Abstract:
:Stiff-person syndrome (SPS) is a rare condition of progressive muscular rigidity and spasm, frequently accompanied by other autoimmune conditions, an association which has been further strengthened by the discovery of anti-GAD antibodies and the response of SPS to immunotherapies. Intravenous immunoglobulin (IVIg) is the mainstay therapy. Because of the rarity of the GAD antibody associated conditions, most of the information regarding treatment is case series and individual case reports. Here we describe the 15 year long management of a subject with SPS who has had a favourable outcome.
journal_name
J Neuroljournal_title
Journal of neurologyauthors
Gnanapavan S,Vincent A,Giovannoni Gdoi
10.1007/s00415-011-6015-zsubject
Has Abstractpub_date
2011-10-01 00:00:00pages
1898-900issue
10eissn
0340-5354issn
1432-1459journal_volume
258pub_type
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journal_title:Journal of neurology
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pub_type: 杂志文章,评审
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更新日期:2020-10-31 00:00:00
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pub_type: 杂志文章,评审
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更新日期:2020-05-27 00:00:00
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journal_title:Journal of neurology
pub_type: 杂志文章
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pub_type: 杂志文章
doi:10.1007/s00415-020-10260-4
更新日期:2020-10-14 00:00:00
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pub_type: 杂志文章,评审
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doi:10.1007/s00415-006-0498-z
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pub_type: 杂志文章
doi:10.1007/s00415-006-0066-6
更新日期:2006-05-01 00:00:00
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journal_title:Journal of neurology
pub_type: 杂志文章
doi:10.1007/s00415-003-1029-9
更新日期:2003-05-01 00:00:00
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pub_type: 杂志文章
doi:10.1007/s00415-018-8851-6
更新日期:2018-06-01 00:00:00
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pub_type: 杂志文章
doi:10.1007/s004150050287
更新日期:1998-12-01 00:00:00
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pub_type: 杂志文章
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更新日期:1985-01-01 00:00:00
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pub_type: 杂志文章,评审
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更新日期:2015-08-01 00:00:00
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pub_type: 杂志文章
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pub_type: 杂志文章
doi:10.1007/BF00313109
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pub_type: 临床试验,杂志文章
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更新日期:2006-06-01 00:00:00
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pub_type: 杂志文章,评审
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journal_title:Journal of neurology
pub_type: 杂志文章
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更新日期:2017-07-01 00:00:00
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journal_title:Journal of neurology
pub_type: 杂志文章
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更新日期:2020-12-01 00:00:00