Assessing hepatic impairment in Fontan-associated liver disease using the HepQuant SHUNT test.

abstract：:Williams-Beuren syndrome (WBS) is a multisystem genetic disorder comprising of craniofacial, developmental, and cardiac malformations. The most common cardiac defects found are supravalvar aortic stenosis and peripheral pulmonary stenosis. However, WBS should be regarded as a general arteriopathy consisting of stenose...

journal_title：Congenital heart disease

authors： Pieles GE,Ofoe V,Morgan GJ

更新日期：2014-05-01 00:00:00

abstract：OBJECTIVE:Management of the patients with transposition of the great arteries and intact ventricular septum may be challenging beyond the newborn period. Herein, we would like to present our alternative strategy for training the left ventricle in these patients. METHODS:Six patients with transposition of the great art...

journal_title：Congenital heart disease

authors： Bilal MS,Özyüksel A,Kemal Avşar M,Demiroluk Ş,Küçükosmanoğlu O,Yalçın Y

更新日期：2019-05-01 00:00:00

abstract：:Brugada syndrome is an arrhythmogenic disease characterized by a pattern of ST segment elevation in the right precordial leads on an electrocardiogram with an increased risk of sudden cardiac death. It is primarily reported in adults with limited data about the prevalence, prognosis, and long-term management in childr...

journal_title：Congenital heart disease

authors： Zaidi AN

更新日期：2010-11-01 00:00:00

abstract：:A 24-year-old woman presented with a recent increase in dyspnea on exertion and development of presyncope. The patient stated that she has reproducible episodes of dizziness and near fainting when she climbs a flight of stairs and activity is limited to a slow gait. ...

journal_title：Congenital heart disease

authors： Sabbath AM,Trivedi K,Klewer SE,Sorrell VL

更新日期：2007-07-01 00:00:00

abstract：OBJECTIVE:It is unclear whether neonates with interrupted aortic arch (IAA) and a smaller left ventricular outflow tract may have improved outcomes with a Yasui operation (ventricular outflow bypass procedure) over a primary complete repair. This study sought to identify preoperative echocardiographic parameters to dif...

journal_title：Congenital heart disease

authors： Abarbanell G,Border WL,Schlosser B,Morrow G,Kelleman M,Sachdeva R

更新日期：2018-05-01 00:00:00

abstract：OBJECTIVE:The use of video-assisted thoracoscopic surgery (VATS) is becoming increasingly common in the treatment of congenital heart defects, particularly for the division of vascular rings. We compare the short-term outcomes of vascular ring division by VATS as opposed to open thoracotomy and discuss new issues raise...

journal_title：Congenital heart disease

authors： Kogon BE,Forbess JM,Wulkan ML,Kirshbom PM,Kanter KR

更新日期：2007-03-01 00:00:00

abstract：OBJECTIVE:Published case reports suggest that congenital portosystemic venous connections (PSVC) and other abdominal venous anomalies may be relatively frequent and potentially important in patients with polysplenia syndrome. Our objective was to investigate the frequency and range of portal and other abdominal systemi...

journal_title：Congenital heart disease

authors： McElhinney DB,Marx GR,Newburger JW

更新日期：2011-01-01 00:00:00

abstract：OBJECTIVE:Obesity affects adults with congenital heart disease (CHD). The effect of an increased body mass index (BMI) with respect to morbidity and mortality has not been evaluated in adults with complex CHD. Our objective was to evaluate the effects of increased BMI on heart failure and mortality in univentricular pa...

journal_title：Congenital heart disease

authors： Martinez SC,Byku M,Novak EL,Cedars AM,Eghtesady P,Ludbrook PA,Billadello JJ

更新日期：2016-01-01 00:00:00

abstract：OBJECTIVES:To determine if patients evaluated using the pediatric chest pain standardized clinical assessment and management plan (SCAMP) in cardiology clinic were later diagnosed with unrecognized cardiac pathology, and to determine if other patients with cardiac pathology not enrolled in the SCAMP would have been ide...

journal_title：Congenital heart disease

authors： Kane DA,Friedman KG,Fulton DR,Geggel RL,Saleeb SF

更新日期：2016-09-01 00:00:00

abstract：BACKGROUND:Open cardiac surgery has traditionally been the gold standard for repair of ventricular septal defect (VSD). The inherent risks and complications associated with open surgery and the incidence of postoperative residual VSD are significant disadvantages of the open surgical approach. OBJECTIVE:To evaluate th...

journal_title：Congenital heart disease

authors： Zhou W,Li F,Fu L,Gao W,Guo Y,Liu T,Huang M,Zhang Y

更新日期：2016-07-01 00:00:00

abstract：OBJECTIVE:Cardiovascular lesions are the leading cause of morbidity and mortality in patients with Williams syndrome. Recent studies have rebutted conventional reports about the natural course of cardiovascular anomalies in Williams syndrome. DESIGN:Retrospective study. SETTING:Single tertiary center. PATIENTS:Eight...

journal_title：Congenital heart disease

authors： Cha SG,Song MK,Lee SY,Kim GB,Kwak JG,Kim WH,Bae EJ

更新日期：2019-09-01 00:00:00

abstract：:Clinically significant patent ductus arteriosus (PDA) has been associated with significant morbidity in extremely low birth weight (ELBW) infants. Current management of ELBW infants with hemodynamically significant PDA includes supportive treatment, pharmacological therapy, and surgical ligation. All of these therapeu...

journal_title：Congenital heart disease

authors： Almeida-Jones M,Tang NY,Reddy A,Zahn E

更新日期：2019-01-01 00:00:00

abstract：OBJECTIVE:This study aimed to quantitatively compare findings of emotional functioning across studies of adolescents and adults with congenital heart disease (CHD) through meta-analysis. DESIGN:The current meta-analysis included 22 studies of adolescent and adult survivors of CHD who completed measures of emotional fu...

journal_title：Congenital heart disease

authors： Jackson JL,Misiti B,Bridge JA,Daniels CJ,Vannatta K

更新日期：2015-01-01 00:00:00

abstract：:Crisscross heart is a rare congenital cardiac anomaly in which systemic and pulmonary venous streams cross without mixing at atrioventricular level. We report a case of crisscross heart with tricuspid atresia, double outlet right ventricle, and pulmonary stenosis, which was diagnosed prenatally. ...

journal_title：Congenital heart disease

authors： Ayabakan C,Binnetoğlu K,Sarısoy Ö,Tokel K

更新日期：2013-09-01 00:00:00

abstract：BACKGROUND:Transient elastography (TE) offers a noninvasive correlate with the degree of hepatic fibrosis. However, factors other than fibrosis affect liver stiffness. We sought to determine whether hepatic congestion related to hemodynamics in Fontan circulation influences liver stiffness measurement (LSM) assessed by...

journal_title：Congenital heart disease

authors： Wu FM,Opotowsky AR,Raza R,Harney S,Ukomadu C,Landzberg MJ,Valente AM,Breitbart RE,Singh MN,Gauvreau K,Jonas MM

更新日期：2014-09-01 00:00:00

abstract：:Iron deficiency state in patients with cyanotic congenital heart disease can mimic as well as aggravate hyperviscosity symptoms. Correction of iron deficiency in these cases is expected to improve symptoms. We report an unexpected occurrence of refractory cyanotic spell in a child with tetralogy of Fallot due to throm...

journal_title：Congenital heart disease

authors： Gupta SK,Saxena A,Anil OM,Bisoi AK

更新日期：2012-07-01 00:00:00

abstract：OBJECTIVES:The primary objective of this study was to demonstrate that pulmonary artery (PA) debanding via cardiac catheterization using balloon angioplasty is feasible and safe in swine. The secondary objectives were to determine the acute and long-term effects of this therapy. DESIGN:This is a chronic survival exper...

journal_title：Congenital heart disease

authors： Perez M,Kumar TS,Hoskoppal D,Akkhawattanangkul Y,Allen K,Knott-Craig CJ,Waller BR,Sathanandam S

更新日期：2017-05-01 00:00:00

abstract：PURPOSE:Right ventricular (RV) failure and ventricular dyssynchrony are strong determinants of prognosis in patients with adult congenital heart disease (ACHD). The aim of this study was to investigate the relationship between interventricular dyssynchrony (IVD) using cine-tagged magnetic resonance imaging (MRI) and RV...

journal_title：Congenital heart disease

authors： Nagao M,Yamasaki Y,Yonezawa M,Matsuo Y,Kamitani T,Yamamura K,Sakamoto I,Abe K,Kawanami S,Honda H

更新日期：2015-05-01 00:00:00

abstract：OBJECTIVE:The aim is to present current clinical practice of thoracic aorta screening in a tertiary referral center. We identified how often imaging techniques were used for screening and established the value of transthoracic echocardiography (TTE) in comparison with computed tomography (CT) to detect aortic dilation....

journal_title：Congenital heart disease

authors： Bons LR,Uchoa de Assis L,Dekker S,Kauling RM,Cuypers JAAE,Verhagen HJM,Budde RPJ,Roos-Hesselink JW

更新日期：2018-11-01 00:00:00

abstract：:We present a rare case of spontaneous closure of a fistula between the left coronary artery and the right ventricle (RV) within a few days of newborn period. A 14-day-old male newborn was referred to our clinic for investigation of tachypnea and cardiac murmur. A color flow Doppler echocardiography revealed turbulent ...

journal_title：Congenital heart disease

authors： Yilmazer MM,Demir F,Yolbaş I,Bilici M

更新日期：2014-01-01 00:00:00

abstract：BACKGROUND:Mean platelet volume (MPV), platecrit, and platelet distribution width (PDW) are markers of platelet activation. Previous studies have found that platelet activation occurs in patients with pulmonary arterial hypertension. Platelet indices including MPV, PDW, and platecrit have not been studied in children w...

journal_title：Congenital heart disease

authors： Mese T,Guven B,Yilmazer MM,Karadeniz C,Ozdemir R,Doksoz O

更新日期：2018-07-01 00:00:00

abstract：OBJECTIVE:The purpose of this study was to compare neurological development of children with cyanotic or hemodynamically impaired congenital heart disease (CHD) and healthy controls by using "Bayley Scales of Infant and Toddler Development Screening Test, Third Edition" (Bayley-III). PATIENTS:Children with CHD (n = 37...

journal_title：Congenital heart disease

authors： Hallioglu O,Gurer G,Bozlu G,Karpuz D,Makharoblidze K,Okuyaz C

更新日期：2015-11-01 00:00:00

abstract：:Transcatheter management of native coarctation of the aorta in 3 children with Turner syndrome is reported. Two children, 12 and 17 years of age, underwent stent implantation and 1 child, 3 years old, underwent balloon angioplasty alone. In all children the procedures were successful, both hemodynamically and angiogra...

journal_title：Congenital heart disease

authors： Kataoka K,Ozawa A,Inage A,Benson LN

更新日期：2006-11-01 00:00:00

abstract：:Absence of the aortic valve is a rare congenital heart defect that is detectable in the prenatal period. In this condition, functional aortic valve leaflets are absent; in their place are rudimentary, immobile noncoapting plate-like structures at the level of the annulus resulting in severe aortic regurgitation. We re...

journal_title：Congenital heart disease

authors： Sabati AA,Wong PC,Randolph L,Pruetz JD

更新日期：2014-05-01 00:00:00

abstract：OBJECTIVE:The need for conduit replacement in the growing child remains a major problem after right ventricular outflow tract reconstruction. We compared two diverse surgical centers with considerable practice variation in Europe and the United States to identify modifiable risk factors that can increase conduit longev...

journal_title：Congenital heart disease

authors： Niemantsverdriet MB,Ottenkamp J,Gauvreau K,Del Nido PJ,Hazenkamp MG,Jenkins KJ

更新日期：2008-05-01 00:00:00

abstract：:Scimitar syndrome is characterized by anomalous pulmonary venous drainage of a part or the whole of the right lung into the inferior vena cava (IVC). It is extremely uncommon in scimitar syndrome for the pulmonary veins to drain anomalously to a site other than the IVC. The following case report describes an otherwise...

journal_title：Congenital heart disease

authors： Kotecha MK,Krishnamanohar SR,Kumar RS

更新日期：2012-01-01 00:00:00

abstract：:In patients with Kawasaki disease (KD) and coronary artery aneurysms (CAAs), serial evaluation with multiple imaging modalities is recommended to guide risk stratification and management. We present the case of a 7-year-old boy with a history of KD and multiple giant CAAs who developed thrombosis in one of the aneurys...

journal_title：Congenital heart disease

authors： Prsa M,Hussain T,McCrindle BW,Grosse-Wortmann L

更新日期：2014-11-01 00:00:00

abstract：OBJECTIVES:We aimed (1) determine if systemic right ventricle filling parameters influence systemic right ventricle stroke volume in adult patients with D-transposition of the great arteries (D-TGA) palliated by atrial switch, using cardiac magnetic resonance imaging and echocardiography, and (2) to study relationship ...

journal_title：Congenital heart disease

authors： Ladouceur M,Kachenoura N,Soulat G,Bollache E,Redheuil A,Azizi M,Delclaux C,Chatellier G,Boutouyrie P,Iserin L,Bonnet D,Mousseaux E

更新日期：2017-07-01 00:00:00

abstract：:This is a case report reviewing the presentation and clinical course of a patient diagnosed with abdominal aortic atresia at the level caudal to the superior mesenteric artery. Patients with abdominal aortic atresia need to be evaluated for associated underlying syndromes or diseases. Although the prognosis for this d...

journal_title：Congenital heart disease

authors： Brown J,Shehata BM,Campbell R

更新日期：2011-05-01 00:00:00

abstract：:A 52-year-old male patient, with a medical history of surgically repaired double outlet right ventricle presented with severe aortic stenosis (AS) and hepatitis C with cirrhosis, presented with New York Heart Association Class IV heart failure. During evaluation for a liver transplant, he was deemed a poor surgical ca...

journal_title：Congenital heart disease

authors： Keswani A,Verma A,Dann K,Ventura L,Lucas V,Shah S,Ramee S

更新日期：2014-09-01 00:00:00