Early liver transplantation is indicated for tyrosinemia type I.

abstract：:Calcium absorption from tricalcium phosphate (TCP) was compared to that from calcium chloride, CaCl2, in the presence and absence of carrageenan in the rat model. There was no difference in percent calcium absorption as indicated by femur uptake of TCP or CaCl2 intrinsically labeled with 45Ca given by gavage (78.4 +/-...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Koo J,Weaver CM,Neylan MJ

更新日期：1993-10-01 00:00:00

abstract：:The clinical usefulness of serum gamma-glutamyl transpeptidase (gamma GT) assay for the diagnosis of liver disease in children was assessed retrospectively in 398 children investigated from 1981 to 1986, in whom diagnosis was ascertained according to currently accepted criteria including liver histology in each case. ...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Maggiore G,Bernard O,Hadchouel M,Lemonnier A,Alagille D

更新日期：1991-01-01 00:00:00

abstract：OBJECTIVES:Gastroesophageal reflux is common but remains a controversial disease to diagnose and treat and little is known about the role of reflux testing in predicting clinical outcomes, particularly in children at risk for extraesophageal reflux complications. The aim of this study was to determine if rates of hospi...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Duncan DR,Amirault J,Johnston N,Mitchell P,Larson K,Rosen RL

更新日期：2016-08-01 00:00:00

abstract：:Cholestatic liver disorders account for a large proportion of chronic liver ailments in adults, children and infants, and are among the leading indications for liver transplantation in all age groups. Recent studies have begun to characterize the cellular and molecular mechanisms of hepatocyte injury caused by the ret...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Sokol RJ,Devereaux M,Dahl R,Gumpricht E

更新日期：2006-07-01 00:00:00

abstract：OBJECTIVE:P-glycoprotein (P-gp), the functional product of the multidrug resistance gene (MDR), is a transmembrane protein that extrudes substrates from the intracellular environment. P-gp is expressed on the apical surface of epithelial cells and on cells from the hematopoietic lineage. Human MDR polymorphisms have be...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Staley EM,Dimmitt RA,Schoeb TR,Tanner SM,Lorenz RG

更新日期：2011-12-01 00:00:00

abstract：:Ornithine transcarbamylase deficiency (OTCD) is the most common of the urea cycle disorders and follows an X-linked inheritance pattern. The classical form in male infants causes vomiting and lethargy in the neonatal period; if untreated the severe hyperammonaemia can cause acute neurotoxic complications and permanent...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Selvanathan A,Hertzog A,Lemberg DA,Ellaway C

更新日期：2020-08-01 00:00:00

abstract：OBJECTIVES:Children with coeliac disease (CD) have an increased number of chromosome aberrations in peripheral blood lymphocytes. Whether genetically determined or a secondary phenomenon in CD, chromosome abnormalities may be involved in the predisposition to cancer in CD patients. The aim of the study was to follow a ...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Kolacek S,Jadresin O,Petković I,Misak Z,Sonicki Z,Booth IW

更新日期：2004-02-01 00:00:00

abstract：:Visceral hypersensitivity and abnormal coping are common in children with functional abdominal pain disorders (FAPDs). Thus, it would be expected that children with visceral hypersensitivity would report more pain if their gut is acutely inflamed. The aim of the study was to compare clinical symptoms and somatization ...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Saps M,Mintjens S,Pusatcioglu CK,Cohen DM,Sternberg P

更新日期：2017-08-01 00:00:00

abstract：:A 17-year-old male with Crohn's disease presented with persistent fever and right upper quadrant tenderness. Ultrasonography and abdominal computerized axial tomography (CAT scan) showed two large loculated abscess cavities in the right lobe of the liver. Surgical drainage and antibiotic therapy led to resolution of b...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Weinberg RJ,Klish WJ,Brown MR,Smalley JR,Emmens RW

更新日期：1983-01-01 00:00:00

abstract：BACKGROUND:There are few data concerning the risk of contamination of enteral feeding systems via gastrostomy in children, and none for conditions that pertain to home-based care. METHODS:To investigate the risk of contamination of enteral feeding systems during the home-based care of 20 children receiving gastrostomy...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Bott L,Husson MO,Guimber D,Michaud L,Arnaud-Battandier F,Turck D,Gottrand F

更新日期：2001-09-01 00:00:00

abstract：BACKGROUND:Duodenal gastric metaplasia is rarely reported in untreated celiac disease, although it is seen in 60% to 100% of duodenal biopsy specimens in nonceliac patients with histologic duodenitis. The low incidence could represent underreporting, a decreased incidence in pediatric patients generally, or the more di...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Shaoul R,Marcon MA,Okada Y,Cutz E,Forstner G

更新日期：2000-04-01 00:00:00

abstract：OBJECTIVES:The aim of the study was to evaluate erosive esophagitis healing and symptom improvement with once-daily esomeprazole in children ages 12 to 36 months with endoscopically or histologically proven gastroesophageal reflux disease (GERD). PATIENTS AND METHODS:Data from children ages 12 to 36 months were includ...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Tolia V,Gilger MA,Barker PN,Illueca M

更新日期：2010-11-01 00:00:00

abstract：BACKGROUND:Vitamin A deficiency is a common manifestation in cystic fibrosis (CF), but high levels of vitamin A in the liver have also been described. High levels of vitamin A in the liver are toxic, while normal levels might be protective against liver damage. In order to investigate whether liver damage in patients w...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Lindblad A,Diczfalusy U,Hultcrantz R,Thorell A,Strandvik B

更新日期：1997-03-01 00:00:00

abstract：BACKGROUND AND AIM:Pediatric gastroenterology is the only pediatric subspecialty with nutrition as part of its official curriculum and objective; however, pediatric gastroenterology fellows believe that their baseline knowledge in nutrition is suboptimal. The purpose of the present study was to assess the perceived eff...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Lin HC,Kahana D,Vos MB,Black D,Port Z,Shulman R,Scheimann A,Mascarenhas MR

更新日期：2013-02-01 00:00:00

abstract：:Constipation is a common pediatric problem. To assist health care professionals who care for children with constipation, the North American Society for Pediatric Gastroenterology, Hepatology and Nutrition (NASPGHAN) previously published a clinical guideline based on an integration of medical evidence with expert opini...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： North American Society for Pediatric Gastroenterology, Hepatology and Nutrition.

更新日期：2006-09-01 00:00:00

abstract：BACKGROUND:In contrast to human milk, current infant formulas in the United States do not contain omega3 and omega6 long-chain polyunsaturated fatty acids. This may lead to suboptimal blood lipid fatty acid profiles and to a measurable diminution of visual function in developing term infants. The need for docosahexaeno...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Hoffman DR,Birch EE,Birch DG,Uauy R,Castañeda YS,Lapus MG,Wheaton DH

更新日期：2000-11-01 00:00:00

abstract：:The prolonged intestinal retention of a Watson biopsy capsule in a 12-year-old girl with chronic diarrhea is reported. Radiological investigation showed a duodenal obstruction due to superior mesenteric artery syndrome. A preliminary barium study of the upper gastrointestinal tract, before performing blind intestinal ...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Bonamico M,Roggini M,Pierro A,Dionisi Vici C,Bitti IM

更新日期：1985-02-01 00:00:00

abstract：:Cyclic vomiting syndrome (CVS) is a disorder noted for its unique intensity of vomiting, repeated emergency department visits and hospitalizations, and reduced quality of life. It is often misdiagnosed due to the unappreciated pattern of recurrence and lack of confirmatory testing. Because no accepted approach to mana...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Li BU,Lefevre F,Chelimsky GG,Boles RG,Nelson SP,Lewis DW,Linder SL,Issenman RM,Rudolph CD,North American Society for Pediatric Gastroenterology, Hepatology, and Nutrition.

更新日期：2008-09-01 00:00:00

abstract：:An enzyme-linked immunosorbent assay technique was developed to determine serum antigliadin antibodies of the IgA, IgE, IgG, and IgM classes. The antibody level of each serum specimen was expressed as an index value, i.e., optical density of test serum/optical density of cutoff, where cutoff was calculated for each im...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Juto P,Fredrikzon B,Hernell O

更新日期：1985-10-01 00:00:00

abstract：:To characterize the mechanisms leading to dietary evoked increases of lactase and sucrase activities by carbohydrates, we performed a quantitative comparison of the effects of lactose and sucrose on the corresponding disaccharidases in the jejunum of 2-month-old rats. For 7-10 days the rats were fed a low-starch (5 ca...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Goda T,Bustamante S,Koldovský

更新日期：1985-12-01 00:00:00

abstract：:In a double-blind, placebo-controlled, randomized study we measured the effect of 1 mg/kg intravenous metoclopramide on the gastric emptying of a 15 ml/kg 5% glucose meal, using a phenol red dye dilution technique. In a group of nine infants referred for multiple daily episodes of regurgitation, metoclopramide doubled...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Hyman PE,Abrams CE,Dubois A

更新日期：1988-03-01 00:00:00

abstract：OBJECTIVES:The aim of the present study was to evaluate whether polymorphisms of the mannose-binding lectin (MBL-2) gene and MBL serum levels on admission to neonatal intensive care unit are associated with necrotizing enterocolitis (NEC) in preterm infants and to verify MBL expression in NEC bowels. METHODS:In this r...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Prencipe G,Azzari C,Moriondo M,Devito R,Inglese R,Pezzullo M,Piersigilli F,Trucchi A,De Benedetti F,Auriti C

更新日期：2012-08-01 00:00:00

abstract：:The nutritional management of intractable diarrhea and short bowel syndrome remains a challenging problem. The advantage of continuous nasogastric infusion is undisputed, but what to feed remains in question, and no studies, to these authors' knowledge, have yet compared two widely used specially designed protein hydr...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Galeano NF,Lepage G,Leroy C,Belli D,Levy E,Roy CC

更新日期：1988-01-01 00:00:00

abstract：:Eighty-eight consecutive children with inflammatory bowel disease were studied, and upper gastrointestinal endoscopy was performed in 80 of them as one of the initial investigations before commencing medical or nutritional treatment. Forty-one children were found to have Crohn's disease and 47, ulcerative colitis. Upp...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Ruuska T,Vaajalahti P,Arajärvi P,Mäki M

更新日期：1994-08-01 00:00:00

abstract：OBJECTIVES:Polyethylene glycol (PEG) is a frequently used laxative agent. It is unknown, however, whether PEG affects the absorptive capacity of the intestine. Reduced lipid (dietary fat and cholesterol) absorption induced by long-term PEG treatment could negatively affect growth in children. We tested whether PEG acce...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： van der Wulp MY,Cuperus FJ,Stellaard F,van Dijk TH,Dekker J,Rings EH,Groen AK,Verkade HJ

更新日期：2012-10-01 00:00:00

abstract：:In order to study the influence of biliary secretions on the in situ kinetic data of brush border disaccharidases in relation to small intestinal villus-crypt architecture, an anastomosis was constructed between the common bile duct, which had been divided before its entrance into the pancreatic head, and the ileum in...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Gutschmidt S,Gartemann H

更新日期：1983-11-01 00:00:00

abstract：OBJECTIVE:To determine the natural history of treated and untreated eosinophilic esophagitis (EE) and examine the presenting symptoms of EE. PATIENTS AND METHODS:Retrospective and prospective chart review of all patients diagnosed with EE at The Children's Hospital of Philadelphia. EE was defined as greater than 20 eo...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Spergel JM,Brown-Whitehorn TF,Beausoleil JL,Franciosi J,Shuker M,Verma R,Liacouras CA

更新日期：2009-01-01 00:00:00

abstract：OBJECTIVES:Intestinal epithelial restitution is the first part in the process of mucosal repair after injury in the intestine. Integrity of the intestinal mucosal barrier is important as a first line of defense against bacteria and endotoxin. Necrotizing enterocolitis (NEC) is a major cause of morbidity and mortality i...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Richter JM,Schanbacher BL,Huang H,Xue J,Bauer JA,Giannone PJ

更新日期：2012-05-01 00:00:00

abstract：:Hypercalciuria and bone disease are frequently associated with total parenteral nutrition (TPN) in children and adults. The aim of this study was to assess the influence of calcium, phosphorus, and vitamin D intakes on hypercalciuria. We observed seven children aged 4-13 years receiving home cyclic TPN for 4 consecuti...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Larchet M,Garabédian M,Bourdeau A,Gorski AM,Goulet O,Ricour C

更新日期：1991-11-01 00:00:00

abstract：:This study was designed to establish whether the starting time of breast-feeding (BF) may have affected gut closure for macromolecules during the earliest postnatal period. An increase of serum IgA concentrations was taken as the index of gut permeability to macromolecules. In 14 neonates, BF started 1-6 h after birth...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Vukavić T

更新日期：1984-11-01 00:00:00