Variants of windmill nystagmus.

Abstract:

:Windmill nystagmus is characterized by a clock-like rotation of the beating direction of a jerk nystagmus suggesting separate horizontal and vertical oscillators, usually 90° out of phase. We report oculographic characteristics in three patients with variants of windmill nystagmus in whom the common denominator was profound visual loss due to retinal diseases. Two patients showed a clock-like pattern, while in the third, the nystagmus was largely diagonal (in phase or 180° out of phase) but also periodically changed direction by 180°. We hypothesize that windmill nystagmus is a unique manifestation of "eye movements of the blind." It emerges when the central structures, including the cerebellum, that normally keep eye movements calibrated and gaze steady can no longer perform their task, because they are deprived of the retinal image motion that signals a need for adaptive recalibration.

journal_name

J Neurol

journal_title

Journal of neurology

authors

Choi KD,Shin HK,Kim JS,Kim SH,Choi JH,Kim HJ,Zee DS

doi

10.1007/s00415-016-8152-x

subject

Has Abstract

pub_date

2016-07-01 00:00:00

pages

1375-81

issue

7

eissn

0340-5354

issn

1432-1459

pii

10.1007/s00415-016-8152-x

journal_volume

263

pub_type

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