Circulating biomarkers of left ventricular hypertrophy in pediatric coarctation of the aorta.

abstract：BACKGROUND:Patients with a Fontan circulation are at risk of renal dysfunction. We analyzed cross-sectional data in pediatric and adult Fontan patients in order to assess the accuracy of commonly used serum creatinine-based methods in estimating glomerular filtration rate (GFR). METHODS:A total of 124 Fontan patients ...

journal_title：Congenital heart disease

authors： Wilson TG,d'Udekem Y,Winlaw DS,Cordina RL,Ayer J,Gentles TL,Weintraub RG,Grigg LE,Cheung M,Cain TM,Rao P,Verrall C,Plessis KD,Rice K,Iyengar AJ

更新日期：2019-05-01 00:00:00

abstract：:Dilated cardiomyopathy and ventricular noncompaction have been reported in association with deletion 1p36 syndrome. Previous descriptions include echocardiographic and/or gross pathologic descriptions. There are no previous reports of microscopic findings. We report a case with descriptions of echocardiographic, gross...

journal_title：Congenital heart disease

authors： Pearce FB,Litovsky SH,Dabal RJ,Robin N,Dure LJ,George JF,Kirklin JK

更新日期：2012-01-01 00:00:00

abstract：:Isolated left ventricular (LV) apical hypoplasia is a recently described congenital abnormality characterized by: (1) a truncated and spherical LV configuration with rightward bulging of the interventricular septum, (2) deficiency of the myocardium within the LV apex with adipose tissue infiltrating the apex, (3) orig...

journal_title：Congenital heart disease

authors： Vanhecke TE,Decker J,Leonowicz N,Chinnaiyan KM

更新日期：2011-11-01 00:00:00

abstract：:A 22-year-old female with no medical history presented to the emergency room with 2 weeks of rapidly worsening dyspnea on exertion, orthopnea, and cough. On cardiac auscultation, she was noted to have to-and-fro murmurs and a continuous murmur with signs of right heart failure. Echocardiographic images obtained showed...

journal_title：Congenital heart disease

authors： Yang EH,Rawal M,Pillutla P,Criley JM

更新日期：2011-03-01 00:00:00

abstract：:Scimitar syndrome is characterized by anomalous pulmonary venous drainage of a part or the whole of the right lung into the inferior vena cava (IVC). It is extremely uncommon in scimitar syndrome for the pulmonary veins to drain anomalously to a site other than the IVC. The following case report describes an otherwise...

journal_title：Congenital heart disease

authors： Kotecha MK,Krishnamanohar SR,Kumar RS

更新日期：2012-01-01 00:00:00

abstract：BACKGROUND:Deficits in swallowing physiology are a leading morbidity for infants with functional single ventricles and systemic outflow tract obstruction following stage 1 palliation. Despite the high prevalence of this condition, the underlying deficits that cause this post-operative impairment remain poorly understoo...

journal_title：Congenital heart disease

authors： McGrattan KE,McGhee H,DeToma A,Hill EG,Zyblewski SC,Lefton-Greif M,Halstead L,Bradley SM,Martin-Harris B

更新日期：2017-05-01 00:00:00

abstract：INTRODUCTION:Cardiovascular diseases in pediatric pathologies have emerged in the recent years in sub-Saharan Africa (SSA), with congenital heart diseases (CHDs) being the most frequent. Unfortunately, their diagnosis is usually delayed, thereby increasing childhood morbidity and mortality. OBJECTIVES:Describe the cli...

journal_title：Congenital heart disease

authors： Kamdem F,Kedy Koum D,Hamadou B,Yemdji M,Luma H,Doualla MS,Noukeu D,Barla E,Akazong C,Dzudie A,Ngote H,Monkam Y,Mouliom S,Kingue S

更新日期：2018-01-01 00:00:00

abstract：OBJECTIVE:The need for conduit replacement in the growing child remains a major problem after right ventricular outflow tract reconstruction. We compared two diverse surgical centers with considerable practice variation in Europe and the United States to identify modifiable risk factors that can increase conduit longev...

journal_title：Congenital heart disease

authors： Niemantsverdriet MB,Ottenkamp J,Gauvreau K,Del Nido PJ,Hazenkamp MG,Jenkins KJ

更新日期：2008-05-01 00:00:00

abstract：BACKGROUND:Hyponatremia (HN) is relatively common in adults with congenital heart disease and is a powerful predictor of mortality. However, the precise relationship of HN to the Fontan pathophysiology remains unknown. PURPOSE:Our study aimed to clarify the association of HN to the Fontan pathophysiology. METHODS AND...

journal_title：Congenital heart disease

authors： Ohuchi H,Negishi J,Ono S,Miyake A,Toyota N,Tamaki W,Miyazaki A,Yamada O

更新日期：2011-07-01 00:00:00

abstract：INTRODUCTION:Health care-associated infections (HAIs) increase mortality, length of stay, and cost in hospitalized patients. The incidence of and risk factors for developing HAIs in the pediatric population after cardiac surgery have been studied. This study evaluates the impact of HAIs on length of stay, inpatient mor...

journal_title：Congenital heart disease

authors： Tweddell S,Loomba RS,Cooper DS,Benscoter AL

更新日期：2019-09-01 00:00:00

abstract：:We report on a 3-year-old male who underwent transcatheter stent fenestration of the inferior portion of an extracardiac total cavopulmonary connection in the setting of hypoplastic left heart syndrome. Transhepatic approach, following an unsuccessful attempt from the femoral vein facilitated delivery of a diabolo-sha...

journal_title：Congenital heart disease

authors： Kenny D,McMahon C,Walsh KP

更新日期：2011-05-01 00:00:00

abstract：:This is a case report reviewing the presentation and clinical course of a patient diagnosed with abdominal aortic atresia at the level caudal to the superior mesenteric artery. Patients with abdominal aortic atresia need to be evaluated for associated underlying syndromes or diseases. Although the prognosis for this d...

journal_title：Congenital heart disease

authors： Brown J,Shehata BM,Campbell R

更新日期：2011-05-01 00:00:00

abstract：:To evaluate the influence of echocardiographic examination in the clinical management of the sick neonate, 241 patients, admitted to the neonatal intensive care unit of a tertiary referral center that had echocardiograms with data available for review, were enrolled in a retrospective study. Asymptomatic murmurs (45%)...

journal_title：Congenital heart disease

authors： Kadivar M,Kiani A,Kocharian A,Shabanian R,Nasehi L,Ghajarzadeh M

更新日期：2008-09-01 00:00:00

abstract：BACKGROUND:As the prevalence of obesity continues to increase, it now includes the growing number of patients with congenital heart disease (CHD). This particular obese patient population may pose additional intraoperative as well as postoperative challenges that may contribute to poor outcomes. Our aims were to determ...

journal_title：Congenital heart disease

authors： Zaidi AN,Bauer JA,Michalsky MP,Olshove V,Boettner B,Phillips A,Cook SC

更新日期：2011-05-01 00:00:00

abstract：OBJECTIVE:The aims of this study were to compare the level of posttraumatic stress disorder between adults with and without congenital heart disease, and to examine the correlates of posttraumatic stress disorder (e.g., sociodemographics). DESIGN:Cross-sectional. SETTING:Two university-affiliated heart hospitals in T...

journal_title：Congenital heart disease

authors： Eslami B

更新日期：2017-05-01 00:00:00

abstract：INTRODUCTION:Perturbations in the CACNA1C-encoded L-type calcium channel α-subunit have been linked recently to heritable arrhythmia syndromes, including Timothy syndrome, Brugada syndrome, early repolarization syndrome, and long QT syndrome. These heritable arrhythmia syndromes may serve as a pathogenic basis for auto...

journal_title：Congenital heart disease

authors： Sutphin BS,Boczek NJ,Barajas-Martínez H,Hu D,Ye D,Tester DJ,Antzelevitch C,Ackerman MJ

更新日期：2016-12-01 00:00:00

abstract：OBJECTIVES:To investigate functional health status among adults previously operated for aortic coarctation (CoA) compared with healthy subjects; to assess the influence of medication and exercise capacity on patients' functional health. DESIGN:Questionnaire-based investigation among 119 patients who underwent surgical...

journal_title：Congenital heart disease

authors： Pedersen TA,Røpcke DM,Hjortdal VE

更新日期：2011-11-01 00:00:00

abstract：OBJECTIVE:To describe treatment, survival, and morbidity for liveborn infants with isolated transposition of great arteries (TGA). DESIGN:Population-based data from 7 European registries of congenital malformations (EUROCAT). RESULTS:Ninety-seven infants were diagnosed with isolated TGA and livebirth prevalence was 2...

journal_title：Congenital heart disease

authors： Garne E,Loane MA,Nelen V,Bakker MK,Gener B,Abramsky L,Addor MC,Queisser-Luft A

更新日期：2007-05-01 00:00:00

abstract：OBJECTIVE:Congenital cardiac defects represent the most common group of birth defects, affecting an estimated six per 1000 births. Genetic characterization of patients and families with cardiac defects has identified a number of genes required for heart development. Yet, despite the rapid pace of these advances, mutati...

journal_title：Congenital heart disease

authors： Thorsson T,Russell WW,El-Kashlan N,Soemedi R,Levine J,Geisler SB,Ackley T,Tomita-Mitchell A,Rosenfeld JA,Töpf A,Tayeh M,Goodship J,Innis JW,Keavney B,Russell MW

更新日期：2015-05-01 00:00:00

abstract：:Down syndrome (DS) patients are prone to pulmonary hypertension (PHTN) due to various cardiopulmonary causes. However, the association of DS with pulmonary vein stenosis (PVS) is not adequately described. We illustrate three cases from our center and an additional 13 cases from an extensive review of the literature of...

journal_title：Congenital heart disease

authors： Gowda S,Bhat D,Feng Z,Chang CH,Ross RD

更新日期：2014-05-01 00:00:00

abstract：OBJECTIVE:Published case reports suggest that congenital portosystemic venous connections (PSVC) and other abdominal venous anomalies may be relatively frequent and potentially important in patients with polysplenia syndrome. Our objective was to investigate the frequency and range of portal and other abdominal systemi...

journal_title：Congenital heart disease

authors： McElhinney DB,Marx GR,Newburger JW

更新日期：2011-01-01 00:00:00

abstract：OBJECTIVE:Stent placement has become a widely used method of treatment for coarctation of the aorta (COA). Our goal was to find echocardiographic indices that would correlate best with directly measured gradients across the coarctation stent. MATERIAL AND METHODS:Pediatric patients with COA who underwent intra-aortic ...

journal_title：Congenital heart disease

authors： Tang L,Forbes TJ,Du W,Zilberman MV

更新日期：2009-07-01 00:00:00

abstract：:In patients with Kawasaki disease (KD) and coronary artery aneurysms (CAAs), serial evaluation with multiple imaging modalities is recommended to guide risk stratification and management. We present the case of a 7-year-old boy with a history of KD and multiple giant CAAs who developed thrombosis in one of the aneurys...

journal_title：Congenital heart disease

authors： Prsa M,Hussain T,McCrindle BW,Grosse-Wortmann L

更新日期：2014-11-01 00:00:00

abstract：AIMS:To outline the etiology, clinical course, short-term survival to discharge and neurological outcome of infants (<1 yr) with new cardiac diagnoses presenting to a pediatric intensive care (PICU) unit with acute cardiac compromise. METHODS:Retrospective search of a computerized database and medical case notes for a...

journal_title：Congenital heart disease

authors： Dhandayuthapani G,Chakrabarti S,Ranasinghe A,Hunt L,Grant D,Martin RP,Kenny D

更新日期：2010-09-01 00:00:00

abstract：OBJECTIVE:The aim is to present current clinical practice of thoracic aorta screening in a tertiary referral center. We identified how often imaging techniques were used for screening and established the value of transthoracic echocardiography (TTE) in comparison with computed tomography (CT) to detect aortic dilation....

journal_title：Congenital heart disease

authors： Bons LR,Uchoa de Assis L,Dekker S,Kauling RM,Cuypers JAAE,Verhagen HJM,Budde RPJ,Roos-Hesselink JW

更新日期：2018-11-01 00:00:00

abstract：:A 52-year-old male patient, with a medical history of surgically repaired double outlet right ventricle presented with severe aortic stenosis (AS) and hepatitis C with cirrhosis, presented with New York Heart Association Class IV heart failure. During evaluation for a liver transplant, he was deemed a poor surgical ca...

journal_title：Congenital heart disease

authors： Keswani A,Verma A,Dann K,Ventura L,Lucas V,Shah S,Ramee S

更新日期：2014-09-01 00:00:00

abstract：:Iron deficiency state in patients with cyanotic congenital heart disease can mimic as well as aggravate hyperviscosity symptoms. Correction of iron deficiency in these cases is expected to improve symptoms. We report an unexpected occurrence of refractory cyanotic spell in a child with tetralogy of Fallot due to throm...

journal_title：Congenital heart disease

authors： Gupta SK,Saxena A,Anil OM,Bisoi AK

更新日期：2012-07-01 00:00:00

abstract：UNLABELLED:BACKGROUND; Several studies have demonstrated the utility of B-type natriuretic peptide (BNP) in the months following cardiac transplant. The purpose of this study was to analyze longitudinal BNP data in pediatric cardiac transplant patients and determine the efficacy of BNP in routine follow-up of transplan...

journal_title：Congenital heart disease

authors： Bramlet M,Moore R,Murphy D,Caldwell R,Darragh R,Schamberger M

更新日期：2010-05-01 00:00:00

abstract：:Absence of the aortic valve is a rare congenital heart defect that is detectable in the prenatal period. In this condition, functional aortic valve leaflets are absent; in their place are rudimentary, immobile noncoapting plate-like structures at the level of the annulus resulting in severe aortic regurgitation. We re...

journal_title：Congenital heart disease

authors： Sabati AA,Wong PC,Randolph L,Pruetz JD

更新日期：2014-05-01 00:00:00

abstract：OBJECTIVE:Determine the accuracy of echocardiography to diagnose coronary anatomy in transposition of the great arteries and to evaluate the effect of accuracy on surgical outcomes and changes in accuracy over time. DESIGN:Retrospective chart review of neonates admitted February 1999 to March 2013 with transposition. ...

journal_title：Congenital heart disease

authors： Fundora MP,Aregullin EO,Wernovsky G,Welch EM,Muniz JC,Sasaki N,Hannan RL,Burke RP,Lopez L

更新日期：2016-12-01 00:00:00