Isolated left ventricular apical hypoplasia.

Abstract:

:Isolated left ventricular (LV) apical hypoplasia is a recently described congenital abnormality characterized by: (1) a truncated and spherical LV configuration with rightward bulging of the interventricular septum, (2) deficiency of the myocardium within the LV apex with adipose tissue infiltrating the apex, (3) origin of the papillary muscle in the flattened anterior apex, and (4) elongation of the right ventricle wrapping around the deficient LV apex. In this report, we demonstrate these characteristic features with cardiac magnetic resonance imaging and summarize the existing information on isolated LV apical hypoplasia.

journal_name

Congenit Heart Dis

journal_title

Congenital heart disease

authors

Vanhecke TE,Decker J,Leonowicz N,Chinnaiyan KM

doi

10.1111/j.1747-0803.2011.00489.x

subject

Has Abstract

pub_date

2011-11-01 00:00:00

pages

646-9

issue

6

eissn

1747-079X

issn

1747-0803

journal_volume

6

pub_type

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