Echocardiography and management of sick neonates in the intensive care unit.

abstract：INTRODUCTION:Ketamine is a drug often used for procedural sedation or as adjunct agent for general sedation in children with congenital heart disease. In the clinical realm, there is often confusion regarding the effects of ketamine on hemodynamics, particularly pulmonary vascular resistance and systemic vascular resis...

journal_title：Congenital heart disease

authors： Loomba RS,Gray SB,Flores S

更新日期：2018-09-01 00:00:00

abstract：:A genetic basis of congenital heart disease (CHD) has been known for decades. In addition to the sequence of the genome, the contribution of epigenetics to pediatric cardiology is increasingly recognized. Multiple epigenetic mechanisms, including DNA methylation, histone modification, and RNA-based regulation, are kno...

journal_title：Congenital heart disease

authors： Spearman AD

更新日期：2017-12-01 00:00:00

abstract：:Currently, the role of stress echocardiography primarily resides in diagnosing acquired coronary artery disease (CAD) in adults. Besides an increasing concern for traditional CAD in young patients due to obesity and other chronic pediatric diseases, there is also a growing population of adolescents and young adults wi...

journal_title：Congenital heart disease

authors： Ermis P

更新日期：2017-09-01 00:00:00

abstract：OBJECTIVE:The purpose of this study was to compare neurological development of children with cyanotic or hemodynamically impaired congenital heart disease (CHD) and healthy controls by using "Bayley Scales of Infant and Toddler Development Screening Test, Third Edition" (Bayley-III). PATIENTS:Children with CHD (n = 37...

journal_title：Congenital heart disease

authors： Hallioglu O,Gurer G,Bozlu G,Karpuz D,Makharoblidze K,Okuyaz C

更新日期：2015-11-01 00:00:00

abstract：OBJECTIVE:Stent placement has become a widely used method of treatment for coarctation of the aorta (COA). Our goal was to find echocardiographic indices that would correlate best with directly measured gradients across the coarctation stent. MATERIAL AND METHODS:Pediatric patients with COA who underwent intra-aortic ...

journal_title：Congenital heart disease

authors： Tang L,Forbes TJ,Du W,Zilberman MV

更新日期：2009-07-01 00:00:00

abstract：:This is a case report reviewing the presentation and clinical course of a patient diagnosed with abdominal aortic atresia at the level caudal to the superior mesenteric artery. Patients with abdominal aortic atresia need to be evaluated for associated underlying syndromes or diseases. Although the prognosis for this d...

journal_title：Congenital heart disease

authors： Brown J,Shehata BM,Campbell R

更新日期：2011-05-01 00:00:00

abstract：:In medical literature, few cases of Rasmussen's aneurysm have been reported until now, and to the best of our knowledge, there has been no description of a case of Rasmussen's aneurysm in childhood. The child described in the case report had a restrictive cardiomyopathy, complicated by pulmonary hypertension, in assoc...

journal_title：Congenital heart disease

authors： Gesuete V,Corzani A,Bronzetti G,Lovato L,Picchio FM

更新日期：2013-03-01 00:00:00

abstract：OBJECTIVE:Traditionally, karyotype and fluorescence in situ hybridization (FISH) were used for cytogenetic testing of infants with congenital heart disease (CHD) who underwent cardiac surgery at our institution. Recently, chromosome microarray analysis (CMA) has been performed in lieu of the traditional tests. A standa...

journal_title：Congenital heart disease

authors： Buckley JR,Kavarana MN,Chowdhury SM,Scheurer MA

更新日期：2015-05-01 00:00:00

abstract：BACKGROUND & AIMS:Fontan surgery for single ventricle congenital heart disease leads to Fontan-associated liver disease (FALD). Typical laboratory tests, imaging, and histopathology cannot predict clinical severity in FALD. HepQuant SHUNT is a proprietary serum test of hepatic function and physiology that has not yet b...

journal_title：Congenital heart disease

authors： Lemmer A,VanWagner L,Gasanova Z,Helmke S,Everson GT,Ganger D

更新日期：2019-11-01 00:00:00

abstract：OBJECTIVES:To investigate survival and freedom from reintervention after aortic coarctation repair in Maltese patients and to compare cardiovascular mortality in coarctation repair survivors with that in the general population. DESIGN:All 72 aortic coarctation patients with any type of repair, born by end-1997 and log...

journal_title：Congenital heart disease

authors： Caruana M,Grech V

更新日期：2017-09-01 00:00:00

abstract：UNLABELLED:BACKGROUND; Several studies have demonstrated the utility of B-type natriuretic peptide (BNP) in the months following cardiac transplant. The purpose of this study was to analyze longitudinal BNP data in pediatric cardiac transplant patients and determine the efficacy of BNP in routine follow-up of transplan...

journal_title：Congenital heart disease

authors： Bramlet M,Moore R,Murphy D,Caldwell R,Darragh R,Schamberger M

更新日期：2010-05-01 00:00:00

abstract：INTRODUCTION:Health care-associated infections (HAIs) increase mortality, length of stay, and cost in hospitalized patients. The incidence of and risk factors for developing HAIs in the pediatric population after cardiac surgery have been studied. This study evaluates the impact of HAIs on length of stay, inpatient mor...

journal_title：Congenital heart disease

authors： Tweddell S,Loomba RS,Cooper DS,Benscoter AL

更新日期：2019-09-01 00:00:00

abstract：:Dexmedetomidine is a selective alpha-2 adrenergic agonist that is used frequently for short-term sedation in children. It has been noted to cause hypertension, hypotension, bradycardia, and sinus pauses; however, QTc prolongation has not been reported with dexmedetomidine administration. We describe a case of marked Q...

journal_title：Congenital heart disease

authors： Burns KM,Greene EA

更新日期：2014-01-01 00:00:00

abstract：BACKGROUND:Transient elastography (TE) offers a noninvasive correlate with the degree of hepatic fibrosis. However, factors other than fibrosis affect liver stiffness. We sought to determine whether hepatic congestion related to hemodynamics in Fontan circulation influences liver stiffness measurement (LSM) assessed by...

journal_title：Congenital heart disease

authors： Wu FM,Opotowsky AR,Raza R,Harney S,Ukomadu C,Landzberg MJ,Valente AM,Breitbart RE,Singh MN,Gauvreau K,Jonas MM

更新日期：2014-09-01 00:00:00

abstract：OBJECTIVE:The aim of this study was to compare the effects of anesthesia by dexmedetomidine and propofol on the hemodynamics and oxygen balance in children with complex congenital heart disease who were undergoing cardiac surgery. METHODS:Fifty-seven children were randomized to receive either a continuous infusion of ...

journal_title：Congenital heart disease

authors： Cheng X,Zuo Y,Zhao Q,Gu E,Huang Y

更新日期：2015-05-01 00:00:00

abstract：OBJECTIVE:To evaluate the efficacy of using fetal heart size measurements derived from axial echocardiography to predict homozygous α-thalassemia-1. DESIGN:Prospective diagnostic study. SETTING:The carrier rate of α-thalassemia-1 (-/αα) in China's Guangxi Zhuang Autonomous Region is approximately 15%. If both parents...

journal_title：Congenital heart disease

authors： Li X,Qiu X,Huang H,Zhao Y,Li X,Li M,Tian X

更新日期：2018-03-01 00:00:00

abstract：:Dilated cardiomyopathy and ventricular noncompaction have been reported in association with deletion 1p36 syndrome. Previous descriptions include echocardiographic and/or gross pathologic descriptions. There are no previous reports of microscopic findings. We report a case with descriptions of echocardiographic, gross...

journal_title：Congenital heart disease

authors： Pearce FB,Litovsky SH,Dabal RJ,Robin N,Dure LJ,George JF,Kirklin JK

更新日期：2012-01-01 00:00:00

abstract：OBJECTIVE:Amiodarone is a highly effective antiarrhythmic therapy, however its toxicity profile often limits treatment. This is particularly relevant in adults with congenital heart disease (CHD), who are often young and in whom other antiarrhythmic agents commonly fail or are contraindicated. We sought to determine in...

journal_title：Congenital heart disease

authors： Moore BM,Cordina RL,McGuire MA,Celermajer DS

更新日期：2018-11-01 00:00:00

abstract：:In patients with Kawasaki disease (KD) and coronary artery aneurysms (CAAs), serial evaluation with multiple imaging modalities is recommended to guide risk stratification and management. We present the case of a 7-year-old boy with a history of KD and multiple giant CAAs who developed thrombosis in one of the aneurys...

journal_title：Congenital heart disease

authors： Prsa M,Hussain T,McCrindle BW,Grosse-Wortmann L

更新日期：2014-11-01 00:00:00

abstract：:Marfan syndrome is a well-described autosomal dominant syndrome with widely variable clinical manifestations. Cardiovascular complications include mitral valve prolapse with or without associated mitral valve insufficiency, aortic root dilatation, and most importantly the occasional development of aortic aneurysms or ...

journal_title：Congenital heart disease

authors： Zangwill SD,Brown MD,Bryke CR,Cava JR,Segura AD

更新日期：2006-09-01 00:00:00

abstract：:There has been a steady rise in the prevalence of severe congenital heart disease (CHD) in adults because of improved treatment and survival during childhood. This has resulted in a shift in CHD morbidity and mortality beyond 18 years of age. The healthcare community must be prepared to meet this new challenge. Adult ...

journal_title：Congenital heart disease

authors： Kalra N,Klewer SE,Raasch H,Sorrell VL

更新日期：2010-05-01 00:00:00

abstract：OBJECTIVE:To examine the knowledge and attitudes of anesthesia providers in relation to the care of adult congenital heart disease (ACHD) patients presenting for noncardiac surgery. DESIGN/SETTING:A novel survey was designed and administered to 168 anesthesiologists across a single academic department in a range of pr...

journal_title：Congenital heart disease

authors： Maxwell BG,Williams GD,Ramamoorthy C

更新日期：2014-01-01 00:00:00

abstract：OBJECTIVE:Pulmonary autograft aortic root replacement (Ross' operation) is now associated with low operative risk. Recent series suggest that patients with primary aortic insufficiency have diminished autograft durability and that patients with large discrepancies between pulmonary and aortic valve sizes have a low but...

journal_title：Congenital heart disease

authors： Morales DL,Carberry KE,Balentine C,Heinle JS,McKenzie ED,Fraser CD Jr

更新日期：2008-11-01 00:00:00

abstract：OBJECTIVE:It is unclear whether neonates with interrupted aortic arch (IAA) and a smaller left ventricular outflow tract may have improved outcomes with a Yasui operation (ventricular outflow bypass procedure) over a primary complete repair. This study sought to identify preoperative echocardiographic parameters to dif...

journal_title：Congenital heart disease

authors： Abarbanell G,Border WL,Schlosser B,Morrow G,Kelleman M,Sachdeva R

更新日期：2018-05-01 00:00:00

abstract：OBJECTIVE:Nurse practitioners (NPs) have an established role for delivering competent care to patients in the primary care setting. The aim of this study was to compare satisfaction of patients managed by NPs vs. physicians in the outpatient adult congenital heart disease (CHD) clinic. DESIGN:A prospective study condu...

journal_title：Congenital heart disease

authors： Maul TM,Zaidi A,Kowalski V,Hickey J,Schnug R,Hindes M,Cook S

更新日期：2015-09-01 00:00:00

abstract：OBJECTIVE:Patients undergoing surgical repair of aortic coarctation have a 50% risk of pathologic left ventricular remodeling (increased left ventricular mass or relative wall thickness). Endothelin 1, ST2, galectin 3, norepinephrine and B-natriuretic peptide are biomarkers that have been associated with pathologic LV ...

journal_title：Congenital heart disease

authors： Frank BS,Urban TT,Lewis K,Tong S,Cassidy C,Mitchell MB,Nichols CS,Davidson JA

更新日期：2019-05-01 00:00:00

abstract：BACKGROUND:Deficits in swallowing physiology are a leading morbidity for infants with functional single ventricles and systemic outflow tract obstruction following stage 1 palliation. Despite the high prevalence of this condition, the underlying deficits that cause this post-operative impairment remain poorly understoo...

journal_title：Congenital heart disease

authors： McGrattan KE,McGhee H,DeToma A,Hill EG,Zyblewski SC,Lefton-Greif M,Halstead L,Bradley SM,Martin-Harris B

更新日期：2017-05-01 00:00:00

abstract：OBJECTIVES:To investigate functional health status among adults previously operated for aortic coarctation (CoA) compared with healthy subjects; to assess the influence of medication and exercise capacity on patients' functional health. DESIGN:Questionnaire-based investigation among 119 patients who underwent surgical...

journal_title：Congenital heart disease

authors： Pedersen TA,Røpcke DM,Hjortdal VE

更新日期：2011-11-01 00:00:00

abstract：PURPOSE:The aim of this article was to assess the role of MRI in the diagnosis and management of a variety of complex aortic arch anomalies. MATERIALS AND METHODS:Imaging was performed on a 1.5T Philips Gyroscan Intera. We retrospectively reviewed all cardiac MR scans performed from November 2003 to February 2007 at o...

journal_title：Congenital heart disease

authors： Cantinotti M,Hegde S,Bell A,Razavi R

更新日期：2008-03-01 00:00:00

abstract：BACKGROUND:It has been reported that gender differences in cardiovascular outcomes found in adults also are present in children who undergo surgical repair for congenital heart disease. METHODS:California statewide hospital discharge data 1989-99 were used to study outcomes in children <18 years undergoing cardiac sur...

journal_title：Congenital heart disease

authors： Klitzner TS,Lee M,Rodriguez S,Chang RK

更新日期：2006-05-01 00:00:00