Hyponatremia and its association with the neurohormonal activity and adverse clinical events in children and young adult patients after the Fontan operation.

abstract：OBJECTIVE:Traditionally, karyotype and fluorescence in situ hybridization (FISH) were used for cytogenetic testing of infants with congenital heart disease (CHD) who underwent cardiac surgery at our institution. Recently, chromosome microarray analysis (CMA) has been performed in lieu of the traditional tests. A standa...

journal_title：Congenital heart disease

authors： Buckley JR,Kavarana MN,Chowdhury SM,Scheurer MA

更新日期：2015-05-01 00:00:00

abstract：OBJECTIVE:The objective of this study was to characterize the natural history of metabolic uncoupling (type B hyperlactemia and hyperglycemia) following cardiopulmonary bypass (CPB), and to determine the impact of insulin therapy on time to lactate normalization in patients without low cardiac output. DESIGN:The desig...

journal_title：Congenital heart disease

authors： Palermo RA,Palac HL,Wald EL,Wainwright MS,Costello JM,Eltayeb OM,Backer CL,Epting CL

更新日期：2015-11-01 00:00:00

abstract：BACKGROUND:Patients with a Fontan circulation are at risk of renal dysfunction. We analyzed cross-sectional data in pediatric and adult Fontan patients in order to assess the accuracy of commonly used serum creatinine-based methods in estimating glomerular filtration rate (GFR). METHODS:A total of 124 Fontan patients ...

journal_title：Congenital heart disease

authors： Wilson TG,d'Udekem Y,Winlaw DS,Cordina RL,Ayer J,Gentles TL,Weintraub RG,Grigg LE,Cheung M,Cain TM,Rao P,Verrall C,Plessis KD,Rice K,Iyengar AJ

更新日期：2019-05-01 00:00:00

abstract：:Iron deficiency state in patients with cyanotic congenital heart disease can mimic as well as aggravate hyperviscosity symptoms. Correction of iron deficiency in these cases is expected to improve symptoms. We report an unexpected occurrence of refractory cyanotic spell in a child with tetralogy of Fallot due to throm...

journal_title：Congenital heart disease

authors： Gupta SK,Saxena A,Anil OM,Bisoi AK

更新日期：2012-07-01 00:00:00

abstract：OBJECTIVE:Stent placement has become a widely used method of treatment for coarctation of the aorta (COA). Our goal was to find echocardiographic indices that would correlate best with directly measured gradients across the coarctation stent. MATERIAL AND METHODS:Pediatric patients with COA who underwent intra-aortic ...

journal_title：Congenital heart disease

authors： Tang L,Forbes TJ,Du W,Zilberman MV

更新日期：2009-07-01 00:00:00

abstract：:We describe a simple technique for chest wall reconstruction in pentalogy of Cantrell using split-thickness cartilage grafts. This technique provides a robust reconstruction, gives immediate and excellent cosmetic results, allows for skeletal and tissue growth, and avoids the use of synthetic material. ...

journal_title：Congenital heart disease

authors： Grudziak J,Kogon B

更新日期：2013-01-01 00:00:00

abstract：INTRODUCTION:The neurodevelopmental outcome of children with repaired congenital heart defect has risen in importance with improved survival. This study compares neurodevelopmental outcomes of children who had CHD with single ventricle physiology with those who had CHD with two-ventricle physiology. PATIENTS AND METHO...

journal_title：Congenital heart disease

authors： Hoskoppal A,Roberts H,Kugler J,Duncan K,Needelman H

更新日期：2010-03-01 00:00:00

abstract：OBJECTIVE:To describe treatment, survival, and morbidity for liveborn infants with isolated transposition of great arteries (TGA). DESIGN:Population-based data from 7 European registries of congenital malformations (EUROCAT). RESULTS:Ninety-seven infants were diagnosed with isolated TGA and livebirth prevalence was 2...

journal_title：Congenital heart disease

authors： Garne E,Loane MA,Nelen V,Bakker MK,Gener B,Abramsky L,Addor MC,Queisser-Luft A

更新日期：2007-05-01 00:00:00

abstract：BACKGROUND:Interatrial shunts, caused by either atrial septal defect (ASD) or patent foramen ovale, have been reported to have a familial association. We sought to examine the familial risk of isolated interatrial shunt and explore associated comorbidities of stroke, transient ischemic attack (TIA), and migraine using ...

journal_title：Congenital heart disease

authors： Steenblik MH,Mineau GP,Pimentel R,Michaels AD

更新日期：2009-11-01 00:00:00

abstract：AIM:The Fontan circulation is highly dependent on ventilation, improving pulmonary blood flow and cardiac output. A reduced ventilatory function is reported in these patients. The extent of this impairment and its relation to exercise capacity and quality of life is unknown and objective of this study. METHODS:This mu...

journal_title：Congenital heart disease

authors： Callegari A,Neidenbach R,Milanesi O,Castaldi B,Christmann M,Ono M,Müller J,Ewert P,Hager A

更新日期：2019-03-01 00:00:00

abstract：INTRODUCTION:Cardiovascular diseases in pediatric pathologies have emerged in the recent years in sub-Saharan Africa (SSA), with congenital heart diseases (CHDs) being the most frequent. Unfortunately, their diagnosis is usually delayed, thereby increasing childhood morbidity and mortality. OBJECTIVES:Describe the cli...

journal_title：Congenital heart disease

authors： Kamdem F,Kedy Koum D,Hamadou B,Yemdji M,Luma H,Doualla MS,Noukeu D,Barla E,Akazong C,Dzudie A,Ngote H,Monkam Y,Mouliom S,Kingue S

更新日期：2018-01-01 00:00:00

abstract：OBJECTIVE:We previously identified a pathogenic germline DICER1 variant in a child with transposition of the great arteries who was a member of a family with DICER1 syndrome. In view of a report linking Dicer1 knockout in murine cardiomyocytes to cardiac outflow defects, we investigated the involvement of DICER1 in tra...

journal_title：Congenital heart disease

authors： Sabbaghian N,Digilio MC,Blue GM,Revil T,Winlaw DS,Foulkes WD

更新日期：2018-05-01 00:00:00

abstract：:In patients with Kawasaki disease (KD) and coronary artery aneurysms (CAAs), serial evaluation with multiple imaging modalities is recommended to guide risk stratification and management. We present the case of a 7-year-old boy with a history of KD and multiple giant CAAs who developed thrombosis in one of the aneurys...

journal_title：Congenital heart disease

authors： Prsa M,Hussain T,McCrindle BW,Grosse-Wortmann L

更新日期：2014-11-01 00:00:00

abstract：OBJECTIVES:The primary objective of this study was to demonstrate that pulmonary artery (PA) debanding via cardiac catheterization using balloon angioplasty is feasible and safe in swine. The secondary objectives were to determine the acute and long-term effects of this therapy. DESIGN:This is a chronic survival exper...

journal_title：Congenital heart disease

authors： Perez M,Kumar TS,Hoskoppal D,Akkhawattanangkul Y,Allen K,Knott-Craig CJ,Waller BR,Sathanandam S

更新日期：2017-05-01 00:00:00

abstract：OBJECTIVE:The study aims to assess whether the increasing use of cardiovascular magnetic resonance imaging in place of diagnostic cardiac catheterization in the management of pediatric patients with congenital heart disease has had an impact on pediatric cardiac care. DESIGN:Retrospective analysis of data was used. S...

journal_title：Congenital heart disease

authors： Heathfield E,Hussain T,Qureshi S,Valverde I,Witter T,Douiri A,Bell A,Beerbaum P,Razavi R,Greil GF

更新日期：2013-07-01 00:00:00

abstract：INTRODUCTION:Ketamine is a drug often used for procedural sedation or as adjunct agent for general sedation in children with congenital heart disease. In the clinical realm, there is often confusion regarding the effects of ketamine on hemodynamics, particularly pulmonary vascular resistance and systemic vascular resis...

journal_title：Congenital heart disease

authors： Loomba RS,Gray SB,Flores S

更新日期：2018-09-01 00:00:00

abstract：:Marfan syndrome is a well-described autosomal dominant syndrome with widely variable clinical manifestations. Cardiovascular complications include mitral valve prolapse with or without associated mitral valve insufficiency, aortic root dilatation, and most importantly the occasional development of aortic aneurysms or ...

journal_title：Congenital heart disease

authors： Zangwill SD,Brown MD,Bryke CR,Cava JR,Segura AD

更新日期：2006-09-01 00:00:00

abstract：OBJECTIVE:We sought to define what clinical parameters were related to the ultimate outcome in Fontan patients who had developed protein-losing enteropathy (PLE). BACKGROUND:PLE is a serious complication of the Fontan operation. Several preoperative and perioperative findings are associated with later PLE. However, th...

journal_title：Congenital heart disease

authors： Silvilairat S,Cabalka AK,Cetta F,Grogan M,Hagler DJ,O'Leary PW

更新日期：2008-07-01 00:00:00

abstract：BACKGROUND:Physician burnout has many undesirable consequences, including negative impact on patient care delivery and physician career satisfaction. Electronic health records (EHRs) may exacerbate burnout by increasing physician workload. OBJECTIVE:To determine burnout in adult congenital heart disease (ACHD) special...

journal_title：Congenital heart disease

authors： Marckini DN,Samuel BP,Parker JL,Cook SC

更新日期：2019-05-01 00:00:00

abstract：OBJECTIVE:The aims of this study were to compare the level of posttraumatic stress disorder between adults with and without congenital heart disease, and to examine the correlates of posttraumatic stress disorder (e.g., sociodemographics). DESIGN:Cross-sectional. SETTING:Two university-affiliated heart hospitals in T...

journal_title：Congenital heart disease

authors： Eslami B

更新日期：2017-05-01 00:00:00

abstract：OBJECTIVE:This study aimed to quantitatively compare findings of emotional functioning across studies of adolescents and adults with congenital heart disease (CHD) through meta-analysis. DESIGN:The current meta-analysis included 22 studies of adolescent and adult survivors of CHD who completed measures of emotional fu...

journal_title：Congenital heart disease

authors： Jackson JL,Misiti B,Bridge JA,Daniels CJ,Vannatta K

更新日期：2015-01-01 00:00:00

abstract：OBJECTIVE:The 2016 American Board of Pediatrics (ABP) content outline is comprehensive, including more than 50 cardiology-specific objectives within eight content areas. This study complements the quantitative analysis of a Kentucky-wide survey of trainees, pediatricians, and pediatric cardiologists asking them to iden...

journal_title：Congenital heart disease

authors： Neal AE,Lehto E,Miller KH,Davis E,Ziegler C

更新日期：2018-09-01 00:00:00

abstract：:Dilated cardiomyopathy and ventricular noncompaction have been reported in association with deletion 1p36 syndrome. Previous descriptions include echocardiographic and/or gross pathologic descriptions. There are no previous reports of microscopic findings. We report a case with descriptions of echocardiographic, gross...

journal_title：Congenital heart disease

authors： Pearce FB,Litovsky SH,Dabal RJ,Robin N,Dure LJ,George JF,Kirklin JK

更新日期：2012-01-01 00:00:00

abstract：:Transcatheter management of native coarctation of the aorta in 3 children with Turner syndrome is reported. Two children, 12 and 17 years of age, underwent stent implantation and 1 child, 3 years old, underwent balloon angioplasty alone. In all children the procedures were successful, both hemodynamically and angiogra...

journal_title：Congenital heart disease

authors： Kataoka K,Ozawa A,Inage A,Benson LN

更新日期：2006-11-01 00:00:00

abstract：:As physicians and caregivers of children with congenital heart disease, we are aware of the increasing need for procedures requiring anesthesia. While these procedures may be ideal for medical and cardiac surgical management, the risks and benefits must be assessed carefully. There are well known risks of cardiovascul...

journal_title：Congenital heart disease

authors： Char D,Ramamoorthy C,Wise-Faberowski L

更新日期：2016-05-01 00:00:00

abstract：:The Fontan operation has gone through multiple incarnations since Fontan and Baudet's initial description in 1971. Through the medical dossier of a patient with a single ventricle, we plot the history of medical, surgical, and percutaneous interventions over the past 40 years, specifically focusing on the Fontan proce...

journal_title：Congenital heart disease

authors： AboulHosn JA,Shavelle DM,Castellon Y,Criley JM,Plunkett M,Pelikan P,Dinh H,Child JS

更新日期：2007-01-01 00:00:00

abstract：:Appropriate interpretation of a screening test's validity poses a challenge to the clinician. The purpose of this review is to revisit the terms sensitivity, specificity, likelihood ratio, and pre- and posttest probability and their application to the clinical setting. For illustration, we use a recently published art...

journal_title：Congenital heart disease

authors： Bolin E,Lam W

更新日期：2013-09-01 00:00:00

abstract：OBJECTIVE:Atrial septal defect (ASD) is the second most common congenital heart defect (CHD) and is observed in families as an autosomal dominant trait as well as in nonfamilial CHD. Mutations in the NKX2-5 gene, located on chromosome 5, are associated with ASD, often combined with conduction disturbances, cardiomyopat...

journal_title：Congenital heart disease

authors： Ellesøe SG,Johansen MM,Bjerre JV,Hjortdal VE,Brunak S,Larsen LA

更新日期：2016-05-01 00:00:00

abstract：OBJECTIVE:Nurse practitioners (NPs) have an established role for delivering competent care to patients in the primary care setting. The aim of this study was to compare satisfaction of patients managed by NPs vs. physicians in the outpatient adult congenital heart disease (CHD) clinic. DESIGN:A prospective study condu...

journal_title：Congenital heart disease

authors： Maul TM,Zaidi A,Kowalski V,Hickey J,Schnug R,Hindes M,Cook S

更新日期：2015-09-01 00:00:00

abstract：OBJECTIVE:To examine the knowledge and attitudes of anesthesia providers in relation to the care of adult congenital heart disease (ACHD) patients presenting for noncardiac surgery. DESIGN/SETTING:A novel survey was designed and administered to 168 anesthesiologists across a single academic department in a range of pr...

journal_title：Congenital heart disease

authors： Maxwell BG,Williams GD,Ramamoorthy C

更新日期：2014-01-01 00:00:00