Abstract:
:Alagille syndrome, or arteriohepatic dysplasia, is a disorder characterized by paucity of intrahepatic bile ducts, peculiar facies and skeletal anomalies. We report a typical case of this syndrome in an 18-year-old girl, in whom abdominal CT showed bilateral renal cysts and aortic wall calcification, findings unreported in the radiological literature.
journal_name
Pediatr Radioljournal_title
Pediatric radiologyauthors
Pombo F,Isla C,Gayol A,Bargiela Adoi
10.1007/BF02011114subject
Has Abstractpub_date
1995-01-01 00:00:00pages
314-5issue
4eissn
0301-0449issn
1432-1998journal_volume
25pub_type
杂志文章abstract::In pediatric oncology, therapeutic decisions are made based on tumor response to chemotherapeutic agents. Sequential measurement of tumor bulk and its percent change on therapy must be accurately assessed. Will 3-dimensional (3-D) volumetric determination improve our ability to assess tumor response to therapy? Forty-...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF02020828
更新日期:1995-01-01 00:00:00
abstract:BACKGROUND:Emergent MRI is now a viable alternative to CT for evaluating appendicitis while avoiding the detrimental effects of ionizing radiation. However, primary employment of MRI in the setting of clinically suspected pediatric appendicitis has remained significantly underutilized. OBJECTIVE:To describe our instit...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-012-2412-4
更新日期:2012-09-01 00:00:00
abstract::Loss of bowel gas was observed in 18 out of 49 neonates on mechanical ventilation (37%). Its occurrence was correlated to the outcome and to the use of sedative or neuromuscular paralysing drugs. None of the babies had gastrointestinal disorders requiring surgical intervention. A gasless abdomen was found in 6 our of ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF01221704
更新日期:1982-01-01 00:00:00
abstract::Umbilical catheters are commonly used in the neonatal period for blood sampling or for administering medication or parenteral nutrition. The position of the catheter is usually confirmed with radiography. However, many complications associated with the use of umbilical catheters, such as liver collections from extrava...
journal_title:Pediatric radiology
pub_type: 杂志文章,评审
doi:10.1007/s00247-018-4214-9
更新日期:2018-12-01 00:00:00
abstract::A patient with the characteristic changes of Sturge-Weber syndrome on the right side was found to have a large arteriovenous malformation on the left side which involved the superior ophthalmic vein. This association, although previously reported, is extremely rare. ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF02015455
更新日期:1994-01-01 00:00:00
abstract::Two cases of neonatal spontaneous rupture of the esophagus are described, one of which is associated with a duodenal stenosis. Seventeen cases have been reported. They present clinically with non-specific signs of respiratory insufficiency and radiologically by a right-sided hydropneumothorax. Esophageal opacification...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF02386871
更新日期:1986-01-01 00:00:00
abstract::We present two cases of benign retroperitoneal lipomas in children. Intravenous urography in both revealed large masses of fat density displacing the ipsilateral kidney superomediad. Angiography in one showed an avascular mass. The other patient had a markedly echogenic mass with indistinct margins on ultrasonography,...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF00971768
更新日期:1982-01-01 00:00:00
abstract::We describe five boys, all of whom presented with urinary tract infection or acquired urinary incontinence some years after surgery for a high anorectal malformation (ARM). All were found to have a posterior urethral diverticulum thought to represent the remains of the original rectourethral fistula accompanying the h...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF01372089
更新日期:1996-01-01 00:00:00
abstract::Basilar impression (BI) assessed by either plain lateral skull radiograph or computerized tomography (CT) sagittal reconstruction of the craniocervical junction is a common finding occurring in 25% of subjects with osteogenesis imperfecta (OI). It appears to occur with highest frequency in a group of subjects with OI ...
journal_title:Pediatric radiology
pub_type: 杂志文章,评审
doi:10.1007/BF02011910
更新日期:1994-01-01 00:00:00
abstract::A boy is described with severe hyperostosis of the cranium and facial bones, and many other abnormalities including macrocephaly, abnormal facies, cleft palate, conductive hearing loss, speech defect, dental and digital anomalies, delayed skeletal development, short fibulas, short stature of postnatal onset, cervical ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF02387953
更新日期:1986-01-01 00:00:00
abstract:PURPOSE:This prospective study was designed to determine the effect of patient positioning on sonographic measurements of renal length in children. Materials and methods. Two dedicated pediatric ultrasonographers (observers A and B) measured the sonographic lengths of 48 kidneys in 25 children (two had unilateral renal...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF01372240
更新日期:1996-01-01 00:00:00
abstract::Current imaging modalities are accurate in establishing the diagnosis and extent of thoracic Hodgkin disease. After treatment, however, it is extremely difficult to differentiate potential residual active neoplastic disease from scar tissue, or identify early recurrence. We evaluated the contribution of MRI in the ass...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF02010921
更新日期:1993-01-01 00:00:00
abstract::We present a pictorial review of neonatal ischemic brain injury and look at its pathophysiology, imaging features and differential diagnoses from a radiologist's perspective. The concept of perinatal stroke is defined and its distinction from hypoxic-ischemic injury is emphasized. A brief review of recent imaging adva...
journal_title:Pediatric radiology
pub_type: 杂志文章,评审
doi:10.1007/s00247-011-2332-8
更新日期:2012-05-01 00:00:00
abstract::Rib fractures are a common skeletal manifestation of non-accidental injury (NAI) in infants and young children and are generally considered to be highly specific for abuse. There are, however, relatively few descriptions of fractures involving the costochondral junctions in NAI. We present three children (two boys, on...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s002470050436
更新日期:1998-09-01 00:00:00
abstract::Imaging pediatric elbow trauma in the acute setting remains diagnostically challenging given difficult patient positioning, multiple ossification centers of the pediatric elbow, overlapping structures, and complex joint anatomy. Digital tomosynthesis is a technique where the X-ray source travels across a limited arc a...
journal_title:Pediatric radiology
pub_type: 杂志文章,评审
doi:10.1007/s00247-019-04444-y
更新日期:2019-11-01 00:00:00
abstract::Hypertension due to transplant renal artery stenosis was treated with percutaneous transluminal angioplasty (PTA) in 6 children. 8 angioplasties were performed and the follow-up period varied between 3 and 66 months (average 23 months). The stenoses were located at the site of anastomosis in 4 children and distal to t...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF02012999
更新日期:1992-01-01 00:00:00
abstract:BACKGROUND:High-signal T2-weighted bone marrow changes can be found in both bone marrow edema and hematopoietic marrow and are often seen on pediatric MR images of the feet and ankle. OBJECTIVE:To evaluate whether high-signal T2 changes of the bone marrow seen on pediatric MRI of feet and ankles represent residual hem...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-006-0129-y
更新日期:2006-07-01 00:00:00
abstract::We present two cases of granulocytic sarcoma of the cervical lymph nodes with central necrosis as an initial manifestation of childhood leukaemia, focusing on the imaging features. Recognition of the CT and MR imaging findings of granulocytic sarcoma involving the cervical lymph nodes assists the differential diagnosi...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-008-0748-6
更新日期:2008-06-01 00:00:00
abstract::The fetal alcohol syndrome has recently been clinically recognised and has a characteristic facial phenotype. The condition is the result of chronic maternal alcohol ingestion affecting the first trimester. A survey of our cases has shown that skeletal maldevelopment is a part of the syndrome and can help in its early...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF00971818
更新日期:1981-01-01 00:00:00
abstract::As the number of patients with liver transplants continues to increase, radiologists need to be aware of the normal post-operative appearance of the different liver transplants currently performed along with the wide variety of complications encountered. The complications commonly affect the biliar and vascular system...
journal_title:Pediatric radiology
pub_type: 杂志文章,评审
doi:10.1007/s00247-010-1545-6
更新日期:2010-04-01 00:00:00
abstract:BACKGROUND:Dose reduction by combined tube current modulation has not been evaluated in pediatric low-dose CT. OBJECTIVE:This study was performed to evaluate tube current reduction in non-ECG-gated heart CT angiography in children by combined tube current modulation, and to assess the effects of body weight, age, sex,...
journal_title:Pediatric radiology
pub_type: 临床试验,杂志文章
doi:10.1007/s00247-005-0105-y
更新日期:2006-04-01 00:00:00
abstract::We present the CT and MRI findings of an 8-day-old infant with an infected cephalhaematoma complicated by skull osteomyelitis, venous sinus thrombosis and left cerebellar haemorrhage. ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-001-0647-6
更新日期:2002-05-01 00:00:00
abstract::We describe a 4-year-old girl with an inflammatory pseudotumour of the pancreas, which was preceded by varicella-zoster infection. Inflammatory pseudotumour may involve a variety of tissues, the lungs and liver being typical sites of predilection. Imaging and laboratory tests are nonspecific, and for this reason the d...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s002470000331
更新日期:2000-11-01 00:00:00
abstract:BACKGROUND:Preterm and low-birth-weight infants have an increased risk of sensorineural hearing loss. Brainstem auditory-evoked potentials (BAEP) are an effective method to detect subtle deficits in impulse conduction in the auditory pathway. Abnormalities on diffusion tensor imaging (DTI) have been shown to be associa...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-009-1278-6
更新日期:2009-08-01 00:00:00
abstract:BACKGROUND:Accurate diagnosis of hepatic vein (HV) stenosis by real-time and color Doppler US (CD-US) after segmental liver transplantation in children can decrease morbidity because it allows unnecessary biopsy, obstruction or thrombosis and loss of the graft to be avoided. OBJECTIVE:To evaluate CD-US parameters to p...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-007-0731-7
更新日期:2008-04-01 00:00:00
abstract::A study was performed to establish the value of a computed radiography (CR) system in neonatal respiratory distress syndrome (RDS). CR images obtained with various X-ray doses were compared with the images of a standard film-screen system. The image quality of CR taken with about one half radiation exposure, was compa...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF02388647
更新日期:1989-01-01 00:00:00
abstract::We report a case of perforation, fistula formation, and small bowel obstruction in a 2-year-old child who had ingested 32 small magnets. Multiple magnets will attract one another through the bowel wall and lead to pressure necrosis with complications. We recommend early surgical intervention before the onset of gastro...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-005-0056-3
更新日期:2006-03-01 00:00:00
abstract::Cutis verticis gyrata (CVG) is a skin condition characterized by thick folds and deep furrows, resembling a cortical gyral pattern. There is a recognized but rare association with Noonan syndrome. We report the antenatal imaging, including three-dimensional surface-rendered sonography and MRI, of a fetus with CVG who ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-008-0747-7
更新日期:2008-05-01 00:00:00
abstract::Mid-cervical kyphosis in diastrophic dysplasia (DD) with cord compression and weakness has been recognized for the last three decades. A strikingly similar situation exists in Larsen's syndrome (LS), an otherwise unrelated problem of weakness with lay joints and dislocations with typical facies. Forty patients with DD...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF02010328
更新日期:1995-01-01 00:00:00
abstract::Lap belt restraints in motor vehicle collisions have been associated with a variety of injuries, mainly bowel and lumbar spine. Cephalad positioning of the belt over the intended position across the anterior superior iliac spines (which typically occurs in younger children) is thought to be responsible for the observe...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-002-0779-3
更新日期:2002-12-01 00:00:00