Abstract:
:Electrophysiological findings in 40 cases of non-progressive myopathies are reported, and compared with a group of 20 cases of Duchenne progressive muscular dystrophy and a control group. In all cases the electrophysiological changes were of the mild s. c. myogenic type. The involvement of proximal and distal muscles was equal without prevalence in proximal muscles as is typical for Duchenne's dystrophy. EMG reexaminations showed a slight progression of the diseases. A peculiar feature of myotubular myopathy was spontaneous activity (fibrillation) in 70% of muscles. A myogenic character of the process of congenital deficiency of muscle innervation with preserved number of motor units is suggested.
journal_name
J Neuroljournal_title
Journal of neurologyauthors
Hausmanowa-Petrusewicz I,Ryniewicz Bdoi
10.1007/BF00313234subject
Has Abstractpub_date
1976-02-13 00:00:00pages
241-51issue
3eissn
0340-5354issn
1432-1459journal_volume
211pub_type
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abstract:: ...
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