Focal nodular hyperplasia in a child with Beckwith-Wiedemann syndrome.

Abstract:

:Beckwith-Wiedemann Syndrome (BWS) is associated with somatic overgrowth and a high risk for embryonal tumors, including hepatoblastoma, a highly malignant liver tumor of childhood. Focal nodular hyperplasia (FNH), on the other hand, is a benign tumor of the liver that is uncommon in childhood. Herein we describe a case of FNH in a child with BWS, the first such report in the literature.

journal_name

Pediatr Surg Int

authors

Bordeianou L,Ryan DP,Goldstein AM

doi

10.1007/s00383-005-1469-7

subject

Has Abstract

pub_date

2005-09-01 00:00:00

pages

742-4

issue

9

eissn

0179-0358

issn

1437-9813

journal_volume

21

pub_type

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