Abstract:
:Opsoclonus myoclonus ataxia (OMA) is a rare neurological disorder (incidence = approximately 1/5 million) primarily associated with involuntary conjugate saccadic eye movements, involuntary muscle jerks, cerebellar ataxia, and neuropsychological impairments. Unfortunately, there is limited published data regarding the nature and course of neuropsychological impairments following OMA diagnosis and treatment. This study presents neuropsychological data obtained at 1, 4, and 18 months post-diagnosis of a 52-year-old male with OMA. The patient initially demonstrated significant global neurocognitive, psychomotor, and psychological difficulties with substantial improvement over time. Treatment included medication management, physical rehabilitation, and psychological intervention.
journal_name
Neurocasejournal_title
Neurocaseauthors
Smith ML,Thawani N,Johnstone B,Stucky Rdoi
10.1080/13554791003620264subject
Has Abstractpub_date
2010-08-01 00:00:00pages
352-7issue
4eissn
1355-4794issn
1465-3656pii
921942838journal_volume
16pub_type
杂志文章相关文献
NEUROCASE文献大全abstract::Oculocutaneous albinism (OCA) is a group of autosomal recessive disorders characterized by impairment in the melanin synthesis. We report two siblings with OCA who presented with symptoms of autism spectrum disorder and attention deficit hyperactivity disorder (ADHD). Ocular side effects occured after methylphenidate ...
journal_title:Neurocase
pub_type: 杂志文章
doi:10.1080/13554794.2020.1853174
更新日期:2020-12-01 00:00:00
abstract::We summarize two case studies as a context for discussing the use of neuroimaging as a convergent methodology in the study of neuroplasticity in single subjects. Throughout this paper we argue for a different approach for including neuroimaging in these types of study. Previous case studies of neuroplasticity in patie...
journal_title:Neurocase
pub_type: 杂志文章
doi:10.1076/neur.8.4.355.16187
更新日期:2002-01-01 00:00:00
abstract::A case report is presented detailing the successful use of awake intraoperative memory testing while using white matter stimulation in order to isolate the fornix tracks involved in memory function. The identification of the white matter tracks of the fornix that were involved in memory function was used to tailor the...
journal_title:Neurocase
pub_type: 杂志文章
doi:10.1080/13554794.2010.547509
更新日期:2012-02-01 00:00:00
abstract::Synaesthesia is often triggered by numbers, although it is conceivable that different aspects of numerical representation are responsible for different variants of synaesthesia. For individuals with "higher synaesthesia" it is assumed that number meaning (or numerosity) is responsible for the elicitation of synaesthet...
journal_title:Neurocase
pub_type: 杂志文章
doi:10.1080/13554790701300518
更新日期:2007-04-01 00:00:00
abstract::Prior research on developmental dyslexia using Stroop tasks with young participants has found increased interference in participants with dyslexia relative to controls. Here we extend these findings to adult participants, and introduce a novel test of Stroop incongruity, whereby the color names appeared on an object c...
journal_title:Neurocase
pub_type: 杂志文章
doi:10.1080/13554794.2014.914544
更新日期:2015-01-01 00:00:00
abstract::It is a common finding in tests of false recognition that amnesic patients recognize fewer related lures than healthy controls, and this has led to assumptions that gist memory is damaged in these patients (Schacter, Verfaellie, & Anes, 1997, Neuropsychology, 11; Schacter, Verfaellie, Anes, & Racine, 1998, Journal of ...
journal_title:Neurocase
pub_type: 杂志文章
doi:10.1080/13554794.2012.701637
更新日期:2013-01-01 00:00:00
abstract::The amygdala nuclei appear to be critically implicated in emotional memory. However, in most studies, encoding and consolidation processes cannot be analyzed separately. We thus studied the verbal emotional memory in a young woman with a ganglioglioma of the left amygdala and analyzed its impact (1) on each step of th...
journal_title:Neurocase
pub_type: 杂志文章
doi:10.1080/13554794.2015.1037843
更新日期:2016-01-01 00:00:00
abstract::A 75 year-old man had a two-year history of progressive memory loss, trouble with finances and getting lost. On examination, he scored 16/30 in MoCA test, noticeably impaired on the attentional tasks. His screening bloodtests werenormal. Brain imaging revealed hippocampal atrophy and bilaterallarge areas of leukoaraio...
journal_title:Neurocase
pub_type: 杂志文章
doi:10.1080/13554794.2020.1769138
更新日期:2020-08-01 00:00:00
abstract::Recent research revealed decreased access to semantic and associative networks in acute cocaine withdrawal. In autism, such behavioral outcomes are associated with decreased functional connectivity using functional magnetic resonance imaging. Therefore, we wished to determine whether connectivity is also decreased in ...
journal_title:Neurocase
pub_type: 杂志文章
doi:10.1080/13554794.2011.627341
更新日期:2012-01-01 00:00:00
abstract::Cerebral lesions are held to induce plastic changes of the brain. Less well established, however, is how much space-occupying brain lesions may only displace functional representations. In a 66-year-old man we show, by means of functional magnetic resonance imaging and transcranial magnetic stimulation, a profound dis...
journal_title:Neurocase
pub_type: 杂志文章
doi:10.1080/13554790701849910
更新日期:2007-10-01 00:00:00
abstract::Vocal emblems, such as shh and brr, are speech sounds that have linguistic and nonlinguistic features; thus, it is unclear how they are processed in the brain. Five adult dextral individuals with left-brain damage and moderate-severe Wernicke's aphasia, five adult dextral individuals with right-brain damage, and five ...
journal_title:Neurocase
pub_type: 杂志文章
doi:10.1080/13554794.2012.667122
更新日期:2013-01-01 00:00:00
abstract::Confabulation may be present in Alzheimer's disease (AD), but usually it is not a primary feature of either its typical or atypical variants. In this report, we describe the case of an AD patient who showed an unusual and enduring neuropsychiatric phenotype characterized by early and prominent spontaneous confabulatio...
journal_title:Neurocase
pub_type: 杂志文章
doi:10.1080/13554794.2016.1239743
更新日期:2016-10-01 00:00:00
abstract::A 62-year-old male presented with progressive isolated writing and spelling difficulties. Neurological, neuropsychological, speech, and language evaluations identified only minimal additional abnormalities. The presenting characteristics did not meet criteria for any particular variant of primary progressive aphasia; ...
journal_title:Neurocase
pub_type: 杂志文章
doi:10.1080/13554794.2018.1454963
更新日期:2018-04-01 00:00:00
abstract::Short melodies are commonly linked to referents in jingles, ringtones, movie themes, and even auditory displays (i.e., sounds used in human-computer interactions). While melody associations can be quite effective, auditory alarms in medical devices are generally poorly learned and highly confused. Here, we draw on app...
journal_title:Neurocase
pub_type: 杂志文章
doi:10.1080/13554794.2016.1253751
更新日期:2016-12-01 00:00:00
abstract::Studies of patients with brain lesions have demonstrated that language and praxis are mediated by dissociable networks. However, language has the capacity to influence the selection of purposeful actions. The abilities to use language and to program purposeful movements are often mediated by networks that have anatomi...
journal_title:Neurocase
pub_type: 杂志文章
doi:10.1080/13554794.2013.770883
更新日期:2014-06-01 00:00:00
abstract::Patients with memory disorders have severely restricted learning and memory. For instance, patients with anterograde amnesia can learn motor procedures and retain some restricted ability to learn new words and factual information. However, such learning is inflexible and frequently inaccessible to conscious awareness....
journal_title:Neurocase
pub_type: 杂志文章
doi:10.1080/13554790903405701
更新日期:2010-06-01 00:00:00
abstract::The purpose of this study was to determine if differential reading and spelling mechanisms were involved in a Japanese patient with aphasia. In our case, the patient scored low on all of the administered reading tasks, suggesting that both the reading lexical and non-lexical routes were impaired. In contrast, his writ...
journal_title:Neurocase
pub_type: 杂志文章
doi:10.1080/13554794.2015.1137950
更新日期:2016-06-01 00:00:00
abstract::The impact of epileptiform activity on the functional organization of various cortical regions is currently a widely discussed topic. Our patient, suffering from left-sided temporal lobe epilepsy with typical mesiotemporal sclerosis, had a remarkable history of a clear-cut handedness shift in early childhood. In this ...
journal_title:Neurocase
pub_type: 杂志文章
doi:10.1080/13554790490507669
更新日期:2004-08-01 00:00:00
abstract::Primary progressive apraxia of speech (PPAOS) is a neurodegenerative disorder in which AOS is the sole presenting complaint. We report clinical and neuroimaging data spanning 10 years from disease onset-to-death in a 49 year-old male PPAOS patient, DY, who died with corticobasal degeneration. He presented with AOS wit...
journal_title:Neurocase
pub_type: 杂志文章
doi:10.1080/13554794.2018.1477963
更新日期:2018-04-01 00:00:00
abstract::This article describes an investigation into the residual writing skills of a severely dysgraphic patient (DA). We found that they were powerfully influenced by a number of lexical variables (lexicality, frequency, imageability, length and geminates). His error pattern was characterized by semantic, lexical, substitut...
journal_title:Neurocase
pub_type: 杂志文章
doi:10.1080/13554790490893995
更新日期:2004-12-01 00:00:00
abstract::An adult female complained of enlargement of right eyes in other people. Diffusion-weighted imaging detected an abnormal high-intensity area in the region from the splenium of the corpus callosum to the major forceps on the right side. The patient reported that right eyes appeared larger in size, which suggested proso...
journal_title:Neurocase
pub_type: 杂志文章
doi:10.1080/13554794.2020.1797819
更新日期:2020-10-01 00:00:00
abstract::According to Liepmann, patients with limb-kinetic apraxia (LKA) have a loss of upper limb deftness-dexterity. Prior studies have revealed in right-handed patients that, whereas injury of the left hemisphere induces an ipsilesional LKA, injury to the right hemisphere does not induce an ipsilesional LKA. There are at le...
journal_title:Neurocase
pub_type: 杂志文章
doi:10.1080/13554794.2013.826683
更新日期:2014-01-01 00:00:00
abstract::We report the case of a 71 year-old female patient (DC) with a left parietal lesion resulting in a peripheral dysgraphia essentially characterized by difficulties in letter sequences writing. The aim of our experiments was to analyze the influence of motor difficulties on the visual perception of both writing and reac...
journal_title:Neurocase
pub_type: 杂志文章
doi:10.1080/13554790490495113
更新日期:2004-06-01 00:00:00
abstract::Frontotemporal lobar degeneration with ubiquitin-positive inclusions (FTLD-U) is one of the most common pathological findings associated with the clinical FTLD syndromes. However, molecular characterization with genetic sequencing and protein expression techniques are recognizing many new subtypes for FTLDs. FTLDs are...
journal_title:Neurocase
pub_type: 杂志文章
doi:10.1080/13554794.2011.654217
更新日期:2013-01-01 00:00:00
abstract::After a stroke involving the left occipitotemporal cortex our patient shows a word-length effect and has problems to identify letters or numbers in strings of symbols. But he is normal in identifying isolated letters and in non-verbally categorizing even complex images such as faces or natural scenes. His cortical les...
journal_title:Neurocase
pub_type: 杂志文章
doi:10.1080/13554794.2019.1634739
更新日期:2019-10-01 00:00:00
abstract::Debates about the role of language in human thinking are increasingly prominent in the cognitive sciences. There are claims that certain forms of reasoning can only be performed through access to the resources of the language faculty. In particular, a component of social cognition involving the representation of the m...
journal_title:Neurocase
pub_type: 杂志文章
doi:10.1093/neucas/7.6.489
更新日期:2001-01-01 00:00:00
abstract::Central pontine and extrapontine myelinolysis (CPEM) is a rare neurological condition usually due to rapid correction of hyponatremia. CPEM is mainly characterized by motor deficits (typically quadraparesis or extrapyramidal features) but neurobehavioral symptoms were also reported in the literature. However, very few...
journal_title:Neurocase
pub_type: 杂志文章
doi:10.1080/13554794.2011.633528
更新日期:2012-01-01 00:00:00
abstract::We investigated the neural systems that support number processing in a patient (JL) who had damage to the left ventral occipito-temporal cortex (LvOT). JL had severely impaired written word recognition but he was remarkably accurate in number tasks, albeit slower than normal. This suggests LvOT activation is necessary...
journal_title:Neurocase
pub_type: 杂志文章
doi:10.1080/13554794.2011.588179
更新日期:2012-01-01 00:00:00
abstract::Monocular patching might improve perceptual-attentional, not motor-intentional deficits in a patient with chronic post-stroke left spatial neglect. Performing a line-cancellation task, his omission errors were associated with a perceptual-attentional 'where' deficit, while perseverative errors were associated with 'ai...
journal_title:Neurocase
pub_type: 杂志文章
doi:10.1080/13554790902776888
更新日期:2009-08-01 00:00:00
abstract::A current debate in the literature is whether all declarative memories and associated memory processes rely on the same neural substrate. Here, we show that H.C., a developmental amnesic person with selective bilateral hippocampal volume loss, has a mild deficit in personal episodic memory, and a more pronounced defic...
journal_title:Neurocase
pub_type: 杂志文章
doi:10.1080/13554794.2010.532138
更新日期:2011-10-01 00:00:00