanagiotou-Schenkel I

更新日期：2012-10-01 00:00:00

abstract：:Guillain Barré syndrome (GBS; Synonyma: Polyneuritis, Polyradikulitis) is an acute, inflammatory, demyelinating disease of the peripheral nerve system. Clinical hallmarks are symmetric muscle paralysis, areflexia and pronounced autonomic disturbances. Respiratory failure and cardiovascular instability are the main rea...

journal_title：Klinische Padiatrie

authors： Erler T,Weidner B,Wetzel U,Grunske A

更新日期：2008-03-01 00:00:00

abstract：:160 children aged 1 to 12 years with clinical diagnosis of bacterial pharyngitis and/or tonsillitis were treated either with cefixime ready-to-use-suspension or penicillin V in an open, controlled and randomized multicenter study. Before treatment a rapid antigen detection test was accomplished and throat swabs were t...

journal_title：Klinische Padiatrie

authors： Adam D,Hostalek U,Tröster K

更新日期：1996-09-01 00:00:00

abstract：:We report on a 13.2 years old boy who was treated for tall stature (expected target height of 204.8 +/- 5.4 cm) with high dose of testosterone. Therapy for height reduction was started with testosterone injections (250 mg Testoviron Depot i.m.) once a week. There occurred no side effects during 6 months of treatment. ...

journal_title：Klinische Padiatrie

authors： Weimann E,Böhles HJ

更新日期：1999-09-01 00:00:00

abstract：BACKGROUND:Empirical results about the cognitive, motor and psychic development in patients with d-transposition of the great arteries after arterial switch operation remain unclear. Potential reasons are the patients' initial status, improved perinatal care or the quality of surgery. To exclude quality of surgery as t...

journal_title：Klinische Padiatrie

authors： Vahsen N,Kavsek M,Toussaint-Götz N,Schneider K,Urban AE,Schneider M

更新日期：2009-01-01 00:00:00

abstract：:We analyzed episodes of peritonitis and/or sepsis associated with the idiopathic nephrotic syndrome (ns) in 23 children treated between 1975 and 1985 at our clinic. 37.5% of the children with infantile ns, 16% of those with steroidsensible ns, and 13.6% of those with steroidresistant ns developed peritonitis. Children...

journal_title：Klinische Padiatrie

authors： Feldhoff C,Kleine L,Bachmann H

更新日期：1988-01-01 00:00:00

abstract：:From 1975-1986 6 boys with congenital nephrogenic diabetes insipidus were diagnosed at the age of 3 months to 10 years. Symptoms appeared within the first few weeks of life. The diagnosis was confirmed by polyuria, low urinary osmolality (97-225 mosm/kg H20), hypernatraemia (max. 171 mmol/l) and the missing response t...

journal_title：Klinische Padiatrie

authors： Kaulitz R,Brodehl J

更新日期：1989-11-01 00:00:00

abstract：:16 patients of studies AML-BFM-83 and -87 with allogeneic bone marrow transplantation (BMT) in first complete remission (CR) were compared with matched controls with postremission chemotherapy (CT-MC). CT-MC were selected from 250 non-grafted patients with a minimum of remission duration corresponding to the median in...

journal_title：Klinische Padiatrie

authors： Creutzig U,Bender-Götze C,Klingebiel T,Ebell W,Friedrich W,Stollmann-Gibbels B,Schmidt H,Suttorp M,Gratwohl A,Heyen P

更新日期：1992-07-01 00:00:00

abstract：:To evaluate the impact of megatherapy on the outcome of high risk neuroblastoma, 39 patients with stage IV neuroblastoma, who underwent megatherapy, were analyzed retrospectively and compared to 49 patients, who continued chemotherapy according to the German cooperative trial NB85. The groups were comparable concernin...

journal_title：Klinische Padiatrie

authors： Hero B,Kremens B,Klingebiel T,Bender-Götze C,Burdach S,Schrappe M,Berthold F

更新日期：1997-07-01 00:00:00

abstract：:Dimenhydrinate overdosage in a 3(1/2) year-old-girl with dilative cardiomyopathy. Dimenhydrinate (Vomex(R)) is frequently used in the treatment of sickness and vomiting. The symptoms of overdosage present like an anticholinergic syndrome. We report on the clinical findings of an intoxication with dimenhydrinate in a 3...

journal_title：Klinische Padiatrie

authors： Girisch M,Hofbeck M,Rauch R,Apitz C,Sieverding L

更新日期：2009-01-01 00:00:00

abstract：BACKGROUND:In the German guidelines for prophylaxis of group B streptococcal (GBS) early onset sepsis in neonates (EOS), GBS screening of all pregnant women has been recommended, but is not yet included in the Maternity Directives. Aim of the study was to identify temporal trends in incidence of EOS and their associati...

journal_title：Klinische Padiatrie

authors： Sorg AL,Obermeier V,Armann J,Klemme M,von Kries R

更新日期：2021-01-01 00:00:00