Abstract：
UNLABELLED:Sickle cell disease is a chronic hematologic disease with variable but often severe systemic symptoms. In this report, we describe a 6-year-old boy presenting with acute bowel pseudo-obstruction. During this episode, previously undiagnosed sickle cell disease was discovered upon peripheral blood smear analysis. The condition was therefore interpreted as a massive intestinal vaso-occlusive crisis or "girdle syndrome". Conservative treatment with hydration therapy, analgesia and a manual partial exchange transfusion was initiated. The patient fully recovered within 5 days. CONCLUSION:Girdle syndrome is a rare but severe adverse event associated with sickle cell disease that must be considered as differential diagnosis in patients with sickle cell disease.
journal_name
Klin Padiatrjournal_title
Klinische Padiatrieauthors
Knorr M,Bienemann K,Walde G,Kaufhold A,Schündeln MMdoi
10.1055/s-0034-1389907subject
Has Abstractpub_date
2014-11-01 00:00:00pages
372-4issue
6-7eissn
0300-8630issn
1439-3824journal_volume
226pub_type
杂志文章abstract：UNLABELLED:It was the aim of the cooperative therapy study HD-82 for children with Hodgkin's disease to reduce chemo- and radiotherapy and to investigate of a strategy for selective splenectomy previously developed in the Hodgkin study HD-78. Between December 1981 and December 1984 207 patients (131 boys and 76 girls) ...
journal_title：Klinische Padiatrie
pub_type： 临床试验,杂志文章
doi：10.1055/s-2008-1026870
更新日期：1986-05-01 00:00:00
abstract：:This report describes the case of a 10 days old newborn of a diabetic mother with gestosis, who developed erythema and swelling of the right cheek. A diagnosis of acute suppurative parotitis due to S. aureus was made. Following this case report the most important facts of epidemiology, pathogenesis, clinical manifesta...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-2004-822675
更新日期：2005-03-01 00:00:00
abstract：:Scoring systems for evaluation of the degree of severity in patients with cystic fibrosis are critically evaluated. Cross-sectional comparison of Shwachman's score, Cooperman's score, Taussig-NIH score, Bernese score and Huang score reveals that advantages and disadvantages of each score exist. In early days used as a...
journal_title：Klinische Padiatrie
pub_type： 杂志文章,评审
doi：10.1055/s-2007-1025188
更新日期：1993-01-01 00:00:00
abstract：:The oscillatory resistance to respiration (Ros) was measured in 218 children and 260 adults using the Siregnost FD5 (Siemens, Erlangen), and compared with whole body plethysmography (Raw) and with spirometry. There was a markedly better correlation between Ros and Raw (r=0.82;n=88) in children than in adults (r=0.53;n...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-2008-1034434
更新日期：1981-03-01 00:00:00
abstract：:Background: Transient synovitis is the most common hip joint disorder in children. Perthes disease occurs around the same age and may not be distinguishable to an episode of transient synovitis in the early stage. Therefore all children in our clinic with transient synovitis underwent a follow-up X-ray 3 months later ...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-0042-116150
更新日期：2017-03-01 00:00:00
abstract：:Members of the histone deacetylase (HDAC) family exhibit great promise as potential drug targets in pediatric tumors including neuroblastoma, medulloblastoma, ependymoma and Ewing's sarcoma. HDAC inhibitors of various structural classes have shown anti-tumoral effects in pre-clinical pediatric tumor models as single a...
journal_title：Klinische Padiatrie
pub_type： 杂志文章,多中心研究
doi：10.1055/s-0032-1323692
更新日期：2012-10-01 00:00:00
abstract：:Initially a right sided pulmonary hypoplasia was diagnosed in our patient at the age of 9 years. The previous years were characterized by recurrent pneumonia, bronchitis and daily coughing fits. Findings of the chest radiograph suggested the diagnosis of right sided hypoplasia. The right hemithorax was small with medi...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-2007-1025500
更新日期：1990-03-01 00:00:00
abstract：:Problems of terminology, differential diagnosis, etiology and therapy of language development disorders are demonstrated by a casuistic example. Besides the importance of clinical date special attention was laid on neuropsychological diagnostic procedures and their therapeutic implications. Therapeutic interventions c...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：
更新日期：1978-09-01 00:00:00
abstract：:Case report of arthrogryposis multiplex congenita with histologically proved neutrogene atrophy of muscles. The also existing reduction deformities of the limbs, showing aplasia and hypoplasia of phalanges may hypothetically be of neuropathic origin. ...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：
更新日期：1979-05-01 00:00:00
abstract：BACKGROUND:Up to now, no German language test for children has been controlled for diagnostic accuracy. Therefore the application of language tests in clinical diagnostics is limited. The aim of the study was to determine the diagnostic validity of the SBE-3-KT, a parent questionnaire for identification of children wit...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-0030-1267156
更新日期：2010-12-01 00:00:00
abstract：:About 2% of the general population and up to 6% of children suffer from food allergy. Cow's milk is charged with a important role in infancy after weaning, since conventional formula are based on its procession. IgE-mediated and Non-IgE- mediated allergic reactions, which are different in manifestation and pathogenesi...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-2006-921357
更新日期：2007-07-01 00:00:00
abstract：:Although the etiology of maldescended testes is multifactorial, dysfunction of hypothalamic-pituitary-gonadal axis should be considered as the most important factor. The hormonal treatment with Gn-RH on its own or followed by hCG can provoke testicular descent and should be applied at 10th month of life. Failure, part...
journal_title：Klinische Padiatrie
pub_type： 杂志文章,评审
doi：10.1055/s-2008-1026745
更新日期：1989-11-01 00:00:00
abstract：BACKGROUND:Hypoallergenic infant formulas (HAF) were developed for atopy prevention in infants with high risk of atopy if these cannot be breastfed. HAF mount an antigen-specific immune response in infants. The aim of the study was to analyse the immune response in infants fed with a new infant formula based on a whey ...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-2003-42664
更新日期：2003-09-01 00:00:00
abstract：BACKGROUND:Most recent studies analyzing candidate biological prognostic factors in childhood medulloblastoma (MB) are limited by small patient numbers due to dependence on fresh-frozen tumor material. By contrast, large archives of formalin-fixed, paraffin-embedded MB samples exist from homogeneously treated patients....
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-2007-985843
更新日期：2007-11-01 00:00:00
abstract：:We report the first case of non-immune hydrops fetalis (NIHF) with trisomy 15q11/17q22.5 resulting from a familial translocation 15/17. Furthermore the cytogenetic findings of 50 cases with hydrops fetalis are presented. Of the 30 cytogenetic analyzable cases 7 showed chromosomal abnormalities (4x45,X; 2x47,XY,+21; 1x...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-2008-1026810
更新日期：1987-07-01 00:00:00
abstract：:This notebook which is of postcard size contains important information in case of emergency and details about the current illness and treatment. It contains follow-up information about the pattern of growth, endocrinological development and assessment of renal tubular function. The necessary follow-up investigations a...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-2008-1046621
更新日期：1994-07-01 00:00:00
abstract：:160 children aged 1 to 12 years with clinical diagnosis of bacterial pharyngitis and/or tonsillitis were treated either with cefixime ready-to-use-suspension or penicillin V in an open, controlled and randomized multicenter study. Before treatment a rapid antigen detection test was accomplished and throat swabs were t...
journal_title：Klinische Padiatrie
pub_type： 临床试验,杂志文章,多中心研究,随机对照试验
doi：10.1055/s-2008-1046489
更新日期：1996-09-01 00:00:00
abstract：BACKGROUND:Thyroglossal duct cysts arise from mucus production in an incomplete regressed thyroglossal duct. Often they are only noticed in case of infection or secondary fistulation. The operative management is a Sistrunk procedure. METHOD AND PATIENTS:In a retrospective study we analyse 26 patients aged 0,3 - 10 yea...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-2001-17223
更新日期：2001-09-01 00:00:00
abstract：:A multi-center retrospective survey was conducted to evaluate the incidence and types of hemostatic complications occurring in children with acute lymphoblastic leukemia (ALL) during treatment according to the ALL-BFM-90 treatment protocol. All of the BFM-treatment centers (n = 77) were approached and a 95% response r...
journal_title：Klinische Padiatrie
pub_type： 杂志文章,多中心研究
doi：10.1055/s-2008-1043788
更新日期：1999-07-01 00:00:00
abstract：:Between 1981 and 2000, 6 609 children (<18 years of age) were treated in 5 consecutive trials of the Berlin-Frankfurt-Münster (BFM) study group for childhood acute lymphoblastic leukemia (ALL). Patients were treated in up to 82 centers in Germany, Austria, and Switzerland. Probability of 10-year event-free survival (s...
journal_title：Klinische Padiatrie
pub_type： 传,历史文章,杂志文章
doi：10.1055/s-0033-1337966
更新日期：2013-05-01 00:00:00
abstract：:Longitudinal growth was assessed in 10 children aged 0.8 to 11.8 years with adrenocortical tumors. All children had signs of androgen excess. In addition, 5 children had glucocorticoid excess, 1 child had estrogen excess. Multiple height recordings, expressed as height standard deviation score for chronological age, w...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-2007-1025405
更新日期：1991-03-01 00:00:00
abstract：:The diagnosis of HFI is easily missed during childhood. It should be suspected in children presenting with hepatomegaly and an isolated increase in GGT. A carefully taken nutritional history forms the basis of the diagnosis of HFI which can be confirmed by molecular analysis with a sensitivity of > 95%. I.v. fructose ...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：
更新日期：2000-05-01 00:00:00
abstract：:Meconium ileus equivalent (MIE) complicating cystic fibrosis of the pancreas (CF) increases in frequently with increasing age of patients. In the present paper the course of 11 children and adolescents with MIE diagnosed and treated at the University Dept. of Paediatrics in Zürich during the last 15 years, i.e. 9% of ...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-2008-1034390
更新日期：1983-09-01 00:00:00
abstract：BACKGROUND:Modern neonatal and pediatric intensive care includes a sophisticated pharmacotherapy with numerous drugs, mainly administered intravenously. Often, despite the use of multi-lumen central venous lines, more peripheral venous accesses are required. To reduce the necessity of numerous venous lines on one hand ...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-2005-836937
更新日期：2007-01-01 00:00:00
abstract：:340 consecutive patients with neuroblastoma stage IV were analyzed for the possible impact of chemotherapy on general condition, remission status, event free survival and survival. The children entered the trials NB 79, NB 82 and NB 85 of the German Pediatric Oncology Society (GPO). The patients did benefit from chemo...
journal_title：Klinische Padiatrie
pub_type： 临床试验,杂志文章,多中心研究,随机对照试验
doi：10.1055/s-2007-1025531
更新日期：1990-07-01 00:00:00
abstract：:Guillain Barré syndrome (GBS; Synonyma: Polyneuritis, Polyradikulitis) is an acute, inflammatory, demyelinating disease of the peripheral nerve system. Clinical hallmarks are symmetric muscle paralysis, areflexia and pronounced autonomic disturbances. Respiratory failure and cardiovascular instability are the main rea...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-2007-971050
更新日期：2008-03-01 00:00:00
abstract：:Oncological diseases in children and adolescents represent a considerable burden for the children themselves and for their families. In order to position such concomitants of a life-threatening disease appropriately among the diagnostic options of psychosocial cancer care one is repeatedly confronted with the issue of...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-2007-985872
更新日期：2007-11-01 00:00:00
abstract：:Aim of the present study was to test whether six-hour (6 h) urine specimens predict the 24-hour (24 h) mineral homeostasis in individual infants born preterm. Urinary Calcium (Ca) and Phosphate (P) concentrations were studied in 60 stable infants; gestational age 34 (25-42) weeks. In 58 infants four 6 h urine specimen...
journal_title：Klinische Padiatrie
pub_type： 杂志文章
doi：10.1055/s-0031-1301361
更新日期：2012-03-01 00:00:00
abstract：:Doxorubicin serum levels were measured with a highly specific reversed-phase HPLC-method in patients undergoing combination chemotherapy. Serum elimination kinetics of doxorubicin follow a bi- or triphasic first order pattern with a high interpatient variability. T 1/2 of the first distribution phase was 5.4 min. T 1/...
journal_title：Klinische Padiatrie
pub_type： 临床试验,杂志文章
doi：10.1055/s-2008-1026889
更新日期：1986-05-01 00:00:00
abstract：:The are various opinions about the optimal therapy of endemic goiter in adolescents. From 106 patients (75 girls) suffering from endemic goiter 50 patients (group A) were treated with 300 micrograms iodine per day and 56 patients (group B) with 100 micrograms iodine plus 100 micrograms levothyroxine per day. Before th...
journal_title：Klinische Padiatrie
pub_type： 临床试验,杂志文章,随机对照试验
doi：10.1055/s-2008-1046460
更新日期：1996-05-01 00:00:00
