Atypical association of semantic dementia, corticobasal syndrome, and 4R tauopathy.

abstract：:While language characteristics of logopenic variant primary progressive aphasia (lvPPA) are well-defined, behavioral characteristics are less understood. We investigated correlations between language and behavioral scores across three variants of primary progressive aphasia (PPA) and found language performance and beh...

journal_title：Neurocase

authors： Keator LM,Wright AE,Saxena S,Kim K,Demsky C,Sebastian R,Sheppard SM,Breining B,Hillis AE,Tippett DC

更新日期：2019-01-01 00:00:00

abstract：:Children (aged 9-12) training in an El Sistema-inspired program (OrKidstra) and a matched comparison group participated in an auditory Go/No-Go task while event-related potentials (ERPs) were recorded. Entire-sweep waveform patterns correlated with known ERP peaks associated with executive and other cognitive function...

journal_title：Neurocase

authors： Hedayati N,Schibli K,D'Angiulli A

更新日期：2016-12-01 00:00:00

abstract：:Creatine transporter deficit (CT1) is an inherited metabolic disorder that causes mental retardation, epilepsy, speech, language and behavioral deficits. Until now, no treatment has been proven to be successful for this condition. We describe 1-year follow-up study of a child, aged 9.6 years, with CT1 defect, on oral ...

journal_title：Neurocase

authors： Chilosi A,Leuzzi V,Battini R,Tosetti M,Ferretti G,Comparini A,Casarano M,Moretti E,Alessandri MG,Bianchi MC,Cioni G

更新日期：2008-01-01 00:00:00

abstract：:The purpose of the present study was to investigate differences in brain activation with functional magnetic resonance imaging (fMRI) during imagery of painful and non-painful 'finger movements' and 'hand positioning' in a subject with an amputated arm. The subject was a right-handed man in his mid-thirties who lost h...

journal_title：Neurocase

authors： Rosén G,Hugdahl K,Ersland L,Lundervold A,Smievoll AI,Barndon R,Sundberg H,Thomsen T,Roscher BE,Tjølsen A,Engelsen B

更新日期：2001-01-01 00:00:00

abstract：:Previous studies on visual form agnosic patients have shown that their color perception is relatively preserved when monochromatic figures are used. However, it is unclear whether their color perception remains normal when figures are composed of two parts in different colors. The results showed that patient X.F. had ...

journal_title：Neurocase

authors： Yang J,Wu M,Shen Z

更新日期：2007-10-01 00:00:00

abstract：:Cerebral lesions are held to induce plastic changes of the brain. Less well established, however, is how much space-occupying brain lesions may only displace functional representations. In a 66-year-old man we show, by means of functional magnetic resonance imaging and transcranial magnetic stimulation, a profound dis...

journal_title：Neurocase

authors： Nickel J,Jörgens S,Bussfeld P,Seitz RJ

更新日期：2007-10-01 00:00:00

abstract：:Recent research revealed decreased access to semantic and associative networks in acute cocaine withdrawal. In autism, such behavioral outcomes are associated with decreased functional connectivity using functional magnetic resonance imaging. Therefore, we wished to determine whether connectivity is also decreased in ...

journal_title：Neurocase

authors： Narayanan A,White CA,Saklayen SS,Abduljalil A,Schmalbrock P,Pepper TH,Lander BN,Beversdorf DQ

更新日期：2012-01-01 00:00:00

abstract：:To further understand the nature of the visual-spatial representations required for successful acquisition of written language skills, we investigated the written language abilities of two individuals with Williams syndrome (WS) a developmental genetic disorder in which the presence of severe visual-spatial developmen...

journal_title：Neurocase

authors： Dessalegn B,Landau B,Rapp B

更新日期：2013-08-01 00:00:00

abstract：:The degree of abnormality and rate of change in cognitive functions, positron emission tomography Pittsburg compound B (PET PIB), and fluorodeoxyglucose (FDG) measures were studied for 8 years in an autopsy-confirmed Alzheimer's disease (AD) patient, who died 61 years old (Mini-Mental State Examination (MMSE) score 7)...

journal_title：Neurocase

authors： Almkvist O,Kadir A,Nordberg A

更新日期：2015-01-01 00:00:00

abstract：:We report a 4-year-old child with severe semi-lobar holoprosencephaly (HPE) not expected to survive after birth. Magnetic resonance imaging (MRI) revealed agenesis of the corpus callosum, absence of the third ventricle, fused thalami and basal ganglia. To investigate sensory function, visual, auditory and somatosensor...

journal_title：Neurocase

authors： Liasis A,Hildebrand D,Clark C,Katz X,Gunny R,Stieltjes B,Taylor D

更新日期：2009-01-01 00:00:00

abstract：:This article describes an investigation into the residual writing skills of a severely dysgraphic patient (DA). We found that they were powerfully influenced by a number of lexical variables (lexicality, frequency, imageability, length and geminates). His error pattern was characterized by semantic, lexical, substitut...

journal_title：Neurocase

authors： Cipolotti L,Bird CM,Glasspool DW,Shallice T

更新日期：2004-12-01 00:00:00

abstract：:Patients with memory disorders have severely restricted learning and memory. For instance, patients with anterograde amnesia can learn motor procedures and retain some restricted ability to learn new words and factual information. However, such learning is inflexible and frequently inaccessible to conscious awareness....

journal_title：Neurocase

authors： Olson IR,Berryhill ME,Drowos DB,Brown L,Chatterjee A

更新日期：2010-06-01 00:00:00

abstract：:Primary progressive apraxia of speech (PPAOS) is a neurodegenerative disorder in which AOS is the sole presenting complaint. We report clinical and neuroimaging data spanning 10 years from disease onset-to-death in a 49 year-old male PPAOS patient, DY, who died with corticobasal degeneration. He presented with AOS wit...

journal_title：Neurocase

authors： Tetzloff KA,Duffy JR,Strand EA,Machulda MM,Boland SM,Utianski RL,Botha H,Senjem ML,Schwarz CG,Josephs KA,Whitwell JL

更新日期：2018-04-01 00:00:00

abstract：:A quantitative assessment of a distortion involving the left side of space, both in two-dimensional (drawing), and three-dimensional (modeling), visuo-constructional tasks is reported in a patient with a right temporoparieto-occipital lesion, and left hemianopia, without visuospatial neglect. In drawing and clay model...

journal_title：Neurocase

authors： Rode G,Revol P,Rossetti Y,Vallar G

更新日期：2008-01-01 00:00:00

abstract：:Central pontine and extrapontine myelinolysis (CPEM) is a rare neurological condition usually due to rapid correction of hyponatremia. CPEM is mainly characterized by motor deficits (typically quadraparesis or extrapyramidal features) but neurobehavioral symptoms were also reported in the literature. However, very few...

journal_title：Neurocase

authors： Arciero S,Kempf C,Bernard F,Gosselin N

更新日期：2012-01-01 00:00:00

abstract：:It is a common finding in tests of false recognition that amnesic patients recognize fewer related lures than healthy controls, and this has led to assumptions that gist memory is damaged in these patients (Schacter, Verfaellie, & Anes, 1997, Neuropsychology, 11; Schacter, Verfaellie, Anes, & Racine, 1998, Journal of ...

journal_title：Neurocase

authors： Nissan J,Abrahams S,Sala SD

更新日期：2013-01-01 00:00:00

abstract：:In this paper, we adopt a neurodevelopmental stance to examining frontal variant frontotemporal dementia (fv-FTD) by using experimental procedures from the literature on the growth of social behaviour in children to examine the deficits in social reasoning which may underpin behavioural disturbance in fv-FTD. We prese...

journal_title：Neurocase

authors： Lough S,Gregory C,Hodges JR

更新日期：2001-01-01 00:00:00

abstract：:Regressive behavior is a known sequela after severe traumatic brain injury (TBI). However, prolonged "infantile-like" behavior has received little attention in the literature, suggesting that this is a rare phenomenon. It is typically characterized by long-lasting childish, extremely dependent, and sometimes aggressiv...

journal_title：Neurocase

authors： Heled E,Sverdlik A,Agranov E

更新日期：2014-01-01 00:00:00

abstract：:An adult female complained of enlargement of right eyes in other people. Diffusion-weighted imaging detected an abnormal high-intensity area in the region from the splenium of the corpus callosum to the major forceps on the right side. The patient reported that right eyes appeared larger in size, which suggested proso...

journal_title：Neurocase

authors： Ogawa K,Akimoto T,Takahashi K,Hara M,Morita A,Kamei S,Nakajima H,Fujishiro M,Suzuki Y,Soma M,Shikata E,Futamura A,Kawamura M

更新日期：2020-10-01 00:00:00

abstract：:With injury of the anterior two-thirds of the corpus callosum, each hemisphere's attentional bias to contralateral hemispace becomes manifest with each hand deviating ipsilaterally during line bisection tasks. Patients with infarctions in the right posterior cerebral artery distribution with occipital and splenial dam...

journal_title：Neurocase

authors： Kesayan T,Gasoyan H,Heilman KM

更新日期：2018-08-01 00:00:00

abstract：:BVR was 77 years old when he sustained a large posterior cerebral artery territory infarct. Medical, cognitive and functional data collected on four occasions over 10 years initially revealed circumscribed neurological signs, no functional or cognitive deficits. BVR became significantly impaired only after two other s...

journal_title：Neurocase

authors： Piguet O,Bennett HP,Waite LM,Kril JJ,Creasey H,Anthony Broe G,Halliday GM

更新日期：2006-04-01 00:00:00

abstract：:The concreteness effect occurs in both normal and language-disordered populations. Research suggests that abstract and concrete concepts elicit differing neural activation patterns in healthy young adults, but this is undocumented in persons with aphasia (PWA). Three PWA and three age-matched controls were scanned usi...

journal_title：Neurocase

authors： Sandberg C,Kiran S

更新日期：2014-08-01 00:00:00

abstract：:In a previous report, we presented longitudinal clinical, cognitive and anatomical data of a right-handed woman, whose clinical picture evolved from progressive nonfluent aphasia with apraxia of speech to corticobasal syndrome (CBS) in the last stage of the disease. The patient died at age 57 and pathological examinat...

journal_title：Neurocase

authors： Sánchez-Valle R,Forman MS,Miller BL,Gorno-Tempini ML

更新日期：2006-12-01 00:00:00

abstract：:A current debate in the literature is whether all declarative memories and associated memory processes rely on the same neural substrate. Here, we show that H.C., a developmental amnesic person with selective bilateral hippocampal volume loss, has a mild deficit in personal episodic memory, and a more pronounced defic...

journal_title：Neurocase

authors： Rosenbaum RS,Carson N,Abraham N,Bowles B,Kwan D,Köhler S,Svoboda E,Levine B,Richards B

更新日期：2011-10-01 00:00:00

abstract：:A 57-year-old man suffered severe amnesia and disorientation, accompanied by content-specific confabulation, due to an alcoholic Wernicke-Korsakoff syndrome. For months, he was deeply concerned about a single obligation that he thought he had to respond to, but which he had already assumed 20 years previously. This mo...

journal_title：Neurocase

authors： Schnider A,Nahum L,Pignat JM,Leemann B,Lövblad KO,Wissmeyer M,Ptak R

更新日期：2013-01-01 00:00:00

abstract：:Monocular patching might improve perceptual-attentional, not motor-intentional deficits in a patient with chronic post-stroke left spatial neglect. Performing a line-cancellation task, his omission errors were associated with a perceptual-attentional 'where' deficit, while perseverative errors were associated with 'ai...

journal_title：Neurocase

authors： Khurshid S,Longin H,Crucian GP,Barrett AM

更新日期：2009-08-01 00:00:00

abstract：:A striking special ability in arranging picture stories was reported in an Asperger child (C.M.) showing an exceptional performance on Wechsler picture arrangement subtest. Neuropsychological examination did not disclose visuoperceptual and spatial defects, or working memory, attention and executive disorders, but rev...

journal_title：Neurocase

authors： Conson M,Salzano S,Grossi D

更新日期：2011-08-01 00:00:00

abstract：:According to Liepmann, patients with limb-kinetic apraxia (LKA) have a loss of upper limb deftness-dexterity. Prior studies have revealed in right-handed patients that, whereas injury of the left hemisphere induces an ipsilesional LKA, injury to the right hemisphere does not induce an ipsilesional LKA. There are at le...

journal_title：Neurocase

authors： Acosta LM,Bennett JA,Heilman KM

更新日期：2014-01-01 00:00:00

abstract：:Physical symptoms of myoclonus dystonia due to epsilon-sarcoglycan mutations are well documented; however, the progression of neuropsychiatric and cognitive symptoms remains unclear. We present a case of a 34-year-old woman with early childhood onset of myoclonic jerks, dystonic posture and developmental delay due to ...

journal_title：Neurocase

authors： Multani N,Moro E,Lang A,Zurowski M,Duff Canning S,Tartaglia MC

更新日期：2016-01-01 00:00:00

abstract：:It has been suggested that formal thought disorder, the incoherent speech of schizophrenia, may involve a language disturbance among other abnormalities, or even be a form of dysphasia. Six patients with and seven without formal thought disorder were evaluated on an aphasia test battery. Spontaneous speech was also an...

journal_title：Neurocase

authors： Oh TM,McCarthy RA,McKenna PJ

更新日期：2002-01-01 00:00:00