A Practical Approach to Juvenile Dermatomyositis and Juvenile Scleroderma.

Abstract:

:Juvenile dermatomyositis and juvenile scleroderma are rare multisystem autoimmune disorders. Although they share some pathognomonic hallmarks with adult onset myositis or scleroderma, there are significant differences in presentation, characteristics and associated features when the diseases present in childhood. In view of this, and the rarity of the conditions, it is important for care to be led by teams with expertise in pediatric rheumatology conditions. Prognosis has improved significantly in the West; likely due to early diagnosis and aggressive treatment with immunosuppressive medications. However, this trend is not replicated in the developing world. Early recognition of these diseases is crucial to achieve rapid and sustained remission and prevent disease or medication associated complications. This article aims to provide a practical overview for recognition, diagnosis and treatment of these conditions.

journal_name

Indian J Pediatr

authors

McCann LJ,Pain CE

doi

10.1007/s12098-015-1907-z

subject

Has Abstract

pub_date

2016-02-01 00:00:00

pages

163-71

issue

2

eissn

0019-5456

issn

0973-7693

pii

10.1007/s12098-015-1907-z

journal_volume

83

pub_type

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