Fetal heart size measurements as new predictors of homozygous α-thalassemia-1 in mid-pregnancy.

abstract：BACKGROUND:Patients with a Fontan circulation are at risk of renal dysfunction. We analyzed cross-sectional data in pediatric and adult Fontan patients in order to assess the accuracy of commonly used serum creatinine-based methods in estimating glomerular filtration rate (GFR). METHODS:A total of 124 Fontan patients ...

journal_title：Congenital heart disease

authors： Wilson TG,d'Udekem Y,Winlaw DS,Cordina RL,Ayer J,Gentles TL,Weintraub RG,Grigg LE,Cheung M,Cain TM,Rao P,Verrall C,Plessis KD,Rice K,Iyengar AJ

更新日期：2019-05-01 00:00:00

abstract：:In medical literature, few cases of Rasmussen's aneurysm have been reported until now, and to the best of our knowledge, there has been no description of a case of Rasmussen's aneurysm in childhood. The child described in the case report had a restrictive cardiomyopathy, complicated by pulmonary hypertension, in assoc...

journal_title：Congenital heart disease

authors： Gesuete V,Corzani A,Bronzetti G,Lovato L,Picchio FM

更新日期：2013-03-01 00:00:00

abstract：INTRODUCTION:Ketamine is a drug often used for procedural sedation or as adjunct agent for general sedation in children with congenital heart disease. In the clinical realm, there is often confusion regarding the effects of ketamine on hemodynamics, particularly pulmonary vascular resistance and systemic vascular resis...

journal_title：Congenital heart disease

authors： Loomba RS,Gray SB,Flores S

更新日期：2018-09-01 00:00:00

abstract：OBJECTIVE:To describe treatment, survival, and morbidity for liveborn infants with isolated transposition of great arteries (TGA). DESIGN:Population-based data from 7 European registries of congenital malformations (EUROCAT). RESULTS:Ninety-seven infants were diagnosed with isolated TGA and livebirth prevalence was 2...

journal_title：Congenital heart disease

authors： Garne E,Loane MA,Nelen V,Bakker MK,Gener B,Abramsky L,Addor MC,Queisser-Luft A

更新日期：2007-05-01 00:00:00

abstract：OBJECTIVE:The aims of this study were to compare the level of posttraumatic stress disorder between adults with and without congenital heart disease, and to examine the correlates of posttraumatic stress disorder (e.g., sociodemographics). DESIGN:Cross-sectional. SETTING:Two university-affiliated heart hospitals in T...

journal_title：Congenital heart disease

authors： Eslami B

更新日期：2017-05-01 00:00:00

abstract：:We report the use of the Amplatzer Duct Occluder for transcatheter closure of a rare subclavian artery to innominate vein fistula in a neonate. ...

journal_title：Congenital heart disease

authors： Evans K,Jones TK,Johnston TA

更新日期：2006-01-01 00:00:00

abstract：OBJECTIVE:Enteral feeding is associated with decreased infection rates, decreased mechanical ventilation, decreased hospital length of stay, and improved wound healing. Enteral feeding difficulties are common in congenital heart disease. Our objective was to develop experience-based newborn feeding guidelines for the i...

journal_title：Congenital heart disease

authors： Simsic JM,Carpenito KR,Kirchner K,Peters S,Miller-Tate H,Joy B,Galantowicz M

更新日期：2017-05-01 00:00:00

abstract：:So-called heterotaxy affects lateralization of the thoracic and abdominal organs. Congenital malformations may be present in one of several organ systems. Cardiac involvement includes both structural and conduction abnormalities. Data regarding arrhythmias in heterotaxy come from case reports and small case series. We...

journal_title：Congenital heart disease

authors： Loomba RS,Willes RJ,Kovach JR,Anderson RH

更新日期：2016-01-01 00:00:00

abstract：BACKGROUND:Children and adolescents with congenital heart disease (CHD) and their families require qualified combined medical and psychosocial information, care, and counseling. This study aimed to analyze CHD patients' and parents' perception of disease-specific knowledge, state of health, and impairments experienced ...

journal_title：Congenital heart disease

authors： Helm PC,Kempert S,Körten MA,Lesch W,Specht K,Bauer UMM

更新日期：2018-05-01 00:00:00

abstract：OBJECTIVE:The objective of this study was to characterize the natural history of metabolic uncoupling (type B hyperlactemia and hyperglycemia) following cardiopulmonary bypass (CPB), and to determine the impact of insulin therapy on time to lactate normalization in patients without low cardiac output. DESIGN:The desig...

journal_title：Congenital heart disease

authors： Palermo RA,Palac HL,Wald EL,Wainwright MS,Costello JM,Eltayeb OM,Backer CL,Epting CL

更新日期：2015-11-01 00:00:00

abstract：OBJECTIVE:Arterial switch operation has become the treatment of choice for neonates with transposition of the great arteries. The most important step of the procedure is transferring the coronary arteries to the neoaorta successfully. This study shows the impact of coronary anatomy on early mortality and morbidity afte...

journal_title：Congenital heart disease

authors： Altin FH,Sengul FS,Yildiz O,Tosun O,Ozturk E,Kyaruzi M,Cine N,Guzeltas A,Yeniterzi M,Bakir İ

更新日期：2016-03-01 00:00:00

abstract：OBJECTIVE:Intraatrial Mustard baffle repair of dextro-transposition of the great arteries (d-TGA) is vulnerable to complications, typically obstruction and leaks. Because patients often require pacemakers or intracardiac electrophysiology studies (EPS)/ablation for arrhythmias, narrowed or obstructed baffles restrict c...

journal_title：Congenital heart disease

authors： Patel S,Shah D,Chintala K,Karpawich PP

更新日期：2011-09-01 00:00:00

abstract：OBJECTIVE:It was examined whether women and men (17-45 years) with operated congenital heart disease differ with respect to chances of employment. Patients were compared with the general population. DESIGN:Patients (n = 314) were classified by type of surgery (curative, reparative, palliative) as indicator of initial ...

journal_title：Congenital heart disease

authors： Geyer S,Norozi K,Buchhorn R,Wessel A

更新日期：2009-01-01 00:00:00

abstract：:Clinically significant patent ductus arteriosus (PDA) has been associated with significant morbidity in extremely low birth weight (ELBW) infants. Current management of ELBW infants with hemodynamically significant PDA includes supportive treatment, pharmacological therapy, and surgical ligation. All of these therapeu...

journal_title：Congenital heart disease

authors： Almeida-Jones M,Tang NY,Reddy A,Zahn E

更新日期：2019-01-01 00:00:00

abstract：:Crisscross heart is a rare congenital cardiac anomaly in which systemic and pulmonary venous streams cross without mixing at atrioventricular level. We report a case of crisscross heart with tricuspid atresia, double outlet right ventricle, and pulmonary stenosis, which was diagnosed prenatally. ...

journal_title：Congenital heart disease

authors： Ayabakan C,Binnetoğlu K,Sarısoy Ö,Tokel K

更新日期：2013-09-01 00:00:00

abstract：:A genetic basis of congenital heart disease (CHD) has been known for decades. In addition to the sequence of the genome, the contribution of epigenetics to pediatric cardiology is increasingly recognized. Multiple epigenetic mechanisms, including DNA methylation, histone modification, and RNA-based regulation, are kno...

journal_title：Congenital heart disease

authors： Spearman AD

更新日期：2017-12-01 00:00:00

abstract：OBJECTIVE:Patients undergoing surgical repair of aortic coarctation have a 50% risk of pathologic left ventricular remodeling (increased left ventricular mass or relative wall thickness). Endothelin 1, ST2, galectin 3, norepinephrine and B-natriuretic peptide are biomarkers that have been associated with pathologic LV ...

journal_title：Congenital heart disease

authors： Frank BS,Urban TT,Lewis K,Tong S,Cassidy C,Mitchell MB,Nichols CS,Davidson JA

更新日期：2019-05-01 00:00:00

abstract：OBJECTIVE:Determine the accuracy of echocardiography to diagnose coronary anatomy in transposition of the great arteries and to evaluate the effect of accuracy on surgical outcomes and changes in accuracy over time. DESIGN:Retrospective chart review of neonates admitted February 1999 to March 2013 with transposition. ...

journal_title：Congenital heart disease

authors： Fundora MP,Aregullin EO,Wernovsky G,Welch EM,Muniz JC,Sasaki N,Hannan RL,Burke RP,Lopez L

更新日期：2016-12-01 00:00:00

abstract：OBJECTIVE:Published case reports suggest that congenital portosystemic venous connections (PSVC) and other abdominal venous anomalies may be relatively frequent and potentially important in patients with polysplenia syndrome. Our objective was to investigate the frequency and range of portal and other abdominal systemi...

journal_title：Congenital heart disease

authors： McElhinney DB,Marx GR,Newburger JW

更新日期：2011-01-01 00:00:00

abstract：BACKGROUND:Hyponatremia (HN) is relatively common in adults with congenital heart disease and is a powerful predictor of mortality. However, the precise relationship of HN to the Fontan pathophysiology remains unknown. PURPOSE:Our study aimed to clarify the association of HN to the Fontan pathophysiology. METHODS AND...

journal_title：Congenital heart disease

authors： Ohuchi H,Negishi J,Ono S,Miyake A,Toyota N,Tamaki W,Miyazaki A,Yamada O

更新日期：2011-07-01 00:00:00

abstract：PURPOSE:Right ventricular (RV) failure and ventricular dyssynchrony are strong determinants of prognosis in patients with adult congenital heart disease (ACHD). The aim of this study was to investigate the relationship between interventricular dyssynchrony (IVD) using cine-tagged magnetic resonance imaging (MRI) and RV...

journal_title：Congenital heart disease

authors： Nagao M,Yamasaki Y,Yonezawa M,Matsuo Y,Kamitani T,Yamamura K,Sakamoto I,Abe K,Kawanami S,Honda H

更新日期：2015-05-01 00:00:00

abstract：:We report the case of a 30 year-old male with congenitally corrected transposition of the great arteries, atrial, and ventricular septal defects (VSD), and pulmonary stenosis. He previously underwent three palliative surgical procedures before undergoing intracardiac repair at age 20 with a left ventricular to pulmona...

journal_title：Congenital heart disease

authors： Aboulhosn J,Levi D,Sopher M,Johnson A,Child JS,Laks H

更新日期：2010-01-01 00:00:00

abstract：INTRODUCTION:Surveillance and management guidelines for Fontan patients are lacking due to the paucity of evidence in the literature of screening efficacy on outcome measures. METHODS:The Fontan Working Group within the New England Congenital Cardiology Association designed an electronic survey to assess surveillance ...

journal_title：Congenital heart disease

authors： Davey BT,Toro-Salazar OH,Gauthier N,Valente AM,Elder RW,Wu FM,Berman N,Pollack P,Lee JH,Rathod RH

更新日期：2019-11-01 00:00:00

abstract：BACKGROUND AND AIMS:Patients who underwent a successful repair of the aortic coarctation show chronic hyperdynamic state and normal left ventricular (LV) geometry; however, there are few data regarding the LV systolic function in the long term. Accordingly, we assessed LV systolic mechanics and factors associated with ...

journal_title：Congenital heart disease

authors： Faganello G,Fisicaro M,Russo G,Iorio A,Mazzone C,Grande E,Humar F,Cherubini A,Pandullo C,Barbati G,Tarantini L,Benettoni A,Pozzi M,Di Lenarda A,Cioffi G

更新日期：2016-05-01 00:00:00

abstract：OBJECTIVE:The study aims to assess whether the increasing use of cardiovascular magnetic resonance imaging in place of diagnostic cardiac catheterization in the management of pediatric patients with congenital heart disease has had an impact on pediatric cardiac care. DESIGN:Retrospective analysis of data was used. S...

journal_title：Congenital heart disease

authors： Heathfield E,Hussain T,Qureshi S,Valverde I,Witter T,Douiri A,Bell A,Beerbaum P,Razavi R,Greil GF

更新日期：2013-07-01 00:00:00

abstract：OBJECTIVE:The surgical management of adults with congenital heart disease (ACHD) offers a great challenge, with a large number of anomalies with complex pathophysiology necessitating specific treatments. Pre- and postoperative morbidity has been relatively high, and the influencing factors are not completely identified...

journal_title：Congenital heart disease

authors： Nozohoor S,Gustafsson R,Kallonen J,Sjögren J

更新日期：2013-07-01 00:00:00

abstract：OBJECTIVE:We sought to define what clinical parameters were related to the ultimate outcome in Fontan patients who had developed protein-losing enteropathy (PLE). BACKGROUND:PLE is a serious complication of the Fontan operation. Several preoperative and perioperative findings are associated with later PLE. However, th...

journal_title：Congenital heart disease

authors： Silvilairat S,Cabalka AK,Cetta F,Grogan M,Hagler DJ,O'Leary PW

更新日期：2008-07-01 00:00:00

abstract：OBJECTIVE:Cardiovascular lesions are the leading cause of morbidity and mortality in patients with Williams syndrome. Recent studies have rebutted conventional reports about the natural course of cardiovascular anomalies in Williams syndrome. DESIGN:Retrospective study. SETTING:Single tertiary center. PATIENTS:Eight...

journal_title：Congenital heart disease

authors： Cha SG,Song MK,Lee SY,Kim GB,Kwak JG,Kim WH,Bae EJ

更新日期：2019-09-01 00:00:00

abstract：OBJECTIVE:  The objective of this study is to evaluate the safety and feasibility of the AZUR hydrogel-polymer coated platinum coil (hydrocoil) for vascular occlusion in patients with congenital cardiovascular disease (CCVD). DESIGN:  Retrospective case review. PATIENTS:  Eight patients with CCVD who underwent attemp...

journal_title：Congenital heart disease

authors： Goldstein BH,Aiyagari R,Bocks ML,Armstrong AK

更新日期：2012-05-01 00:00:00

abstract：:Carditis is a common manifestation of adult patients with Lyme disease affecting 4-10% of Lyme patients in the United States. However, children with Lyme disease rarely present with acute carditis. The management of pediatric patients with complete heart block (CHB) secondary to Lyme carditis has not been well describ...

journal_title：Congenital heart disease

authors： Silver E,Pass RH,Kaufman S,Hordof AJ,Liberman L

更新日期：2007-09-01 00:00:00