Glanzmann's thrombasthenia.

Abstract:

:Glanzmann's thrombasthenia (GT) is an uncommon cause of bleeding in children. We diagnosed two siblings as having GT on the basis of flow cytometric studies. Both had cutaneous bleedings and epistaxis since early childhood. Hematological investigations revealed prolonged bleeding time and a normal platelet count. Both the patients had absence of aggregation of platelets with the agonist adenosine diphosphate. Absence of the GPIIb/IIIa receptor was confirmed by flow cytometry. A short review of the disorder is presented.

journal_name

Indian J Pediatr

authors

Tullu MS,Dixit PS,Nair SB,Kamat JR,Vaswani RK,Shetty SD,Pawar AR

doi

10.1007/BF02723255

keywords:

subject

Has Abstract

pub_date

2001-06-01 00:00:00

pages

563-6

issue

6

eissn

0019-5456

issn

0973-7693

journal_volume

68

pub_type

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