Absent aortic valve associated with double outlet right ventricle and aortopulmonary window: physiologic implications of a rare malformation in both the fetus and neonate.

abstract：OBJECTIVE:To provide data on the value of fused cardiac hybrid imaging with coronary computed tomography angiography (CCTA) and positron emission tomography myocardial perfusion imaging (PET-MPI) in patients with complex coronary artery anomalies (CCAA). DESIGN/SETTING:This is a retrospective, single-center study. PA...

journal_title：Congenital heart disease

authors： Gräni C,Benz DC,Possner M,Clerc OF,Mikulicic F,Vontobel J,Stehli J,Fuchs TA,Pazhenkottil AP,Gaemperli O,Kaufmann PA,Buechel RR

更新日期：2017-01-01 00:00:00

abstract：BACKGROUND:Robust risk-adjustment algorithms are often necessary if data from clinical registries is to be used to compare rates of important clinical outcomes between participating centers. Although such algorithms have been successfully developed for surgical and catheter-based cardiac interventions in children, outc...

journal_title：Congenital heart disease

authors： Triedman JK,Pfeiffer P,Berman A,Blaufox AD,Cannon BC,Fish FA,Perry J,Pflaumer A,Seslar SP,Pediatric and Congenital Electrophysiology Society (PACES) MAP-IT Taskforce.

更新日期：2013-09-01 00:00:00

abstract：OBJECTIVE:The current study aims to identify the rates of lapses in care and loss to follow-up before age one through age five for white and nonwhite congenital heart disease (CHD) survivors. Nonwhite CHD survivors were hypothesized to experience an earlier lapse in care and be lost to follow-up than whites. DESIGN:Pa...

journal_title：Congenital heart disease

authors： Jackson JL,Morack J,Harris M,DeSalvo J,Daniels CJ,Chisolm DJ

更新日期：2019-03-01 00:00:00

abstract：INTRODUCTION:Following congenital heart surgery, pediatric patients may experience persistent respiratory failure that requires tracheostomy placement. Currently, definitive knowledge of the optimal timing for tracheostomy placement in this patient population is lacking. METHODS:An 8-year retrospective review of 17 pe...

journal_title：Congenital heart disease

authors： Costello JP,Emerson DA,Shu MK,Peer SM,Zurakowski D,Reilly BK,Klugman D,Jonas RA,Nath DS

更新日期：2015-01-01 00:00:00

abstract：:Obesity is pandemic in Western society. Currently, approximately 100 million Americans are overweight (body mass index > 25 kg/m2) or obese (body mass index > 30 kg/m2). The pandemic is largely attributable to the relatively recent (from an evolutionary perspective) adoption of a sedentary lifestyle, coupled with the ...

journal_title：Congenital heart disease

authors： Lopez KN,Knudson JD

更新日期：2012-03-01 00:00:00

abstract：:There has been a steady rise in the prevalence of severe congenital heart disease (CHD) in adults because of improved treatment and survival during childhood. This has resulted in a shift in CHD morbidity and mortality beyond 18 years of age. The healthcare community must be prepared to meet this new challenge. Adult ...

journal_title：Congenital heart disease

authors： Kalra N,Klewer SE,Raasch H,Sorrell VL

更新日期：2010-05-01 00:00:00

abstract：:We report the use of the Amplatzer Duct Occluder for transcatheter closure of a rare subclavian artery to innominate vein fistula in a neonate. ...

journal_title：Congenital heart disease

authors： Evans K,Jones TK,Johnston TA

更新日期：2006-01-01 00:00:00

abstract：OBJECTIVE:Patients undergoing surgical repair of aortic coarctation have a 50% risk of pathologic left ventricular remodeling (increased left ventricular mass or relative wall thickness). Endothelin 1, ST2, galectin 3, norepinephrine and B-natriuretic peptide are biomarkers that have been associated with pathologic LV ...

journal_title：Congenital heart disease

authors： Frank BS,Urban TT,Lewis K,Tong S,Cassidy C,Mitchell MB,Nichols CS,Davidson JA

更新日期：2019-05-01 00:00:00

abstract：OBJECTIVE:To assess how obesity or diabetes mellitus impacts outcomes in patients undergoing cardiac surgery in pediatric hospitals. DESIGN:A multi-institutional, matched case-control study of the Pediatric Health Information System database was performed. SETTING:Tertiary children's hospitals in the United States. ...

journal_title：Congenital heart disease

authors： Shamszad P,Rossano JW,Marino BS,Lowry AW,Knudson JD

更新日期：2016-09-01 00:00:00

abstract：:Brugada syndrome is an arrhythmogenic disease characterized by a pattern of ST segment elevation in the right precordial leads on an electrocardiogram with an increased risk of sudden cardiac death. It is primarily reported in adults with limited data about the prevalence, prognosis, and long-term management in childr...

journal_title：Congenital heart disease

authors： Zaidi AN

更新日期：2010-11-01 00:00:00

abstract：BACKGROUND:Mean platelet volume (MPV), platecrit, and platelet distribution width (PDW) are markers of platelet activation. Previous studies have found that platelet activation occurs in patients with pulmonary arterial hypertension. Platelet indices including MPV, PDW, and platecrit have not been studied in children w...

journal_title：Congenital heart disease

authors： Mese T,Guven B,Yilmazer MM,Karadeniz C,Ozdemir R,Doksoz O

更新日期：2018-07-01 00:00:00

abstract：OBJECTIVE:Amiodarone is a highly effective antiarrhythmic therapy, however its toxicity profile often limits treatment. This is particularly relevant in adults with congenital heart disease (CHD), who are often young and in whom other antiarrhythmic agents commonly fail or are contraindicated. We sought to determine in...

journal_title：Congenital heart disease

authors： Moore BM,Cordina RL,McGuire MA,Celermajer DS

更新日期：2018-11-01 00:00:00

abstract：:Carditis is a common manifestation of adult patients with Lyme disease affecting 4-10% of Lyme patients in the United States. However, children with Lyme disease rarely present with acute carditis. The management of pediatric patients with complete heart block (CHB) secondary to Lyme carditis has not been well describ...

journal_title：Congenital heart disease

authors： Silver E,Pass RH,Kaufman S,Hordof AJ,Liberman L

更新日期：2007-09-01 00:00:00

abstract：OBJECTIVE:Pulmonary autograft aortic root replacement (Ross' operation) is now associated with low operative risk. Recent series suggest that patients with primary aortic insufficiency have diminished autograft durability and that patients with large discrepancies between pulmonary and aortic valve sizes have a low but...

journal_title：Congenital heart disease

authors： Morales DL,Carberry KE,Balentine C,Heinle JS,McKenzie ED,Fraser CD Jr

更新日期：2008-11-01 00:00:00

abstract：OBJECTIVE:Approximately one-third of adult congenital heart disease (ACHD) patients have mood or anxiety disorders, the majority of which go untreated. The extent to which this group of patients is interested in psychological services is, however, unknown. This study investigated the perceived psychological needs of pa...

journal_title：Congenital heart disease

authors： Kovacs AH,Bendell KL,Colman J,Harrison JL,Oechslin E,Silversides C

更新日期：2009-05-01 00:00:00

abstract：BACKGROUND:Pulmonary atresia with intact ventricular septum is a unique congenital malformation of the heart in which patients may undergo single-, two- or 1½- ventricle repair. Size of the tricuspid valve annulus, morphology of the right ventricle and presence of ventriculocoronary connections can all impact the selec...

journal_title：Congenital heart disease

authors： Loomba RS,Pelech AN

更新日期：2018-01-01 00:00:00

abstract：:Marfan syndrome is a well-described autosomal dominant syndrome with widely variable clinical manifestations. Cardiovascular complications include mitral valve prolapse with or without associated mitral valve insufficiency, aortic root dilatation, and most importantly the occasional development of aortic aneurysms or ...

journal_title：Congenital heart disease

authors： Zangwill SD,Brown MD,Bryke CR,Cava JR,Segura AD

更新日期：2006-09-01 00:00:00

abstract：BACKGROUND:Interatrial shunts, caused by either atrial septal defect (ASD) or patent foramen ovale, have been reported to have a familial association. We sought to examine the familial risk of isolated interatrial shunt and explore associated comorbidities of stroke, transient ischemic attack (TIA), and migraine using ...

journal_title：Congenital heart disease

authors： Steenblik MH,Mineau GP,Pimentel R,Michaels AD

更新日期：2009-11-01 00:00:00

abstract：:Scimitar syndrome is characterized by anomalous pulmonary venous drainage of a part or the whole of the right lung into the inferior vena cava (IVC). It is extremely uncommon in scimitar syndrome for the pulmonary veins to drain anomalously to a site other than the IVC. The following case report describes an otherwise...

journal_title：Congenital heart disease

authors： Kotecha MK,Krishnamanohar SR,Kumar RS

更新日期：2012-01-01 00:00:00

abstract：PURPOSE:Right ventricular (RV) failure and ventricular dyssynchrony are strong determinants of prognosis in patients with adult congenital heart disease (ACHD). The aim of this study was to investigate the relationship between interventricular dyssynchrony (IVD) using cine-tagged magnetic resonance imaging (MRI) and RV...

journal_title：Congenital heart disease

authors： Nagao M,Yamasaki Y,Yonezawa M,Matsuo Y,Kamitani T,Yamamura K,Sakamoto I,Abe K,Kawanami S,Honda H

更新日期：2015-05-01 00:00:00

abstract：OBJECTIVE:The purpose of this study was to identify factors that influence postoperative intensive care unit length of stay (ICULOS) in infants less than 6 months of age undergoing congenital heart surgery. METHODS:Records from a single institution, from January 2000 to December 2000, were reviewed. For analysis, surg...

journal_title：Congenital heart disease

authors： Gillespie M,Kuijpers M,Van Rossem M,Ravishankar C,Gaynor JW,Spray T,Clark B 3rd

更新日期：2006-07-01 00:00:00

abstract：INTRODUCTION:Cardiovascular diseases in pediatric pathologies have emerged in the recent years in sub-Saharan Africa (SSA), with congenital heart diseases (CHDs) being the most frequent. Unfortunately, their diagnosis is usually delayed, thereby increasing childhood morbidity and mortality. OBJECTIVES:Describe the cli...

journal_title：Congenital heart disease

authors： Kamdem F,Kedy Koum D,Hamadou B,Yemdji M,Luma H,Doualla MS,Noukeu D,Barla E,Akazong C,Dzudie A,Ngote H,Monkam Y,Mouliom S,Kingue S

更新日期：2018-01-01 00:00:00

abstract：INTRODUCTION:The right ventricle (RV) supports the systemic circulation in patients who have had an intraatrial repair of transposition of the great arteries or have congenitally corrected transposition. There is concern about the ability of a systemic RV to support the additional volume load of pregnancy, and previous...

journal_title：Congenital heart disease

authors： Bowater SE,Selman TJ,Hudsmith LE,Clift PF,Thompson PJ,Thorne SA

更新日期：2013-07-01 00:00:00

abstract：OBJECTIVE:The National Pediatric Cardiology Quality Improvement Collaborative (NPC-QIC) was established in 2008 to improve outcomes of hypoplastic left heart syndrome (HLHS) during the interstage period. They evaluated changes in patient variables and practice variation between early and late eras. DESIGN:Data includi...

journal_title：Congenital heart disease

authors： Carlo WF,Cnota JF,Dabal RJ,Anderson JB

更新日期：2017-05-01 00:00:00

abstract：BACKGROUND:Patients with a Fontan circulation are at risk of renal dysfunction. We analyzed cross-sectional data in pediatric and adult Fontan patients in order to assess the accuracy of commonly used serum creatinine-based methods in estimating glomerular filtration rate (GFR). METHODS:A total of 124 Fontan patients ...

journal_title：Congenital heart disease

authors： Wilson TG,d'Udekem Y,Winlaw DS,Cordina RL,Ayer J,Gentles TL,Weintraub RG,Grigg LE,Cheung M,Cain TM,Rao P,Verrall C,Plessis KD,Rice K,Iyengar AJ

更新日期：2019-05-01 00:00:00

abstract：:Dexmedetomidine is a selective alpha-2 adrenergic agonist that is used frequently for short-term sedation in children. It has been noted to cause hypertension, hypotension, bradycardia, and sinus pauses; however, QTc prolongation has not been reported with dexmedetomidine administration. We describe a case of marked Q...

journal_title：Congenital heart disease

authors： Burns KM,Greene EA

更新日期：2014-01-01 00:00:00

abstract：OBJECTIVE:Enteral feeding is associated with decreased infection rates, decreased mechanical ventilation, decreased hospital length of stay, and improved wound healing. Enteral feeding difficulties are common in congenital heart disease. Our objective was to develop experience-based newborn feeding guidelines for the i...

journal_title：Congenital heart disease

authors： Simsic JM,Carpenito KR,Kirchner K,Peters S,Miller-Tate H,Joy B,Galantowicz M

更新日期：2017-05-01 00:00:00

abstract：OBJECTIVES:To investigate survival and freedom from reintervention after aortic coarctation repair in Maltese patients and to compare cardiovascular mortality in coarctation repair survivors with that in the general population. DESIGN:All 72 aortic coarctation patients with any type of repair, born by end-1997 and log...

journal_title：Congenital heart disease

authors： Caruana M,Grech V

更新日期：2017-09-01 00:00:00

abstract：:Clinically significant patent ductus arteriosus (PDA) has been associated with significant morbidity in extremely low birth weight (ELBW) infants. Current management of ELBW infants with hemodynamically significant PDA includes supportive treatment, pharmacological therapy, and surgical ligation. All of these therapeu...

journal_title：Congenital heart disease

authors： Almeida-Jones M,Tang NY,Reddy A,Zahn E

更新日期：2019-01-01 00:00:00

abstract：INTRODUCTION:The neurodevelopmental outcome of children with repaired congenital heart defect has risen in importance with improved survival. This study compares neurodevelopmental outcomes of children who had CHD with single ventricle physiology with those who had CHD with two-ventricle physiology. PATIENTS AND METHO...

journal_title：Congenital heart disease

authors： Hoskoppal A,Roberts H,Kugler J,Duncan K,Needelman H

更新日期：2010-03-01 00:00:00