Abstract:
:When the common pulmonary vein fails to develop, the embryonic connections of the pulmonary veins to one or more of the systemic veins almost always persist. Anomalous pulmonary venous connections to the inferior vena cava (IVC) are typically characterized by hypoplasia of the involved pulmonary veins and pulmonary artery, as well as abnormal parenchyma of the involved lung. Such cases have been described as "scimitar syndrome." We report the case of a young female patient in whom all the left pulmonary veins converged into a common vessel that drained into the IVC but who had a normal left pulmonary artery and left lung. Surgical intervention was successful, and our patient is still alive.
journal_name
Pediatr Cardioljournal_title
Pediatric cardiologyauthors
Juraszek AL,Cohn H,Van Praagh R,Van Praagh Sdoi
10.1007/s00246-005-0920-9subject
Has Abstractpub_date
2005-11-01 00:00:00pages
846-7issue
6eissn
0172-0643issn
1432-1971journal_volume
26pub_type
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