Abstract:
:Pachydermodactyly describes a rare condition of localized fibromatosis, usually symmetrically affecting the interphalangeal joints of both hands. We describe a case of a new subtype of pachydermodactyly in a 14-year-old boy, which we term 'unilateral pachydermodactyly transgrediens'. This atypical pattern is caused by specific localized mechanical manipulation of the hands. This condition contributes to the completely indolent spectrum of pachydermodactyly, and usually does not need therapy. Therefore it is essential not to misinterpret it as an inflammatory state such as juvenile idiopathic arthritis. The correct diagnosis of pachydermodactyly and its rare subtypes, as we describe in this case, often spares the affected patients unnecessary invasive diagnostic procedures and immunosuppressive therapy.
journal_name
Clin Exp Dermatoljournal_title
Clinical and experimental dermatologyauthors
Nicolay JP,Faulhaber J,Kutzner H,Schneider SWdoi
10.1111/ced.12617subject
Has Abstractpub_date
2015-08-01 00:00:00pages
633-5issue
6eissn
0307-6938issn
1365-2230journal_volume
40pub_type
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