Ornithine Transcarbamylase Deficiency Presenting as Acute Liver Failure in Girls: A Paediatric Case Series.

abstract：BACKGROUND:Duodenal gastric metaplasia is rarely reported in untreated celiac disease, although it is seen in 60% to 100% of duodenal biopsy specimens in nonceliac patients with histologic duodenitis. The low incidence could represent underreporting, a decreased incidence in pediatric patients generally, or the more di...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Shaoul R,Marcon MA,Okada Y,Cutz E,Forstner G

更新日期：2000-04-01 00:00:00

abstract：BACKGROUND AND AIM:Gastroduodenal disease is more common among adults and children with cagA+ Helicobacter pylori infection, but disease severity varies among those infected with cagA+ strains. We examined whether cagA in situ expression can predict disease manifestations among H pylori-infected children. PATIENTS AND...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Rick JR,Goldman M,Semino-Mora C,Liu H,Olsen C,Rueda-Pedraza E,Sullivan C,Dubois A

更新日期：2010-02-01 00:00:00

abstract：:Enteral nutrition support (ENS) involves both the delivery of nutrients via feeding tubes and the provision of specialised oral nutritional supplements. ENS is indicated in a patient with at least a partially functioning digestive tract when oral intake is inadequate or intake of normal food is inappropriate to meet t...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Braegger C,Decsi T,Dias JA,Hartman C,Kolacek S,Koletzko B,Koletzko S,Mihatsch W,Moreno L,Puntis J,Shamir R,Szajewska H,Turck D,van Goudoever J,ESPGHAN Committee on Nutrition:.

更新日期：2010-07-01 00:00:00

abstract：BACKGROUND:Immunologic development of soy-fed infants has not been extensively studied. Early studies of soy flour-based formulas showed decreased immunoglobulin production when soy protein intake was limited. However, there were no significant differences in rotavirus vaccine responses between breast-fed and soy prote...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Ostrom KM,Cordle CT,Schaller JP,Winship TR,Thomas DJ,Jacobs JR,Blatter MM,Cho S,Gooch WM 3rd,Granoff DM,Faden H,Pickering LK

更新日期：2002-02-01 00:00:00

abstract：OBJECTIVES:Adult-based guidelines support the use of the pull (extraction) endoscopic technique in managing esophageal food bolus impactions (FBIs) but allow the consideration of the push (advancement) technique with caution based on available published literature. The North American Society for Pediatric Gastroenterol...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Kriem J,Rahhal R

更新日期：2018-01-01 00:00:00

abstract：:A calcium absorption investigation was carried out with the purpose of determining whether lactose-hydrolyzed milk facilitates calcium absorption in subjects with lactose malabsorption. Nine children participated in the study, which was divided into two investigation periods separated by at least 1 week. During the fi...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Nielsen OH,Schiøtz PO,Rasmussen SN,Krasilnikoff PA

更新日期：1984-03-01 00:00:00

abstract：OBJECTIVE:Eosinophilic oesophagitis (EE) is a clinical entity characterised by a set of symptoms and eosinophilic infiltration of the oesophageal epithelium. Recent reports indicate that EE is increasingly diagnosed in paediatric patients. We aimed to evaluate the epidemiology of paediatric EE in a European population....

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Dalby K,Nielsen RG,Kruse-Andersen S,Fenger C,Bindslev-Jensen C,Ljungberg S,Larsen K,Walsted AM,Husby S

更新日期：2010-09-01 00:00:00

abstract：OBJECTIVES:Oxidative stress has been implicated in the development of nonalcoholic fatty liver disease (NAFLD) and progression to the more severe form, nonalcoholic steatohepatitis (NASH), in children. We aimed to study the clinical correlation between bilirubin, a potent endogenous antioxidant with cytoprotective prop...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Puri K,Nobili V,Melville K,Corte CD,Sartorelli MR,Lopez R,Feldstein AE,Alkhouri N

更新日期：2013-07-01 00:00:00

abstract：:Alkaline phosphatase (AP) activity is an accepted marker of epithelial cell differentiation and integrity in intestinal mucosal explant systems. In experiments involving AP it is usually expressed as activity per unit protein in tissue culture. It has been previously demonstrated that during organ culture a considerab...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Ashkenazi A,Idar D,Maimon M,Hegesh E,Frank E,Hahn T,Wolman Y,Levin S

更新日期：1984-03-01 00:00:00

abstract：:This study of 200 Uruguayans between 0 and 86 years old was designed to determine the prevalence of lactose malabsorption. Lactose intolerance is defined as a clinical syndrome of abdominal pain, diarrhea, flatulence, and bloating after the ingestion of a standard lactose tolerance test dose (2 g of lactose per kilogr...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Maggi R,Sayagues B,Fernandez A,Romero B,Barusso P,Hernandez C,Magariños M,Mendez G,Dilascio C,Martell M

更新日期：1987-05-01 00:00:00

abstract：:The macronutrient, trace mineral, and immunological contents of milk of five moderately controlled, insulin-dependent diabetic women were studied at 3 months postpartum. Concentrations of total nitrogen, lactose, fat, and energy were not distinguishable from those in milk of nondiabetic women. Glucose concentrations i...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Butte NF,Garza C,Burr R,Goldman AS,Kennedy K,Kitzmiller JL

更新日期：1987-11-01 00:00:00

abstract：BACKGROUND:Feeding impairment frequently complicates the course of children with neurologic disorders and places them at risk for malnutrition and growth failure. Although feeding abnormalities have been reported in female patients with Rett syndrome, the mechanisms that account for these findings have not been elucida...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Motil KJ,Schultz RJ,Browning K,Trautwein L,Glaze DG

更新日期：1999-07-01 00:00:00

abstract：OBJECTIVES:Predicting short-term relapses and long-term prognosis is of utmost importance in paediatric inflammatory bowel disease (IBD). Our aim was to investigate the short-term disease outcome and medication during the first year in a paediatric incident cohort from Hungary. In addition, association laboratory marke...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Müller KE,Lakatos PL,Kovacs JB,Arato A,Varkonyi A,Nemes E,Tarnok A,Toth G,Papp M,Solyom E,Horvath A,Guthy I,Kovacs M,Veres G,Hungarian Pediatric IBD Registry Group.

更新日期：2016-01-01 00:00:00

abstract：OBJECTIVES:To analyze the long-term results of Boerema anterior gastropexy using the Visick grading system in a university teaching hospital. METHODS:Retrospective review of 247 children with severe or complicated gastroesophageal reflux disease (GERD). Patients who underwent primary gastropexy between 1990 and 2001 w...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Kloek JJ,van de Laar GA,Deurloo JA,Aronson DC,Benninga MA,Taminiau JA,Heij HA

更新日期：2006-07-01 00:00:00

abstract：OBJECTIVES:The aim of the study was to validate a brief Bowel Habit Questionnaire (BHQ) with prospectively obtained data from a 14-day diary and to determine whether the BHQ predicts the development of medically significant constipation (MSC) during the following year. MATERIALS AND METHODS:The BHQ was distributed to ...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Wald ER,Jagodzinski TD,Moyer SC,Wald A,Eickhoff JC,Edmonson MB

更新日期：2011-11-01 00:00:00

abstract：BACKGROUND:We analyzed the role that nutrition and the insulin-like growth factors IGF-I and IGFBP-3 play on neonatal growth. METHODS:Full-term and preterm infants with 1 and 3 weeks of postnatal life (n = 54 and n = 33, respectively) were studied. Anthropmetric variables, daily intake of energy and nutrients, and ser...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Díaz-Gómez NM,Domenech E,Barroso F

更新日期：1997-03-01 00:00:00

abstract：OBJECTIVES:Data on the outcomes of children with perianal Crohn disease (pCD) are limited, although its presence is often used for justifying early use of biologics. We aimed to assess whether pCD in children is associated with more severe outcomes as found in adults. METHODS:Data were extracted from the ImageKids dat...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Assa A,Amitai M,Greer ML,Castro DA,Kuint RC,Martínez-León M,Herman-Sucharska I,Coppenrath E,Anupindi S,Towbin A,Moote D,Konen O,Pratt LT,Griffiths A,Turner D,ImageKids Study Group.

更新日期：2017-09-01 00:00:00

abstract：:The influence of maternal folate status and human milk folate content on infant folate status was studied in 11 lactating women taking folate supplements throughout pregnancy and lactation. Nursing mothers not taking folate supplements, as well as nonpregnant, nonlactating women, were also studied. Maternal and infant...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Smith AM,Picciano MF,Deering RH

更新日期：1983-11-01 00:00:00

abstract：BACKGROUND AND OBJECTIVES:Breast milk contains several bioactive factors including human milk oligosaccharides (HMOs) and microbes that shape the infant gut microbiota. HMO profile is determined by secretor status; however, their influence on milk microbiota is still uncovered. This study is aimed to determine the impa...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Cabrera-Rubio R,Kunz C,Rudloff S,García-Mantrana I,Crehuá-Gaudiza E,Martínez-Costa C,Collado MC

更新日期：2019-02-01 00:00:00

abstract：OBJECTIVES:The association between snacking habits and overweight in adolescents is unclear. We evaluated the relation between snacking patterns and overweight/obesity in a cohort of 11- to 13-year-old Italian adolescents. METHODS:The dietary habits of 400 randomly selected adolescents were evaluated; those with body ...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Bo S,De Carli L,Venco E,Fanzola I,Maiandi M,De Michieli F,Durazzo M,Beccuti G,Cavallo-Perin P,Ghigo E,Ganzit GP

更新日期：2014-10-01 00:00:00

abstract：:Proton pump inhibitors such as lansoprazole are used in the treatment of gastroesophageal reflux disease (GERD), but dosing guidelines for infants have not been determined. The objective of this study was to assess the clinical efficacy of 2 dosing regimens of lansoprazole in infants with GERD using the revised infant...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Khoshoo V,Dhume P

更新日期：2008-03-01 00:00:00

abstract：:Current research is directed toward innovative dietary compositions that exert specific effects on health promotion and reducing the risk of diseases. For example, the demonstration that the gut microbiota is an important constituent in the intestine's mucosal barrier has led to new therapeutic strategies for infectio...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Isolauri E

更新日期：2007-12-01 00:00:00

abstract：OBJECTIVES:Microvillous inclusion disease (MVID) is a cause of intractable diarrhea in infancy. In its classic form, the disease is characterized by a severe persistent watery diarrhea starting within the first days of life. Parenteral nutrition and small bowel transplantation are the only known treatments for the affe...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Perry A,Bensallah H,Martinez-Vinson C,Berrebi D,Arbeille B,Salomon J,Goulet O,Marinier E,Drunat S,Samson-Bouma ME,Gérard B,Hugot JP

更新日期：2014-12-01 00:00:00

abstract：:Parasitic infection of the gut is highly prevalent in developing countries and contributes to the severe malnutrition associated with persistent diarrhoea in children. Using random faecal alpha 1-antitrypsin measurements as an index of protein-losing enteropathy, we examined children with and without parasitic infecti...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Sullivan PB,Lunn PG,Northrop-Clewes CA,Farthing MJ

更新日期：1992-11-01 00:00:00

abstract：OBJECTIVES:Current pediatric guidelines allow noninvasive diagnosis of celiac disease in selected children. We investigated in a large cohort study whether the severity of villous atrophy at diagnosis is associated with clinical characteristics or long-term health outcomes, thus having a prognostic significance. METHO...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Kröger S,Kurppa K,Repo M,Huhtala H,Kaukinen K,Lindfors K,Arvola T,Kivelä L

更新日期：2020-07-01 00:00:00

abstract：OBJECTIVES:Infant colic (IC), with an estimated prevalence of 5% to 25%, has a high impact on health care costs. Furthermore, reported negative sequelae are disturbed parent-infant interaction, increased susceptibility to abdominal pain, and even child abuse. Its etiology remains unknown, leading to a wide variety in i...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Steutel NF,Benninga MA,Langendam MW,de Kruijff I,Tabbers MM

更新日期：2014-09-01 00:00:00

abstract：OBJECTIVES:Wilson disease (WD) is a rare inborn error of copper metabolism with diverse manifestations. There has been no study of zinc (Zn), the copper's antagonist, in WD diagnosis and severity so far. Our aims were to evaluate serum Zn in WD and its correlation with the disease severity score (revised WD index). Alt...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Sintusek P,Kyrana E,Dhawan A

更新日期：2018-09-01 00:00:00

abstract：BACKGROUND:Early postnatal glucocorticoid exposure accelerates the maturation of the bowel mucosa but results in bowel wall thinning in the newborn mouse ileum and increases the risk of focal ileal perforation in extremely premature infants. We have previously demonstrated a redistribution of insulin-like growth factor...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Gordon PV,Moats-Staats BM,Stiles AD,Price WA

更新日期：2002-10-01 00:00:00

abstract：OBJECTIVES:Gastroesophageal reflux is common but remains a controversial disease to diagnose and treat and little is known about the role of reflux testing in predicting clinical outcomes, particularly in children at risk for extraesophageal reflux complications. The aim of this study was to determine if rates of hospi...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Duncan DR,Amirault J,Johnston N,Mitchell P,Larson K,Rosen RL

更新日期：2016-08-01 00:00:00

abstract：OBJECTIVE:To describe the longitudinal pattern of dietary energy and macronutrient intakes during the first 10 years of life in a sample of healthy Italian children. PATIENTS AND METHODS:Sixty-one healthy children were followed from birth to 10 years of age. At 1, 5, 8, and 10 years of age, anthropometric measurements...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Verduci E,Radaelli G,Stival G,Salvioni M,Giovannini M,Scaglioni S

更新日期：2007-07-01 00:00:00