Exercise responses in children and adults with a Fontan circulation at simulated altitude.

abstract：OBJECTIVE:It was examined whether women and men (17-45 years) with operated congenital heart disease differ with respect to chances of employment. Patients were compared with the general population. DESIGN:Patients (n = 314) were classified by type of surgery (curative, reparative, palliative) as indicator of initial ...

journal_title：Congenital heart disease

authors： Geyer S,Norozi K,Buchhorn R,Wessel A

更新日期：2009-01-01 00:00:00

abstract：OBJECTIVES:To determine if patients evaluated using the pediatric chest pain standardized clinical assessment and management plan (SCAMP) in cardiology clinic were later diagnosed with unrecognized cardiac pathology, and to determine if other patients with cardiac pathology not enrolled in the SCAMP would have been ide...

journal_title：Congenital heart disease

authors： Kane DA,Friedman KG,Fulton DR,Geggel RL,Saleeb SF

更新日期：2016-09-01 00:00:00

abstract：:Scimitar syndrome is characterized by anomalous pulmonary venous drainage of a part or the whole of the right lung into the inferior vena cava (IVC). It is extremely uncommon in scimitar syndrome for the pulmonary veins to drain anomalously to a site other than the IVC. The following case report describes an otherwise...

journal_title：Congenital heart disease

authors： Kotecha MK,Krishnamanohar SR,Kumar RS

更新日期：2012-01-01 00:00:00

abstract：OBJECTIVE:Congenital cardiac defects represent the most common group of birth defects, affecting an estimated six per 1000 births. Genetic characterization of patients and families with cardiac defects has identified a number of genes required for heart development. Yet, despite the rapid pace of these advances, mutati...

journal_title：Congenital heart disease

authors： Thorsson T,Russell WW,El-Kashlan N,Soemedi R,Levine J,Geisler SB,Ackley T,Tomita-Mitchell A,Rosenfeld JA,Töpf A,Tayeh M,Goodship J,Innis JW,Keavney B,Russell MW

更新日期：2015-05-01 00:00:00

abstract：:Singleton pregnancy in patients with single ventricle after the Fontan operation has been reported with significant offspring and maternal complications. We report a twin pregnancy and premature delivery, in a patient following the Fontan operation. ...

journal_title：Congenital heart disease

authors： Nir A,Elchalal U,Hammerman C,Rein AJ

更新日期：2013-11-01 00:00:00

abstract：OBJECTIVE:To describe treatment, survival, and morbidity for liveborn infants with isolated transposition of great arteries (TGA). DESIGN:Population-based data from 7 European registries of congenital malformations (EUROCAT). RESULTS:Ninety-seven infants were diagnosed with isolated TGA and livebirth prevalence was 2...

journal_title：Congenital heart disease

authors： Garne E,Loane MA,Nelen V,Bakker MK,Gener B,Abramsky L,Addor MC,Queisser-Luft A

更新日期：2007-05-01 00:00:00

abstract：INTRODUCTION:The neurodevelopmental outcome of children with repaired congenital heart defect has risen in importance with improved survival. This study compares neurodevelopmental outcomes of children who had CHD with single ventricle physiology with those who had CHD with two-ventricle physiology. PATIENTS AND METHO...

journal_title：Congenital heart disease

authors： Hoskoppal A,Roberts H,Kugler J,Duncan K,Needelman H

更新日期：2010-03-01 00:00:00

abstract：OBJECTIVE:The 2016 American Board of Pediatrics (ABP) content outline is comprehensive, including more than 50 cardiology-specific objectives within eight content areas. This study complements the quantitative analysis of a Kentucky-wide survey of trainees, pediatricians, and pediatric cardiologists asking them to iden...

journal_title：Congenital heart disease

authors： Neal AE,Lehto E,Miller KH,Davis E,Ziegler C

更新日期：2018-09-01 00:00:00

abstract：PURPOSE:Right ventricular (RV) failure and ventricular dyssynchrony are strong determinants of prognosis in patients with adult congenital heart disease (ACHD). The aim of this study was to investigate the relationship between interventricular dyssynchrony (IVD) using cine-tagged magnetic resonance imaging (MRI) and RV...

journal_title：Congenital heart disease

authors： Nagao M,Yamasaki Y,Yonezawa M,Matsuo Y,Kamitani T,Yamamura K,Sakamoto I,Abe K,Kawanami S,Honda H

更新日期：2015-05-01 00:00:00

abstract：OBJECTIVE:Stent placement has become a widely used method of treatment for coarctation of the aorta (COA). Our goal was to find echocardiographic indices that would correlate best with directly measured gradients across the coarctation stent. MATERIAL AND METHODS:Pediatric patients with COA who underwent intra-aortic ...

journal_title：Congenital heart disease

authors： Tang L,Forbes TJ,Du W,Zilberman MV

更新日期：2009-07-01 00:00:00

abstract：OBJECTIVE:The surgical management of adults with congenital heart disease (ACHD) offers a great challenge, with a large number of anomalies with complex pathophysiology necessitating specific treatments. Pre- and postoperative morbidity has been relatively high, and the influencing factors are not completely identified...

journal_title：Congenital heart disease

authors： Nozohoor S,Gustafsson R,Kallonen J,Sjögren J

更新日期：2013-07-01 00:00:00

abstract：OBJECTIVE:We studied, as a physiological benchmark, acute effects of right ventricular (RV) apical, RV outflow, and left ventricular (LV) pacing in children with normal cardiac function on LV and RV function and ventricular-ventricular interactions. DESIGN:The design of the study was a prospective, acute intervention....

journal_title：Congenital heart disease

authors： Friedberg MK,Dubin AM,Van Hare GF,McDaniel G,Niksch A,Rosenthal DN

更新日期：2009-09-01 00:00:00

abstract：:Appropriate interpretation of a screening test's validity poses a challenge to the clinician. The purpose of this review is to revisit the terms sensitivity, specificity, likelihood ratio, and pre- and posttest probability and their application to the clinical setting. For illustration, we use a recently published art...

journal_title：Congenital heart disease

authors： Bolin E,Lam W

更新日期：2013-09-01 00:00:00

abstract：INTRODUCTION:Pectus excavatum is commonly viewed as a benign condition. Associated alterations in hemodynamics are rare. We present an unusual case of right ventricular inflow obstruction and hemodynamic compromise as a consequence of pectus excavatum encountered during surgical intervention. CASE:a 15-year-old male w...

journal_title：Congenital heart disease

authors： Galas JM,van der Velde ME,Chiravuri SD,Farley F,Parra D,Ensing GJ

更新日期：2009-05-01 00:00:00

abstract：OBJECTIVE:To assess how obesity or diabetes mellitus impacts outcomes in patients undergoing cardiac surgery in pediatric hospitals. DESIGN:A multi-institutional, matched case-control study of the Pediatric Health Information System database was performed. SETTING:Tertiary children's hospitals in the United States. ...

journal_title：Congenital heart disease

authors： Shamszad P,Rossano JW,Marino BS,Lowry AW,Knudson JD

更新日期：2016-09-01 00:00:00

abstract：OBJECTIVE:Inappropriate implantable cardioverter defibrillator (ICD) shocks in children and patients with congenital heart disease (CHD) remain a major complication of device therapy, occurring in as many as 50% of children with ICDs. New generation devices include algorithms designed to minimize inappropriate shocks. ...

journal_title：Congenital heart disease

authors： Goldstein SA,LaPage MJ,Dechert BE,Serwer GA,Yu S,Lowery RE,Bradley DJ

更新日期：2018-05-01 00:00:00

abstract：OBJECTIVES:The primary objective of this study was to demonstrate that pulmonary artery (PA) debanding via cardiac catheterization using balloon angioplasty is feasible and safe in swine. The secondary objectives were to determine the acute and long-term effects of this therapy. DESIGN:This is a chronic survival exper...

journal_title：Congenital heart disease

authors： Perez M,Kumar TS,Hoskoppal D,Akkhawattanangkul Y,Allen K,Knott-Craig CJ,Waller BR,Sathanandam S

更新日期：2017-05-01 00:00:00

abstract：OBJECTIVE:We sought to define what clinical parameters were related to the ultimate outcome in Fontan patients who had developed protein-losing enteropathy (PLE). BACKGROUND:PLE is a serious complication of the Fontan operation. Several preoperative and perioperative findings are associated with later PLE. However, th...

journal_title：Congenital heart disease

authors： Silvilairat S,Cabalka AK,Cetta F,Grogan M,Hagler DJ,O'Leary PW

更新日期：2008-07-01 00:00:00

abstract：BACKGROUND:Pulmonary atresia with intact ventricular septum is a unique congenital malformation of the heart in which patients may undergo single-, two- or 1½- ventricle repair. Size of the tricuspid valve annulus, morphology of the right ventricle and presence of ventriculocoronary connections can all impact the selec...

journal_title：Congenital heart disease

authors： Loomba RS,Pelech AN

更新日期：2018-01-01 00:00:00

abstract：OBJECTIVE:Amiodarone is a highly effective antiarrhythmic therapy, however its toxicity profile often limits treatment. This is particularly relevant in adults with congenital heart disease (CHD), who are often young and in whom other antiarrhythmic agents commonly fail or are contraindicated. We sought to determine in...

journal_title：Congenital heart disease

authors： Moore BM,Cordina RL,McGuire MA,Celermajer DS

更新日期：2018-11-01 00:00:00

abstract：INTRODUCTION:Cardiovascular diseases in pediatric pathologies have emerged in the recent years in sub-Saharan Africa (SSA), with congenital heart diseases (CHDs) being the most frequent. Unfortunately, their diagnosis is usually delayed, thereby increasing childhood morbidity and mortality. OBJECTIVES:Describe the cli...

journal_title：Congenital heart disease

authors： Kamdem F,Kedy Koum D,Hamadou B,Yemdji M,Luma H,Doualla MS,Noukeu D,Barla E,Akazong C,Dzudie A,Ngote H,Monkam Y,Mouliom S,Kingue S

更新日期：2018-01-01 00:00:00

abstract：BACKGROUND:Interatrial shunts, caused by either atrial septal defect (ASD) or patent foramen ovale, have been reported to have a familial association. We sought to examine the familial risk of isolated interatrial shunt and explore associated comorbidities of stroke, transient ischemic attack (TIA), and migraine using ...

journal_title：Congenital heart disease

authors： Steenblik MH,Mineau GP,Pimentel R,Michaels AD

更新日期：2009-11-01 00:00:00

abstract：:We present a rare case of spontaneous closure of a fistula between the left coronary artery and the right ventricle (RV) within a few days of newborn period. A 14-day-old male newborn was referred to our clinic for investigation of tachypnea and cardiac murmur. A color flow Doppler echocardiography revealed turbulent ...

journal_title：Congenital heart disease

authors： Yilmazer MM,Demir F,Yolbaş I,Bilici M

更新日期：2014-01-01 00:00:00

abstract：INTRODUCTION:The right ventricle (RV) supports the systemic circulation in patients who have had an intraatrial repair of transposition of the great arteries or have congenitally corrected transposition. There is concern about the ability of a systemic RV to support the additional volume load of pregnancy, and previous...

journal_title：Congenital heart disease

authors： Bowater SE,Selman TJ,Hudsmith LE,Clift PF,Thompson PJ,Thorne SA

更新日期：2013-07-01 00:00:00

abstract：OBJECTIVE:Enteral feeding is associated with decreased infection rates, decreased mechanical ventilation, decreased hospital length of stay, and improved wound healing. Enteral feeding difficulties are common in congenital heart disease. Our objective was to develop experience-based newborn feeding guidelines for the i...

journal_title：Congenital heart disease

authors： Simsic JM,Carpenito KR,Kirchner K,Peters S,Miller-Tate H,Joy B,Galantowicz M

更新日期：2017-05-01 00:00:00

abstract：OBJECTIVE:Atrial septal defect (ASD) is the second most common congenital heart defect (CHD) and is observed in families as an autosomal dominant trait as well as in nonfamilial CHD. Mutations in the NKX2-5 gene, located on chromosome 5, are associated with ASD, often combined with conduction disturbances, cardiomyopat...

journal_title：Congenital heart disease

authors： Ellesøe SG,Johansen MM,Bjerre JV,Hjortdal VE,Brunak S,Larsen LA

更新日期：2016-05-01 00:00:00

abstract：OBJECTIVE:Management of the patients with transposition of the great arteries and intact ventricular septum may be challenging beyond the newborn period. Herein, we would like to present our alternative strategy for training the left ventricle in these patients. METHODS:Six patients with transposition of the great art...

journal_title：Congenital heart disease

authors： Bilal MS,Özyüksel A,Kemal Avşar M,Demiroluk Ş,Küçükosmanoğlu O,Yalçın Y

更新日期：2019-05-01 00:00:00

abstract：OBJECTIVE:Atypical development, behavioral difficulties, and academic underachievement are common morbidities in children with a history of congenital heart defects and impact quality of life. Language and social-cognitive deficits have been described, which are associated with autism spectrum disorders. The current st...

journal_title：Congenital heart disease

authors： Bean Jaworski JL,Flynn T,Burnham N,Chittams JL,Sammarco T,Gerdes M,Bernbaum JC,Clancy RR,Solot CB,Zackai EH,McDonald-McGinn DM,Gaynor JW

更新日期：2017-07-01 00:00:00

abstract：BACKGROUND & AIMS:Fontan surgery for single ventricle congenital heart disease leads to Fontan-associated liver disease (FALD). Typical laboratory tests, imaging, and histopathology cannot predict clinical severity in FALD. HepQuant SHUNT is a proprietary serum test of hepatic function and physiology that has not yet b...

journal_title：Congenital heart disease

authors： Lemmer A,VanWagner L,Gasanova Z,Helmke S,Everson GT,Ganger D

更新日期：2019-11-01 00:00:00

abstract：BACKGROUND:Congenital heart defects affect nearly 1% of all children born per year in the United States, and complete atrioventricular canal (CAVC) accounts for 2%-9%. While several patch materials have been used for septal defect closure during CAVC repair, clear superiority of one material over another has yet to be ...

journal_title：Congenital heart disease

authors： Al Haddad E,LaPar DJ,Dayton J,Stephens EH,Bacha E

更新日期：2018-11-01 00:00:00