Abstract：
:Idiopathic "benign" intracranial hypertension is an uncommon but important cause of headache that can lead to visual loss. This study was undertaken to review our experience in the diagnosis and management of idiopathic intracranial hypertension, giving special attention to treatments used. A retrospective chart review was conducted on 32 patients diagnosed with idiopathic intracranial hypertension between 1984 and 1995. Subjects included 23 females and ranged in age from 2 to 17.5 years. Headache was the most common symptom, followed by nausea and vomiting, double vision, and visual loss. Papilledema was the most common sign. Others were VIth cranial nerve palsy and compromised visual acuity at or within 3 months of presentation. Management included administration of acetazolamide or corticosteroids, lumboperitoneal shunt, optic nerve fenestration, and repeat lumbar puncture. Treatment combinations were used in 40% of cases. During follow-up, headache, papilledema, and decreased visual acuity persisted for longer than 10 months in a significant number of patients. We conclude that idiopathic intracranial hypertension causes significant short- and long-term morbidity with no proven effective treatment available. A prospective study is needed to establish the indications for treatment and the efficacy of the treatments used.
journal_name
J Child Neuroljournal_title
Journal of child neurologyauthors
Salman MS,Kirkham FJ,MacGregor DLdoi
10.1177/088307380101600701subject
Has Abstractpub_date
2001-07-01 00:00:00pages
465-70issue
7eissn
0883-0738issn
1708-8283journal_volume
16pub_type
杂志文章abstract：:We describe a case of pediatric Sjögren's syndrome with progressive neurologic involvement. At age 4 years, she had been diagnosed with Melkersson-Rosenthal syndrome. After being stable with facial diplegia and swelling for 5 years, she acutely presented with diplopia, vertigo, and ataxia. Cranial magnetic resonance i...
journal_title：Journal of child neurology
pub_type： 杂志文章
doi：10.1177/088307380101600911
更新日期：2001-09-01 00:00:00
abstract：:The past 10 years' experience with bone marrow transplantation from normal, immunologically compatible donors indicates its possible use in various neurometabolic diseases, particularly in a patient who has not suffered irreparable brain damage. This experience may be a prelude to treatment by somatic gene therapy. Th...
journal_title：Journal of child neurology
pub_type： 杂志文章,评审
doi：10.1177/08830738920070011711
更新日期：1992-04-01 00:00:00
abstract：:Lissencephaly is a brain malformation manifested by a smooth cerebral surface and caused by incomplete neuronal migration. Clinical sequellae include minor craniofacial changes (bitemporal hollowing, small jaw), severe mental retardation, and other neurological abnormalities. Patients with classical or type I lissence...
journal_title：Journal of child neurology
pub_type： 杂志文章
doi：10.1177/088307389000500113
更新日期：1990-01-01 00:00:00
abstract：:The aim of the present study was to assess the emotional and cognitive aspects of social cognition among patients with rolandic epilepsy. A computerized neuropsychological battery was used for cognitive evaluation. Affective and cognitive social cognition were evaluated using two computerized Theory of Mind tasks. Cog...
journal_title：Journal of child neurology
pub_type： 杂志文章
doi：10.1177/0883073811414420
更新日期：2012-02-01 00:00:00
abstract：BACKGROUND:The classic phenotype of CLN2 disease (neuronal ceroid lipofuscinosis type 2) typically manifests between ages 2 and 4 years with a predictable clinical course marked by epilepsy, language developmental delay, and rapid psychomotor decline. Atypical phenotypes exhibit variable time of onset, symptomatology, ...
journal_title：Journal of child neurology
pub_type： 杂志文章
doi：10.1177/0883073820977997
更新日期：2020-12-23 00:00:00
abstract：:The standard physical examination evaluation for a proprioception abnormality depends upon the patient's ability to follow directions and respond to the examiner, a skill not yet developed in toddlers. This study demonstrates a new proprioception examination method that may allow for better localization of lesions and...
journal_title：Journal of child neurology
pub_type： 杂志文章
doi：10.1177/0883073818812348
更新日期：2019-03-01 00:00:00
abstract：:This study sought to investigate cognitive outcomes following pediatric arterial ischemic stroke and explore predictors. Participants included 36 children with perinatal or childhood arterial ischemic stroke and a comparison group of 15 children with asthma. Outcomes included cognitive ability, executive functions, an...
journal_title：Journal of child neurology
pub_type： 杂志文章,多中心研究
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更新日期：2014-07-01 00:00:00
abstract：:Corpus callosotomy is a palliative procedure performed to reduce the severity of drug-resistant epilepsy. The authors assessed its efficacy on different seizure types in 20 subjects (age range 5-19 years); 8 with active vagus nerve stimulator. Fifteen had complete callosotomy, 3 had anterior 2/3, and 2 had anterior 2/...
journal_title：Journal of child neurology
pub_type： 杂志文章
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更新日期：2017-06-01 00:00:00
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journal_title：Journal of child neurology
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更新日期：2009-05-01 00:00:00
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journal_title：Journal of child neurology
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更新日期：2012-02-01 00:00:00
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journal_title：Journal of child neurology
pub_type： 杂志文章
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更新日期：2018-06-01 00:00:00
abstract：:Diamond-Blackfan anemia is a congenital hypoproliferative anemia known to be associated with diverse physical anomalies affecting the thumb, craniofacial bones, urogenital system, and heart; prematurity; and fetal demise. We report the case of a 16-month-old boy with Diamond-Blackfan anemia noted to have decreased use...
journal_title：Journal of child neurology
pub_type： 杂志文章
doi：10.1177/08830738030180111301
更新日期：2003-11-01 00:00:00
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journal_title：Journal of child neurology
pub_type： 杂志文章
doi：10.1177/0883073807307099
更新日期：2007-11-01 00:00:00
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journal_title：Journal of child neurology
pub_type： 杂志文章
doi：10.1177/0883073809338326
更新日期：2010-03-01 00:00:00
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journal_title：Journal of child neurology
pub_type： 杂志文章
doi：10.1177/088307380101601213
更新日期：2001-12-01 00:00:00
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journal_title：Journal of child neurology
pub_type： 杂志文章,评审
doi：10.1177/08830738040190100401
更新日期：2004-10-01 00:00:00
abstract：:The spectrum of clinical disease in juvenile Huntington's disease differs from that seen in adults. Younger patients often present with seizures, dystonia and rigidity. The mechanism and type of seizures, timing of onset and electrographic features have not been well characterized in either adults or children. We desc...
journal_title：Journal of child neurology
pub_type： 杂志文章
doi：
更新日期：2004-07-01 00:00:00
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journal_title：Journal of child neurology
pub_type： 杂志文章,评审
doi：10.1177/0883073807304011
更新日期：2007-06-01 00:00:00
abstract：:The most devastating complications of tuberous sclerosis complex affect the central nervous system and include epilepsy, mental retardation, autism, and glial tumors. Mutations in one of two genes, TSC1 and TSC2, result in a similar disease phenotype by disrupting the normal interaction of their protein products, hama...
journal_title：Journal of child neurology
pub_type： 杂志文章,评审
doi：10.1177/08830738040190091401
更新日期：2004-09-01 00:00:00
abstract：:Postinfectious encephalomyelitis and multiple sclerosis have clinical, immunologic, and neuroradiographic similarities. We studied HLA determinants in six white children consecutively diagnosed with postinfectious encephalomyelitis. Each of the children had HLA determinants which have been associated with multiple scl...
journal_title：Journal of child neurology
pub_type： 杂志文章
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更新日期：1989-07-01 00:00:00
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journal_title：Journal of child neurology
pub_type： 杂志文章,评审
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journal_title：Journal of child neurology
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journal_title：Journal of child neurology
pub_type： 杂志文章
doi：10.1177/088307389200700214
更新日期：1992-04-01 00:00:00
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journal_title：Journal of child neurology
pub_type： 杂志文章
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更新日期：2014-03-01 00:00:00
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journal_title：Journal of child neurology
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更新日期：2013-11-01 00:00:00
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journal_title：Journal of child neurology
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doi：10.1177/088307380201700707
更新日期：2002-07-01 00:00:00
abstract：:An infant with a neonatal form of nemaline myopathy showed ultrastructural features of muscle immaturity. Immaturity was characterized by an abnormal presence of myotubes, as well as cells in clusters within a common basement membrane and a great number of satellite cells adhering to very small muscle fibers. In addit...
journal_title：Journal of child neurology
pub_type： 杂志文章
doi：10.1177/088307389000500209
更新日期：1990-04-01 00:00:00
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journal_title：Journal of child neurology
pub_type： 杂志文章,评审
doi：
更新日期：1995-11-01 00:00:00
abstract：:Intracranial tumors are the most common solid tumors in children. The infratentorial compartment will be the primary site for 60% to 70% of these tumors, including astrocytomas, medulloblastomas, and ependymomas. Several technological advancements have increased our knowledge of the cell biology of pediatric brain tum...
journal_title：Journal of child neurology
pub_type： 杂志文章,评审
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更新日期：2008-10-01 00:00:00
abstract：:This population-based cross-sectional study evaluates the clinical value of electroretinography and visual evoked potentials in childhood brain tumor survivors. A flash electroretinography and a checkerboard reversal pattern visual evoked potential (or alternatively a flash visual evoked potential) were done for 51 su...
journal_title：Journal of child neurology
pub_type： 杂志文章
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更新日期：2016-07-01 00:00:00
