Racial disparities in clinic follow-up early in life among survivors of congenital heart disease.

abstract：:Absence of the aortic valve is a rare congenital heart defect that is detectable in the prenatal period. In this condition, functional aortic valve leaflets are absent; in their place are rudimentary, immobile noncoapting plate-like structures at the level of the annulus resulting in severe aortic regurgitation. We re...

journal_title：Congenital heart disease

authors： Sabati AA,Wong PC,Randolph L,Pruetz JD

更新日期：2014-05-01 00:00:00

abstract：OBJECTIVE:The need for conduit replacement in the growing child remains a major problem after right ventricular outflow tract reconstruction. We compared two diverse surgical centers with considerable practice variation in Europe and the United States to identify modifiable risk factors that can increase conduit longev...

journal_title：Congenital heart disease

authors： Niemantsverdriet MB,Ottenkamp J,Gauvreau K,Del Nido PJ,Hazenkamp MG,Jenkins KJ

更新日期：2008-05-01 00:00:00

abstract：OBJECTIVE:We sought to define what clinical parameters were related to the ultimate outcome in Fontan patients who had developed protein-losing enteropathy (PLE). BACKGROUND:PLE is a serious complication of the Fontan operation. Several preoperative and perioperative findings are associated with later PLE. However, th...

journal_title：Congenital heart disease

authors： Silvilairat S,Cabalka AK,Cetta F,Grogan M,Hagler DJ,O'Leary PW

更新日期：2008-07-01 00:00:00

abstract：:Brugada syndrome is an arrhythmogenic disease characterized by a pattern of ST segment elevation in the right precordial leads on an electrocardiogram with an increased risk of sudden cardiac death. It is primarily reported in adults with limited data about the prevalence, prognosis, and long-term management in childr...

journal_title：Congenital heart disease

authors： Zaidi AN

更新日期：2010-11-01 00:00:00

abstract：OBJECTIVE:Amiodarone is a highly effective antiarrhythmic therapy, however its toxicity profile often limits treatment. This is particularly relevant in adults with congenital heart disease (CHD), who are often young and in whom other antiarrhythmic agents commonly fail or are contraindicated. We sought to determine in...

journal_title：Congenital heart disease

authors： Moore BM,Cordina RL,McGuire MA,Celermajer DS

更新日期：2018-11-01 00:00:00

abstract：OBJECTIVE:The purpose of this study was to identify factors that influence postoperative intensive care unit length of stay (ICULOS) in infants less than 6 months of age undergoing congenital heart surgery. METHODS:Records from a single institution, from January 2000 to December 2000, were reviewed. For analysis, surg...

journal_title：Congenital heart disease

authors： Gillespie M,Kuijpers M,Van Rossem M,Ravishankar C,Gaynor JW,Spray T,Clark B 3rd

更新日期：2006-07-01 00:00:00

abstract：OBJECTIVE:To evaluate the efficacy of using fetal heart size measurements derived from axial echocardiography to predict homozygous α-thalassemia-1. DESIGN:Prospective diagnostic study. SETTING:The carrier rate of α-thalassemia-1 (-/αα) in China's Guangxi Zhuang Autonomous Region is approximately 15%. If both parents...

journal_title：Congenital heart disease

authors： Li X,Qiu X,Huang H,Zhao Y,Li X,Li M,Tian X

更新日期：2018-03-01 00:00:00

abstract：:Down syndrome (DS) patients are prone to pulmonary hypertension (PHTN) due to various cardiopulmonary causes. However, the association of DS with pulmonary vein stenosis (PVS) is not adequately described. We illustrate three cases from our center and an additional 13 cases from an extensive review of the literature of...

journal_title：Congenital heart disease

authors： Gowda S,Bhat D,Feng Z,Chang CH,Ross RD

更新日期：2014-05-01 00:00:00

abstract：:Scimitar syndrome is characterized by anomalous pulmonary venous drainage of a part or the whole of the right lung into the inferior vena cava (IVC). It is extremely uncommon in scimitar syndrome for the pulmonary veins to drain anomalously to a site other than the IVC. The following case report describes an otherwise...

journal_title：Congenital heart disease

authors： Kotecha MK,Krishnamanohar SR,Kumar RS

更新日期：2012-01-01 00:00:00

abstract：:Carditis is a common manifestation of adult patients with Lyme disease affecting 4-10% of Lyme patients in the United States. However, children with Lyme disease rarely present with acute carditis. The management of pediatric patients with complete heart block (CHB) secondary to Lyme carditis has not been well describ...

journal_title：Congenital heart disease

authors： Silver E,Pass RH,Kaufman S,Hordof AJ,Liberman L

更新日期：2007-09-01 00:00:00

abstract：:We report on a 3-year-old male who underwent transcatheter stent fenestration of the inferior portion of an extracardiac total cavopulmonary connection in the setting of hypoplastic left heart syndrome. Transhepatic approach, following an unsuccessful attempt from the femoral vein facilitated delivery of a diabolo-sha...

journal_title：Congenital heart disease

authors： Kenny D,McMahon C,Walsh KP

更新日期：2011-05-01 00:00:00

abstract：:To evaluate the influence of echocardiographic examination in the clinical management of the sick neonate, 241 patients, admitted to the neonatal intensive care unit of a tertiary referral center that had echocardiograms with data available for review, were enrolled in a retrospective study. Asymptomatic murmurs (45%)...

journal_title：Congenital heart disease

authors： Kadivar M,Kiani A,Kocharian A,Shabanian R,Nasehi L,Ghajarzadeh M

更新日期：2008-09-01 00:00:00

abstract：:Currently, the role of stress echocardiography primarily resides in diagnosing acquired coronary artery disease (CAD) in adults. Besides an increasing concern for traditional CAD in young patients due to obesity and other chronic pediatric diseases, there is also a growing population of adolescents and young adults wi...

journal_title：Congenital heart disease

authors： Ermis P

更新日期：2017-09-01 00:00:00

abstract：BACKGROUND:Pulmonary atresia with intact ventricular septum is a unique congenital malformation of the heart in which patients may undergo single-, two- or 1½- ventricle repair. Size of the tricuspid valve annulus, morphology of the right ventricle and presence of ventriculocoronary connections can all impact the selec...

journal_title：Congenital heart disease

authors： Loomba RS,Pelech AN

更新日期：2018-01-01 00:00:00

abstract：:Pulmonary hypertension (PH) is a complex condition with a broad range of etiologies that result in a common outcome--elevated pulmonary arterial pressure. For the pediatric cardiologist, this entity provides a manifest demonstration of the interrelationship of cardiac and pulmonary physiology. A thoughtful approach mu...

journal_title：Congenital heart disease

authors： Kyle WB

更新日期：2012-11-01 00:00:00

abstract：:Iron deficiency state in patients with cyanotic congenital heart disease can mimic as well as aggravate hyperviscosity symptoms. Correction of iron deficiency in these cases is expected to improve symptoms. We report an unexpected occurrence of refractory cyanotic spell in a child with tetralogy of Fallot due to throm...

journal_title：Congenital heart disease

authors： Gupta SK,Saxena A,Anil OM,Bisoi AK

更新日期：2012-07-01 00:00:00

abstract：OBJECTIVE:Intravascular stents are now routinely used to treat young patients with vascular stenoses. Future stent redilations are often necessary to account for somatic growth. The purpose of this study was to compile a database of characteristics for stents commonly used in the treatment of congenital heart disease p...

journal_title：Congenital heart disease

authors： Danon S,Gray RG,Crystal MA,Morgan G,Gruenstein DH,Goldstein BH,Gordon BM

更新日期：2016-12-01 00:00:00

abstract：OBJECTIVE:We hypothesized that a right aortic arch in situs solitus, with or without an associated cardiovascular malformation, is often associated with a vascular ring. METHODS:From those born in Southern Nevada between March 2012 and March 2017, we identified 50 (3.6 per 10,000 live births) with a right aortic arch ...

journal_title：Congenital heart disease

authors： Evans WN,Acherman RJ,Ciccolo ML,Carrillo SA,Mayman GA,Luna CF,Rollins RC,Castillo WJ,Galindo A,Rothman A,Alexander JA,Kwan TW,Restrepo H

更新日期：2017-09-01 00:00:00

abstract：OBJECTIVE:Assess the early and intermediate results with respect to blood pressure control in older children undergoing endovascular stenting for native coarctation of the aorta. DESIGN:Eleven hypertensive patients (10 +/- 3 years of age) underwent endovascular stenting via standard techniques for native coarctation o...

journal_title：Congenital heart disease

authors： Weber HS,Cyran SE

更新日期：2008-01-01 00:00:00

abstract：BACKGROUND:Open cardiac surgery has traditionally been the gold standard for repair of ventricular septal defect (VSD). The inherent risks and complications associated with open surgery and the incidence of postoperative residual VSD are significant disadvantages of the open surgical approach. OBJECTIVE:To evaluate th...

journal_title：Congenital heart disease

authors： Zhou W,Li F,Fu L,Gao W,Guo Y,Liu T,Huang M,Zhang Y

更新日期：2016-07-01 00:00:00

abstract：INTRODUCTION:Perturbations in the CACNA1C-encoded L-type calcium channel α-subunit have been linked recently to heritable arrhythmia syndromes, including Timothy syndrome, Brugada syndrome, early repolarization syndrome, and long QT syndrome. These heritable arrhythmia syndromes may serve as a pathogenic basis for auto...

journal_title：Congenital heart disease

authors： Sutphin BS,Boczek NJ,Barajas-Martínez H,Hu D,Ye D,Tester DJ,Antzelevitch C,Ackerman MJ

更新日期：2016-12-01 00:00:00

abstract：:Transcatheter management of native coarctation of the aorta in 3 children with Turner syndrome is reported. Two children, 12 and 17 years of age, underwent stent implantation and 1 child, 3 years old, underwent balloon angioplasty alone. In all children the procedures were successful, both hemodynamically and angiogra...

journal_title：Congenital heart disease

authors： Kataoka K,Ozawa A,Inage A,Benson LN

更新日期：2006-11-01 00:00:00

abstract：INTRODUCTION:With increasing survival of children with HLHS and other single ventricle lesions, the complexity of medical care for these patients is substantial. Establishing and adhering to best practice models may improve outcome, but requires careful coordination and monitoring. METHODS:In 2013 our Heart Center beg...

journal_title：Congenital heart disease

authors： Texter K,Davis JAM,Phelps C,Cheatham S,Cheatham J,Galantowicz M,Feltes TF

更新日期：2017-07-01 00:00:00

abstract：OBJECTIVE:Clinical genetic testing is expanding rapidly, but the application of new testing has not been reported in an unselected, comprehensive congenital heart disease (CHD) patient population. This study aims to identify cytogenetic testing practices and diagnostic yield in infants with CHD as an important first st...

journal_title：Congenital heart disease

authors： Connor JA,Hinton RB,Miller EM,Sund KL,Ruschman JG,Ware SM

更新日期：2014-03-01 00:00:00

abstract：:The Fontan operation has gone through multiple incarnations since Fontan and Baudet's initial description in 1971. Through the medical dossier of a patient with a single ventricle, we plot the history of medical, surgical, and percutaneous interventions over the past 40 years, specifically focusing on the Fontan proce...

journal_title：Congenital heart disease

authors： AboulHosn JA,Shavelle DM,Castellon Y,Criley JM,Plunkett M,Pelikan P,Dinh H,Child JS

更新日期：2007-01-01 00:00:00

abstract：:Dilated cardiomyopathy and ventricular noncompaction have been reported in association with deletion 1p36 syndrome. Previous descriptions include echocardiographic and/or gross pathologic descriptions. There are no previous reports of microscopic findings. We report a case with descriptions of echocardiographic, gross...

journal_title：Congenital heart disease

authors： Pearce FB,Litovsky SH,Dabal RJ,Robin N,Dure LJ,George JF,Kirklin JK

更新日期：2012-01-01 00:00:00

abstract：:A 22-year-old female with no medical history presented to the emergency room with 2 weeks of rapidly worsening dyspnea on exertion, orthopnea, and cough. On cardiac auscultation, she was noted to have to-and-fro murmurs and a continuous murmur with signs of right heart failure. Echocardiographic images obtained showed...

journal_title：Congenital heart disease

authors： Yang EH,Rawal M,Pillutla P,Criley JM

更新日期：2011-03-01 00:00:00

abstract：BACKGROUND & AIMS:Fontan surgery for single ventricle congenital heart disease leads to Fontan-associated liver disease (FALD). Typical laboratory tests, imaging, and histopathology cannot predict clinical severity in FALD. HepQuant SHUNT is a proprietary serum test of hepatic function and physiology that has not yet b...

journal_title：Congenital heart disease

authors： Lemmer A,VanWagner L,Gasanova Z,Helmke S,Everson GT,Ganger D

更新日期：2019-11-01 00:00:00

abstract：BACKGROUND:Physician burnout has many undesirable consequences, including negative impact on patient care delivery and physician career satisfaction. Electronic health records (EHRs) may exacerbate burnout by increasing physician workload. OBJECTIVE:To determine burnout in adult congenital heart disease (ACHD) special...

journal_title：Congenital heart disease

authors： Marckini DN,Samuel BP,Parker JL,Cook SC

更新日期：2019-05-01 00:00:00

abstract：PURPOSE:Right ventricular (RV) failure and ventricular dyssynchrony are strong determinants of prognosis in patients with adult congenital heart disease (ACHD). The aim of this study was to investigate the relationship between interventricular dyssynchrony (IVD) using cine-tagged magnetic resonance imaging (MRI) and RV...

journal_title：Congenital heart disease

authors： Nagao M,Yamasaki Y,Yonezawa M,Matsuo Y,Kamitani T,Yamamura K,Sakamoto I,Abe K,Kawanami S,Honda H

更新日期：2015-05-01 00:00:00