Abstract:
:We report a rare case of tetralogy of Fallot with total anomalous pulmonary venous return, left heart hypoplasia, right lung hypoplasia, and left ocular-mandibular synchinesia (Marcus-Gunn phenomenon), correctly diagnosed by cardiovascular magnetic resonance imaging and successfully operated by modified Glenn anastomosis.
journal_name
Pediatr Cardioljournal_title
Pediatric cardiologyauthors
Festa P,Lamia AA,Murzi B,Bini MRdoi
10.1007/s00246-004-0769-3subject
Has Abstractpub_date
2005-07-01 00:00:00pages
467-9issue
4eissn
0172-0643issn
1432-1971journal_volume
26pub_type
杂志文章abstract::The primary objective was to create a clinically relevant model of right ventricular hypertension and to study right ventricular myocardial pathophysiology in growing organism. The secondary objective was to analyse the effect of oral enoximone (phosphodiesterase inhibitor) therapy on right ventricular haemodynamic pa...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-016-1463-y
更新日期:2016-12-01 00:00:00
abstract::Killian-Pallister syndrome is a rare dysmorphic condition characterized by specific clinical manifestations and tetrasomy 12p. Although the association of this condition with congenital heart disease has been previously documented, no cases have been reported in association with Fallot's tetralogy. We report one such ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002469900420
更新日期:1999-03-01 00:00:00
abstract::Aortopulmonary window is a relatively uncommon congenital heart defect. We report on a patient with a small aortopulmonary window, who presented with an asymptomatic murmur and in whom catheter closure was successfully performed with an Amplatzer Duct Occluder. ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-002-0307-0
更新日期:2003-05-01 00:00:00
abstract::A 10-month-old boy was referred for tachypnea and heart murmur. An echocardiogram showed unexplained left heart dilation without evidence of an intracardiac shunt. A 64-slice computed tomographic contrast-enhanced angiography showed a large tortuous anomalous artery arising from the descending thoracic aorta and suppl...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-008-9287-z
更新日期:2009-01-01 00:00:00
abstract::Serum troponin (Tn) is often elevated in viral myocarditis; however, its prognostic significance is unknown. We tested the hypothesis that abnormal serum Tn is associated with mortality in children hospitalized with myocarditis. We retrospectively studied data from six large children's hospitals participating in the P...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-018-1871-2
更新日期:2018-08-01 00:00:00
abstract::Fetal echocardiography has impacted the fetus with congenital heart disease in many important ways. Advances in fetal echocardiography have allowed for more accurate and earlier detection of cardiac abnormalities. In turn, the prenatal diagnosis of cardiac abnormalities has improved the care and outcome of selected fe...
journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
doi:10.1007/s00246-003-0593-1
更新日期:2004-05-01 00:00:00
abstract::The effect of patent ductus arteriosus (PDA) treatment with cyclooxygenase (COX) inhibitors (indomethacin [INDO] and ibuprofen [IBU]) on regional oxygenation requires further clarification. The authors hypothesized that both INDO and IBU reduce regional tissue oxygenation in preterm neonates with PDA but that the risk...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0309-5
更新日期:2012-12-01 00:00:00
abstract::B-type natriuretic peptide (BNP) reflects volume overload on left ventricle and pulmonary hypertension (PH) in patients with ventricular septal defect (VSD). Pulmonary vascular resistance (PVR) has been reported to correlate positively with BNP in VSD patients with various degrees of PH. We aimed to investigate the re...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-007-9037-7
更新日期:2008-01-01 00:00:00
abstract::This review examines the mechanism of estrogen signaling in cardiomyocytes, with an emphasis on mechanisms that might be important in cardioprotection. It investigates estrogen signaling mediated by the nuclear estrogen receptors alpha and beta and the G-protein-coupled receptor (GPR 30/GPER). Estrogen signaling via n...
journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
doi:10.1007/s00246-010-9877-4
更新日期:2011-03-01 00:00:00
abstract::The reported prenatal detection rates (PDRs) for significant congenital heart disease (sCHD) have been suboptimal, even in the current era. Changes in prenatal ultrasound policy and training may lead to improved prenatal detection of sCHD. This study analyzed the results of a policy to assess fetal cardiac outflow tra...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0526-y
更新日期:2013-03-01 00:00:00
abstract::Three patients (ages 3, 5, and 8 years) with various forms of functionally univentricular heart lesions received a total cavopulmonary connection with an extracardiac conduit as a final reconstructive procedure. Failure of the Fontan circulation occurred immediately after surgery because of spontaneous closure of surg...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-004-0693-6
更新日期:2005-01-01 00:00:00
abstract::Conotruncal cardiac defects are partially prevented by maternal folic acid supplementation. However, the biochemical mechanism is unknown. Maternal autoantibodies to folate receptors, previously associated with increased risk for neural tube defects, also may account for this effect. This study aimed to examine the ti...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0485-3
更新日期:2013-03-01 00:00:00
abstract::Cardiac surgery for congenital heart disease often necessitates a period of myocardial ischemia during cardiopulmonary bypass and cardioplegic arrest, followed by reperfusion after aortic cross-clamp removal. In experimental models, myocardial ischemia-reperfusion is associated with significant oxidative stress and ve...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-016-1345-3
更新日期:2016-04-01 00:00:00
abstract::It is documented that exercise can increase serum cardiac troponins in adults and adolescents; however, there is a lack of related studies concerning the release of cardiac troponins in children. This study investigated the influence of table tennis training on cardiac biomarkers in children. Twenty-eight male childre...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-013-0842-x
更新日期:2014-04-01 00:00:00
abstract::Right-ventricular diverticula (RVD), although rare, have particular characteristics. Our study describes the morphology of anterosuperior diverticula of the right ventricle (RV) and patient outcome for this anomaly. Retrospective analysis was performed on all patients with anterosuperior RVD diagnosed in two tertiary ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-014-0885-7
更新日期:2014-08-01 00:00:00
abstract::Anomalous origin of left coronary artery (LCA) from the right coronary cusp with an intramural course is usually managed with unroofing of the intramural segment. Available literature demonstrates an uneventful course following surgery in most patients. Coronary stenosis following the unroofing procedure treated with ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-018-2005-6
更新日期:2019-01-01 00:00:00
abstract::Echocardiography has previously been of limited use in visualizing the aorta in neonates and infants. Using a new technique--right parasternal scanning--the aortic arch and brachiocephalic vessels were studied in 50 children under 18 months of age. Complete visualization was accomplished in 47 patients including those...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02426973
更新日期:1982-01-01 00:00:00
abstract::Fetal atrioventricular dissociation is a dysrhythmia associated with significant antenatal and postnatal morbidity and mortality. We present a case of a 19-week-old fetus with atrioventricular dissociation, which spontaneously resolved. The mother had no signs of autoimmune disease. The fetus had an uneventful gestati...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002469900366
更新日期:1998-11-01 00:00:00
abstract::A primary rhabdomyosarcoma of the heart observed in a 3-week-old infant, provides an opportunity to review this rare clinical entity; 61 reported cases are collated. The more common sites are right ventricle, left atrium, and right atrium; the tumour may protrude into the cavity and cause obstruction. Echocardiography...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02265621
更新日期:1982-01-01 00:00:00
abstract::Increasingly the importance of how and why we make decisions in the medical arena has been questioned. Traditionally the aeronautical and business worlds have shed a light on this complex area of human decision-making. In this review we reflect on what we already know about the complexity of decision-making in additio...
journal_title:Pediatric cardiology
pub_type: 杂志文章,评审
doi:10.1007/s00246-020-02295-1
更新日期:2020-03-01 00:00:00
abstract::Patients post-bidirectional Glenn (BDG) operation are at risk of left and right pulmonary artery (LPA and RPA) hypoplasia. Transthoracic echocardiograms (TTE) in active children can miss essential elements of anatomy. Procedural sedation improves image quality but increases risk of adverse events. We hypothesized that...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-020-02342-x
更新日期:2020-06-01 00:00:00
abstract::The COVID-19 pandemic has had devastating direct consequences on the health of affected patients. It has also had a significant impact on the ability of unaffected children to be physically active. We evaluated the effect of deconditioning from social distancing and school shutdowns implemented during the COVID-19 pan...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-020-02513-w
更新日期:2021-01-04 00:00:00
abstract::A 2-year-old girl with cor triatriatum with unroofed coronary sinus and persistent left superior vena cava underwent preoperative radiofrequency catheter ablation for atrial tachycardia attack that developed after admission to our hospital. The procedure was not successful. Cryoablation was successfully performed duri...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-002-0376-0
更新日期:2003-09-01 00:00:00
abstract::Warfarin dosing is challenging due to a multitude of factors affecting its pharmacokinetics (PK) and pharmacodynamics (PD). A novel personalised dosing algorithm predicated on a warfarin PK/PD model and incorporating CYP2C9 and VKORC1 genotype information has been developed for children. The present prospective, obser...
journal_title:Pediatric cardiology
pub_type: 杂志文章,随机对照试验
doi:10.1007/s00246-019-02215-y
更新日期:2019-12-01 00:00:00
abstract::The data on the outcomes of children with heart disease and Down syndrome receiving extracorporeal membrane oxygenation (ECMO) for cardiac or respiratory failure are limited. This study aimed to evaluate morbidity and mortality associated with ECMO in children with Down syndrome and heart disease. Children younger tha...
journal_title:Pediatric cardiology
pub_type: 杂志文章,多中心研究
doi:10.1007/s00246-014-0945-z
更新日期:2014-12-01 00:00:00
abstract::To determine whether diastolic ventricular interdependence mechanisms would act in the presence of an open pericardial sac, as during cardiac surgery, moderate acute right ventricle afterload increases were applied to eight dogs with the chest and pericardium open while left ventricular filling dynamics were being ass...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02505087
更新日期:1996-03-01 00:00:00
abstract::A five-day-old infant with transposition of the great arteries, ventricular septal defect, and an interrupted right aortic arch underwent successful balloon septostomy, pulmonary artery banding, and aortic arch repair. The infant also had abnormal facies with severe refractory hypocalcemia and depressed T-lymphocyte n...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02427049
更新日期:1984-07-01 00:00:00
abstract::Congenital heart defect (CHD) represents the most prevalent birth defect, and accounts for substantial morbidity and mortality in humans. Aggregating evidence demonstrates the genetic basis for CHD. However, CHD is a heterogeneous disease, and the genetic determinants underlying CHD in most patients remain unknown. In...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-018-1822-y
更新日期:2018-04-01 00:00:00
abstract::To evaluate the feasibility and efficacy of the right subaxillary vertical mini-incision (RAVI) used for the closure of doubly committed subarterial ventricular septal defect (SAVSD) through tricuspid approach only. From June 2015 to September 2016, 32 SAVSD patients (mean age 2.4 ± 1.9 years, range 0.7-8 years) under...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-019-02144-w
更新日期:2019-08-01 00:00:00
abstract::The purpose of this study was to describe the long-term outcome of infants with hypoplastic left heart syndrome (HLHS) who underwent placement of internal pulmonary artery bands as part of a transcatheter palliation procedure followed by primary heart transplantation. Transcatheter palliation included stenting of the ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-009-9424-3
更新日期:2009-05-01 00:00:00