Cholesteryl ester storage disease: protean presentations of lysosomal acid lipase deficiency.

abstract：:Acetylcholinesterase (AChE) activity was measured in rectal suction biopsies from 392 patients investigated for Hirschsprung's disease (HD). Results in HD (2.7-23.7 RU; n = 37) were not clearly differentiated from those in patients without HD (0.6-18.0 RU; n = 355). Sample instability was shown not to be a significant...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Wells FE,Addison GM

更新日期：1986-11-01 00:00:00

abstract：OBJECTIVE:The aim of the present study was to examine the effects of early and high intravenous (IV) amino acid (AA) supplementation on growth, health, and neurodevelopment of extremely-low-birth-weight (ELBW) infants throughout their first 2 years of life. METHODS:Infants were prospectively randomized in a double-mas...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Blanco CL,Gong AK,Schoolfield J,Green BK,Daniels W,Liechty EA,Ramamurthy R

更新日期：2012-05-01 00:00:00

abstract：OBJECTIVE:Fortified spreads (FSs) have proven effective in the rehabilitation of severely malnourished children. We examined acceptability, growth and change in blood haemoglobin (Hb) concentration among moderately underweight ambulatory infants given FS. METHODS:This was a randomised, controlled, parallel-group, inve...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Kuusipalo H,Maleta K,Briend A,Manary M,Ashorn P

更新日期：2006-10-01 00:00:00

abstract：:Milk was collected from eight mothers. Total lipid and free fatty acids were determined on collection. The samples were divided into aliquots and stored at 25, 4, or -11 degrees C for 6, 12, 24, or 48 h. Additional samples were stored at -11 or -70 degrees C for 1, 2, 4, 6, or 8 weeks. The effect of temperature, lengt...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Lavine M,Clark RM

更新日期：1987-09-01 00:00:00

abstract：OBJECTIVES:We conducted this mass screening study to determine the prevalence of celiac disease (CD) and characterize the celiac iceberg among Saudi pediatric population in Riyadh, the capital city of Saudi Arabia. METHODS:During the study period (January 2014-June 2016), we have conducted a cross-sectional, mass scre...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Al-Hussaini A,Troncone R,Khormi M,AlTuraiki M,Alkhamis W,Alrajhi M,Halal T,Fagih M,Alharbi S,Bashir MS,Chentoufi AA

更新日期：2017-12-01 00:00:00

abstract：OBJECTIVES:Intestinal failure (IF) is a common consequence of neonatal small bowel pathology. In our experience, bowel dilatation is often responsible for the IF state in patients who fail to adapt despite adequate residual bowel length. The aim of the present study was to investigate the role of surgery to reduce bowe...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Almond SL,Haveliwala Z,Khalil B,Morabito A

更新日期：2013-06-01 00:00:00

abstract：:Current research is directed toward innovative dietary compositions that exert specific effects on health promotion and reducing the risk of diseases. For example, the demonstration that the gut microbiota is an important constituent in the intestine's mucosal barrier has led to new therapeutic strategies for infectio...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Isolauri E

更新日期：2007-12-01 00:00:00

abstract：BACKGROUND:Subacute nonsuppurative cholangitis (cholangitis lenta) is an uncommon yet important histological finding in liver biopsies from pediatric liver transplant recipients. The histopathological features include proliferation of bile ductules at the edges of portal tracts, inspissated bile within dilated bile duc...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Lin CC,Sundaram SS,Hart J,Whitington PF

更新日期：2007-08-01 00:00:00

abstract：:This study of 200 Uruguayans between 0 and 86 years old was designed to determine the prevalence of lactose malabsorption. Lactose intolerance is defined as a clinical syndrome of abdominal pain, diarrhea, flatulence, and bloating after the ingestion of a standard lactose tolerance test dose (2 g of lactose per kilogr...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Maggi R,Sayagues B,Fernandez A,Romero B,Barusso P,Hernandez C,Magariños M,Mendez G,Dilascio C,Martell M

更新日期：1987-05-01 00:00:00

abstract：:The serum levels of five acute phase proteins (APP) were measured in 18 children with Crohn's Disease (CD) or ulcerative colitis (UC) and in two control groups. The levels of C-reactive protein, alpha 1-acid glycoprotein, alpha 1-antitrypsin, C9, and Factor B were significantly raised in patients with CD and UC with g...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Campbell CA,Walker-Smith JA,Hindocha P,Adinolfi M

更新日期：1982-01-01 00:00:00

abstract：OBJECTIVES:Impaired growth has been reported in children born with esophageal atresia (EA). Their nutritional fate at adulthood remains uncertain though. Our objectives were to determine the body mass index (BMI) of adult patients with EA followed up from 2009 to 2011 in the EA clinic of a university-affiliated hospita...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Presse N,Taillefer J,Maynard S,Bouin M

更新日期：2016-03-01 00:00:00

abstract：BACKGROUND:Immune response to hepatitis B virus (HBV) antigens or mitogens in Asian children with chronic HBV infection who are mainly perinatally infected has not been studied in connection with the production of various cytokines, although these patients are considered to be less responsive to antiviral therapy. MET...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Hsu HY,Chang MH,Ni YH,Lee PI

更新日期：1999-11-01 00:00:00

abstract：OBJECTIVES:To assess and compare the long-term therapeutic response to lamivudine compared with interferon-alpha (IFN-alpha) in children with chronic hepatitis B. METHODS:A total of 40 children (27 male; age, 1.3-18 y, mean, 7.7 y) with chronic hepatitis B who received lamivudine for at least 12 months were followed f...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Choe BH,Lee JH,Jang YC,Jang CH,Oh KW,Kwon S,Hyun MC,Ko CW,Lee KS,Lee WK

更新日期：2007-01-01 00:00:00

abstract：BACKGROUND:The IMPACT-III measures health-related quality of life (HRQOL) in pediatric patients with Inflammatory Bowel Disease (IBD). The original IMPACT domain structure was developed based on expert opinion and was not psychometrically validated. This study developed a new domain structure based on the current IMPAC...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Grant A,MacIntyre B,Kappelman MD,Otley AR

更新日期：2020-10-01 00:00:00

abstract：BACKGROUND:Early postnatal glucocorticoid exposure accelerates the maturation of the bowel mucosa but results in bowel wall thinning in the newborn mouse ileum and increases the risk of focal ileal perforation in extremely premature infants. We have previously demonstrated a redistribution of insulin-like growth factor...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Gordon PV,Moats-Staats BM,Stiles AD,Price WA

更新日期：2002-10-01 00:00:00

abstract：:Management of extreme short bowel syndrome (SBS) has changed dramatically over the last 20 years with notable improvements in survival and quality of life in patients with this syndrome. A review of our institution's medical records over a 12-year period (1980-1992) revealed 32 patients with < 100 cm (range, 14-94; me...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Chaet MS,Farrell MK,Ziegler MM,Warner BW

更新日期：1994-10-01 00:00:00

abstract：BACKGROUND:Patients receiving home parenteral nutrition (HPN) are at high-risk for central line-associated bloodstream infections (CLABSI). There are no published management guidelines, however, for the antibiotic treatment of suspected CLABSI in this population. Historical microbiology data may help inform empiric ant...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Raphael BP,Fournier G,McLaughlin SR,Puder M,Jones S,Flett KB

更新日期：2020-01-01 00:00:00

abstract：:Quality training in pediatric gastroenterology, hepatology, and nutrition is essential for the future of our specialty from advancing the science through research to providing clinical care for children with gastrointestinal, hepatic and nutritional disorders. As educational theory has developed, both the American Boa...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Sauer CG,Robson J,Turmelle YP,Cerezo CS,Loomes KM,Huang JS,Quiros-Tejeira RE,Benkov KJ,Narkewicz MR,Leichtner A,Weinstein T

更新日期：2020-07-01 00:00:00

abstract：OBJECTIVE:Data suggest an increase in the incidence of pediatric inflammatory bowel disease (IBD). We examined the trend of the incidence of IBD in children. PATIENTS AND METHODS:A retrospective investigation was conducted on a cohort of children diagnosed with IBD between 1991 and 2002 who were registered in the IBD ...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Malaty HM,Fan X,Opekun AR,Thibodeaux C,Ferry GD

更新日期：2010-01-01 00:00:00

abstract：OBJECTIVES:Parents of children with autism spectrum disorders (ASDs) often report gastrointestinal (GI) dysfunction in their children. The objectives of the present study were to determine whether infants at high risk for developing ASD (ie, siblings of children diagnosed as having ASD) show greater prevalence of GI pr...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Penn AH,Carver LJ,Herbert CA,Lai TS,McIntire MJ,Howard JT,Taylor SF,Schmid-Schönbein GW,Dobkins KR

更新日期：2016-02-01 00:00:00

abstract：OBJECTIVES:The aims of this study were to compare laboratory indices of spontaneous bacterial peritonitis (SBP) and noninfected ascites in children with chronic liver disease and to determine the infectious agents involved in SBP. METHODS:The medical records of 90 children with chronic liver disease and ascites studie...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Preto-Zamperlini M,Farhat SC,Perondi MB,Pestana AP,Cunha PS,Pugliese RP,Schvartsman C

更新日期：2014-01-01 00:00:00

abstract：BACKGROUND:We analyzed the role that nutrition and the insulin-like growth factors IGF-I and IGFBP-3 play on neonatal growth. METHODS:Full-term and preterm infants with 1 and 3 weeks of postnatal life (n = 54 and n = 33, respectively) were studied. Anthropmetric variables, daily intake of energy and nutrients, and ser...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Díaz-Gómez NM,Domenech E,Barroso F

更新日期：1997-03-01 00:00:00

abstract：OBJECTIVES:The aim of the study was to understand the association between parents' perceptions of the decision process and the decision outcomes in decisions about the use of biologics in pediatric chronic conditions. METHODS:We mailed surveys to parents of children with inflammatory bowel disease or juvenile idiopath...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Lipstein EA,Lovell DJ,Denson LA,Kim SC,Spencer C,Ittenbach RF,Britto MT

更新日期：2016-12-01 00:00:00

abstract：BACKGROUND:Previously, a gluten challenge was customary to establish the diagnosis of celiac disease in children. There are no clear recommendations on how to perform this challenge or what markers to rely on for timing the biopsy after the challenge. The authors' aim was to monitor gluten intake, clinical symptoms, an...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Laurin P,Wolving M,Fälth-Magnusson K

更新日期：2002-01-01 00:00:00

abstract：BACKGROUND:Vedolizumab (VDZ) is effective for treating both adult and pediatric onset inflammatory bowel disease (IBD). Clinical outcomes, however, have been reported to be superior in patients naïve to anti-tumor necrosis factor (TNF). With the growing interest in endoscopic endpoints, we aimed to describe rates of mu...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Jossen J,Kiernan BD,Pittman N,Dubinsky MC

更新日期：2020-03-01 00:00:00

abstract：BACKGROUND AND AIMS:The aim of the present study was to evaluate proinflammatory and anti-inflammatory cytokine levels in children with irritable bowel syndrome (IBS). PATIENTS AND METHODS:Thirty-five children with IBS (17 diarrhea-predominant, 7 constipation-predominant, and 11 mixed type) and 25 healthy children as ...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Hua MC,Lai MW,Kuo ML,Yao TC,Huang JL,Chen SM

更新日期：2011-04-01 00:00:00

abstract：BACKGROUND:Health-related quality of life (HRQOL) describes the physical, social, and emotional attitudes and behavior of people in relation to health status. By the 1980s, HRQOL was noted to be impaired in chronic diseases but inflammatory bowel disease, had not been extensively described. METHODS:This review summari...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Irvine EJ

更新日期：1999-04-01 00:00:00

abstract：:The synthetic opiate loperamide (LPMD) is an antidiarrheal compound which affects both intestinal motility and the transport of water and electrolytes. We have investigated its effects on ion transport in the stripped ileal mucosa of rabbits, mounted in Ussing chambers in vitro. Addition of LPMD to serosal bathing med...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Guandalini S,Fasano A,Rao MC,Ferola A,Migliavacca M,Marchesano G,Rubino A

更新日期：1984-09-01 00:00:00

abstract：OBJECTIVES:Beneficial therapeutic effect of probiotics has been reported in children with the irritable bowel syndrome (IBS) but not consistently in other functional abdominal pain-related disorders. The aim of the present study was to investigate the effect of Lactobacillus reuteri DSM 17938 in the treatment of functi...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Jadrešin O,Hojsak I,Mišak Z,Kekez AJ,Trbojević T,Ivković L,Kolaček S

更新日期：2017-06-01 00:00:00

abstract：OBJECTIVES:Data on the outcomes of children with perianal Crohn disease (pCD) are limited, although its presence is often used for justifying early use of biologics. We aimed to assess whether pCD in children is associated with more severe outcomes as found in adults. METHODS:Data were extracted from the ImageKids dat...

journal_title：Journal of pediatric gastroenterology and nutrition

authors： Assa A,Amitai M,Greer ML,Castro DA,Kuint RC,Martínez-León M,Herman-Sucharska I,Coppenrath E,Anupindi S,Towbin A,Moote D,Konen O,Pratt LT,Griffiths A,Turner D,ImageKids Study Group.

更新日期：2017-09-01 00:00:00