Two different mechanisms for omission and substitution errors in neglect dyslexia.

abstract：:Primary progressive apraxia of speech (PPAOS) is a neurodegenerative disorder in which AOS is the sole presenting complaint. We report clinical and neuroimaging data spanning 10 years from disease onset-to-death in a 49 year-old male PPAOS patient, DY, who died with corticobasal degeneration. He presented with AOS wit...

journal_title：Neurocase

authors： Tetzloff KA,Duffy JR,Strand EA,Machulda MM,Boland SM,Utianski RL,Botha H,Senjem ML,Schwarz CG,Josephs KA,Whitwell JL

更新日期：2018-04-01 00:00:00

abstract：:Oculocutaneous albinism (OCA) is a group of autosomal recessive disorders characterized by impairment in the melanin synthesis. We report two siblings with OCA who presented with symptoms of autism spectrum disorder and attention deficit hyperactivity disorder (ADHD). Ocular side effects occured after methylphenidate ...

journal_title：Neurocase

authors： Ünsel Bolat G

更新日期：2020-12-01 00:00:00

abstract：:The psychoses of epilepsy are well recognized complications of seizure disorders, diagnosed easily from the history. However, in the absence of recognized seizures, the diagnosis can be challenging. We present a 27-year-old female, who suffered a treatment refractory psychosis for 6 years. She did not report, or dis...

journal_title：Neurocase

authors： Needham E,Hamelijnck J

更新日期：2012-01-01 00:00:00

abstract：:Neurophysiological and functional brain imaging studies suggest the importance of dorsolateral area 9/46 for modality-independent working memory. However, the behavioural manifestations following isolated damage to this area have not been clearly outlined. Here, we describe the dramatic derangement of pragmatic memory...

journal_title：Neurocase

authors： Ptak R,Schnider A

更新日期：2004-02-01 00:00:00

abstract：:After a stroke involving the left occipitotemporal cortex our patient shows a word-length effect and has problems to identify letters or numbers in strings of symbols. But he is normal in identifying isolated letters and in non-verbally categorizing even complex images such as faces or natural scenes. His cortical les...

journal_title：Neurocase

authors： Spang KM,Grimsen C,Brunner F,Fahle MW

更新日期：2019-10-01 00:00:00

abstract：:A 62-year-old male presented with progressive isolated writing and spelling difficulties. Neurological, neuropsychological, speech, and language evaluations identified only minimal additional abnormalities. The presenting characteristics did not meet criteria for any particular variant of primary progressive aphasia; ...

journal_title：Neurocase

authors： Utianski RL,Duffy JR,Savica R,Whitwell JL,Machulda MM,Josephs KA

更新日期：2018-04-01 00:00:00

abstract：:A current debate in the literature is whether all declarative memories and associated memory processes rely on the same neural substrate. Here, we show that H.C., a developmental amnesic person with selective bilateral hippocampal volume loss, has a mild deficit in personal episodic memory, and a more pronounced defic...

journal_title：Neurocase

authors： Rosenbaum RS,Carson N,Abraham N,Bowles B,Kwan D,Köhler S,Svoboda E,Levine B,Richards B

更新日期：2011-10-01 00:00:00

abstract：:To further understand the nature of the visual-spatial representations required for successful acquisition of written language skills, we investigated the written language abilities of two individuals with Williams syndrome (WS) a developmental genetic disorder in which the presence of severe visual-spatial developmen...

journal_title：Neurocase

authors： Dessalegn B,Landau B,Rapp B

更新日期：2013-08-01 00:00:00

abstract：:Vagus Nerve Stimulation (VNS) is approved by the FDA for treatment of both epilepsy and depression. Recent work has shown that VNS acutely affects pain perception in humans, actually increasing pain sensitivity momentarily while the device is firing. It is unclear how this acutely increased sensitivity might change ov...

journal_title：Neurocase

authors： Borckardt JJ,Anderson B,Andrew Kozel F,Nahas Z,Richard Smith A,Jackson Thomas K,Kose S,George MS

更新日期：2006-08-01 00:00:00

abstract：:Neurodegenerative diseases are caused by aggregation of specific proteins that catalyze a cascade of changes that ultimately lead to neurodegeneration. This concept guides current diagnostic approaches, as well as clinical trials, that focus on detecting or removing amyloid or tau from the brain. The semantic variant ...

journal_title：Neurocase

authors： Caplan A,Marx G,Elofson J,Lis C,Grinberg L,Miller B,Rosen H

更新日期：2018-04-01 00:00:00

abstract：:A striking special ability in arranging picture stories was reported in an Asperger child (C.M.) showing an exceptional performance on Wechsler picture arrangement subtest. Neuropsychological examination did not disclose visuoperceptual and spatial defects, or working memory, attention and executive disorders, but rev...

journal_title：Neurocase

authors： Conson M,Salzano S,Grossi D

更新日期：2011-08-01 00:00:00

abstract：:Vocal emblems, such as shh and brr, are speech sounds that have linguistic and nonlinguistic features; thus, it is unclear how they are processed in the brain. Five adult dextral individuals with left-brain damage and moderate-severe Wernicke's aphasia, five adult dextral individuals with right-brain damage, and five ...

journal_title：Neurocase

authors： Neumann-Werth Y,Levy ES,Obler LK

更新日期：2013-01-01 00:00:00

abstract：:Metamemory is a multifaceted concept, which deals with an individual's knowledge and control of his or her own memory system. The ability to monitor memory performance accurately was examined in 16 patients with Alzheimer's disease (AD), 6 patients with frontotemporal lobe dementia (FTD) and 16 elderly subjects. Parti...

journal_title：Neurocase

authors： Souchay C,Isingrini M,Pillon B,Gil R

更新日期：2003-12-01 00:00:00

abstract：:Physical symptoms of myoclonus dystonia due to epsilon-sarcoglycan mutations are well documented; however, the progression of neuropsychiatric and cognitive symptoms remains unclear. We present a case of a 34-year-old woman with early childhood onset of myoclonic jerks, dystonic posture and developmental delay due to ...

journal_title：Neurocase

authors： Multani N,Moro E,Lang A,Zurowski M,Duff Canning S,Tartaglia MC

更新日期：2016-01-01 00:00:00

abstract：:Subject PI demonstrated superior memory using a variant of a Method of Loci (MOL) technique to recite the first digits of the mathematical constant pi to more than 2(16) decimal places. We report preliminary behavioral, functional magnetic resonance imaging (fMRI), and brain volumetric data from PI. fMRI data collecte...

journal_title：Neurocase

authors： Raz A,Packard MG,Alexander GM,Buhle JT,Zhu H,Yu S,Peterson BS

更新日期：2009-10-01 00:00:00

abstract：:The concreteness effect occurs in both normal and language-disordered populations. Research suggests that abstract and concrete concepts elicit differing neural activation patterns in healthy young adults, but this is undocumented in persons with aphasia (PWA). Three PWA and three age-matched controls were scanned usi...

journal_title：Neurocase

authors： Sandberg C,Kiran S

更新日期：2014-08-01 00:00:00

abstract：:Monocular patching might improve perceptual-attentional, not motor-intentional deficits in a patient with chronic post-stroke left spatial neglect. Performing a line-cancellation task, his omission errors were associated with a perceptual-attentional 'where' deficit, while perseverative errors were associated with 'ai...

journal_title：Neurocase

authors： Khurshid S,Longin H,Crucian GP,Barrett AM

更新日期：2009-08-01 00:00:00

abstract：:This paper reports the case of a patient, M.P., who developed delusion of inanimate doubles, without Capgras syndrome, after traumatic brain injury. His delusional symptoms were studied longitudinally and the cognitive impairments associated with delusion were investigated. Data suggest that M.P. did 'perceive' the ac...

journal_title：Neurocase

authors： Abbate C,Trimarchi PD,Salvi GP,Quarenghi AM,Vergani C,Luzzatti C

更新日期：2012-01-01 00:00:00

abstract：:We hypothesized that distinct acute right hemisphere lesions disrupt separate components of valuation and emotional response to winning and losing money and of emotional empathy in observing a partner win or lose money. We measured skin conductance response (SCR) and ratings of emotions when acute right hemisphere str...

journal_title：Neurocase

authors： Kim EH,Chien JH,Liu CC,Oishi K,Oishi K,Sebastian R,Demsky C,Lenz F,Hillis AE

更新日期：2017-02-01 00:00:00

abstract：:Recent research revealed decreased access to semantic and associative networks in acute cocaine withdrawal. In autism, such behavioral outcomes are associated with decreased functional connectivity using functional magnetic resonance imaging. Therefore, we wished to determine whether connectivity is also decreased in ...

journal_title：Neurocase

authors： Narayanan A,White CA,Saklayen SS,Abduljalil A,Schmalbrock P,Pepper TH,Lander BN,Beversdorf DQ

更新日期：2012-01-01 00:00:00

abstract：:Chediak-Higashi syndrome (CHS) is a rare autosomal disorder characterized by immunodeficiency, albinism, and progressive neurologic abnormalities. While survivors of the childhood-onset disease are known to exhibit learning disabilities and neuropsychiatric disorders followed by middle-age dementia, we lack detailed d...

journal_title：Neurocase

authors： Yliranta A,Mäkinen J

更新日期：2020-12-09 00:00:00

abstract：:In this paper, we adopt a neurodevelopmental stance to examining frontal variant frontotemporal dementia (fv-FTD) by using experimental procedures from the literature on the growth of social behaviour in children to examine the deficits in social reasoning which may underpin behavioural disturbance in fv-FTD. We prese...

journal_title：Neurocase

authors： Lough S,Gregory C,Hodges JR

更新日期：2001-01-01 00:00:00

abstract：:Expanding our knowledge of the history of dementia may be beneficial for its holistic understanding. This article aims to review the trajectory of the concepts of dementia in the world and Japan. Historical backgrounds of major dementia diseases are also addressed. The first reference to "imbecility" appeared in Greec...

journal_title：Neurocase

authors： Fukui T

更新日期：2015-01-01 00:00:00

abstract：:In large early cortical lesions, one of the most devastating consequences is the impaired motor dexterity of the contralateral limb. We present the case of an 8-year-old girl with a large left hemispherical porencephaly. Unlike previous reports, the girl exhibited high dexterity of the contralateral hand with preserve...

journal_title：Neurocase

authors： Weber B,Fliessbach K,Elger CE

更新日期：2006-10-01 00:00:00

abstract：:BVR was 77 years old when he sustained a large posterior cerebral artery territory infarct. Medical, cognitive and functional data collected on four occasions over 10 years initially revealed circumscribed neurological signs, no functional or cognitive deficits. BVR became significantly impaired only after two other s...

journal_title：Neurocase

authors： Piguet O,Bennett HP,Waite LM,Kril JJ,Creasey H,Anthony Broe G,Halliday GM

更新日期：2006-04-01 00:00:00

abstract：:In this paper we report the results of a longitudinal study which examined memory for a single routine activity of daily living in people with dementia of the Alzheimer type. We assessed memory in a natural setting, visiting volunteers in their homes. We video-taped performance on the selected task and analysed the re...

journal_title：Neurocase

authors： Rusted J,Sheppard L

更新日期：2002-01-01 00:00:00

abstract：:Opsoclonus myoclonus ataxia (OMA) is a rare neurological disorder (incidence = approximately 1/5 million) primarily associated with involuntary conjugate saccadic eye movements, involuntary muscle jerks, cerebellar ataxia, and neuropsychological impairments. Unfortunately, there is limited published data regarding the...

journal_title：Neurocase

authors： Smith ML,Thawani N,Johnstone B,Stucky R

更新日期：2010-08-01 00:00:00

abstract：:A hexanucleotide repeat expansion in the chromosome 9 open reading frame 72 (C9ORF72) gene was recently discovered as the cause underlying frontotemporal degeneration (FTD) and/or amyotrophic lateral sclerosis (ALS) linked to chromosome 9 (c9FTD/ALS). In this atypical case of c9FTD/ALS, the proband presented with amne...

journal_title：Neurocase

authors： Adeli A,Savica R,Lowe VJ,Vemuri P,Knopman DS,Dejesus-Hernandez M,Rademakers R,Fields JA,Crum BA,Jack CR,Petersen RC,Boeve BF

更新日期：2014-01-01 00:00:00

abstract：:Regressive behavior is a known sequela after severe traumatic brain injury (TBI). However, prolonged "infantile-like" behavior has received little attention in the literature, suggesting that this is a rare phenomenon. It is typically characterized by long-lasting childish, extremely dependent, and sometimes aggressiv...

journal_title：Neurocase

authors： Heled E,Sverdlik A,Agranov E

更新日期：2014-01-01 00:00:00

abstract：:An investigation of non-verbal auditory comprehension in two patients with global aphasia following stroke is reported. The primary aim of the investigation was to establish whether refractory access disorders can affect non-verbal input modalities. All previous reports of refractoriness, a cognitive syndrome characte...

journal_title：Neurocase

authors： Crutch SJ,Warrington EK

更新日期：2008-01-01 00:00:00