An unusual case of Brugada syndrome in a 10-year-old child with fevers.

abstract：:The origin of pulmonary artery branches (particularly the left pulmonary artery) from the ascending aorta is a rare condition. We detected prominent hypoplasia of the main and right pulmonary arteries in a 3.5-month-old 3.7 kg female infant who had tetralogy of Fallot with origin of the left pulmonary artery in the as...

journal_title：Congenital heart disease

authors： Saritas T,Erdem A,Karaci AR,Demir F,Celebi A

更新日期：2012-05-01 00:00:00

abstract：OBJECTIVE:The electrocardiogram (ECG) is used to detect left ventricular hypertrophy (LVH) in children and young adults, and it is considered an important screening tool for the most common causes of sudden cardiac arrest in the United States. However, the reliability and accuracy of the ECG in the detection of LVH are...

journal_title：Congenital heart disease

authors： Bratincsák A,Williams M,Kimata C,Perry JC

更新日期：2015-07-01 00:00:00

abstract：:To evaluate the influence of echocardiographic examination in the clinical management of the sick neonate, 241 patients, admitted to the neonatal intensive care unit of a tertiary referral center that had echocardiograms with data available for review, were enrolled in a retrospective study. Asymptomatic murmurs (45%)...

journal_title：Congenital heart disease

authors： Kadivar M,Kiani A,Kocharian A,Shabanian R,Nasehi L,Ghajarzadeh M

更新日期：2008-09-01 00:00:00

abstract：INTRODUCTION:Perturbations in the CACNA1C-encoded L-type calcium channel α-subunit have been linked recently to heritable arrhythmia syndromes, including Timothy syndrome, Brugada syndrome, early repolarization syndrome, and long QT syndrome. These heritable arrhythmia syndromes may serve as a pathogenic basis for auto...

journal_title：Congenital heart disease

authors： Sutphin BS,Boczek NJ,Barajas-Martínez H,Hu D,Ye D,Tester DJ,Antzelevitch C,Ackerman MJ

更新日期：2016-12-01 00:00:00

abstract：:This case report demonstrated an apical muscular ventricular septal defect (VSD) that was a large defect but behaved like a small defect because of the restrictive flow across the anomalous muscle bundles in the right ventricular (RV) apex. The anomalous muscle bundles separated the RV sinus into two parts: the RV ape...

journal_title：Congenital heart disease

authors： Khositseth A

更新日期：2007-01-01 00:00:00

abstract：:Marfan syndrome is a well-described autosomal dominant syndrome with widely variable clinical manifestations. Cardiovascular complications include mitral valve prolapse with or without associated mitral valve insufficiency, aortic root dilatation, and most importantly the occasional development of aortic aneurysms or ...

journal_title：Congenital heart disease

authors： Zangwill SD,Brown MD,Bryke CR,Cava JR,Segura AD

更新日期：2006-09-01 00:00:00

abstract：OBJECTIVE:This study aimed to quantitatively compare findings of emotional functioning across studies of adolescents and adults with congenital heart disease (CHD) through meta-analysis. DESIGN:The current meta-analysis included 22 studies of adolescent and adult survivors of CHD who completed measures of emotional fu...

journal_title：Congenital heart disease

authors： Jackson JL,Misiti B,Bridge JA,Daniels CJ,Vannatta K

更新日期：2015-01-01 00:00:00

abstract：:There has been a steady rise in the prevalence of severe congenital heart disease (CHD) in adults because of improved treatment and survival during childhood. This has resulted in a shift in CHD morbidity and mortality beyond 18 years of age. The healthcare community must be prepared to meet this new challenge. Adult ...

journal_title：Congenital heart disease

authors： Kalra N,Klewer SE,Raasch H,Sorrell VL

更新日期：2010-05-01 00:00:00

abstract：OBJECTIVE:To provide data on the value of fused cardiac hybrid imaging with coronary computed tomography angiography (CCTA) and positron emission tomography myocardial perfusion imaging (PET-MPI) in patients with complex coronary artery anomalies (CCAA). DESIGN/SETTING:This is a retrospective, single-center study. PA...

journal_title：Congenital heart disease

authors： Gräni C,Benz DC,Possner M,Clerc OF,Mikulicic F,Vontobel J,Stehli J,Fuchs TA,Pazhenkottil AP,Gaemperli O,Kaufmann PA,Buechel RR

更新日期：2017-01-01 00:00:00

abstract：:Protein-losing enteropathy (PLE) is a rare, but serious complication in single ventricle patients after Fontan palliation, and is associated with a 5-year mortality of 46%. We describe a patient with PLE after Fontan palliation who achieved remission with high-dose spironolactone (an aldosterone antagonist), but had t...

journal_title：Congenital heart disease

authors： Grattan MJ,McCrindle BW

更新日期：2010-03-01 00:00:00

abstract：OBJECTIVES:To determine if patients evaluated using the pediatric chest pain standardized clinical assessment and management plan (SCAMP) in cardiology clinic were later diagnosed with unrecognized cardiac pathology, and to determine if other patients with cardiac pathology not enrolled in the SCAMP would have been ide...

journal_title：Congenital heart disease

authors： Kane DA,Friedman KG,Fulton DR,Geggel RL,Saleeb SF

更新日期：2016-09-01 00:00:00

abstract：OBJECTIVE:The objective of this study was to characterize the natural history of metabolic uncoupling (type B hyperlactemia and hyperglycemia) following cardiopulmonary bypass (CPB), and to determine the impact of insulin therapy on time to lactate normalization in patients without low cardiac output. DESIGN:The desig...

journal_title：Congenital heart disease

authors： Palermo RA,Palac HL,Wald EL,Wainwright MS,Costello JM,Eltayeb OM,Backer CL,Epting CL

更新日期：2015-11-01 00:00:00

abstract：PURPOSE:The aim of this article was to assess the role of MRI in the diagnosis and management of a variety of complex aortic arch anomalies. MATERIALS AND METHODS:Imaging was performed on a 1.5T Philips Gyroscan Intera. We retrospectively reviewed all cardiac MR scans performed from November 2003 to February 2007 at o...

journal_title：Congenital heart disease

authors： Cantinotti M,Hegde S,Bell A,Razavi R

更新日期：2008-03-01 00:00:00

abstract：OBJECTIVE:Congenital cardiac defects represent the most common group of birth defects, affecting an estimated six per 1000 births. Genetic characterization of patients and families with cardiac defects has identified a number of genes required for heart development. Yet, despite the rapid pace of these advances, mutati...

journal_title：Congenital heart disease

authors： Thorsson T,Russell WW,El-Kashlan N,Soemedi R,Levine J,Geisler SB,Ackley T,Tomita-Mitchell A,Rosenfeld JA,Töpf A,Tayeh M,Goodship J,Innis JW,Keavney B,Russell MW

更新日期：2015-05-01 00:00:00

abstract：OBJECTIVE:The aims of this study were to compare the level of posttraumatic stress disorder between adults with and without congenital heart disease, and to examine the correlates of posttraumatic stress disorder (e.g., sociodemographics). DESIGN:Cross-sectional. SETTING:Two university-affiliated heart hospitals in T...

journal_title：Congenital heart disease

authors： Eslami B

更新日期：2017-05-01 00:00:00

abstract：OBJECTIVE:Published case reports suggest that congenital portosystemic venous connections (PSVC) and other abdominal venous anomalies may be relatively frequent and potentially important in patients with polysplenia syndrome. Our objective was to investigate the frequency and range of portal and other abdominal systemi...

journal_title：Congenital heart disease

authors： McElhinney DB,Marx GR,Newburger JW

更新日期：2011-01-01 00:00:00

abstract：:While right ventricle to pulmonary artery homograft is the surgical procedure of choice for relieving right ventricle outflow tract obstruction; it is limited by the need for multiple surgical replacements owing to progressive conduit obstruction, valve dysfunction, or patient growth. Since January 2010, percutaneous ...

journal_title：Congenital heart disease

authors： Bhat DP,Forbes TJ,Aggarwal S

更新日期：2013-11-01 00:00:00

abstract：:Tetralogy of Fallot is the most common cyanotic congenital heart defect. Advances in surgical technique and postoperative care have improved survival which is now very good. Patients now face long-term morbidities such as reduced exercise tolerance and arrthymias. Cardiologists caring for these patients are confronted...

journal_title：Congenital heart disease

authors： Hill G

更新日期：2013-03-01 00:00:00

abstract：UNLABELLED:BACKGROUND; Several studies have demonstrated the utility of B-type natriuretic peptide (BNP) in the months following cardiac transplant. The purpose of this study was to analyze longitudinal BNP data in pediatric cardiac transplant patients and determine the efficacy of BNP in routine follow-up of transplan...

journal_title：Congenital heart disease

authors： Bramlet M,Moore R,Murphy D,Caldwell R,Darragh R,Schamberger M

更新日期：2010-05-01 00:00:00

abstract：OBJECTIVE:The purpose of this study was to identify factors that influence postoperative intensive care unit length of stay (ICULOS) in infants less than 6 months of age undergoing congenital heart surgery. METHODS:Records from a single institution, from January 2000 to December 2000, were reviewed. For analysis, surg...

journal_title：Congenital heart disease

authors： Gillespie M,Kuijpers M,Van Rossem M,Ravishankar C,Gaynor JW,Spray T,Clark B 3rd

更新日期：2006-07-01 00:00:00

abstract：OBJECTIVE:Patients undergoing surgical repair of aortic coarctation have a 50% risk of pathologic left ventricular remodeling (increased left ventricular mass or relative wall thickness). Endothelin 1, ST2, galectin 3, norepinephrine and B-natriuretic peptide are biomarkers that have been associated with pathologic LV ...

journal_title：Congenital heart disease

authors： Frank BS,Urban TT,Lewis K,Tong S,Cassidy C,Mitchell MB,Nichols CS,Davidson JA

更新日期：2019-05-01 00:00:00

abstract：:Crisscross heart is a rare congenital cardiac anomaly in which systemic and pulmonary venous streams cross without mixing at atrioventricular level. We report a case of crisscross heart with tricuspid atresia, double outlet right ventricle, and pulmonary stenosis, which was diagnosed prenatally. ...

journal_title：Congenital heart disease

authors： Ayabakan C,Binnetoğlu K,Sarısoy Ö,Tokel K

更新日期：2013-09-01 00:00:00

abstract：OBJECTIVE:Amiodarone is a highly effective antiarrhythmic therapy, however its toxicity profile often limits treatment. This is particularly relevant in adults with congenital heart disease (CHD), who are often young and in whom other antiarrhythmic agents commonly fail or are contraindicated. We sought to determine in...

journal_title：Congenital heart disease

authors： Moore BM,Cordina RL,McGuire MA,Celermajer DS

更新日期：2018-11-01 00:00:00

abstract：:Appropriate interpretation of a screening test's validity poses a challenge to the clinician. The purpose of this review is to revisit the terms sensitivity, specificity, likelihood ratio, and pre- and posttest probability and their application to the clinical setting. For illustration, we use a recently published art...

journal_title：Congenital heart disease

authors： Bolin E,Lam W

更新日期：2013-09-01 00:00:00

abstract：OBJECTIVE:Clinical genetic testing is expanding rapidly, but the application of new testing has not been reported in an unselected, comprehensive congenital heart disease (CHD) patient population. This study aims to identify cytogenetic testing practices and diagnostic yield in infants with CHD as an important first st...

journal_title：Congenital heart disease

authors： Connor JA,Hinton RB,Miller EM,Sund KL,Ruschman JG,Ware SM

更新日期：2014-03-01 00:00:00

abstract：:In medical literature, few cases of Rasmussen's aneurysm have been reported until now, and to the best of our knowledge, there has been no description of a case of Rasmussen's aneurysm in childhood. The child described in the case report had a restrictive cardiomyopathy, complicated by pulmonary hypertension, in assoc...

journal_title：Congenital heart disease

authors： Gesuete V,Corzani A,Bronzetti G,Lovato L,Picchio FM

更新日期：2013-03-01 00:00:00

abstract：INTRODUCTION:The right ventricle (RV) supports the systemic circulation in patients who have had an intraatrial repair of transposition of the great arteries or have congenitally corrected transposition. There is concern about the ability of a systemic RV to support the additional volume load of pregnancy, and previous...

journal_title：Congenital heart disease

authors： Bowater SE,Selman TJ,Hudsmith LE,Clift PF,Thompson PJ,Thorne SA

更新日期：2013-07-01 00:00:00

abstract：OBJECTIVE:Atypical development, behavioral difficulties, and academic underachievement are common morbidities in children with a history of congenital heart defects and impact quality of life. Language and social-cognitive deficits have been described, which are associated with autism spectrum disorders. The current st...

journal_title：Congenital heart disease

authors： Bean Jaworski JL,Flynn T,Burnham N,Chittams JL,Sammarco T,Gerdes M,Bernbaum JC,Clancy RR,Solot CB,Zackai EH,McDonald-McGinn DM,Gaynor JW

更新日期：2017-07-01 00:00:00

abstract：:Absence of the aortic valve is a rare congenital heart defect that is detectable in the prenatal period. In this condition, functional aortic valve leaflets are absent; in their place are rudimentary, immobile noncoapting plate-like structures at the level of the annulus resulting in severe aortic regurgitation. We re...

journal_title：Congenital heart disease

authors： Sabati AA,Wong PC,Randolph L,Pruetz JD

更新日期：2014-05-01 00:00:00

abstract：OBJECTIVE:Enteral feeding is associated with decreased infection rates, decreased mechanical ventilation, decreased hospital length of stay, and improved wound healing. Enteral feeding difficulties are common in congenital heart disease. Our objective was to develop experience-based newborn feeding guidelines for the i...

journal_title：Congenital heart disease

authors： Simsic JM,Carpenito KR,Kirchner K,Peters S,Miller-Tate H,Joy B,Galantowicz M

更新日期：2017-05-01 00:00:00