Pulmonary hypertension associated with congenital heart disease: a practical review for the pediatric cardiologist.

Abstract:

:Pulmonary hypertension (PH) is a complex condition with a broad range of etiologies that result in a common outcome--elevated pulmonary arterial pressure. For the pediatric cardiologist, this entity provides a manifest demonstration of the interrelationship of cardiac and pulmonary physiology. A thoughtful approach must be applied to each patient with PH in order to achieve a thorough understanding of the nature of disease and to proceed with individualized therapy in an appropriate and timely manner. This article aims to provide a clinically relevant, practical review of current literature related to PH in patients with congenital heart disease, including the causes, diagnostic considerations, and an overview of management.

journal_name

Congenit Heart Dis

journal_title

Congenital heart disease

authors

Kyle WB

doi

10.1111/chd.12012

subject

Has Abstract

pub_date

2012-11-01 00:00:00

pages

575-83

issue

6

eissn

1747-079X

issn

1747-0803

journal_volume

7

pub_type

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