Abstract:
:Mid-cervical kyphosis in diastrophic dysplasia (DD) with cord compression and weakness has been recognized for the last three decades. A strikingly similar situation exists in Larsen's syndrome (LS), an otherwise unrelated problem of weakness with lay joints and dislocations with typical facies. Forty patients with DD were studied of whom seven had cervical spine kyphosis: one patient had spontaneous correction over the ensuing two decades. Seven patients with LS were studied of whom four had cervical spine changes with cord compression. There was one sudden death among the patients with LS and no cases of spontaneous correction. Muscle weakness in DD and LS should lead to evaluation of cervical spine kyphosis with cord compression. Plain films, CT and recently MRI are useful.
journal_name
Pediatr Radioljournal_title
Pediatric radiologyauthors
Forese LL,Berdon WE,Harcke HT,Wagner ML,Lachman R,Chorney GS,Roye DPdoi
10.1007/BF02010328subject
Has Abstractpub_date
1995-01-01 00:00:00pages
136-9issue
2eissn
0301-0449issn
1432-1998journal_volume
25pub_type
杂志文章abstract::A seven month old female having a single arterial trunk arising from the aortic arch is presented. The baby also had severe coarctation of the aorta and a patent ductus arteriosus. This anomaly cannot be explained by Edwards' embryonic double aortic arch model. However, it can be explained by persistence of the fifth ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF02011729
更新日期:1991-01-01 00:00:00
abstract::Rickets is characterized by impaired mineralization and ossification of the growth plates of growing children caused by a variety of disorders, the most frequent of which is nutritional deficiency of vitamin D. Despite ample knowledge of its etiology and the availability of cost-effective methods of preventing it, vit...
journal_title:Pediatric radiology
pub_type: 杂志文章,评审
doi:10.1007/s00247-012-2532-x
更新日期:2013-01-01 00:00:00
abstract::Fourteen intracranial tumors were diagnosed by means of mechanical sector scanning through the infant's open fontanelle in a series consisting of 1150 examinations. In addition, integrated pulsed Doppler-sonography (duplex-scan technique) was used to diagnose malformations of intracranial vessels. We established five ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF01601876
更新日期:1984-01-01 00:00:00
abstract:BACKGROUND:In contrast to adults, intraparenchymal haemorrhage (IPH) is at least as common as ischaemic stroke in children. There is often uncertainty about the most appropriate modality for imaging in the acute stage. OBJECTIVE:To examine the diagnostic value of MRI and MR angiography (MRA) in the detection of underl...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-006-0236-9
更新日期:2006-09-01 00:00:00
abstract::A 6-year-old boy with Bannayan-Riley-Ruvalcaba syndrome (BRRS) presented to the emergency department with periumbilical abdominal pain for 12 h. A contrast-enhanced abdominal and pelvis CT examination revealed significant interval change in the size and appearance of a previously seen hypoattenuating right mesocolic f...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-014-3083-0
更新日期:2015-03-01 00:00:00
abstract::The case report is presented of a neonate with a unilateral multicystic dysplastic kidney. An intravenous pyelogram revealed septations throughout this kidney with late pooling of contrast media within the cystic structures. The pathological data stresses the presence of normal appearing glomeruli interspersed between...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF01000126
更新日期:1975-03-20 00:00:00
abstract:BACKGROUND:Digital radiography (DR) is one of several new products that have changed our work processes from hard copy to digital formats. The transition from analog screen-film radiography to DR requires thorough user education because of differences in image production, processing, storage and evaluation between the ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-010-1904-3
更新日期:2011-05-01 00:00:00
abstract::Radiographic examinations of the paranasal sinuses and chests of 187 patients with C.F. from five months to 27 years of age were reviewed. One hundred eight-five patients consistently had opaque maxillary and ethmoidal sinuses. Forty-five patients had normal chest radiographs. These observations show that the paranasa...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF00977665
更新日期:1980-02-01 00:00:00
abstract::Relapses of lymphoblastic leukaemia traditionally involve the central nervous system and testes in boys. Involvement of the female pelvic organs is frequently found at autopsy; however, involvement of the cervical uterus is rare and even less commonly symptomatic. A 13-cm uterine mass was discovered in a 15-year-old a...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-007-0661-4
更新日期:2008-03-01 00:00:00
abstract::Cancer predisposition syndromes increase the incidence of tumors during childhood and are associated with significant morbidity and mortality. Imaging is paramount for ensuring early detection of neoplasms, impacting therapeutic interventions and potentially improving outcome. While conventional imaging techniques inv...
journal_title:Pediatric radiology
pub_type: 杂志文章,评审
doi:10.1007/s00247-019-04431-3
更新日期:2019-10-01 00:00:00
abstract:BACKGROUND:Food allergy may be partly due to impairment of the intestinal barrier and is frequently associated with atopic dermatitis (AD) in early life. OBJECTIVE:To determine whether bowel wall thickening, as demonstrated by US, is useful for the identification of food allergy. MATERIALS AND METHODS:We used US to s...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-001-0593-3
更新日期:2002-01-01 00:00:00
abstract:BACKGROUND:Additional fractures occur in association with proximal radius fractures, but the extent of these secondary injuries has not been systematically assessed. OBJECTIVE:To ascertain the frequency and nature of additional fractures associated with proximal radius injuries in a large pediatric cohort. MATERIALS ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-019-04445-x
更新日期:2019-08-01 00:00:00
abstract::The mucopolysaccharidoses are a heterogeneous group of inherited lysosomal storage disorders, characterized by the accumulation of undegraded glycosaminoglycans in various organs, leading to tissue damage. Mucopolysaccharidoses include eight individual disorders (IS [Scheie syndrome], IH [Hurler syndrome], II, III, IV...
journal_title:Pediatric radiology
pub_type: 杂志文章,评审
doi:10.1007/s00247-018-4139-3
更新日期:2018-09-01 00:00:00
abstract::Sonographic studies on 52 children with suspected peripheral vascular disease examined between January 1988 and December 1989 were retrospectively reviewed. A technique for examining the jugular, subclavian veins, and superior vena cava (SVC) was developed and is described. The technique for examining the extremities ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF02011718
更新日期:1991-01-01 00:00:00
abstract::The spectrum of congenital anomalies of the male urethra is presented. The embryologic basis of each anomaly, when known, is discussed. Clinical and imaging features of each entity are presented. ...
journal_title:Pediatric radiology
pub_type: 杂志文章,评审
doi:10.1007/s00247-007-0495-0
更新日期:2007-09-01 00:00:00
abstract::Vascular rings and pulmonary slings are congenital anomalies of the aortic arch/great vessels and pulmonary arteries, respectively, that commonly present early during infancy and childhood with respiratory and/or feeding difficulties. The diagnosis of these conditions frequently utilizes a multi-modality radiological ...
journal_title:Pediatric radiology
pub_type: 杂志文章,评审
doi:10.1007/s00247-011-2131-2
更新日期:2011-11-01 00:00:00
abstract::Shaken-baby syndrome (SBS) is a type of child abuse caused by violent shaking of an infant, with or without impact, and characterized by subdural hematomas, retinal hemorrhages, and occult bone fractures. Parenchymal brain lesions in SBS may be missed or underestimated on CT scans, but can be detected at an earlier st...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-003-1025-3
更新日期:2003-12-01 00:00:00
abstract::We report an unusual case of a child with a congenital solitary functional kidney complicated by a sports-related posttraumatic Page kidney. The child developed severe hypertension and renal insufficiency requiring percutaneous intervention to preserve renal function. The literature is sparse with no definitive guidel...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-010-1630-x
更新日期:2010-11-01 00:00:00
abstract::We present an unusual case of popliteal entrapment syndrome type I in an 11-year-old boy. Presenting symptoms were exercise-related pain and pallor in his left lower leg. The diagnosis of popliteal entrapment syndrome was established by acral plethysmography, colour-coded Doppler sonography and MRI. After myotomy of t...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s002470050552
更新日期:1999-02-01 00:00:00
abstract::Abdominal angiography is an extremely valuable modality for the diagnosis of abdominal disease in infants and children. A practical guide to catheter selection, flow rates, and contrast dosage for abdominal angiography in the pediatric patient is presented. ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF00988657
更新日期:1976-10-26 00:00:00
abstract::The Nuss procedure has succeeded in minimizing incisions, blood loss, sternal fracturing, operating room time, recovery time, and length of hospital stay. Knowledge of the pre- and postoperative radiologic considerations is essential in providing appropriate imaging support to the surgeons performing this innovative, ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s002470100455
更新日期:2001-06-01 00:00:00
abstract::Primitive malignant renal tumours comprise 6% of all childhood cancers. Wilms tumour (WT) or nephroblastoma is the most frequent type accounting for more than 90%. Imaging alone cannot differentiate between these tumours with certainty but it plays an important role in screening, diagnostic workup, assessment of thera...
journal_title:Pediatric radiology
pub_type: 杂志文章,评审
doi:10.1007/s00247-010-1584-z
更新日期:2010-06-01 00:00:00
abstract::ACTH is used in childhood to treat infantile spasms and acute cerebellar encephalopathy (opsoclonus-cerebellar ataxia syndrome). We report two infants with ultrasonographic and CT evidence of massive, reversible adrenal enlargement secondary to exogenous ACTH therapy for these disorders. ...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF02012450
更新日期:1993-01-01 00:00:00
abstract::We present a case of bilateral tibial insufficiency fracture in which indium (In)-111 diethylenetriamine pentaacetic acid (DTPA) octreotide scan showed increased activity in the region of the fracture. The scan was performed in a 5-year-old girl with severe refractory hypertension and elevated plasma metanephrines for...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-014-3029-6
更新日期:2015-01-01 00:00:00
abstract:BACKGROUND:Single-shot fast spin echo (SSFSE) is particularly appealing in pediatric patients because of its motion robustness. However radiofrequency energy deposition at 3 tesla forces long pauses between slices, leading to longer scans, longer breath-holds and more between-slice motion. OBJECTIVE:We sought to learn...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-014-3227-2
更新日期:2015-06-01 00:00:00
abstract::Among all causes of death in children from solid tumors, pediatric brain tumors are the most common. This article includes an overview of a subset of infratentorial and supratentorial tumors with a focus on tumor imaging features and molecular advances and treatments of these tumors. Key to understanding the imaging f...
journal_title:Pediatric radiology
pub_type: 杂志文章,评审
doi:10.1007/s00247-015-3326-8
更新日期:2015-09-01 00:00:00
abstract:OBJECTIVE:The purpose of this paper is to review and categorize the CT appearances of primary and secondary intraperitoneal neoplasms in children. MATERIALS AND METHODS:We retrospectively reviewed the CT images of 14 cases of intraperitoneal neoplasms. They were reviewed for bowel wall thickening, mesenteric nodules, ...
journal_title:Pediatric radiology
pub_type: 杂志文章,多中心研究
doi:10.1007/s002470050363
更新日期:1998-05-01 00:00:00
abstract::Twenty patients with massive trichuriasis were studied with double contrast barium enema. The following changes were observed: 1) Impregnation defects of the colonic wall probably due to abundant mucous secretions. 2) Granular features. 3) Pear-shaped caecum. 4) Radiolucid ringlike images with some contrast material i...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF00973995
更新日期:1979-04-19 00:00:00
abstract:BACKGROUND:Glutaric aciduria type 1 is a rare neurometabolic disease with high morbidity. OBJECTIVE:To describe the MR imaging abnormalities in glutaric aciduria type 1 and to identify any association between the clinical and imaging features. MATERIALS AND METHODS:MRI scans of 29 children (mean age: 16.9 months) wit...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/s00247-015-3395-8
更新日期:2015-10-01 00:00:00
abstract::Magnetic resonance (MR) images of 12 pathologically proven lesions of Langerhans cell histiocytosis (LCH) of bone were reviewed retrospectively. MR identified all lesions, three of which were not identified on plain radiographs. In all cases, MR showed greater abnormality than did plain radiographs. With one exception...
journal_title:Pediatric radiology
pub_type: 杂志文章
doi:10.1007/BF02017655
更新日期:1994-01-01 00:00:00