Computed tomography (CT) in late infantile metachromatic leucodystrophy.

Abstract:

:Computed tomographic features of 7 cases of the late infantile form of MLD confirmed by sural nerve biopsy are presented. Diffuse symmetrical white matter, low attenuation of the cerebral parenchyma was the common feature. Hypodensity of the temporal lobes and the cerebellar hemispheres are 2 features which have not been reported earlier. Three patients had brainstem atrophy without evidence of cerebral atrophy. Awareness of the various CT features of MLD may help in more definitive radiological diagnosis of the disease and to differentiate it from other dysmyelinating diseases of the central nervous system.

journal_name

Acta Neurol Scand

authors

Jayakumar PN,Aroor SR,Jha RK,Arya BY

doi

10.1111/j.1600-0404.1989.tb03704.x

subject

Has Abstract

pub_date

1989-01-01 00:00:00

pages

23-6

issue

1

eissn

0001-6314

issn

1600-0404

journal_volume

79

pub_type

杂志文章
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