Pathologic features of dilated cardiomyopathy with localized noncompaction in a child with deletion 1p36 syndrome.

abstract：BACKGROUND:Pulmonary atresia with intact ventricular septum is a unique congenital malformation of the heart in which patients may undergo single-, two- or 1½- ventricle repair. Size of the tricuspid valve annulus, morphology of the right ventricle and presence of ventriculocoronary connections can all impact the selec...

journal_title：Congenital heart disease

authors： Loomba RS,Pelech AN

更新日期：2018-01-01 00:00:00

abstract：BACKGROUND:As the prevalence of obesity continues to increase, it now includes the growing number of patients with congenital heart disease (CHD). This particular obese patient population may pose additional intraoperative as well as postoperative challenges that may contribute to poor outcomes. Our aims were to determ...

journal_title：Congenital heart disease

authors： Zaidi AN,Bauer JA,Michalsky MP,Olshove V,Boettner B,Phillips A,Cook SC

更新日期：2011-05-01 00:00:00

abstract：BACKGROUND:Children and adolescents with congenital heart disease (CHD) and their families require qualified combined medical and psychosocial information, care, and counseling. This study aimed to analyze CHD patients' and parents' perception of disease-specific knowledge, state of health, and impairments experienced ...

journal_title：Congenital heart disease

authors： Helm PC,Kempert S,Körten MA,Lesch W,Specht K,Bauer UMM

更新日期：2018-05-01 00:00:00

abstract：:Crisscross heart is a rare congenital cardiac anomaly in which systemic and pulmonary venous streams cross without mixing at atrioventricular level. We report a case of crisscross heart with tricuspid atresia, double outlet right ventricle, and pulmonary stenosis, which was diagnosed prenatally. ...

journal_title：Congenital heart disease

authors： Ayabakan C,Binnetoğlu K,Sarısoy Ö,Tokel K

更新日期：2013-09-01 00:00:00

abstract：:Pulmonary hypertension (PH) is a complex condition with a broad range of etiologies that result in a common outcome--elevated pulmonary arterial pressure. For the pediatric cardiologist, this entity provides a manifest demonstration of the interrelationship of cardiac and pulmonary physiology. A thoughtful approach mu...

journal_title：Congenital heart disease

authors： Kyle WB

更新日期：2012-11-01 00:00:00

abstract：OBJECTIVE:This study aimed to quantitatively compare findings of emotional functioning across studies of adolescents and adults with congenital heart disease (CHD) through meta-analysis. DESIGN:The current meta-analysis included 22 studies of adolescent and adult survivors of CHD who completed measures of emotional fu...

journal_title：Congenital heart disease

authors： Jackson JL,Misiti B,Bridge JA,Daniels CJ,Vannatta K

更新日期：2015-01-01 00:00:00

abstract：:Clinically significant patent ductus arteriosus (PDA) has been associated with significant morbidity in extremely low birth weight (ELBW) infants. Current management of ELBW infants with hemodynamically significant PDA includes supportive treatment, pharmacological therapy, and surgical ligation. All of these therapeu...

journal_title：Congenital heart disease

authors： Almeida-Jones M,Tang NY,Reddy A,Zahn E

更新日期：2019-01-01 00:00:00

abstract：:A 24-year-old woman presented with a recent increase in dyspnea on exertion and development of presyncope. The patient stated that she has reproducible episodes of dizziness and near fainting when she climbs a flight of stairs and activity is limited to a slow gait. ...

journal_title：Congenital heart disease

authors： Sabbath AM,Trivedi K,Klewer SE,Sorrell VL

更新日期：2007-07-01 00:00:00

abstract：OBJECTIVES:We aimed (1) determine if systemic right ventricle filling parameters influence systemic right ventricle stroke volume in adult patients with D-transposition of the great arteries (D-TGA) palliated by atrial switch, using cardiac magnetic resonance imaging and echocardiography, and (2) to study relationship ...

journal_title：Congenital heart disease

authors： Ladouceur M,Kachenoura N,Soulat G,Bollache E,Redheuil A,Azizi M,Delclaux C,Chatellier G,Boutouyrie P,Iserin L,Bonnet D,Mousseaux E

更新日期：2017-07-01 00:00:00

abstract：UNLABELLED:BACKGROUND; Several studies have demonstrated the utility of B-type natriuretic peptide (BNP) in the months following cardiac transplant. The purpose of this study was to analyze longitudinal BNP data in pediatric cardiac transplant patients and determine the efficacy of BNP in routine follow-up of transplan...

journal_title：Congenital heart disease

authors： Bramlet M,Moore R,Murphy D,Caldwell R,Darragh R,Schamberger M

更新日期：2010-05-01 00:00:00

abstract：INTRODUCTION:Following congenital heart surgery, pediatric patients may experience persistent respiratory failure that requires tracheostomy placement. Currently, definitive knowledge of the optimal timing for tracheostomy placement in this patient population is lacking. METHODS:An 8-year retrospective review of 17 pe...

journal_title：Congenital heart disease

authors： Costello JP,Emerson DA,Shu MK,Peer SM,Zurakowski D,Reilly BK,Klugman D,Jonas RA,Nath DS

更新日期：2015-01-01 00:00:00

abstract：INTRODUCTION:Improved weight gain during the interstage (IS) period has been shown to improve overall outcomes in patients with single ventricle physiology (SVP). This emphasis on nutrition may have untoward effects, such as increasing anxiety/stress levels in caregivers, who are already known to be at risk for increas...

journal_title：Congenital heart disease

authors： Stewart J,Dempster R,Allen R,Miller-Tate H,Dickson G,Fichtner S,Principe AJ,Fonseca R,Nicholson L,Cua CL

更新日期：2015-03-01 00:00:00

abstract：:We report the use of the Amplatzer Duct Occluder for transcatheter closure of a rare subclavian artery to innominate vein fistula in a neonate. ...

journal_title：Congenital heart disease

authors： Evans K,Jones TK,Johnston TA

更新日期：2006-01-01 00:00:00

abstract：OBJECTIVE:Nurse practitioners (NPs) have an established role for delivering competent care to patients in the primary care setting. The aim of this study was to compare satisfaction of patients managed by NPs vs. physicians in the outpatient adult congenital heart disease (CHD) clinic. DESIGN:A prospective study condu...

journal_title：Congenital heart disease

authors： Maul TM,Zaidi A,Kowalski V,Hickey J,Schnug R,Hindes M,Cook S

更新日期：2015-09-01 00:00:00

abstract：:We report on a 3-year-old male who underwent transcatheter stent fenestration of the inferior portion of an extracardiac total cavopulmonary connection in the setting of hypoplastic left heart syndrome. Transhepatic approach, following an unsuccessful attempt from the femoral vein facilitated delivery of a diabolo-sha...

journal_title：Congenital heart disease

authors： Kenny D,McMahon C,Walsh KP

更新日期：2011-05-01 00:00:00

abstract：OBJECTIVE:Atrial septal defect (ASD) is the second most common congenital heart defect (CHD) and is observed in families as an autosomal dominant trait as well as in nonfamilial CHD. Mutations in the NKX2-5 gene, located on chromosome 5, are associated with ASD, often combined with conduction disturbances, cardiomyopat...

journal_title：Congenital heart disease

authors： Ellesøe SG,Johansen MM,Bjerre JV,Hjortdal VE,Brunak S,Larsen LA

更新日期：2016-05-01 00:00:00

abstract：:There has been a steady rise in the prevalence of severe congenital heart disease (CHD) in adults because of improved treatment and survival during childhood. This has resulted in a shift in CHD morbidity and mortality beyond 18 years of age. The healthcare community must be prepared to meet this new challenge. Adult ...

journal_title：Congenital heart disease

authors： Kalra N,Klewer SE,Raasch H,Sorrell VL

更新日期：2010-05-01 00:00:00

abstract：OBJECTIVE:Patients with tetralogy of Fallot (TOF) undergoing surgery in adulthood represent a challenge. We report our experience with such patients in or beyond the fourth decade of life. DESIGN:Retrospective cohort. SETTING:Multispeciality tertiary level referral center PATIENTS:Forty-one (age 30-52 years) with TO...

journal_title：Congenital heart disease

authors： Talwar S,Meena A,Choudhary SK,Saxena A,Kothari SS,Juneja R,Airan B

更新日期：2014-09-01 00:00:00

abstract：OBJECTIVE:We sought to define what clinical parameters were related to the ultimate outcome in Fontan patients who had developed protein-losing enteropathy (PLE). BACKGROUND:PLE is a serious complication of the Fontan operation. Several preoperative and perioperative findings are associated with later PLE. However, th...

journal_title：Congenital heart disease

authors： Silvilairat S,Cabalka AK,Cetta F,Grogan M,Hagler DJ,O'Leary PW

更新日期：2008-07-01 00:00:00

abstract：OBJECTIVES:To investigate survival and freedom from reintervention after aortic coarctation repair in Maltese patients and to compare cardiovascular mortality in coarctation repair survivors with that in the general population. DESIGN:All 72 aortic coarctation patients with any type of repair, born by end-1997 and log...

journal_title：Congenital heart disease

authors： Caruana M,Grech V

更新日期：2017-09-01 00:00:00

abstract：OBJECTIVE:The need for conduit replacement in the growing child remains a major problem after right ventricular outflow tract reconstruction. We compared two diverse surgical centers with considerable practice variation in Europe and the United States to identify modifiable risk factors that can increase conduit longev...

journal_title：Congenital heart disease

authors： Niemantsverdriet MB,Ottenkamp J,Gauvreau K,Del Nido PJ,Hazenkamp MG,Jenkins KJ

更新日期：2008-05-01 00:00:00

abstract：INTRODUCTION:The right ventricle (RV) supports the systemic circulation in patients who have had an intraatrial repair of transposition of the great arteries or have congenitally corrected transposition. There is concern about the ability of a systemic RV to support the additional volume load of pregnancy, and previous...

journal_title：Congenital heart disease

authors： Bowater SE,Selman TJ,Hudsmith LE,Clift PF,Thompson PJ,Thorne SA

更新日期：2013-07-01 00:00:00

abstract：:Marfan syndrome is a well-described autosomal dominant syndrome with widely variable clinical manifestations. Cardiovascular complications include mitral valve prolapse with or without associated mitral valve insufficiency, aortic root dilatation, and most importantly the occasional development of aortic aneurysms or ...

journal_title：Congenital heart disease

authors： Zangwill SD,Brown MD,Bryke CR,Cava JR,Segura AD

更新日期：2006-09-01 00:00:00

abstract：:Williams-Beuren syndrome (WBS) is a multisystem genetic disorder comprising of craniofacial, developmental, and cardiac malformations. The most common cardiac defects found are supravalvar aortic stenosis and peripheral pulmonary stenosis. However, WBS should be regarded as a general arteriopathy consisting of stenose...

journal_title：Congenital heart disease

authors： Pieles GE,Ofoe V,Morgan GJ

更新日期：2014-05-01 00:00:00

abstract：OBJECTIVE:Published case reports suggest that congenital portosystemic venous connections (PSVC) and other abdominal venous anomalies may be relatively frequent and potentially important in patients with polysplenia syndrome. Our objective was to investigate the frequency and range of portal and other abdominal systemi...

journal_title：Congenital heart disease

authors： McElhinney DB,Marx GR,Newburger JW

更新日期：2011-01-01 00:00:00

abstract：:This case report demonstrated an apical muscular ventricular septal defect (VSD) that was a large defect but behaved like a small defect because of the restrictive flow across the anomalous muscle bundles in the right ventricular (RV) apex. The anomalous muscle bundles separated the RV sinus into two parts: the RV ape...

journal_title：Congenital heart disease

authors： Khositseth A

更新日期：2007-01-01 00:00:00

abstract：BACKGROUND:Transient elastography (TE) offers a noninvasive correlate with the degree of hepatic fibrosis. However, factors other than fibrosis affect liver stiffness. We sought to determine whether hepatic congestion related to hemodynamics in Fontan circulation influences liver stiffness measurement (LSM) assessed by...

journal_title：Congenital heart disease

authors： Wu FM,Opotowsky AR,Raza R,Harney S,Ukomadu C,Landzberg MJ,Valente AM,Breitbart RE,Singh MN,Gauvreau K,Jonas MM

更新日期：2014-09-01 00:00:00

abstract：OBJECTIVE:We aimed to study the efficiency and safety of once-a-week outpatient rehabilitation followed by home program with tele-monitoring in patients with complex cyanotic congenital heart disease. DESIGN:Prospective nonrandomized study. METHOD:Patients who have been diagnosed either Eisenmenger's syndrome or inop...

journal_title：Congenital heart disease

authors： Bhasipol A,Sanjaroensuttikul N,Pornsuriyasak P,Yamwong S,Tangcharoen T

更新日期：2018-11-01 00:00:00

abstract：:Carditis is a common manifestation of adult patients with Lyme disease affecting 4-10% of Lyme patients in the United States. However, children with Lyme disease rarely present with acute carditis. The management of pediatric patients with complete heart block (CHB) secondary to Lyme carditis has not been well describ...

journal_title：Congenital heart disease

authors： Silver E,Pass RH,Kaufman S,Hordof AJ,Liberman L

更新日期：2007-09-01 00:00:00

abstract：:We describe a simple technique for chest wall reconstruction in pentalogy of Cantrell using split-thickness cartilage grafts. This technique provides a robust reconstruction, gives immediate and excellent cosmetic results, allows for skeletal and tissue growth, and avoids the use of synthetic material. ...

journal_title：Congenital heart disease

authors： Grudziak J,Kogon B

更新日期：2013-01-01 00:00:00