Haem arginate in acute hereditary coproporphyria.

Abstract:

:An 11 year old boy presented with severe acute hereditary coproporphyria. Despite supportive measures his condition deteriorated after admission. Haem arginate, started two days after presentation, produced appreciable inhibition of porphyrin precursor overproduction and clinical improvement.

journal_name

Arch Dis Child

authors

Manning DJ,Gray TA

doi

10.1136/adc.66.6.730

subject

Has Abstract

pub_date

1991-06-01 00:00:00

pages

730-1

issue

6

eissn

0003-9888

issn

1468-2044

journal_volume

66

pub_type

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