Abstract:
:We describe a case of pediatric Sjögren's syndrome with progressive neurologic involvement. At age 4 years, she had been diagnosed with Melkersson-Rosenthal syndrome. After being stable with facial diplegia and swelling for 5 years, she acutely presented with diplopia, vertigo, and ataxia. Cranial magnetic resonance imaging (MRI) showed a left dorsal midbrain lesion. Serologic and histopathologic findings confirmed primary Sjögren's syndrome. She responded well to intravenous methylprednisolone, with subsequent clinical improvement and MRI resolution. This report reviews the pediatric literature and underscores the importance of considering Sjögren's syndrome in a child with unexplained facial weakness and in the differential diagnosis of pediatric stroke.
journal_name
J Child Neuroljournal_title
Journal of child neurologyauthors
Gottfried JA,Finkel TH,Hunter JV,Carpentieri DF,Finkel RSdoi
10.1177/088307380101600911subject
Has Abstractpub_date
2001-09-01 00:00:00pages
683-5issue
9eissn
0883-0738issn
1708-8283journal_volume
16pub_type
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