Aortic calcification and renal cysts demonstrated by CT in a teenager with Alagille syndrome.

Abstract:

:Alagille syndrome, or arteriohepatic dysplasia, is a disorder characterized by paucity of intrahepatic bile ducts, peculiar facies and skeletal anomalies. We report a typical case of this syndrome in an 18-year-old girl, in whom abdominal CT showed bilateral renal cysts and aortic wall calcification, findings unreported in the radiological literature.

journal_name

Pediatr Radiol

journal_title

Pediatric radiology

authors

Pombo F,Isla C,Gayol A,Bargiela A

doi

10.1007/BF02011114

subject

Has Abstract

pub_date

1995-01-01 00:00:00

pages

314-5

issue

4

eissn

0301-0449

issn

1432-1998

journal_volume

25

pub_type

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