Darrow-Gamble disease: ultrasonographic and radiographic findings.

Abstract:

:A case of Darrow-Gamble disease is presented with review of the radiographic and ultrasonographic appearance of this rare cause of profound chronic diarrhea beginning at birth. The disease is caused by a defect of active intestinal chloride transport which results in a large loss of the electrolytes and water. To prevent growth retardation and renal involvement an adequate replacement therapy is necessary. This uncommon anomaly was detected by ultrasound 3 weeks before delivery. Both sonography and radiography were useful diagnostic tools in the postnatal period. The clinical features of the lesion are also discussed.

journal_name

Pediatr Radiol

journal_title

Pediatric radiology

authors

Poggiani C,Auriemma A,Menghini P,Lando B,Bonhoeffer P,Colombo A

doi

10.1007/BF02020230

subject

Has Abstract

pub_date

1993-01-01 00:00:00

pages

65-6

issue

1

eissn

0301-0449

issn

1432-1998

journal_volume

23

pub_type

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