Generalized lymphangiomatosis and chylothorax in the pediatric age group.

Abstract:

:Four patients with generalized lymphangiomatosis presenting with chylothoraces are described. All four had bone involvement, two had involvement of the spleen, and one of the pericardium. The diagnosis was confirmed by typical radiology, histology, and in three patients by immunohistochemistry. Treatment was mainly palliative. Three patients died within 1/2 to three years of presentation.

journal_name

Pediatr Pulmonol

journal_title

Pediatric pulmonology

authors

Shah AR,Dinwiddie R,Woolf D,Ramani R,Higgins JN,Matthew DJ

doi

10.1002/ppul.1950140211

subject

Has Abstract

pub_date

1992-10-01 00:00:00

pages

126-30

issue

2

eissn

8755-6863

issn

1099-0496

journal_volume

14

pub_type

杂志文章
  • Mechanically ventilated premature babies have sex differences in specific elastance: A pilot study.

    abstract:OBJECTIVES:A pilot study to compare pulmonary mechanics in a neonatal intensive care unit (NICU) cohort, specifically, comparing lung elastance between male and female infants in the NICU. HYPOTHESIS:Anecdotally, male infants are harder to ventilate than females. We hypothesize that males have higher model-based elast...

    journal_title:Pediatric pulmonology

    pub_type: 杂志文章

    doi:10.1002/ppul.24538

    authors: Kim KT,Knopp J,Dixon B,Chase JG

    更新日期:2020-01-01 00:00:00

  • Pulmonary testing using peak flow meters of very low birth weight children born in the perisurfactant era and school controls at age 10 years.

    abstract::We determined lung function at age 10 years in very low birthweight (VLBW,

    journal_title:Pediatric pulmonology

    pub_type: 杂志文章

    doi:10.1002/ppul.20662

    authors: Palta M,Sadek-Badawi M,Madden K,Green C

    更新日期:2007-09-01 00:00:00

  • Aerosolized metaproterenol compared to subcutaneous epinephrine in the emergency treatment of acute childhood asthma.

    abstract::In a double-blind, randomized trial, we compared the effects of aerosolized metaproterenol to subcutaneous epinephrine in 35 episodes of acute asthma in children between 6 and 19 years of age. Patients were randomized to two parallel groups and then received both a placebo medication and an active medication to a maxi...

    journal_title:Pediatric pulmonology

    pub_type: 临床试验,杂志文章,随机对照试验

    doi:10.1002/ppul.1950020411

    authors: Ruddy RM,Kolski G,Scarpa N,Wilmott R

    更新日期:1986-07-01 00:00:00

  • Nonsurgical management of an enlarging pneumatocele by fibrin sealant injection via pigtail catheter.

    abstract::Most pneumatoceles disappear spontaneously and do not cause severe symptoms. Treatment alternatives include various conventional or surgical methods. However, an enlarging, complicated pneumatocele with cardiorespiratory instability requires imaging-guided catheter drainage or surgery. Here, we report the case of a ne...

    journal_title:Pediatric pulmonology

    pub_type: 杂志文章

    doi:10.1002/ppul.23311

    authors: Park TH,Kim JK

    更新日期:2016-02-01 00:00:00

  • Lung clearance index: normal values, repeatability, and reproducibility in healthy children and adolescents.

    abstract::There is increasing interest in using the Multiple Breath Washout technique and the lung clearance index (LCI) for detecting early pulmonary changes, for example, in cystic fibrosis lung disease. However, there are still limited data regarding equipment specific reference ranges, repeatability and reproducibility. The...

    journal_title:Pediatric pulmonology

    pub_type: 杂志文章

    doi:10.1002/ppul.21093

    authors: Fuchs SI,Eder J,Ellemunter H,Gappa M

    更新日期:2009-12-01 00:00:00

  • Obstructive sleep apnea in infancy: a 7-year experience at a pediatric sleep center.

    abstract:PURPOSE:To investigate the common indications for polysomnogram (PSG) associated co-morbid conditions, evaluation strategies, treatment options, and outcomes in a series of infants diagnosed with obstructive sleep apnea (OSA) by a PSG. METHODS:Retrospective chart review of infants who underwent PSG over a 7-year perio...

    journal_title:Pediatric pulmonology

    pub_type: 杂志文章

    doi:10.1002/ppul.22867

    authors: Ramgopal S,Kothare SV,Rana M,Singh K,Khatwa U

    更新日期:2014-06-01 00:00:00

  • Ventilation homogeneity improves with growth early in life.

    abstract::Some studies have suggested that lung clearance index (LCI) is age-independent among healthy subjects early in life, which implies that ventilation distribution does not vary with growth. However, other studies of older children and adolescents suggest that ventilation becomes more homogenous with somatic growth. We d...

    journal_title:Pediatric pulmonology

    pub_type: 杂志文章

    doi:10.1002/ppul.21553

    authors: Chakr VC,Llapur CJ,Sarria EE,Mattiello R,Kisling J,Tiller C,Kimmel R,Poindexter B,Tepper RS

    更新日期:2012-04-01 00:00:00

  • Longitudinal assessment of lung function in children with sickle cell disease.

    abstract:OBJECTIVES:To prospectively assess longitudinal lung function in children with sickle cell disease (SCD). WORKING HYPOTHESIS:Lung function in SCD children deteriorates with increasing age and the decline is more marked in younger children who have recently suffered ACS episodes. STUDY DESIGN:Two prospective longitudi...

    journal_title:Pediatric pulmonology

    pub_type: 杂志文章

    doi:10.1002/ppul.23367

    authors: Lunt A,McGhee E,Sylvester K,Rafferty G,Dick M,Rees D,Height S,Thein SL,Greenough A

    更新日期:2016-07-01 00:00:00

  • Foreign-body aspiration mimicking congenital lobar emphysema in a forty-eight-day-old girl.

    abstract::Foreign-body aspiration (FBA) is a commonly encountered serious problem during childhood, accounting for 7% of lethal accidents in children aged 1-3 years. Bronchoscopy is indicated when a clear history of FBA is present, but the history may be unreliable. Clinical manifestations can be seen in various diseases, and w...

    journal_title:Pediatric pulmonology

    pub_type: 杂志文章

    doi:10.1002/ppul.20128

    authors: Aslan AT,Yalcin E,Ozcelik U,Ciftci AO,Kiper N

    更新日期:2005-02-01 00:00:00

  • Daily inhaled corticosteroids or montelukast for preschoolers with asthma or recurrent wheezing: A systematic review.

    abstract:BACKGROUND:Most international asthma guidelines recommend that children ≤5 years with asthma or recurrent wheezing be treated with daily low- moderate dose inhaled corticosteroids (ICS) as the preferred controller and leukotriene receptor antagonists (LTRA) as alternative therapy. There is no systematic review comparin...

    journal_title:Pediatric pulmonology

    pub_type: 杂志文章

    doi:10.1002/ppul.24176

    authors: Castro-Rodriguez JA,Rodriguez-Martinez CE,Ducharme FM

    更新日期:2018-12-01 00:00:00

  • Development of the pulmonary airways in the fetal rat and its relation to the prenatal environment.

    abstract::We studied the left lung using multi-focus microphotography in 378 rat fetuses, assessing airway branching from day 13 to day 19 of gestation, and lung growth variables from day 13 to day 21. Longitudinal growth, and monopodial and dichotomous branching brought about a consistent airway pattern with variations within ...

    journal_title:Pediatric pulmonology

    pub_type: 杂志文章

    doi:10.1002/(SICI)1099-0496(199604)21:4<219::AID-PPUL3

    authors: Rotschild A,Massoud EA,Solimano A,Puterman ML,Sekhon HS,Thurlbeck WM

    更新日期:1996-04-01 00:00:00

  • DNA fragmentation in developing lung fibroblasts exposed to Stachybotrys chartarum (atra) toxins.

    abstract::Stachybotrys chartarum (atra) is a toxic mold that grows on water-damaged cellulose-based materials. Research has revealed also that inhalation of S. chartarum spores caused marked changes in respiratory epithelium, especially to developing lungs. We analyzed the epigenetic potential of S. chartarum spore toxins on de...

    journal_title:Pediatric pulmonology

    pub_type: 杂志文章

    doi:10.1002/ppul.20608

    authors: McCrae KC,Rand TG,Shaw RA,Mantsch HH,Sowa MG,Thliveris JA,Scott JE

    更新日期:2007-07-01 00:00:00

  • Bronchial provocation testing with dry powder mannitol in children with cystic fibrosis.

    abstract:BACKGROUND/AIM:There has been recent interest in dry powder inhaled mannitol as a therapeutic agent in patients with cystic fibrosis (CF). It is has been shown to increase mucociliary clearance (MCC) by rehydrating the airway. To date there have been no studies exclusively in children with CF examining the effect of dr...

    journal_title:Pediatric pulmonology

    pub_type: 杂志文章

    doi:10.1002/ppul.20903

    authors: Minasian C,Wallis C,Metcalfe C,Bush A

    更新日期:2008-11-01 00:00:00

  • Fungal pleural effusion secondary to a rare cause of pancreatic pseudocyst.

    abstract::We report a case of fungal pleural effusion secondary to presumed valproate induced pancreatitis with pseudocyst and stricture formation. A child with dyskinetic cerebral palsy who had been on sodium valproate for several years was transferred for drainage of a left sided pleural effusion. Pleural fluid culture consis...

    journal_title:Pediatric pulmonology

    pub_type: 杂志文章

    doi:10.1002/ppul.20982

    authors: Gupta A,Marrs T,Urquhart D,Clarke S,Rosenthal M,Bush A

    更新日期:2009-06-01 00:00:00

  • Long-term pulmonary function in esophageal atresia-A case-control study.

    abstract:BACKGROUND:Esophageal atresia (EA) is a congenital anomaly associated with substantial pulmonary morbidity throughout childhood. AIM:The aim of this study was to evaluate pulmonary complications among 59 five to 15-year-old children and adolescents with surgically corrected congenital EA. METHODS:Participants underwe...

    journal_title:Pediatric pulmonology

    pub_type: 杂志文章

    doi:10.1002/ppul.23477

    authors: Pedersen RN,Markøw S,Kruse-Andersen S,Qvist N,Gerke O,Husby S,Agertoft L

    更新日期:2017-01-01 00:00:00

  • Dalhousie dyspnea scales: Pictorial scales to measure dyspnea during induced bronchoconstriction.

    abstract::The aim of this study was to validate our Dalhousie Dyspnea Scales in children referred for histamine bronchoprovocation challenge. Seventy-four children rated their dyspnea after each FEV(1) measurement following inhalation of doubling histamine concentrations from 0.125 to 8.0 mg/ml by the standard tidal breathing m...

    journal_title:Pediatric pulmonology

    pub_type: 杂志文章

    doi:10.1002/ppul.20512

    authors: Pianosi P,Smith CP,Almudevar A,McGrath PJ

    更新日期:2006-12-01 00:00:00

  • Use of azithromycin for the prevention of bronchopulmonary dysplasia in preterm infants: a randomized, double-blind, placebo controlled trial.

    abstract:OBJECTIVE:Since preventive therapies for bronchopulmonary dysplasia (BPD) are limited we treated preterm infants with azithromycin to decrease the incidence of BPD. METHODS:Infants less than 1,250 g birth weight were randomized to azithromycin or placebo within 12 hr of beginning mechanical ventilation and within 72 h...

    journal_title:Pediatric pulmonology

    pub_type: 杂志文章,随机对照试验

    doi:10.1002/ppul.21352

    authors: Ballard HO,Shook LA,Bernard P,Anstead MI,Kuhn R,Whitehead V,Grider D,Crawford TN,Hayes D Jr

    更新日期:2011-02-01 00:00:00

  • Asthma and COVID-19 in children: A systematic review and call for data.

    abstract:RATIONALE:Whether asthma constitutes a risk factor for coronavirus disease-2019 (COVID-19) is unclear. Here, we aimed to assess whether asthma, the most common chronic disease in children, is associated with higher COVID-19 risk or severity in pediatric populations. METHODS:We performed a systematic literature search ...

    journal_title:Pediatric pulmonology

    pub_type: 杂志文章,meta分析

    doi:10.1002/ppul.24909

    authors: Castro-Rodriguez JA,Forno E

    更新日期:2020-09-01 00:00:00

  • Standardized procedure for measurement of nasal potential difference: an outcome measure in multicenter cystic fibrosis clinical trials.

    abstract::Patients with cystic fibrosis (CF) can be discriminated from healthy subjects by measurement of the nasal potential difference, which has become a useful outcome measure for therapies directed toward correcting defective electrolyte transport in CF. A standard operating procedure was developed by a CF Foundation clini...

    journal_title:Pediatric pulmonology

    pub_type: 杂志文章,多中心研究

    doi:10.1002/ppul.10448

    authors: Standaert TA,Boitano L,Emerson J,Milgram LJ,Konstan MW,Hunter J,Berclaz PY,Brass L,Zeitlin PL,Hammond K,Davies Z,Foy C,Noone PG,Knowles MR

    更新日期:2004-05-01 00:00:00

  • Pulmonary hypertension in childhood interstitial lung disease: A systematic review of the literature.

    abstract::Childhood interstitial lung disease (chILD) comprises a wide heterogeneous group of rare parenchymal lung disorders associated with substantial morbidity and mortality. Pulmonary hypertension is a common comorbidity in adults with interstitial lung disease (ILD) and associated with poor survival. We aimed to systemati...

    journal_title:Pediatric pulmonology

    pub_type: 杂志文章,评审

    doi:10.1002/ppul.23632

    authors: Bromley S,Vizcaya D

    更新日期:2017-05-01 00:00:00

  • Hering-Breuer reflex in young asthmatic children.

    abstract::The aim of this study was to assess if the Hering-Breuer reflex could be provoked in young children. Thirty asthmatic children with a mean age of 5.3 years and 18 healthy children with a mean age of 7.0 years were studied. The presence of the reflex was indicated by prolongation of the spontaneous expiratory time foll...

    journal_title:Pediatric pulmonology

    pub_type: 杂志文章

    doi:10.1002/ppul.1950110412

    authors: Greenough A,Pool J

    更新日期:1991-01-01 00:00:00

  • Spontaneous hemopneumothorax simulating acute abdominal affections.

    abstract::Spontaneous hemopneumothorax (SHP) is a rare potentially life-threatening condition that occurs in predominantly young adolescents. The resultant massive hemorrhage leading to hypovolemic shock can be a surgical emergency. It constitutes 1-12% of all spontaneous pneumothoraces and presents with two cardinal features, ...

    journal_title:Pediatric pulmonology

    pub_type: 杂志文章

    doi:10.1002/ppul.22712

    authors: Chen TH,Tseng YH,Tseng CM,Chiang HH,Lin TJ

    更新日期:2014-01-01 00:00:00

  • Mucus obstruction and inflammation in early cystic fibrosis lung disease: Emerging role of the IL-1 signaling pathway.

    abstract::Mucus plugging constitutes a nutrient-rich nidus for a bacterial infection that has long been recognized as a potent stimulus for neutrophilic airway inflammation driving progressive lung damage in people with cystic fibrosis (CF). However, mucus plugging and neutrophilic inflammation are already present in many infan...

    journal_title:Pediatric pulmonology

    pub_type: 杂志文章,评审

    doi:10.1002/ppul.24462

    authors: Balázs A,Mall MA

    更新日期:2019-11-01 00:00:00

  • Airway epithelial cell signaling in response to bacterial pathogens.

    abstract::The airway epithelium represents a primary site for the introduction and deposition of potentially pathogenic microorganisms into the body, through inspired air. The epithelial mucosa is an important component of the innate immune system that recognizes conserved structures in microorganisms and initiates appropriate ...

    journal_title:Pediatric pulmonology

    pub_type: 杂志文章,评审

    doi:10.1002/ppul.20735

    authors: Gómez MI,Prince A

    更新日期:2008-01-01 00:00:00

  • Predictors of proper inhaler technique and asthma control in pediatric patients with asthma.

    abstract:BACKGROUND:Improper use of asthma inhalers is one of the potential factors of poor asthma control among children. This study aimed to assess the proper handling of asthma inhalers and asthma control in addition to factors influencing them among pediatric patients who self-administer their inhalers. METHODS:A cross-sec...

    journal_title:Pediatric pulmonology

    pub_type: 杂志文章

    doi:10.1002/ppul.25263

    authors: Almomani BA,Al-Qawasmeh BS,Al-Shatnawi SF,Awad S,Alzoubi SA

    更新日期:2021-01-26 00:00:00

  • A multi-center controlled trial of growth hormone treatment in children with cystic fibrosis.

    abstract:OBJECTIVES:We evaluated safety and efficacy of recombinant human growth hormone (rhGH) for improving growth, lean body mass (LBM), pulmonary function, and exercise tolerance in children with cystic fibrosis (CF) and growth restriction. STUDY DESIGN:Multicenter, open-label, controlled clinical trial comparing outcomes ...

    journal_title:Pediatric pulmonology

    pub_type: 杂志文章,多中心研究,随机对照试验

    doi:10.1002/ppul.21546

    authors: Stalvey MS,Anbar RD,Konstan MW,Jacobs JR,Bakker B,Lippe B,Geller DE

    更新日期:2012-03-01 00:00:00

  • Effectivenesss of ivacaftor in severe cystic fibrosis patients and non-G551D gating mutations.

    abstract:BACKGROUND:Ivacaftor is a significant innovation in the treatment of cystic fibrosis (CF) with gating mutations. A substantial percentage of patients with CF have severe lung involvement, but these patients are usually excluded from phase III clinical trials. Thus, the effectiveness of ivacaftor in this population has ...

    journal_title:Pediatric pulmonology

    pub_type: 杂志文章

    doi:10.1002/ppul.24424

    authors: Salvatore D,Carnovale V,Iacotucci P,Braggion C,Castellani C,Cimino G,Colangelo C,Francalanci M,Leonetti G,Lucidi V,Manca A,Vitullo P,Ferrara N

    更新日期:2019-09-01 00:00:00

  • Severe bronchiolitis in infancy: can asthma in adolescence be predicted?

    abstract::Bronchiolitis in infancy is a risk factor for development of asthma in the first decades of life, although the majority may be asymptomatic at school age. Respiratory symptoms are common in early life, and prediction of later asthma may be challenging. We aimed to study if simple clinical variables assessed at 2 years...

    journal_title:Pediatric pulmonology

    pub_type: 杂志文章

    doi:10.1002/ppul.22675

    authors: Mikalsen IB,Halvorsen T,Eide GE,Øymar K

    更新日期:2013-06-01 00:00:00

  • Serum eosinophil cationic protein as a predictor of wheezing after bronchiolitis.

    abstract::We have evaluated the role of eosinophil cationic protein (ECP) concentrations in serum in predicting wheezing after bronchiolitis, during infancy and early childhood. A prospective study at a university hospital serving all pediatric patients in a defined area was designed. Serum ECP concentrations were measured in 9...

    journal_title:Pediatric pulmonology

    pub_type: 临床试验,杂志文章,随机对照试验

    doi:10.1002/(sici)1099-0496(199706)23:6<397::aid-ppul1

    authors: Reijonen TM,Korppi M,Kuikka L,Savolainen K,Kleemola M,Mononen I,Remes K

    更新日期:1997-06-01 00:00:00

  • Conservative management of pediatric tracheal rupture.

    abstract::Traumatic injuries to the pediatric trachea are uncommon events that require prompt diagnosis and management. When they do occur, tracheal injuries often arise in the setting of high impact trauma and are accompanied by major injuries to other organ systems. In this report, we present the diagnosis and conservative ma...

    journal_title:Pediatric pulmonology

    pub_type: 杂志文章

    doi:10.1002/ppul.23507

    authors: Sidell DR,Wood RE,Hart CK

    更新日期:2017-01-01 00:00:00