Acute hypoxic respiratory failure as the first manifestation of systemic-onset juvenile rheumatoid arthritis in a child.

Abstract:

:Systemic onset juvenile rheumatoid arthritis is the most common rheumatologic disorder of childhood. Pleuropulmonary manifestations are rare in children in this multiorgan disease, and are usually not severe. The diagnosis of systemic onset juvenile rheumatoid arthritis is made by exclusion, in the presence of clinical findings constellation. We present the case of an 8-year-old girl who developed acute hypoxic respiratory failure as the first manifestation of systemic onset juvenile rheumatoid arthritis, then severe respiratory relapse 16 months later. Clinical and radiological improvement were achieved at both times after high dose pulse methylprednisolone therapy.

journal_name

Pediatr Pulmonol

journal_title

Pediatric pulmonology

authors

Rochat I,Sayegh Y,Gervaix A,Rimensberger PC,Argiroffo CB

doi

10.1002/ppul.20107

subject

Has Abstract

pub_date

2004-12-01 00:00:00

pages

483-7

issue

6

eissn

8755-6863

issn

1099-0496

journal_volume

38

pub_type

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