Abstract:
:The case of a transient third degree atrioventricular block in a 4-year-old patient with familial dysautonomia is reported. A review of the literature follows with analysis of the significance of arrhythmias in the natural history of the patient with familial dysautonomia.
journal_name
Pediatr Cardioljournal_title
Pediatric cardiologyauthors
Rutkowski M,Axelrod FB,Danilowicz Ddoi
10.1007/BF00793955subject
Has Abstractpub_date
1992-07-01 00:00:00pages
184-6issue
3eissn
0172-0643issn
1432-1971journal_volume
13pub_type
杂志文章abstract::Despite improved outcomes following modifications to the Fontan technique, significant morbidity and mortality persist. We sought to determine if abnormal pre-Fontan catheterization hemodynamic data will predict postoperative prolonged hospital stay (PHLOS) and adverse post-discharge outcomes. This is a retrospective ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-020-02430-y
更新日期:2020-12-01 00:00:00
abstract::Intravascular ultrasound (IVUS) has been introduced as an accurate and minimally invasive diagnostic technique for the assessment of vascular anatomy and its abnormalities. We believe that IVUS can be used for clarifying the reasons for failure of balloon angiography in infantile coarctation of the aorta (CoA), becaus...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-020-02503-y
更新日期:2021-01-04 00:00:00
abstract::Cor triatriatum sinistrum (division of the left atrium) is a recognized clinical and surgical entity. Division of the right atrium, also known as cor triatriatum dexter, is an extremely rare congenital abnormality in which persistence of the right valve of the embryonic systemic sinus venosus divides the right atrium ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0443-0
更新日期:2013-01-01 00:00:00
abstract::Pulmonary arterial hypertension (PAH) is a major cause of morbidity and mortality among patients with congenital heart disease (CHD). This study was designed to determine biomarker levels in patients with PAH associated with CHD (PAH-CHD) and CHD patients without PAH and to investigate the relationship of these potent...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0321-9
更新日期:2012-12-01 00:00:00
abstract::A five-day-old infant with transposition of the great arteries, ventricular septal defect, and an interrupted right aortic arch underwent successful balloon septostomy, pulmonary artery banding, and aortic arch repair. The infant also had abnormal facies with severe refractory hypocalcemia and depressed T-lymphocyte n...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02427049
更新日期:1984-07-01 00:00:00
abstract::Pheochromocytoma is a rare disease, which often presents a diagnostic challenge due to a variable symptom presentation complex. We report the case of a child who presented with isolated symptoms of palpitations and was found to have junctional tachycardia with subsequent development of cardiomyopathy. Further evaluati...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-007-9134-7
更新日期:2008-09-01 00:00:00
abstract::Debilitating cardiomyocyte loss underlies the progression to heart failure. Although there have been significant advances in treatment, current therapies are intended to improve or preserve heart function rather than regenerate lost myocardium. A major hurdle in implementing a cell-based regenerative therapy is the in...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-009-9409-2
更新日期:2009-07-01 00:00:00
abstract::Congenital diverticulum of the ventricle is a rare disease, but most cases of congenital left ventricular diverticula are asymptomatic. We present a child with congenital left ventricular diverticulum whose routine electrocardiographic examination showed T-wave inversion in inferior and V4 to V6 leads. He was successf...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-010-9719-4
更新日期:2010-08-01 00:00:00
abstract::Left ventricular (LV) function is impaired by increased afterload in neonates with severe coarctation of the aorta, which may result in endocardial fibroelastosis. Repair of the coarctation usually solves the problem, with LV function normalizing after a few weeks. This report describes a patient who underwent success...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-009-9595-y
更新日期:2010-02-01 00:00:00
abstract::A 6-year-old girl was found to have a combination of accessory mitral valve tissue and subaortic membrane. The association caused left ventricular outflow tract obstruction leading to severe left ventricular dysfunction. Surgical relief of the obstruction resulted in immediate improvement of ventricular function. ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-001-5023-7
更新日期:2002-01-01 00:00:00
abstract::A 9-year-old girl was admitted because she had had palpitations for 2 years. Her electrocardiogram revealed multifocal ectopic beats with left bundle branch morphology, sinoatrial block, and first- and second-degree atrioventricular blocks. Cross-sectional echocardiography demonstrated an enlarged left ventricle and f...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02505810
更新日期:1996-01-01 00:00:00
abstract::Cardiac rhabdomyoma (CR) is the most common cardiac tumor in newborns. Approximately 75% of cases are associated with tuberous sclerosis complex. Although these tumors usually spontaneously regress after 2 years of age, they can be life-threatening when they obstruct major cardiac inflow or outflow pathways. Everolimu...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-017-1688-4
更新日期:2017-10-01 00:00:00
abstract::Atherosclerotic cardiovascular disease (CVD), a leading cause of death globally, has origins in childhood. Major risk factors include family history of premature CVD, dyslipidemia, diabetes mellitus, and hypertension. Lipoprotein (a) [Lp(a)], an inherited lipoprotein, is associated with premature CVD, but its impact o...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-018-1927-3
更新日期:2018-12-01 00:00:00
abstract::At the University of California Davis Medical Center, a screening fetal ultrasound examination (level I or II) incorporates a comprehensive segmental evaluation of the fetal heart. This study evaluated the reliability of the fetal ultrasound exam in the detection of abnormal heart anatomy. Our retrospective study revi...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-001-0073-4
更新日期:2002-11-01 00:00:00
abstract::Internationally, there have been isolated case reports published of children presenting with dilated cardiomyopathy (DCM) in the setting of undiagnosed rickets. Although there has been an increased prevalence of rickets in the United States, there has been only one documented case of associated DCM. At our institution...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-009-9444-z
更新日期:2009-08-01 00:00:00
abstract::We present a neonatal case with intractable atrial flutter that did not respond to digitalization and electrical cardioversion. Intravenous flecainide administration completely resolved the atrial flutter. Proarrhythmic effects were not induced by flecainide administration. Although the efficacy of flecainide for atri...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-003-0226-8
更新日期:2004-03-01 00:00:00
abstract::Long-term ECG is widely used in diagnosis and assessment of many cardiac symptoms which may be caused by dangerous arrhythmias that sometimes can be difficult to document. The PocketECG system is a new technological solution for a long-term, noninvasive, continuous and real-time ECG monitoring that provides automatic ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-016-1534-0
更新日期:2017-03-01 00:00:00
abstract::Although transthoracic echocardiography (TTE) is the first-line examination for the study of coronary lesions in Kawasaki disease, CT coronary angiography (CTCA) is increasingly used and showed good results. Our aim is to evaluate the contribution of CTCA in the detection of coronary lesions and to compare its results...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-018-2044-z
更新日期:2019-02-01 00:00:00
abstract::The response to warfarin is highly variable among individuals and such variability is likely to have some genetic basis. We evaluted the effect of VKORC1 polymorphisms on warfarin response among Japanese, taking advantage of its unique population structure in which CYP2C9 *2 and *3 alleles are relatively rare. Thirty-...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-005-1150-x
更新日期:2006-11-01 00:00:00
abstract::Maintaining patency of the ductus arteriosus pending surgical intervention can be critical to the survival of the neonate with ductal dependent congenital heart disease. Spontaneously delayed ductal closure has been observed clinically and experimentally in newborns with critical pulmonic stenosis. Infants with ductal...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02263445
更新日期:1987-01-01 00:00:00
abstract::Chylous effusions frequently occur after cardiac surgery due to severe damage to the lymphatic system, thus indicating that the insertion of a chest tube may be necessary. Factor XIII (FXIII) is discussed as being essential for wound healing. The aim of this retrospective study was to evaluate whether the application ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-005-0993-5
更新日期:2006-01-01 00:00:00
abstract::A case of aneurysmal enlargement of the right atrium was found accidentally during a routine examination. The patient was asymptomatic and free of palpitations or proven rhythm disturbances. The results of echocardiography, magnetic resonance imaging, and cardiac catheterization excluded cardiac malformation, which co...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002469900341
更新日期:1998-09-01 00:00:00
abstract::A very rare combination including tetralogy of Fallot (TOF), absent pulmonary valve, and isolated left pulmonary artery is described. A 4-month-old girl presented with mild cyanosis and severe dyspnea. Echocardiography established the diagnosis of TOF and absent pulmonary valve with severe pulmonary regurgitation and ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-008-9282-4
更新日期:2008-11-01 00:00:00
abstract::The occurrence of familial heart disease in association with tricuspid atresia is rare. The first reported instance of tricuspid atresia and Ebstein's anomaly in siblings is presented. The presence of these two distinct pathologic variants of tricuspid valve malformations in siblings suggests that these malformations ...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s002469900072
更新日期:1996-09-01 00:00:00
abstract::The longer survival of patients with Duchenne muscular dystrophy due to advances in clinical care has increased the incidence of Duchenne muscular dystrophy-associated cardiomyopathy, a nearly consistent feature in the third decade of life. A 26-year-old patient with Duchenne muscular dystrophy experienced severe acut...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-019-02072-9
更新日期:2019-03-01 00:00:00
abstract::Extracardiac valved conduits are routinely employed in the correction of complex congenital heart lesions. Compression of a conduit and/or of the heart may present serious operative and postoperative complications. We believe its occurrence can be minimized and hemodynamic results improved by adhering to simple surgic...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02242263
更新日期:1983-07-01 00:00:00
abstract::Dexmedetomidine is a new sedative and analgesic agent that has a unique property of lack of respiratory depression. We describe a pediatric case in which the use of dexmedetomidine enabled us to successfully extubate a 12-year-old heart transplant patient with acute pneumonia after several failed attempts with the use...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-005-0683-3
更新日期:2005-09-01 00:00:00
abstract::This report describes a case involving the rare combination of persistent truncus arteriosus type A2, double aortic arch, and mitral stenosis. At the age of 26 days, the patient underwent division of the right-sided aortic arch with tracheal compression and bilateral pulmonary banding. Fontan completion was successful...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-012-0572-5
更新日期:2013-01-01 00:00:00
abstract::The genetic basis of congenital heart disease remains unknown in most of the cases. Recently, a novel mouse model shed new light on the role of CCN1/CYR61, a matricellular regulatory factor, in cardiac morphogenesis. In a candidate gene approach, we analyzed a cohort of 143 patients with atrial septal defects (ASD) by...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/s00246-014-1001-8
更新日期:2015-02-01 00:00:00
abstract::This study is presented to identify and characterize the spectrum of the cardiovascular anomalies in children presenting with Williams-Beuren syndrome and cardiovascular anomalies at The Hospital for Sick Children, Toronto from 1966 to 1988. Forty-nine children were diagnosed and followed. The female to male ratio was...
journal_title:Pediatric cardiology
pub_type: 杂志文章
doi:10.1007/BF02310569
更新日期:1991-10-01 00:00:00