Abstract:
:Three children with neurofibromatosis involving the lower urinary tract are reported and their clinical, radiological and pathological findings are described. Lower urinary tract involvement in neurofibromatosis has previously been reported in 17 children, 12 of whom had other stigmata of von Recklinghausens disease. Lower urinary tract involvement may be asymptomatic and can be found incidentally. Every case with neurofibromatosis presenting with what may appear to be even only insignificant urinary symptoms should be thoroughly investigated urologically. Symptoms are usually related to urinary tract obstruction or neurogenic bladder dysfunction due to the involvement of the nerves supplying the bladder. Urinary diversion is the treatment of choice as surgical removal of the extensive tumour is seldom feasible. Following treatment the prognosis for survival appears to be good.
journal_name
Pediatr Radioljournal_title
Pediatric radiologyauthors
Daneman A,Grattan-Smith Pdoi
10.1007/BF00975350subject
Has Abstractpub_date
1976-04-14 00:00:00pages
161-6issue
3eissn
0301-0449issn
1432-1998journal_volume
4pub_type
杂志文章abstract::Twenty-four patients with repaired diaphragmatic hernia had upper gastrointestinal series to assess the rotation and fixation of the bowel. A spectrum of rotational abnormalities was present in almost all patients, although those with repaired right-sided hernias demonstrated a more obvious anomaly of rotation than th...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF02011092
更新日期:1995-01-01 00:00:00
abstract::Ferumoxytol is an ultra-small superparamagnetic iron oxide (USPIO) particle that is FDA-approved for parenteral treatment of iron deficiency anemia in adults with chronic kidney disease. Because of the association between gadolinium-based contrast agents and nephrogenic systemic fibrosis in patients with severe chroni...
journal_title:Pediatric radiology
pub_type: 杂志文章,评审
doi:10.1007/s00247-016-3605-z
更新日期:2016-08-01 00:00:00
abstract::We present a case of bilateral tibial insufficiency fracture in which indium (In)-111 diethylenetriamine pentaacetic acid (DTPA) octreotide scan showed increased activity in the region of the fracture. The scan was performed in a 5-year-old girl with severe refractory hypertension and elevated plasma metanephrines for...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-014-3029-6
更新日期:2015-01-01 00:00:00
abstract:BACKGROUND:Hepatic involvement is frequent in patients with cystic fibrosis (CF), with focal biliary cirrhosis being the pathognomonic hepatic manifestation. In around one-quarter of CF patients, it results in CF-associated liver disease (CFLD). This occurs as a relatively early complication with the majority of patien...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-009-1531-z
更新日期:2010-07-01 00:00:00
abstract::Fibroblast growth factor receptor mutations cause some of the main short-limb skeletal dysplasias and craniosynostosis syndromes, including achondroplasia, hypochondroplasia, thanatophoric dysplasia, Apert syndrome, Crouzon syndrome, Pfeiffer syndrome, and Jackson-Weiss syndrome. Much work remains to be done in unrave...
journal_title:Pediatric radiology
pub_type: 杂志文章,评审
doi:10.1007/s002470050165
更新日期:1997-05-01 00:00:00
abstract::Isolated oesophageal leiomyomatosis in children is very rare. The association between leiomyomatosis of oesophagus and female genital tract and an Alport like hematuric nephritis has been recognized as a distinct entity by Garcia-Torres and Guarner. Since then few other cases of this syndrome have been observed. Conge...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF02012602
更新日期:1991-01-01 00:00:00
abstract::One of the obstacles in discussing childhood tuberculosis (TB) is the lack of standard descriptive terminology to classify the diverse spectrum of disease. Accurate disease classification is important, because the correct identification of the specific disease entity has definite prognostic significance. Accurate clas...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-004-1238-0
更新日期:2004-11-01 00:00:00
abstract:BACKGROUND:Fluoroscopy is an important tool for diagnosis in the pediatric population, but it carries the risk of radiation exposure. Because radiology resident education and experience in the use of fluoroscopy equipment in children vary, we implemented an intervention to standardize fluoroscopy training. OBJECTIVE:T...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-014-3108-8
更新日期:2015-02-01 00:00:00
abstract::Pediatric radiologists in 40 children's hospitals in North America were interviewed to determine their choice of contrast media in the diagnosis and treatment of intussusception. The respondents indicated that barium was utilized in the vast majority of instances. Almost all indicated that they would proceed with bari...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF02467295
更新日期:1989-01-01 00:00:00
abstract::We present an unusual case of severe hydranencephaly in a term infant who presented with the following additional unique features, which were discovered on CT, MRI and MR angiography examinations: (1) occlusion of the bilateral posterior cerebral arteries, (2) absence of the occipital lobes, (3) an ovoid calcified mas...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-010-1894-1
更新日期:2011-02-01 00:00:00
abstract::We report an unusual case of a child with a congenital solitary functional kidney complicated by a sports-related posttraumatic Page kidney. The child developed severe hypertension and renal insufficiency requiring percutaneous intervention to preserve renal function. The literature is sparse with no definitive guidel...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-010-1630-x
更新日期:2010-11-01 00:00:00
abstract::Contrast-enhanced ultrasound (CEUS) and diffusion-weighted imaging (DWI) are safe, repeatable imaging techniques. The aim of this paper is to discuss the advantages, technical factors and possible clinical applications of these imaging tools in focal renal lesions in children. ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-019-04552-9
更新日期:2020-02-01 00:00:00
abstract:BACKGROUND:Emergent MRI is now a viable alternative to CT for evaluating appendicitis while avoiding the detrimental effects of ionizing radiation. However, primary employment of MRI in the setting of clinically suspected pediatric appendicitis has remained significantly underutilized. OBJECTIVE:To describe our instit...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-012-2412-4
更新日期:2012-09-01 00:00:00
abstract::Juvenile granulosa cell tumor of the testis is a distinct form of sex cord-stromal tumor of neonates and infants [1]. This tumor comprises a significant percentage of testicular tumors in baby boys. We present a patient who had preoperative imaging studies. ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF02012994
更新日期:1992-01-01 00:00:00
abstract::We report a case of a child with D-transposition of the great arteries treated with prostaglandin E1 (PGE1) who subsequently developed extensive brown fat necrosis. To the best of our knowledge, no previous association among congenital heart disease, PGE1, and brown fat necrosis has been reported. ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s002470050536
更新日期:1999-01-01 00:00:00
abstract::Imaging pediatric elbow trauma in the acute setting remains diagnostically challenging given difficult patient positioning, multiple ossification centers of the pediatric elbow, overlapping structures, and complex joint anatomy. Digital tomosynthesis is a technique where the X-ray source travels across a limited arc a...
journal_title:Pediatric radiology
pub_type: 杂志文章,评审
doi:10.1007/s00247-019-04444-y
更新日期:2019-11-01 00:00:00
abstract::Paternal uniparental disomy for chromosome 14 (patUPD14) is a rare condition, this being the eighth report. A male infant, born prematurely, was noted to have extremely lax skin and bilateral inguinal hernias. Skin biopsy confirmed the clinical diagnosis of congenital cutis laxa, but this did not explain the limb abno...
journal_title:Pediatric radiology
pub_type: 杂志文章,评审
doi:10.1007/s00247-003-0931-8
更新日期:2003-07-01 00:00:00
abstract::Venous drainage to the portal vein in pulmonary sequestration is rare. A 7-month-old girl was referred to our hospital following surgery for ventricular septal defect because of a left upper abdominal mass with a large feeding artery from the abdominal aorta and venous drainage to the portal vein. She had had frequent...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s002470000251
更新日期:2000-07-01 00:00:00
abstract::Hardcastle syndrome is a rare, autosomally dominant inherited skeletal dysplasia, characterized by diaphyseal sclerosis, medullary stenosis, pathological fractures, bony infarction, and malignant transformation. A 19-year-old proband is presented and discussed, adding a fourth family to the world literature. Radiograp...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF01356833
更新日期:1996-09-01 00:00:00
abstract::Recently, the state of California enacted a law requiring radiologists to record the radiation dose that each patient receives for a CT scan. Failure to do so is penalized by law. This law becomes effective in July 2012. By July 2013, every facility that performs CT scans must become accredited by one of three profess...
journal_title:Pediatric radiology
pub_type: 杂志文章,评审
doi:10.1007/s00247-011-2105-4
更新日期:2011-09-01 00:00:00
abstract:BACKGROUND:Reversed blood flow has been reported in the superior mesenteric artery (SMA) in 92% of healthy term newborns at 2 h of age. By 24 h after birth the end-diastolic velocity became positive in all of the infants. OBJECTIVE:To characterize hemodynamic changes in the coeliac artery and superior mesenteric arter...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-013-2825-8
更新日期:2014-03-01 00:00:00
abstract:BACKGROUND:Adrenocortical carcinoma (ACC), a tumor that is rare among children, causes clinically evident hormonal disturbances. Imaging methods are used to stage disease and to plan surgical resection. OBJECTIVE:To describe the findings of the various imaging methods used to evaluate ACC. MATERIALS AND METHODS:We re...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s002470050013
更新日期:2000-01-01 00:00:00
abstract:BACKGROUND:Pontine tumors carry the worst prognosis of all brain tumors. In most cases, the diagnosis is based solely on MR imaging, without biopsy. OBJECTIVE:To describe the MR findings of pontine tumors at diagnosis and during follow-up and correlate those with prognosis and to assess the value of MR imaging in pati...
journal_title:Pediatric radiology
pub_type: 杂志文章,评审
doi:10.1007/s00247-005-1502-y
更新日期:2005-09-01 00:00:00
abstract::A patient with the characteristic changes of Sturge-Weber syndrome on the right side was found to have a large arteriovenous malformation on the left side which involved the superior ophthalmic vein. This association, although previously reported, is extremely rare. ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF02015455
更新日期:1994-01-01 00:00:00
abstract:BACKGROUND:A new children's hospital provided the impetus to investigate radiation dose and image quality in a fluoroscope that was specially engineered for pediatric fluoroscopy. Radiation protection management recommends radiation exposures that are as low as reasonably achievable, while still maintaining diagnostic ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s002470050728
更新日期:2000-04-01 00:00:00
abstract::Hydranencephaly is an encephaloclastic central nervous system disorder characterised by severe destruction of the cerebral hemispheres with preservation of posterior fossa structures. We present MRI and neurosonography features of a unique case of hydranencephaly involving cerebellum (in the form of complete liquefact...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-010-1749-9
更新日期:2011-02-01 00:00:00
abstract::Two patients with different patterns of soft tissue and bone involvement demonstrate the variability of extracutaneous manifestations of juvenile xanthogranuloma, a non-X histiocytosis, better known to dermatologists than to radiologists. ...
journal_title:Pediatric radiology
pub_type: 杂志文章,评审
doi:10.1007/BF02016261
更新日期:1992-01-01 00:00:00
abstract::We report an atypical leiomyoma arising in an hepatic vein and extending into the inferior vena cava and right atrium in a fourteen year old boy. US, CT and MRI facilitated diagnosis and removal of this tumor. ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF02012978
更新日期:1990-01-01 00:00:00
abstract:BACKGROUND:Children are better served by radiologists and technical personnel trained in the care of pediatric patients. However, a variety of obstacles may limit the access of children to dedicated pediatric imaging facilities. OBJECTIVE:We designed and implemented two models for providing community-based imaging by ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s002470050003
更新日期:2000-01-01 00:00:00
abstract::With improvements in survival among individuals diagnosed and treated for cancer there is an increasing recognition of the risk of long-term adverse effects of therapy. Second neoplasms represent one of the more serious late effects of treatment and are associated with a substantial level of morbidity and mortality. S...
journal_title:Pediatric radiology
pub_type: 杂志文章,评审
doi:10.1007/s00247-008-1066-8
更新日期:2009-02-01 00:00:00