Lung function in hyper IgE syndrome.

Abstract:

:Pneumatoceles and bronchiectasis are secondary complications of respiratory infections in patients with hyper IgE syndrome (HIgES). We report on a patient with HIgES and recurrent pneumonias since 1 year of age, with progression to pneumatoceles and bronchiectasis and fatal outcome, with disseminated infection and suspected allergic bronchopulmonary aspergillosis, who was subjected to sequential spirometric assessment. We describe the early beginning of respiratory infections, difficulties in the management of pulmonary sequelae and the impact of an early functional diagnosis and follow-up of the patient regarding a disease for which lung function has not been fully described.

journal_name

Pediatr Pulmonol

journal_title

Pediatric pulmonology

authors

Roxo P Jr,Torres LA,Menezes UP,Melo JM

doi

10.1002/ppul.22532

subject

Has Abstract

pub_date

2013-01-01 00:00:00

pages

81-4

issue

1

eissn

8755-6863

issn

1099-0496

journal_volume

48

pub_type

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