Neuropsychological decline/improvement in opsoclonus myoclonus ataxia.

Abstract:

:Opsoclonus myoclonus ataxia (OMA) is a rare neurological disorder (incidence = approximately 1/5 million) primarily associated with involuntary conjugate saccadic eye movements, involuntary muscle jerks, cerebellar ataxia, and neuropsychological impairments. Unfortunately, there is limited published data regarding the nature and course of neuropsychological impairments following OMA diagnosis and treatment. This study presents neuropsychological data obtained at 1, 4, and 18 months post-diagnosis of a 52-year-old male with OMA. The patient initially demonstrated significant global neurocognitive, psychomotor, and psychological difficulties with substantial improvement over time. Treatment included medication management, physical rehabilitation, and psychological intervention.

journal_name

Neurocase

journal_title

Neurocase

authors

Smith ML,Thawani N,Johnstone B,Stucky R

doi

10.1080/13554791003620264

subject

Has Abstract

pub_date

2010-08-01 00:00:00

pages

352-7

issue

4

eissn

1355-4794

issn

1465-3656

pii

921942838

journal_volume

16

pub_type

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