Acute effects of single-site pacing from the left and right ventricle on ventricular function and ventricular-ventricular interactions in children with normal hearts.

abstract：OBJECTIVE:Amiodarone is a highly effective antiarrhythmic therapy, however its toxicity profile often limits treatment. This is particularly relevant in adults with congenital heart disease (CHD), who are often young and in whom other antiarrhythmic agents commonly fail or are contraindicated. We sought to determine in...

journal_title：Congenital heart disease

authors： Moore BM,Cordina RL,McGuire MA,Celermajer DS

更新日期：2018-11-01 00:00:00

abstract：OBJECTIVE:To describe treatment, survival, and morbidity for liveborn infants with isolated transposition of great arteries (TGA). DESIGN:Population-based data from 7 European registries of congenital malformations (EUROCAT). RESULTS:Ninety-seven infants were diagnosed with isolated TGA and livebirth prevalence was 2...

journal_title：Congenital heart disease

authors： Garne E,Loane MA,Nelen V,Bakker MK,Gener B,Abramsky L,Addor MC,Queisser-Luft A

更新日期：2007-05-01 00:00:00

abstract：:Absence of the aortic valve is a rare congenital heart defect that is detectable in the prenatal period. In this condition, functional aortic valve leaflets are absent; in their place are rudimentary, immobile noncoapting plate-like structures at the level of the annulus resulting in severe aortic regurgitation. We re...

journal_title：Congenital heart disease

authors： Sabati AA,Wong PC,Randolph L,Pruetz JD

更新日期：2014-05-01 00:00:00

abstract：:Currently, the role of stress echocardiography primarily resides in diagnosing acquired coronary artery disease (CAD) in adults. Besides an increasing concern for traditional CAD in young patients due to obesity and other chronic pediatric diseases, there is also a growing population of adolescents and young adults wi...

journal_title：Congenital heart disease

authors： Ermis P

更新日期：2017-09-01 00:00:00

abstract：:Marfan syndrome is a well-described autosomal dominant syndrome with widely variable clinical manifestations. Cardiovascular complications include mitral valve prolapse with or without associated mitral valve insufficiency, aortic root dilatation, and most importantly the occasional development of aortic aneurysms or ...

journal_title：Congenital heart disease

authors： Zangwill SD,Brown MD,Bryke CR,Cava JR,Segura AD

更新日期：2006-09-01 00:00:00

abstract：INTRODUCTION:Pectus excavatum is commonly viewed as a benign condition. Associated alterations in hemodynamics are rare. We present an unusual case of right ventricular inflow obstruction and hemodynamic compromise as a consequence of pectus excavatum encountered during surgical intervention. CASE:a 15-year-old male w...

journal_title：Congenital heart disease

authors： Galas JM,van der Velde ME,Chiravuri SD,Farley F,Parra D,Ensing GJ

更新日期：2009-05-01 00:00:00

abstract：OBJECTIVE:The purpose of this study was to compare neurological development of children with cyanotic or hemodynamically impaired congenital heart disease (CHD) and healthy controls by using "Bayley Scales of Infant and Toddler Development Screening Test, Third Edition" (Bayley-III). PATIENTS:Children with CHD (n = 37...

journal_title：Congenital heart disease

authors： Hallioglu O,Gurer G,Bozlu G,Karpuz D,Makharoblidze K,Okuyaz C

更新日期：2015-11-01 00:00:00

abstract：OBJECTIVE:The surgical management of adults with congenital heart disease (ACHD) offers a great challenge, with a large number of anomalies with complex pathophysiology necessitating specific treatments. Pre- and postoperative morbidity has been relatively high, and the influencing factors are not completely identified...

journal_title：Congenital heart disease

authors： Nozohoor S,Gustafsson R,Kallonen J,Sjögren J

更新日期：2013-07-01 00:00:00

abstract：BACKGROUND:Hyponatremia (HN) is relatively common in adults with congenital heart disease and is a powerful predictor of mortality. However, the precise relationship of HN to the Fontan pathophysiology remains unknown. PURPOSE:Our study aimed to clarify the association of HN to the Fontan pathophysiology. METHODS AND...

journal_title：Congenital heart disease

authors： Ohuchi H,Negishi J,Ono S,Miyake A,Toyota N,Tamaki W,Miyazaki A,Yamada O

更新日期：2011-07-01 00:00:00

abstract：PURPOSE:The aim of this article was to assess the role of MRI in the diagnosis and management of a variety of complex aortic arch anomalies. MATERIALS AND METHODS:Imaging was performed on a 1.5T Philips Gyroscan Intera. We retrospectively reviewed all cardiac MR scans performed from November 2003 to February 2007 at o...

journal_title：Congenital heart disease

authors： Cantinotti M,Hegde S,Bell A,Razavi R

更新日期：2008-03-01 00:00:00

abstract：BACKGROUND:Left cardiac sympathetic denervation (LCSD) exerts significant antifibrillatory effects in patients with long QT syndrome (LQTS). Recently, electromechanical window (EMW) has emerged as a novel torsadogenic marker in LQTS, superior to QT interval (QTc) in distinguishing symptomatic from asymptomatic patients...

journal_title：Congenital heart disease

authors： Schneider AE,Bos JM,Ackerman MJ

更新日期：2016-09-01 00:00:00

abstract：OBJECTIVE:The objective of this study was to characterize the natural history of metabolic uncoupling (type B hyperlactemia and hyperglycemia) following cardiopulmonary bypass (CPB), and to determine the impact of insulin therapy on time to lactate normalization in patients without low cardiac output. DESIGN:The desig...

journal_title：Congenital heart disease

authors： Palermo RA,Palac HL,Wald EL,Wainwright MS,Costello JM,Eltayeb OM,Backer CL,Epting CL

更新日期：2015-11-01 00:00:00

abstract：OBJECTIVE:Stent placement has become a widely used method of treatment for coarctation of the aorta (COA). Our goal was to find echocardiographic indices that would correlate best with directly measured gradients across the coarctation stent. MATERIAL AND METHODS:Pediatric patients with COA who underwent intra-aortic ...

journal_title：Congenital heart disease

authors： Tang L,Forbes TJ,Du W,Zilberman MV

更新日期：2009-07-01 00:00:00

abstract：:A 52-year-old male patient, with a medical history of surgically repaired double outlet right ventricle presented with severe aortic stenosis (AS) and hepatitis C with cirrhosis, presented with New York Heart Association Class IV heart failure. During evaluation for a liver transplant, he was deemed a poor surgical ca...

journal_title：Congenital heart disease

authors： Keswani A,Verma A,Dann K,Ventura L,Lucas V,Shah S,Ramee S

更新日期：2014-09-01 00:00:00

abstract：:Isolated left ventricular (LV) apical hypoplasia is a recently described congenital abnormality characterized by: (1) a truncated and spherical LV configuration with rightward bulging of the interventricular septum, (2) deficiency of the myocardium within the LV apex with adipose tissue infiltrating the apex, (3) orig...

journal_title：Congenital heart disease

authors： Vanhecke TE,Decker J,Leonowicz N,Chinnaiyan KM

更新日期：2011-11-01 00:00:00

abstract：INTRODUCTION:Cardiovascular diseases in pediatric pathologies have emerged in the recent years in sub-Saharan Africa (SSA), with congenital heart diseases (CHDs) being the most frequent. Unfortunately, their diagnosis is usually delayed, thereby increasing childhood morbidity and mortality. OBJECTIVES:Describe the cli...

journal_title：Congenital heart disease

authors： Kamdem F,Kedy Koum D,Hamadou B,Yemdji M,Luma H,Doualla MS,Noukeu D,Barla E,Akazong C,Dzudie A,Ngote H,Monkam Y,Mouliom S,Kingue S

更新日期：2018-01-01 00:00:00

abstract：BACKGROUND:It has been reported that gender differences in cardiovascular outcomes found in adults also are present in children who undergo surgical repair for congenital heart disease. METHODS:California statewide hospital discharge data 1989-99 were used to study outcomes in children <18 years undergoing cardiac sur...

journal_title：Congenital heart disease

authors： Klitzner TS,Lee M,Rodriguez S,Chang RK

更新日期：2006-05-01 00:00:00

abstract：BACKGROUND:Transient elastography (TE) offers a noninvasive correlate with the degree of hepatic fibrosis. However, factors other than fibrosis affect liver stiffness. We sought to determine whether hepatic congestion related to hemodynamics in Fontan circulation influences liver stiffness measurement (LSM) assessed by...

journal_title：Congenital heart disease

authors： Wu FM,Opotowsky AR,Raza R,Harney S,Ukomadu C,Landzberg MJ,Valente AM,Breitbart RE,Singh MN,Gauvreau K,Jonas MM

更新日期：2014-09-01 00:00:00

abstract：PURPOSE:Right ventricular (RV) failure and ventricular dyssynchrony are strong determinants of prognosis in patients with adult congenital heart disease (ACHD). The aim of this study was to investigate the relationship between interventricular dyssynchrony (IVD) using cine-tagged magnetic resonance imaging (MRI) and RV...

journal_title：Congenital heart disease

authors： Nagao M,Yamasaki Y,Yonezawa M,Matsuo Y,Kamitani T,Yamamura K,Sakamoto I,Abe K,Kawanami S,Honda H

更新日期：2015-05-01 00:00:00

abstract：AIM:The Fontan circulation is highly dependent on ventilation, improving pulmonary blood flow and cardiac output. A reduced ventilatory function is reported in these patients. The extent of this impairment and its relation to exercise capacity and quality of life is unknown and objective of this study. METHODS:This mu...

journal_title：Congenital heart disease

authors： Callegari A,Neidenbach R,Milanesi O,Castaldi B,Christmann M,Ono M,Müller J,Ewert P,Hager A

更新日期：2019-03-01 00:00:00

abstract：OBJECTIVE:Determine the accuracy of echocardiography to diagnose coronary anatomy in transposition of the great arteries and to evaluate the effect of accuracy on surgical outcomes and changes in accuracy over time. DESIGN:Retrospective chart review of neonates admitted February 1999 to March 2013 with transposition. ...

journal_title：Congenital heart disease

authors： Fundora MP,Aregullin EO,Wernovsky G,Welch EM,Muniz JC,Sasaki N,Hannan RL,Burke RP,Lopez L

更新日期：2016-12-01 00:00:00

abstract：OBJECTIVE:Traditionally, karyotype and fluorescence in situ hybridization (FISH) were used for cytogenetic testing of infants with congenital heart disease (CHD) who underwent cardiac surgery at our institution. Recently, chromosome microarray analysis (CMA) has been performed in lieu of the traditional tests. A standa...

journal_title：Congenital heart disease

authors： Buckley JR,Kavarana MN,Chowdhury SM,Scheurer MA

更新日期：2015-05-01 00:00:00

abstract：:The Fontan operation has gone through multiple incarnations since Fontan and Baudet's initial description in 1971. Through the medical dossier of a patient with a single ventricle, we plot the history of medical, surgical, and percutaneous interventions over the past 40 years, specifically focusing on the Fontan proce...

journal_title：Congenital heart disease

authors： AboulHosn JA,Shavelle DM,Castellon Y,Criley JM,Plunkett M,Pelikan P,Dinh H,Child JS

更新日期：2007-01-01 00:00:00

abstract：OBJECTIVE:Atypical development, behavioral difficulties, and academic underachievement are common morbidities in children with a history of congenital heart defects and impact quality of life. Language and social-cognitive deficits have been described, which are associated with autism spectrum disorders. The current st...

journal_title：Congenital heart disease

authors： Bean Jaworski JL,Flynn T,Burnham N,Chittams JL,Sammarco T,Gerdes M,Bernbaum JC,Clancy RR,Solot CB,Zackai EH,McDonald-McGinn DM,Gaynor JW

更新日期：2017-07-01 00:00:00

abstract：:An 18-year-old patient with a window type of patent ductus arteriosus and acquired rheumatic mitral stenosis is reported for its rarity. The pitfalls in the diagnosis and surgical management of this condition are discussed. ...

journal_title：Congenital heart disease

authors： Talwar S,Upadhyay M,Ramakrishnan S,Gharade P,Choudhary SK,Airan B

更新日期：2013-01-01 00:00:00

abstract：:We present a rare case of spontaneous closure of a fistula between the left coronary artery and the right ventricle (RV) within a few days of newborn period. A 14-day-old male newborn was referred to our clinic for investigation of tachypnea and cardiac murmur. A color flow Doppler echocardiography revealed turbulent ...

journal_title：Congenital heart disease

authors： Yilmazer MM,Demir F,Yolbaş I,Bilici M

更新日期：2014-01-01 00:00:00

abstract：:As physicians and caregivers of children with congenital heart disease, we are aware of the increasing need for procedures requiring anesthesia. While these procedures may be ideal for medical and cardiac surgical management, the risks and benefits must be assessed carefully. There are well known risks of cardiovascul...

journal_title：Congenital heart disease

authors： Char D,Ramamoorthy C,Wise-Faberowski L

更新日期：2016-05-01 00:00:00

abstract：OBJECTIVE:The use of video-assisted thoracoscopic surgery (VATS) is becoming increasingly common in the treatment of congenital heart defects, particularly for the division of vascular rings. We compare the short-term outcomes of vascular ring division by VATS as opposed to open thoracotomy and discuss new issues raise...

journal_title：Congenital heart disease

authors： Kogon BE,Forbess JM,Wulkan ML,Kirshbom PM,Kanter KR

更新日期：2007-03-01 00:00:00

abstract：:Iron deficiency state in patients with cyanotic congenital heart disease can mimic as well as aggravate hyperviscosity symptoms. Correction of iron deficiency in these cases is expected to improve symptoms. We report an unexpected occurrence of refractory cyanotic spell in a child with tetralogy of Fallot due to throm...

journal_title：Congenital heart disease

authors： Gupta SK,Saxena A,Anil OM,Bisoi AK

更新日期：2012-07-01 00:00:00

abstract：:This is a case report reviewing the presentation and clinical course of a patient diagnosed with abdominal aortic atresia at the level caudal to the superior mesenteric artery. Patients with abdominal aortic atresia need to be evaluated for associated underlying syndromes or diseases. Although the prognosis for this d...

journal_title：Congenital heart disease

authors： Brown J,Shehata BM,Campbell R

更新日期：2011-05-01 00:00:00