[Right-sided lung hypoplasia in a 13-year-old boy].

Abstract:

:Initially a right sided pulmonary hypoplasia was diagnosed in our patient at the age of 9 years. The previous years were characterized by recurrent pneumonia, bronchitis and daily coughing fits. Findings of the chest radiograph suggested the diagnosis of right sided hypoplasia. The right hemithorax was small with mediastinal structures being pushed to the right and a clearly reduced blood flow on the same side. DSA of the arteria pulmonalis showed hypoplasia of the right arteria pulmonalis and confirmed our diagnosis. In addition to that an obstructive airway disease was assessed by measurement of lung function. Since the time when the diagnosis was found our patient has inhaled DSCG and beta 2-adrenergic drugs and no surgical treatment has been required as there have been no further episodes of pneumonia.

journal_name

Klin Padiatr

journal_title

Klinische Padiatrie

authors

Riedler J,Rettenbacher L,Weiss P

doi

10.1055/s-2007-1025500

subject

Has Abstract

pub_date

1990-03-01 00:00:00

pages

112-4

issue

2

eissn

0300-8630

issn

1439-3824

journal_volume

202

pub_type

杂志文章
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  • [Evaluation of a Self-Help Supported Counseling Concept for Children and Adolescents with Disproportional Short Stature].

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    更新日期:2016-01-01 00:00:00

  • [The diagnostic value of cytology of the CSF (author's transl)].

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    journal_title:Klinische Padiatrie

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    doi:

    authors: Harms D

    更新日期:1975-03-01 00:00:00

  • [Trans-Sectoral Patient Care in Pediatric Oncology: Quality Assurance by Novel Reimbursement Models for Outpatient Services].

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    authors: Reinke E,Jürgens H,Haier J,Froehlich B,Kontny U,Rossig C

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  • [D-penicillamine-induced IgA deficiency in the therapy of Wilson's disease].

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    doi:10.1055/s-2007-1025560

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    更新日期:1990-11-01 00:00:00

  • [12 years Austrian newborn screening for inborn errors of metabolism. Results with special reference to phenylketonuria, hyperphenylalaninemia and histidinemia (author's transl)].

    abstract::The Austrian Screening Program performed during the last 12 years 5,833.381 tests in 1,003.841 newborns to detect at last 10 different disorders. 225 cases were uncovered: 81 PKU, 1 Dihydropteridine-Reductase-Deficiency, 37 Hyperphenylalaninemias of long duration, 23 Galactosemias by Transferase deficiency, 6 by Kinas...

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    doi:10.1055/s-2008-1035649

    authors: Thalhammer O,Scheibenreiter S,Knoll E,Wehle E,Schön R

    更新日期:1980-11-01 00:00:00

  • [Autoimmune hemolytic anaemia in childhood. Review and report of one case (author's transl)].

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    journal_title:Klinische Padiatrie

    pub_type: 杂志文章

    doi:

    authors: Haas RJ,Pöschl U,Christ M,Schaub J,Belohradsky BH

    更新日期:1977-05-01 00:00:00

  • Seroprevalence and significance of antibodies to hepatitis C virus in pediatric patients with malignant diseases.

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    journal_title:Klinische Padiatrie

    pub_type: 杂志文章

    doi:10.1055/s-2007-1025441

    authors: Schneppenheim R,Rautenberg P,Behnke H,Vietor K

    更新日期:1991-07-01 00:00:00

  • [Immunoglobulin and total protein concentrations in saliva of healthy children (author's transl)].

    abstract::The investigation of Immunoglobulins-and Total protein concentrations in saliva of healthy children shows an agreement with literature, a maturation in individual development of the saliva-producing organs in the mouth. ...

    journal_title:Klinische Padiatrie

    pub_type: 杂志文章

    doi:10.1055/s-2008-1035623

    authors: Tympner KD,Dörfler S

    更新日期:1980-09-01 00:00:00

  • [Reference values for the concentration of free thyroxine and free triiodothyronine in the serum of euthyroid children].

    abstract::Concentrations of free thyroxine (n = 341, male = 205, female = 136) and free triiodothyronine (n = 318, male = 198, female = 120) were determined using the radioimmunoassay method in blood serum of euthyroid children. Beyond the 30. day of life no significant differences were found in different age groups for the fre...

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    pub_type: 杂志文章

    doi:10.1055/s-2008-1026821

    authors: Liappis N,Starke A

    更新日期:1987-09-01 00:00:00

  • [Toxocariasis--a neglected ubiquitous helminthiasis in children and adolescents].

    abstract::More than 40 years ago, Toxocara ssp. was identified as the cause of larva migrans visceralis and ocular larva migrans, which mainly affect infants and children. Although widespread in most parts of the world, the parasitic disease is rarely diagnosed in Germany. Focusing on clinical and pathophysiological similaritie...

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    pub_type: 杂志文章,评审

    doi:10.1055/s-2008-1043867

    authors: Hohenschild S

    更新日期:1998-05-01 00:00:00

  • Prospective multicenter registration of major late sequelae in sarcoma patients using the Late Effects Surveillance System (LESS).

    abstract:BACKGROUND:Late effects become progressively more important for the evaluation of therapeutic success in paediatric oncology. Thus, in 1998, the Late Effects Surveillance System (LESS) started to register and assess multicentrally, prospectively and longitudinally late effects of treatment for the group of Ewing's, sof...

    journal_title:Klinische Padiatrie

    pub_type: 杂志文章

    doi:10.1055/s-2005-836503

    authors: Langer T,Stöhr W,Paulides M,Kremers A,Dörr HG,Göbel U,Beck JD

    更新日期:2005-05-01 00:00:00

  • [Psychosocial intellectual development of children with infantile cystinosis and cerebral atrophy (author's transl)].

    abstract::The psychosocial and intellectual development of 4 boys with nephropathic cystinosis and brain atrophy documented by cranial computerized tomography was investigated by use of biographical data and psychological tests (HAWIK, Deutscher Rechtschreibtest). Inspite of the brain atrophy the patients showed low-normal inte...

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    pub_type: 杂志文章

    doi:

    authors: Ehrich JH,Wolff G,Stoeppler L,Heyer R,Offner G,Brodehl J

    更新日期:1979-09-01 00:00:00

  • [Neurofibromatosis type 1 and associated clinical abnormalities in 27 children].

    abstract::Neurofibromatosis type 1 is the most common of the phakomatoses and the clinical follow-up is an interdisciplinary challenge. The data of 27 patients with NF1 were systematically reviewed and compared to data from the literature. All of our patients had clinical signs of NF1. Besides the classic criteria café-au-lait ...

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    doi:10.1055/s-2007-973086

    authors: Syrbe S,Eberle K,Strenge S,Bernhard MK,Herbertz S,Bierbach U,Hirsch W,Froster UG,Kiess W,Merkenschlager A

    更新日期:2007-11-01 00:00:00

  • [Progress and change in nuclear magnetic resonance diagnosis of congenital and acquired heart defects].

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    pub_type: 杂志文章

    doi:10.1055/s-2007-1025369

    authors: Sieverding L,Jung WI,Fleiter TH,Klose U,Steil E,Hassberg D,Rosendahl W

    更新日期:1992-09-01 00:00:00

  • [Increased incidence of developmental hip dysplasia in hypertrophic newborn infants].

    abstract::"Lack of space" in utero is considered to be a major factor in the aetiology of the congenital dislocation of the hip. This study tries to answer the question whether hypertrophy of a newborn has to be regarded as a risk factor on the basis of the principle mentioned above. The results of postnatal clinical and sonogr...

    journal_title:Klinische Padiatrie

    pub_type: 杂志文章

    doi:10.1055/s-2007-1025256

    authors: Peschgens T,Skopnik H,Casser HR,Rauschning-Sikora K,Heimann G

    更新日期:1993-11-01 00:00:00

  • [Giant lymph nodes in combined autoimmune neutro- and thrombocytopenia].

    abstract::A boy aged 15 years is described in whom a combined autoimmune neutro- and thrombocytopenia developed since the age of 11. Cell-membrane bound IgG antibodies were detected on neutrophils and platelets. A therapy with prednisone and/or immunoglobulins showed only a transient normalization of the peripheral blood values...

    journal_title:Klinische Padiatrie

    pub_type: 杂志文章

    doi:10.1055/s-2008-1033676

    authors: Schneider H,Jobke A,Böhm N

    更新日期:1988-01-01 00:00:00

  • [Familial adenomatosis coli--a precancerous condition].

    abstract::The presented paper includes the medical records of five children with familial adenomatous polyposis coli on the one hand and the detailed description of the pathologic findings of the disease on the other hand. Particular emphasis is given to the morphologic criteria of the disorder predisposing the affected individ...

    journal_title:Klinische Padiatrie

    pub_type: 杂志文章

    doi:10.1055/s-2008-1033975

    authors: Knöpfle G,Födisch HJ,Gharib M,Hollmann G,Gellissen K

    更新日期:1985-05-01 00:00:00

  • [Hereditary heterozygote factor VII deficiency].

    abstract::Hereditary Factor VII deficiency is one of the rare congenital coagulopathies. Prolonged prothrombin time (PT) with normal partial prothrombin time (PTT) may be an indicator for Factor VII deficiency. A family with hereditary heterozygous Factor VII deficiency is presented in whom no symptoms of a bleeding disorder we...

    journal_title:Klinische Padiatrie

    pub_type: 杂志文章

    doi:10.1055/s-2007-1025388

    authors: Laws HJ,Harbrecht U,Köster B

    更新日期:1992-11-01 00:00:00

  • [Sonography of the larynx in children. New perspectives due to the use of computerized sonography: 2: Sonographic findings in a case of laryngeal papillomatosis].

    abstract::On our opinion one important indication for sonographic diagnosis in future are masses in the larynx area: in infancy or childhood mainly laryngeal papillomatosis. In one of our boy patients with massive laryngeal papillomatosis laser surgery was first performed at 15 months of age. After a second and third procedure ...

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    pub_type: 杂志文章

    doi:10.1055/s-2007-1025304

    authors: Grunert D,Schöning M,Stier B,Klingebiel T

    更新日期:1989-05-01 00:00:00

  • [Combined treatment strategy in over 200 children with Hodgkin's disease: graduated chemotherapy, involved field irradiation with low dosage and selective splenectomy. A report of the cooperative therapy study DAL-HD-82].

    abstract:UNLABELLED:It was the aim of the cooperative therapy study HD-82 for children with Hodgkin's disease to reduce chemo- and radiotherapy and to investigate of a strategy for selective splenectomy previously developed in the Hodgkin study HD-78. Between December 1981 and December 1984 207 patients (131 boys and 76 girls) ...

    journal_title:Klinische Padiatrie

    pub_type: 临床试验,杂志文章

    doi:10.1055/s-2008-1026870

    authors: Schellong G,Brämswig J,Ludwig R,Gerein V,Jobke A,Jürgens H,Kabisch H,Stollmann B,Weinel P,Gadner H

    更新日期:1986-05-01 00:00:00

  • Molecular Diagnostics in Pediatric Brain Tumors: Impact on Diagnosis and Clinical Decision-Making - A Selected Case Series.

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    journal_title:Klinische Padiatrie

    pub_type: 杂志文章

    doi:10.1055/a-0637-9653

    authors: Bächli H,Ecker J,van Tilburg C,Sturm D,Selt F,Sahm F,Koelsche C,Grund K,Sutter C,Pietsch T,Witt H,Herold-Mende C,von Deimling A,Jones D,Pfister S,Witt O,Milde T

    更新日期:2018-10-01 00:00:00

  • [Rheumatic iridocyclitis in childhood--differentiation on the basis of clinical and immunological parameters (author's transl)].

    abstract::In approximately 10% of the children suffering from juvenile chronic arthritis (JCA), rheumatic iridocyclitis was also diagnosed. In 90 JCA and iridocyclitis patients we studied relative risk, clinical course and prognosis by means of several clinical and immunological parameters. Antinuclear antibodies (ANA), selecti...

    journal_title:Klinische Padiatrie

    pub_type: 杂志文章

    doi:10.1055/s-2008-1033783

    authors: Michels H,Schuchmann L,Truckenbrodt H,Renz K

    更新日期:1982-03-01 00:00:00

  • [Familial glucocorticoid insufficiency (author's transl)].

    abstract::Familial glucocortivoid insufficiency--also called hereditary lack of response of the adrenals to ACTH-has not yet been described in Europe. Isolated glucocorticoid insufficiency combined with intact secretion of aldosterone and high plasma level of ACTH are characteristic. The diagnostic difficulties are demonstrated...

    journal_title:Klinische Padiatrie

    pub_type: 杂志文章

    doi:

    authors: Petrykowski W,Burmeister P,Böhm N

    更新日期:1975-05-01 00:00:00

  • Laryngomalacia and complicated, life-threatening mTOR-positive Kaposiform hemangioendothelioma cured by Supraglottoplasty and sirolimus.

    abstract::The therapy of complicated Kaposiform hemangioendothelioma (KHE) is still difficult. We present the first case of laryngomalacia with simultaneous mammalian target of Rapamycin (mTOR)-positive KHE of the neck and thoracic inlet and concurrent Kasabach-Meritt Phenomenon (KMP) in an 11-month-old boy suffering life-threa...

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    pub_type: 杂志文章

    doi:10.1055/s-0034-1372587

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    更新日期:2014-11-01 00:00:00

  • [Severe 46,XY virilization deficit due to 17beta-hydroxysteroid dehydrogenase deficiency].

    abstract:BACKGROUND:17beta hydroxysteroid dehydrogenase deficiency is a presumable rare cause for a severe virilization disorder in children with 46,XY karyotype due to a defect in the testicular testosterone biosynthesis from androstenedione. PATIENT:We report on a 14 year old child with 46,XY karyotype with a predominantly f...

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    pub_type: 杂志文章

    doi:10.1055/s-2002-34015

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    更新日期:2002-09-01 00:00:00

  • Meconium aspiration syndrome--a 21-years' experience from a tertiary care center and analysis of risk factors for predicting disease severity.

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    pub_type: 杂志文章

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    更新日期:2013-12-01 00:00:00

  • [Comparison of chemotherapy alone with allogeneic bone marrow transplantation in first full remission in children with acute myeloid leukemia in the AML-BFM-83 and AML-BFM-87 studies--matched pair analysis].

    abstract::16 patients of studies AML-BFM-83 and -87 with allogeneic bone marrow transplantation (BMT) in first complete remission (CR) were compared with matched controls with postremission chemotherapy (CT-MC). CT-MC were selected from 250 non-grafted patients with a minimum of remission duration corresponding to the median in...

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    doi:10.1055/s-2007-1025355

    authors: Creutzig U,Bender-Götze C,Klingebiel T,Ebell W,Friedrich W,Stollmann-Gibbels B,Schmidt H,Suttorp M,Gratwohl A,Heyen P

    更新日期:1992-07-01 00:00:00

  • [Thrombocyte morphology and function during high-dose immunoglobulin therapy in acute and chronic idiopathic thrombocytopenic purpura. 1].

    abstract::We examined the effectiveness of a high-dose Immunglobulin therapy in 8 patients with idiopathic thrombocytopenic purpura (ITP) and measured the number, the morphology and the function of Thrombocytes as well as thrombocyte dependent clotting parameters. 0.5 g/kg/B.W. 7s-Immunglobulin (7s-IgG) per treatment led to nor...

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    pub_type: 杂志文章

    doi:10.1055/s-2008-1034034

    authors: Wahlen W,Graf N,Nienhaus KH,Müller J

    更新日期:1983-01-01 00:00:00

  • [De Barsy-Moens-Dierckx syndrome: unusual course in a neonate].

    abstract::We report about a premature infant with a De Barsy-Moens-Dierckx-syndrome, which is a rare cutaneo-oculo-cerebral malformation-syndrome. It is defined by the combination of a progeroid aspect, cutis laxa, growth retardation, cornea clouding, mental retardation and athetoid movements. Furthermore, the reported case sho...

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    pub_type: 杂志文章

    doi:10.1055/s-2008-1046648

    authors: Schierenberg M,Donné W,Schiafone P,Bald R,Gembruch U,Hansmann M,Rister M

    更新日期:1994-11-01 00:00:00