Abstract：
:Two different forms of dyssegmental dysplasia, mild and severe, can be distinguished on clinical, radiographic and chondro-osseous morphologic grounds. The milder Rolland-Desbuquois type is frequently characterised by survival beyond the newborn period. The lethal Silverman-Handmaker type has distinctive and more severe findings. In this paper, a rare case of the Rolland-Desbuquois type is presented. The case is unusual because although it was the milder form, the child died on the 10th day of life.
journal_name
Pediatr Radioljournal_title
Pediatric radiologyauthors
d'Orey MC,Mateus M,Guimarães H,Miguel C,Costeira MJ,Nogueira R,Montenegro N,Santos NT,Maroteaux Pdoi
10.1007/s002470050279subject
Has Abstractpub_date
1997-12-01 00:00:00pages
948-50issue
12eissn
0301-0449issn
1432-1998journal_volume
27pub_type
杂志文章abstract：:We report neuroimaging findings of intracranial hemorrhage and cerebral edema in an infant with obtundation and seizures, initially suspected to be secondary to non-accidental trauma but finally attributed to hypernatremic dehydration. Neuroimaging findings due to hypernatremic dehydration have not been previously des...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/s002470050232
更新日期：1997-10-01 00:00:00
abstract：:The Computed Tomography (CT) appearance of a pelvic haemangioma involving the rectum in two children, one with the Vater association and one with Klippel-Trenaunay syndrome, is described. Both cases complained of painless rectal bleeding and the diagnosis was suggested by the presence of pelvic phleboliths on the plai...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/BF02387639
更新日期：1989-01-01 00:00:00
abstract：:We review the physiological basis of diffusion-weighted imaging and discuss the implementation of diffusion-weighted imaging pulse sequences and the subsequent postprocessing to yield quantitative estimations of diffusion parameters. We also introduce the concept of directionality of "apparent" diffusion in vivo and t...
journal_title：Pediatric radiology
pub_type： 杂志文章,评审
doi：10.1007/s00247-007-0516-z
更新日期：2007-08-01 00:00:00
abstract：:Purpose. To determine whether gadolinium-enhanced MR imaging can detect early reversible ischemia of the capital femoral epiphysis and physis induced by hip hyperabduction in piglets. Materials and methods. Thirteen 1- to 3-week-old piglets were placed in maximal abduction of both hips and studied with dynamic gadolin...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/BF02011824
更新日期：1995-01-01 00:00:00
abstract：BACKGROUND:Phalangeal microgeodic syndrome is an uncommon benign self-limiting condition that often occurs during cold weather. The etiology and the pathogenesis of the disease remain unclear. OBJECTIVE:To report a series of children with phalangeal microgeodic syndrome. MATERIALS AND METHODS:Twenty children with pha...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/s00247-018-4137-5
更新日期：2018-08-01 00:00:00
abstract：:Abdominal angiography is an extremely valuable modality for the diagnosis of abdominal disease in infants and children. A practical guide to catheter selection, flow rates, and contrast dosage for abdominal angiography in the pediatric patient is presented. ...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/BF00988657
更新日期：1976-10-26 00:00:00
abstract：:We sonographically investigated the internal jugular veins of 40 children who had undergone catheterization of the vein (group A: silastic catheter, n = 24; group B: polyurethane catheter, n = 16) in the neonatal period. The average age at catheter implantation was 43 +/- 73 days, the average birthweight 2414 +/- 1145...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/BF02012737
更新日期：1994-01-01 00:00:00
abstract：:Imaging is a crucial part of the evaluation of children with primary liver malignancies. In addition to staging the intrahepatic extent of the tumour, the 2005 revision of the PRETEXT system specifies certain criteria for assessment of extrahepatic disease. This article reviews the imaging findings of two of these cri...
journal_title：Pediatric radiology
pub_type： 杂志文章,评审
doi：10.1007/s00247-007-0513-2
更新日期：2007-11-01 00:00:00
abstract：BACKGROUND:Hirschsprung disease (HD) is a functional obstruction of the bowel caused by the absence of intrinsic enteric ganglion cells. The diagnosis of total colonic HD (TCHD) based on contrast enemas is difficult in newborns because radiological findings vary. OBJECTIVE:To evaluate the radiographic and contrast ene...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/s00247-008-0952-4
更新日期：2008-11-01 00:00:00
abstract：BACKGROUND:Influenza A (H1N1) can cause severe neurological complications. OBJECTIVE:The purpose of this study was to analyze clinical and MRI features of neurological complications after H1N1 infection in critically ill children. MATERIALS AND METHODS:We retrospectively analyzed clinical and neuroimaging findings in...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/s00247-013-2682-5
更新日期：2013-09-01 00:00:00
abstract：:Sternal clefts have been reported sporadically, but there are no reports describing complete investigations of the malformation. We describe a child with isolated inferior sternal cleft diagnosed at 33 weeks of gestation and thoroughly investigated by prenatal US, MRI and CT and preoperative US. Our report highlights ...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/s00247-011-2318-6
更新日期：2012-08-01 00:00:00
abstract：:Juvenile granulosa cell tumor of the testis is a distinct form of sex cord-stromal tumor of neonates and infants [1]. This tumor comprises a significant percentage of testicular tumors in baby boys. We present a patient who had preoperative imaging studies. ...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/BF02012994
更新日期：1992-01-01 00:00:00
abstract：BACKGROUND:The expected MRI-based dimensions of the intracranial optic nerve and optic tract in neonates are unknown. OBJECTIVE:To evaluate the sizes of the intracranial optic nerve and optic tract in neonates at term-equivalent age using MRI. MATERIALS AND METHODS:We retrospectively analyzed brain MRI examinations i...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/s00247-015-3495-5
更新日期：2016-04-01 00:00:00
abstract：:We describe a 4-year-old girl with an inflammatory pseudotumour of the pancreas, which was preceded by varicella-zoster infection. Inflammatory pseudotumour may involve a variety of tissues, the lungs and liver being typical sites of predilection. Imaging and laboratory tests are nonspecific, and for this reason the d...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/s002470000331
更新日期：2000-11-01 00:00:00
abstract：BACKGROUND:While several studies have investigated the dose from scattered radiation from X-ray procedures in a pediatric nursery, they examined scatter from chest procedures only, or the types of examination were not specified. OBJECTIVE:The aim of this study was to collect scatter and transmission data from several ...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/s00247-003-0999-1
更新日期：2003-10-01 00:00:00
abstract：:Radiographic examinations of the paranasal sinuses and chests of 187 patients with C.F. from five months to 27 years of age were reviewed. One hundred eight-five patients consistently had opaque maxillary and ethmoidal sinuses. Forty-five patients had normal chest radiographs. These observations show that the paranasa...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/BF00977665
更新日期：1980-02-01 00:00:00
abstract：:A case of heterotopic gastric mucosa in the common bile duct, cystic duct and gallbladder is reported in a 3-year-old girl with abdominal pain and jaundice. Abdominal US and CT showed dilatation of the biliary tree and a well-defined mass in the common bile duct that narrowed its lumen. The gallbladder was contracted ...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/s00247-002-0718-3
更新日期：2003-02-01 00:00:00
abstract：:Inflammatory bowel diseases (IBDs), including Crohn disease (CD) and ulcerative colitis (UC), often affect children and adolescents. Their diagnosis is based on the integration of clinical, biological, endoscopic, histological and radiological data. The paediatric radiologist may help the clinician in many ways. In ch...
journal_title：Pediatric radiology
pub_type： 杂志文章,评审
doi：10.1007/s00247-007-0573-3
更新日期：2007-11-01 00:00:00
abstract：BACKGROUND:Unstable posterior pelvic ring fractures and dislocations are uncommon but potentially life-threatening injuries in children. Early definitive management reduces risk of immediate complications as well as chronic pain and gait dysfunction. Conventional operative therapy carries substantial risk of extensive ...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/s00247-004-1291-8
更新日期：2004-12-01 00:00:00
abstract：:Isolated oesophageal leiomyomatosis in children is very rare. The association between leiomyomatosis of oesophagus and female genital tract and an Alport like hematuric nephritis has been recognized as a distinct entity by Garcia-Torres and Guarner. Since then few other cases of this syndrome have been observed. Conge...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/BF02012602
更新日期：1991-01-01 00:00:00
abstract：:A case is reported in whom there was a unilateral complete arrest of differentiation of the otocyst associated with an ipsilateral mild hemifacial hypoplasia and auricular abnormalities. The patient's tympanic membrane and VII nerve function were normal and a normal ossicular mass was identified on CT Scan. This case ...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/BF02467313
更新日期：1989-01-01 00:00:00
abstract：BACKGROUND:Pontine tumors carry the worst prognosis of all brain tumors. In most cases, the diagnosis is based solely on MR imaging, without biopsy. OBJECTIVE:To describe the MR findings of pontine tumors at diagnosis and during follow-up and correlate those with prognosis and to assess the value of MR imaging in pati...
journal_title：Pediatric radiology
pub_type： 杂志文章,评审
doi：10.1007/s00247-005-1502-y
更新日期：2005-09-01 00:00:00
abstract：:We report a 29-month-old girl with osteopathia striata with cranial sclerosis (OS-CS), who showed several unusual manifestations, including short stature, muscular hypotonia, short lingual frenulum, an accessory ear and a granuloma at the oral edge. The most unusual distressing finding was severe cervical kyphosis wit...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/s002470100486
更新日期：2001-09-01 00:00:00
abstract：:We present a 16-year-old boy with autoimmune liver disease and longstanding portal hypertension in whom a CT arteriogram demonstrated a large aneurysm arising from the distal, extra-parenchymal portion of the splenic artery. Because of its location adjacent to multiple venous collaterals, the aneurysm was indistinguis...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/s00247-009-1493-1
更新日期：2010-07-01 00:00:00
abstract：BACKGROUND:Sclerotic bone lesions are often seen on chest CT in adults with tuberous sclerosis complex. OBJECTIVE:To characterize bone lesions at abdominal MRI in children with tuberous sclerosis complex. MATERIALS AND METHODS:This retrospective review included 70 children with tuberous sclerosis complex who had unde...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/s00247-016-3549-3
更新日期：2016-05-01 00:00:00
abstract：:Long-term imaging and clinical findings are reported in six children whose polycystic kidney disease was detected in infancy or early childhood. Over time (2 years to 20 years) all patients developed portal hypertension from hepatic fibrosis, a problem primarily noted in recessive pattern polycystic kidney disease. Mi...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/BF02387555
更新日期：1988-01-01 00:00:00
abstract：:Sakoda complex is a rare but distinct combination of birth defects consisting of a basal cephalocele, agenesis of the corpus callosum, and midline cleft lip/palate. It has been reported in association with ophthalmologic abnormalities, cognitive deficits and severe epilepsy. Here we describe both prenatal and postnata...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/s00247-019-04491-5
更新日期：2019-12-01 00:00:00
abstract：:Appropriate management of the child with malrotation and/or midgut volvulus requires a multi-disciplinary approach with early clinical suspicion, rapid confirmation of diagnosis, and expedient operative intervention in order to obtain the most effective outcomes. ...
journal_title：Pediatric radiology
pub_type： 杂志文章,评审
doi：10.1007/s00247-008-1129-x
更新日期：2009-04-01 00:00:00
abstract：:Magnetic resonance imaging (MRI) was compared with iodine-131-labeled monoclonal antibody scanning for ability to detect bone marrow metastases in the spine, pelvis, and femurs of children with disseminated neuroblastoma. The five patients in this study had received high-dose chemotherapy and radiation, either with (N...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/BF02010638
更新日期：1989-01-01 00:00:00
abstract：BACKGROUND:Demand for pediatric cardiac computed tomography (CT) angiography is increasing due to recent advances that reduce the need for sedation and radiation exposure while enhancing diagnostic accuracy. This has resulted in the increasing use of cardiac CT angiography emergently during weekends and after hours. Th...
journal_title：Pediatric radiology
pub_type： 杂志文章
doi：10.1007/s00247-020-04659-4
更新日期：2020-07-01 00:00:00
