"Frontiers in Fontan failure: A summary of conference proceedings".

Abstract:

:"Frontiers in Fontan Failure" was the title of a 2015 conference sponsored by Children's Healthcare of Atlanta and Emory University School of Medicine. In what is hoped to be the first of many such gatherings, speakers and attendees gathered to discuss the problem of long-term clinical deterioration in these patients. Specific focuses included properly defining the problem and then discussing different treatment strategies, both medical and surgical. The health of the liver after Fontan palliation was a particular point of emphasis, as were quality of life and future directions.

journal_name

Congenit Heart Dis

journal_title

Congenital heart disease

authors

Hebson C,Book W,Elder RW,Ford R,Jokhadar M,Kanter K,Kogon B,Kovacs AH,Levit RD,Lloyd M,Maher K,Reshamwala P,Rodriguez F,Romero R,Tejada T,Marie Valente A,Veldtman G,McConnell M

doi

10.1111/chd.12407

subject

Has Abstract

pub_date

2017-01-01 00:00:00

pages

6-16

issue

1

eissn

1747-079X

issn

1747-0803

journal_volume

12

pub_type

  • Caregiver anxiety due to interstage feeding concerns.

    abstract:INTRODUCTION:Improved weight gain during the interstage (IS) period has been shown to improve overall outcomes in patients with single ventricle physiology (SVP). This emphasis on nutrition may have untoward effects, such as increasing anxiety/stress levels in caregivers, who are already known to be at risk for increas...

    journal_title:Congenital heart disease

    pub_type: 杂志文章

    doi:10.1111/chd.12257

    authors: Stewart J,Dempster R,Allen R,Miller-Tate H,Dickson G,Fichtner S,Principe AJ,Fonseca R,Nicholson L,Cua CL

    更新日期:2015-03-01 00:00:00

  • Acute and long-term effects of endovascular debanding of pulmonary arteries in a swine model.

    abstract:OBJECTIVES:The primary objective of this study was to demonstrate that pulmonary artery (PA) debanding via cardiac catheterization using balloon angioplasty is feasible and safe in swine. The secondary objectives were to determine the acute and long-term effects of this therapy. DESIGN:This is a chronic survival exper...

    journal_title:Congenital heart disease

    pub_type: 杂志文章

    doi:10.1111/chd.12449

    authors: Perez M,Kumar TS,Hoskoppal D,Akkhawattanangkul Y,Allen K,Knott-Craig CJ,Waller BR,Sathanandam S

    更新日期:2017-05-01 00:00:00

  • Overview of transcatheter patent ductus arteriosus closure in preterm infants.

    abstract::Clinically significant patent ductus arteriosus (PDA) has been associated with significant morbidity in extremely low birth weight (ELBW) infants. Current management of ELBW infants with hemodynamically significant PDA includes supportive treatment, pharmacological therapy, and surgical ligation. All of these therapeu...

    journal_title:Congenital heart disease

    pub_type: 杂志文章,评审

    doi:10.1111/chd.12712

    authors: Almeida-Jones M,Tang NY,Reddy A,Zahn E

    更新日期:2019-01-01 00:00:00

  • Population-based assessment of familial inheritance and neurologic comorbidities among patients with an isolated atrial septal defect.

    abstract:BACKGROUND:Interatrial shunts, caused by either atrial septal defect (ASD) or patent foramen ovale, have been reported to have a familial association. We sought to examine the familial risk of isolated interatrial shunt and explore associated comorbidities of stroke, transient ischemic attack (TIA), and migraine using ...

    journal_title:Congenital heart disease

    pub_type: 杂志文章

    doi:10.1111/j.1747-0803.2009.00340.x

    authors: Steenblik MH,Mineau GP,Pimentel R,Michaels AD

    更新日期:2009-11-01 00:00:00

  • Rates of autism and potential risk factors in children with congenital heart defects.

    abstract:OBJECTIVE:Atypical development, behavioral difficulties, and academic underachievement are common morbidities in children with a history of congenital heart defects and impact quality of life. Language and social-cognitive deficits have been described, which are associated with autism spectrum disorders. The current st...

    journal_title:Congenital heart disease

    pub_type: 杂志文章

    doi:10.1111/chd.12461

    authors: Bean Jaworski JL,Flynn T,Burnham N,Chittams JL,Sammarco T,Gerdes M,Bernbaum JC,Clancy RR,Solot CB,Zackai EH,McDonald-McGinn DM,Gaynor JW

    更新日期:2017-07-01 00:00:00

  • Stress echocardiography: An overview for use in pediatric and congenital cardiology.

    abstract::Currently, the role of stress echocardiography primarily resides in diagnosing acquired coronary artery disease (CAD) in adults. Besides an increasing concern for traditional CAD in young patients due to obesity and other chronic pediatric diseases, there is also a growing population of adolescents and young adults wi...

    journal_title:Congenital heart disease

    pub_type: 杂志文章,评审

    doi:10.1111/chd.12495

    authors: Ermis P

    更新日期:2017-09-01 00:00:00

  • Cardiovascular magnetic resonance imaging in congenital heart disease as an alternative to diagnostic invasive cardiac catheterization: a single center experience.

    abstract:OBJECTIVE:The study aims to assess whether the increasing use of cardiovascular magnetic resonance imaging in place of diagnostic cardiac catheterization in the management of pediatric patients with congenital heart disease has had an impact on pediatric cardiac care. DESIGN:Retrospective analysis of data was used. S...

    journal_title:Congenital heart disease

    pub_type: 杂志文章

    doi:10.1111/chd.12032

    authors: Heathfield E,Hussain T,Qureshi S,Valverde I,Witter T,Douiri A,Bell A,Beerbaum P,Razavi R,Greil GF

    更新日期:2013-07-01 00:00:00

  • COMPASS: a novel risk-adjustment model for catheter ablation in pediatric and congenital heart disease patients.

    abstract:BACKGROUND:Robust risk-adjustment algorithms are often necessary if data from clinical registries is to be used to compare rates of important clinical outcomes between participating centers. Although such algorithms have been successfully developed for surgical and catheter-based cardiac interventions in children, outc...

    journal_title:Congenital heart disease

    pub_type: 杂志文章,多中心研究

    doi:10.1111/chd.12050

    authors: Triedman JK,Pfeiffer P,Berman A,Blaufox AD,Cannon BC,Fish FA,Perry J,Pflaumer A,Seslar SP,Pediatric and Congenital Electrophysiology Society (PACES) MAP-IT Taskforce.

    更新日期:2013-09-01 00:00:00

  • Current Practice and Utility of Chromosome Microarray Analysis in Infants Undergoing Cardiac Surgery.

    abstract:OBJECTIVE:Traditionally, karyotype and fluorescence in situ hybridization (FISH) were used for cytogenetic testing of infants with congenital heart disease (CHD) who underwent cardiac surgery at our institution. Recently, chromosome microarray analysis (CMA) has been performed in lieu of the traditional tests. A standa...

    journal_title:Congenital heart disease

    pub_type: 杂志文章

    doi:10.1111/chd.12241

    authors: Buckley JR,Kavarana MN,Chowdhury SM,Scheurer MA

    更新日期:2015-05-01 00:00:00

  • Adverse effects of amiodarone therapy in adults with congenital heart disease.

    abstract:OBJECTIVE:Amiodarone is a highly effective antiarrhythmic therapy, however its toxicity profile often limits treatment. This is particularly relevant in adults with congenital heart disease (CHD), who are often young and in whom other antiarrhythmic agents commonly fail or are contraindicated. We sought to determine in...

    journal_title:Congenital heart disease

    pub_type: 杂志文章

    doi:10.1111/chd.12657

    authors: Moore BM,Cordina RL,McGuire MA,Celermajer DS

    更新日期:2018-11-01 00:00:00

  • Spontaneous closure of a symptomatic coronary artery fistula just within a few days of newborn period.

    abstract::We present a rare case of spontaneous closure of a fistula between the left coronary artery and the right ventricle (RV) within a few days of newborn period. A 14-day-old male newborn was referred to our clinic for investigation of tachypnea and cardiac murmur. A color flow Doppler echocardiography revealed turbulent ...

    journal_title:Congenital heart disease

    pub_type: 杂志文章

    doi:10.1111/chd.12060

    authors: Yilmazer MM,Demir F,Yolbaş I,Bilici M

    更新日期:2014-01-01 00:00:00

  • Chances of employment in women and men after surgery of congenital heart disease: comparisons between patients and the general population.

    abstract:OBJECTIVE:It was examined whether women and men (17-45 years) with operated congenital heart disease differ with respect to chances of employment. Patients were compared with the general population. DESIGN:Patients (n = 314) were classified by type of surgery (curative, reparative, palliative) as indicator of initial ...

    journal_title:Congenital heart disease

    pub_type: 杂志文章

    doi:10.1111/j.1747-0803.2008.00239.x

    authors: Geyer S,Norozi K,Buchhorn R,Wessel A

    更新日期:2009-01-01 00:00:00

  • Platelet activation markers in children with congenital heart disease associated with pulmonary arterial hypertension.

    abstract:BACKGROUND:Mean platelet volume (MPV), platecrit, and platelet distribution width (PDW) are markers of platelet activation. Previous studies have found that platelet activation occurs in patients with pulmonary arterial hypertension. Platelet indices including MPV, PDW, and platecrit have not been studied in children w...

    journal_title:Congenital heart disease

    pub_type: 杂志文章

    doi:10.1111/chd.12616

    authors: Mese T,Guven B,Yilmazer MM,Karadeniz C,Ozdemir R,Doksoz O

    更新日期:2018-07-01 00:00:00

  • Congenital portosystemic venous connections and other abdominal venous abnormalities in patients with polysplenia and functionally univentricular heart disease: a case series and literature review.

    abstract:OBJECTIVE:Published case reports suggest that congenital portosystemic venous connections (PSVC) and other abdominal venous anomalies may be relatively frequent and potentially important in patients with polysplenia syndrome. Our objective was to investigate the frequency and range of portal and other abdominal systemi...

    journal_title:Congenital heart disease

    pub_type: 杂志文章,评审

    doi:10.1111/j.1747-0803.2010.00478.x

    authors: McElhinney DB,Marx GR,Newburger JW

    更新日期:2011-01-01 00:00:00

  • Long-term cardiovascular outcome of Williams syndrome.

    abstract:OBJECTIVE:Cardiovascular lesions are the leading cause of morbidity and mortality in patients with Williams syndrome. Recent studies have rebutted conventional reports about the natural course of cardiovascular anomalies in Williams syndrome. DESIGN:Retrospective study. SETTING:Single tertiary center. PATIENTS:Eight...

    journal_title:Congenital heart disease

    pub_type: 杂志文章

    doi:10.1111/chd.12810

    authors: Cha SG,Song MK,Lee SY,Kim GB,Kwak JG,Kim WH,Bae EJ

    更新日期:2019-09-01 00:00:00

  • Endovascular stenting for native coarctation of the aorta is an effective alternative to surgical intervention in older children.

    abstract:OBJECTIVE:Assess the early and intermediate results with respect to blood pressure control in older children undergoing endovascular stenting for native coarctation of the aorta. DESIGN:Eleven hypertensive patients (10 +/- 3 years of age) underwent endovascular stenting via standard techniques for native coarctation o...

    journal_title:Congenital heart disease

    pub_type: 杂志文章

    doi:10.1111/j.1747-0803.2007.00148.x

    authors: Weber HS,Cyran SE

    更新日期:2008-01-01 00:00:00

  • Efficiency of the home cardiac rehabilitation program for adults with complex congenital heart disease.

    abstract:OBJECTIVE:We aimed to study the efficiency and safety of once-a-week outpatient rehabilitation followed by home program with tele-monitoring in patients with complex cyanotic congenital heart disease. DESIGN:Prospective nonrandomized study. METHOD:Patients who have been diagnosed either Eisenmenger's syndrome or inop...

    journal_title:Congenital heart disease

    pub_type: 杂志文章

    doi:10.1111/chd.12659

    authors: Bhasipol A,Sanjaroensuttikul N,Pornsuriyasak P,Yamwong S,Tangcharoen T

    更新日期:2018-11-01 00:00:00

  • Knowledge and attitudes of anesthesia providers about noncardiac surgery in adults with congenital heart disease.

    abstract:OBJECTIVE:To examine the knowledge and attitudes of anesthesia providers in relation to the care of adult congenital heart disease (ACHD) patients presenting for noncardiac surgery. DESIGN/SETTING:A novel survey was designed and administered to 168 anesthesiologists across a single academic department in a range of pr...

    journal_title:Congenital heart disease

    pub_type: 杂志文章

    doi:10.1111/chd.12076

    authors: Maxwell BG,Williams GD,Ramamoorthy C

    更新日期:2014-01-01 00:00:00

  • Effect of Left Cardiac Sympathetic Denervation on the Electromechanical Window in Patients with either Type 1 or Type 2 Long QT Syndrome: A Pilot Study.

    abstract:BACKGROUND:Left cardiac sympathetic denervation (LCSD) exerts significant antifibrillatory effects in patients with long QT syndrome (LQTS). Recently, electromechanical window (EMW) has emerged as a novel torsadogenic marker in LQTS, superior to QT interval (QTc) in distinguishing symptomatic from asymptomatic patients...

    journal_title:Congenital heart disease

    pub_type: 杂志文章

    doi:10.1111/chd.12332

    authors: Schneider AE,Bos JM,Ackerman MJ

    更新日期:2016-09-01 00:00:00

  • Electronic health record associated stress: A survey study of adult congenital heart disease specialists.

    abstract:BACKGROUND:Physician burnout has many undesirable consequences, including negative impact on patient care delivery and physician career satisfaction. Electronic health records (EHRs) may exacerbate burnout by increasing physician workload. OBJECTIVE:To determine burnout in adult congenital heart disease (ACHD) special...

    journal_title:Congenital heart disease

    pub_type: 杂志文章

    doi:10.1111/chd.12745

    authors: Marckini DN,Samuel BP,Parker JL,Cook SC

    更新日期:2019-05-01 00:00:00

  • A different therapeutic strategy for severe tetralogy of Fallot with origin of the left pulmonary artery from the ascending aorta: stenting of the right ventricular outflow tract before complete repair.

    abstract::The origin of pulmonary artery branches (particularly the left pulmonary artery) from the ascending aorta is a rare condition. We detected prominent hypoplasia of the main and right pulmonary arteries in a 3.5-month-old 3.7 kg female infant who had tetralogy of Fallot with origin of the left pulmonary artery in the as...

    journal_title:Congenital heart disease

    pub_type: 杂志文章

    doi:10.1111/j.1747-0803.2011.00542.x

    authors: Saritas T,Erdem A,Karaci AR,Demir F,Celebi A

    更新日期:2012-05-01 00:00:00

  • Transcatheter aortic valve implantation in surgically repaired double outlet right ventricle.

    abstract::A 52-year-old male patient, with a medical history of surgically repaired double outlet right ventricle presented with severe aortic stenosis (AS) and hepatitis C with cirrhosis, presented with New York Heart Association Class IV heart failure. During evaluation for a liver transplant, he was deemed a poor surgical ca...

    journal_title:Congenital heart disease

    pub_type: 杂志文章,评审

    doi:10.1111/chd.12114

    authors: Keswani A,Verma A,Dann K,Ventura L,Lucas V,Shah S,Ramee S

    更新日期:2014-09-01 00:00:00

  • Clinical, echocardiographic, and therapeutic aspects of congenital heart diseases of children at Douala General Hospital: A cross-sectional study in sub-Saharan Africa.

    abstract:INTRODUCTION:Cardiovascular diseases in pediatric pathologies have emerged in the recent years in sub-Saharan Africa (SSA), with congenital heart diseases (CHDs) being the most frequent. Unfortunately, their diagnosis is usually delayed, thereby increasing childhood morbidity and mortality. OBJECTIVES:Describe the cli...

    journal_title:Congenital heart disease

    pub_type: 杂志文章

    doi:10.1111/chd.12529

    authors: Kamdem F,Kedy Koum D,Hamadou B,Yemdji M,Luma H,Doualla MS,Noukeu D,Barla E,Akazong C,Dzudie A,Ngote H,Monkam Y,Mouliom S,Kingue S

    更新日期:2018-01-01 00:00:00

  • Evaluation of Neurodevelopment Using Bayley-III in Children with Cyanotic or Hemodynamically Impaired Congenital Heart Disease.

    abstract:OBJECTIVE:The purpose of this study was to compare neurological development of children with cyanotic or hemodynamically impaired congenital heart disease (CHD) and healthy controls by using "Bayley Scales of Infant and Toddler Development Screening Test, Third Edition" (Bayley-III). PATIENTS:Children with CHD (n = 37...

    journal_title:Congenital heart disease

    pub_type: 杂志文章

    doi:10.1111/chd.12269

    authors: Hallioglu O,Gurer G,Bozlu G,Karpuz D,Makharoblidze K,Okuyaz C

    更新日期:2015-11-01 00:00:00

  • Deciding without data.

    abstract:INTRODUCTION:Physician decisions drive most of the increases in health care expenditures, yet virtually no published literature has sought to understand the types of evidence used by physicians as they make decisions in real time. METHODS:Ten pediatric cardiologists recorded every clinically significant decision made ...

    journal_title:Congenital heart disease

    pub_type: 杂志文章

    doi:10.1111/j.1747-0803.2010.00433.x

    authors: Darst JR,Newburger JW,Resch S,Rathod RH,Lock JE

    更新日期:2010-07-01 00:00:00

  • Dysphagia in infants with single ventricle anatomy following stage 1 palliation: Physiologic correlates and response to treatment.

    abstract:BACKGROUND:Deficits in swallowing physiology are a leading morbidity for infants with functional single ventricles and systemic outflow tract obstruction following stage 1 palliation. Despite the high prevalence of this condition, the underlying deficits that cause this post-operative impairment remain poorly understoo...

    journal_title:Congenital heart disease

    pub_type: 杂志文章,多中心研究

    doi:10.1111/chd.12456

    authors: McGrattan KE,McGhee H,DeToma A,Hill EG,Zyblewski SC,Lefton-Greif M,Halstead L,Bradley SM,Martin-Harris B

    更新日期:2017-05-01 00:00:00

  • Hemodynamic effects of ketamine in children with congenital heart disease and/or pulmonary hypertension.

    abstract:INTRODUCTION:Ketamine is a drug often used for procedural sedation or as adjunct agent for general sedation in children with congenital heart disease. In the clinical realm, there is often confusion regarding the effects of ketamine on hemodynamics, particularly pulmonary vascular resistance and systemic vascular resis...

    journal_title:Congenital heart disease

    pub_type: 杂志文章

    doi:10.1111/chd.12662

    authors: Loomba RS,Gray SB,Flores S

    更新日期:2018-09-01 00:00:00

  • Congenital left ventricular splint in an adult patient with unrepaired anomalous left coronary artery from the pulmonary artery.

    abstract::A 24-year-old woman presented with a recent increase in dyspnea on exertion and development of presyncope. The patient stated that she has reproducible episodes of dizziness and near fainting when she climbs a flight of stairs and activity is limited to a slow gait. ...

    journal_title:Congenital heart disease

    pub_type: 杂志文章

    doi:10.1111/j.1747-0803.2007.00110.x

    authors: Sabbath AM,Trivedi K,Klewer SE,Sorrell VL

    更新日期:2007-07-01 00:00:00

  • A case of life-threatening Staphylococcus aureus endocarditis involving percutaneous transcatheter prosthetic pulmonary valve.

    abstract::While right ventricle to pulmonary artery homograft is the surgical procedure of choice for relieving right ventricle outflow tract obstruction; it is limited by the need for multiple surgical replacements owing to progressive conduit obstruction, valve dysfunction, or patient growth. Since January 2010, percutaneous ...

    journal_title:Congenital heart disease

    pub_type: 杂志文章

    doi:10.1111/chd.12013

    authors: Bhat DP,Forbes TJ,Aggarwal S

    更新日期:2013-11-01 00:00:00

  • Atresia of abdominal aorta in neonate with recanalization and development of normal aortic architecture: case report and review of literature.

    abstract::This is a case report reviewing the presentation and clinical course of a patient diagnosed with abdominal aortic atresia at the level caudal to the superior mesenteric artery. Patients with abdominal aortic atresia need to be evaluated for associated underlying syndromes or diseases. Although the prognosis for this d...

    journal_title:Congenital heart disease

    pub_type: 杂志文章,评审

    doi:10.1111/j.1747-0803.2010.00454.x

    authors: Brown J,Shehata BM,Campbell R

    更新日期:2011-05-01 00:00:00