Isolated left-sided scimitar vein connecting all left pulmonary veins to the right inferior vena cava.

Abstract:

:When the common pulmonary vein fails to develop, the embryonic connections of the pulmonary veins to one or more of the systemic veins almost always persist. Anomalous pulmonary venous connections to the inferior vena cava (IVC) are typically characterized by hypoplasia of the involved pulmonary veins and pulmonary artery, as well as abnormal parenchyma of the involved lung. Such cases have been described as "scimitar syndrome." We report the case of a young female patient in whom all the left pulmonary veins converged into a common vessel that drained into the IVC but who had a normal left pulmonary artery and left lung. Surgical intervention was successful, and our patient is still alive.

journal_name

Pediatr Cardiol

journal_title

Pediatric cardiology

authors

Juraszek AL,Cohn H,Van Praagh R,Van Praagh S

doi

10.1007/s00246-005-0920-9

subject

Has Abstract

pub_date

2005-11-01 00:00:00

pages

846-7

issue

6

eissn

0172-0643

issn

1432-1971

journal_volume

26

pub_type

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