[Psychosocial intellectual development of children with infantile cystinosis and cerebral atrophy (author's transl)].

abstract：OBJECTIVES:Despite about 3 decades of clinical experience with the therapy of inherited thrombocytopathies (HTP) with desmopressin (DDAVP) the mechanisms of haemostatic effects of DDAVP in these diseases remain unclear. Therefore platelet function diagnostics was carried out in whole blood (WB) from children with aspir...

journal_title：Klinische Padiatrie

authors： Tauer JT,Gneuss A,Lohse JE,Jürgens T,Knöfler R

更新日期：2011-05-01 00:00:00

abstract：:Report of a case with congenital right sided intrapericardial diaphragmatic hernia. This type of a congenital diaphragmatic hernia occurs only rarely. Until 1984 30 cases are recorded in the available literature. ...

journal_title：Klinische Padiatrie

authors： Langer R,Kaufmann HJ

更新日期：1986-07-01 00:00:00

abstract：:We report about two patients with compression of the spinal cord caused by lymphosarcomas. In the first patient the tumour was localized in the lumbal region and destroyed two vertebrae. In the second patient the lymphosarcoma also infiltrated the meninx, the cord, and some internal organs. Both children died. ...

journal_title：Klinische Padiatrie

authors： Kaufmann U

更新日期：1979-03-01 00:00:00

abstract：BACKGROUND:Although considered of high prognostic impact, knowledge on the long-term outcome after neonatal parenchymatous brain lesions (PBL) is limited. PATIENTS:29 children with either unilateral (n = 19) or bilateral (n = 10) hemorrhagic/ischemic PBL. METHODS:The patients were reinvestigated at 9 9/12 +/- 3 4/12 ...

journal_title：Klinische Padiatrie

authors： Häusler M,Merz U,Van Tuil C,Ramaekers VT

更新日期：2004-07-01 00:00:00

abstract：BACKGROUND:After a first afebrile seizure, EEG in addition to cMRI is recommended for pediatric patients. Once indications requiring immediate treatment are excluded, it is of interest to determine if the results provide a prognostic tool for seizure relapses. METHODS:Patients aged between 1 month and 18 years who had...

journal_title：Klinische Padiatrie

authors： Tews W,Weise S,Syrbe S,Hirsch W,Viehweger A,Merkenschlager A,Bertsche A,Kiess W,Bernhard MK

更新日期：2015-03-01 00:00:00

abstract：:Easier access to prenatal diagnostic procedures led to its widespread use as a screening measure. Hence, today it is more common for life-limiting illnesses to be diagnosed during fetal life. The concept of Advance Care Planning (ACP) provides a framework for caregivers, families and their multidisciplinary teams to a...

journal_title：Klinische Padiatrie

authors： Garten L,von der Hude K,Strahleck T,Krones T

更新日期：2020-09-01 00:00:00

abstract：BACKGROUND:Peripheral schwannomas and pilomatrixoma are rare clinical features in childhood. The concomitant presence of these tumors in childhood are not described yet. PATIENTS:We describe the first case of a concomitant peripheral benign schwannoma and pilomatrixoma located at the head in a 10-year-old female patie...

journal_title：Klinische Padiatrie

authors： Bittmann S,Ulus H

更新日期：2005-01-01 00:00:00

abstract：:The pros and cons of home monitoring especially for premature infants with continuing apneic episodes and/or chronic lung disease are an ongoing discussion. The controversy spans socio-economic requirements, medical indication as well as patient and family needs. Here, the costs of home monitoring and follow-up care o...

journal_title：Klinische Padiatrie

authors： Förster KM,Immler S,Ensslen M,Flemmer A,Schulze A,von Poblotzki M,Genzel-Boroviczény O,Heinen F,Hilgendorff A

更新日期：2015-03-01 00:00:00

abstract：:The aetiology and pathogenesis of the Duchenne-type muscular dystrophy (pseudohypertrophic muscular dystrophy) are still largely unknown. The possibilities of treating the disease are rather limited. Treatment is the more successful, the earlier diagnosis was possible, and the earlier treatment is initiated. The CK-Sc...

journal_title：Klinische Padiatrie

authors： Beckmann R

更新日期：1978-11-01 00:00:00

abstract：:We report the first case of non-immune hydrops fetalis (NIHF) with trisomy 15q11/17q22.5 resulting from a familial translocation 15/17. Furthermore the cytogenetic findings of 50 cases with hydrops fetalis are presented. Of the 30 cytogenetic analyzable cases 7 showed chromosomal abnormalities (4x45,X; 2x47,XY,+21; 1x...

journal_title：Klinische Padiatrie

authors： Schmid G,Haverkamp F,Rechmann J,Schwanitz G,Zerres K,Hansmann M,Kowalewski S

更新日期：1987-07-01 00:00:00

abstract：:Background: Transient synovitis is the most common hip joint disorder in children. Perthes disease occurs around the same age and may not be distinguishable to an episode of transient synovitis in the early stage. Therefore all children in our clinic with transient synovitis underwent a follow-up X-ray 3 months later ...

journal_title：Klinische Padiatrie

authors： Lenoir U,Slongo T,Aghayev E,Joeris A

更新日期：2017-03-01 00:00:00

abstract：:In the present study the possibility of immunophenotyping of routinely prepared (air dried) peripheral blood and bone marrow smears is described after storage. The immunoenzymatical alkaline-phosphatase-anti-alkaline-phosphatase (APAAP)-method was carried out in differently stored blood smears (+4 degrees C and -80 de...

journal_title：Klinische Padiatrie

authors： Ebener U,Hauser S,Wehner S,Kornhuber B

更新日期：1989-07-01 00:00:00

abstract：QUESTIONS:Psychosocial variables like stress or a high achievement motivation are discussed as a possible contributory factor to an attack in migraine. The aim of our study was to examine, whether children with migraine may be at risk for impaired achievement motivation. PATIENTS/METHODS:37 children with migraine and ...

journal_title：Klinische Padiatrie

authors： Haverkamp F,Hönscheid A,Rünger M,Krois A,Harbauer A

更新日期：2005-07-01 00:00:00

abstract：BACKGROUND:Drug handling in paediatric intensive care units (PICU) is prone to medication errors. We aimed to identify type and prevalence of those errors and to assess preventative interventions. METHODS:Prospective intervention study investigating a 3-step intervention for preventing errors in drug handling in a 10-...

journal_title：Klinische Padiatrie

authors： Niemann D,Bertsche A,Meyrath D,Oelsner S,Ewen AL,Pickardt B,Henhapl T,Hoffmann G,Meyburg J,Bertsche T

更新日期：2014-04-01 00:00:00

abstract：:Evoked otoacoustic emissions (EOAE) and brainstem acoustic evoked potentials (BAEP) were recorded from 78 children following neonatal intensive care. In 23% no EOAE could be obtained. Hearing impairment in the BAEP was found in 9%. In 22% negative EOAE were found in spite of normal BAEP. According to the latency-inten...

journal_title：Klinische Padiatrie

authors： Lauffer H,Pröschel U,Gerling S,Wenzel D

更新日期：1994-03-01 00:00:00

abstract：:pO2 was measured transcutaneously (commercially available Clark Electrode, Bioelectronics Roche) with two different electrode temperatures in new born infants. The correlation between paO2 (arteria radialis) and ptcO2 was bad (r= 0,74) with electrode temperature of 42 degrees C. When the electrode was heated to 44 deg...

journal_title：Klinische Padiatrie

authors： Haschke F,Häckel F,Hohenauer L

更新日期：1976-01-01 00:00:00

abstract：:Bacterial endocarditis belongs to the rare diseases in childhood. It occurs usually as a single episode and almost exclusively in children with congenital heart disease. In recent years, however, an increased number of renewed endocarditis after the first episode were reported, especially in drug addicts. We present a...

journal_title：Klinische Padiatrie

authors： Hunkert F,Handrick W,Kinzel P,Schneider P,Spencker FB,Günther E

更新日期：1995-01-01 00:00:00

abstract：:Female patients with anorexia nervosa (a.n.) are characterized by distinct endocrine features probably due to hypothalamic pituitary dysfunctions. There is only a limited number of case reports available on patients with a.n.; mostly with few data on hormones. In six male patients with a.n. we examined basal and stimu...

journal_title：Klinische Padiatrie

authors： Toifl K,Waldhauser F,Lischka A,Frisch H

更新日期：1988-07-01 00:00:00

abstract：BACKGROUND:A fast and comprehensive diagnostic by means of whole-body CT has been shown to reduce mortality in the adult trauma population. Therefore whole-body CT seems to be the standard in adult trauma-patients. Due to the higher radiation exposure of whole-body CT the use of this diagnostic toll in pediatric trauma...

journal_title：Klinische Padiatrie

authors： Hilbert-Carius P,Hofmann GO,Lefering R,Stuttmann R,Bucher M,Goebel P,Gronwald GH

更新日期：2015-07-01 00:00:00

abstract：HINTERGRUND: Die zeitliche Verzögerung zwischen Symptombeginn und Diagnose ist eine Herausforderung in der Behandlung von Kindern mit arteriell ischämischem Schlaganfall. Frühere Studien zur klinischen Präsentation beschäftigten sich v. a. mit kumulativen Symptomen. ZIELSETZUNG: Ziel dieser Studie ist es, mögliche Sym...

journal_title：Klinische Padiatrie

authors： Gerstl L,Weinberger R,von Kries R,Heinen F,Sebastian Schroeder A,Veronika Bonfert M,Borggräfe I,Tacke M,Vill K,N Landgraf M,Kurnik K,Olivieri M

更新日期：2018-10-01 00:00:00

abstract：:A follow-up study was undertaken to determine the predictors of the course of recurrent wheezing episodes in children (between 0 to 8 years). In 1991, 600 children with wheezing episodes had been recorded by physicians who participated in a sentinel practice network. On each consultation with the same physicians from ...

journal_title：Klinische Padiatrie

authors： Seidler A,Schlaud M,Raum E,Schwartz FW

更新日期：1998-01-01 00:00:00

abstract：:Iron concentration was determined by the aid of the ESA Ferrochem 3050 analyzer and the bathophenanthroline method with deproteinization. Both methods showed a good precision and accuracy. The investigation was carried out in 505 sera with an iron concentration between 9 and 333 micrograms/dl. The comparison of the tw...

journal_title：Klinische Padiatrie

authors： Liappis N

更新日期：1982-01-01 00:00:00

abstract：BACKGROUND:Late effects become progressively more important for the evaluation of therapeutic success in paediatric oncology. Thus, in 1998, the Late Effects Surveillance System (LESS) started to register and assess multicentrally, prospectively and longitudinally late effects of treatment for the group of Ewing's, sof...

journal_title：Klinische Padiatrie

authors： Langer T,Stöhr W,Paulides M,Kremers A,Dörr HG,Göbel U,Beck JD

更新日期：2005-05-01 00:00:00

abstract：BACKGROUND:The aim of the present study was to evaluate paediatric reference values for platelet function using a point-of-care whole blood impedance aggregometry. METHODS, RESULTS & CONCLUSION: In 265 healthy infants and children aged

journal_title：Klinische Padiatrie

authors： Halimeh S,Angelis Gd,Sander A,Edelbusch C,Rott H,Thedieck S,Mesters R,Schlegel N,Nowak-Göttl U

更新日期：2010-05-01 00:00:00

abstract：:630 neonates with risk factors of perinatal hearing impairment were screened of hearing loss by means of registration of transient otoacoustic emissions before discharge from the newborn nursery. Neonates were screened additionally by means of brainstem evoked response audiometry, if they had bilateral negative emissi...

journal_title：Klinische Padiatrie

authors： Sitka U,Rehm K,Rasinski C

更新日期：1998-03-01 00:00:00

abstract：BACKGROUND:The aim of most of the trials of the Competence Network Malignant Lymphoma is to optimize the standard treatment of lymphoma using only registered drugs in the case of medicinal therapies (quality assurance protocols). In contrast to regulatory trials, special regulations for quality assurance protocols are ...

journal_title：Klinische Padiatrie

authors： Pfistner B,Mehl C,Klöss M,Löffler M,Herrmann-Frank A,Diehl V

更新日期：2003-11-01 00:00:00

abstract：:Possibilities of recognizing cerebral function disturbances in newborns as early as the acute phase of the condition, and of prognosticating permanent brain damage are described. Clinical findings such as lethargy or spasms in the second and third weeks of life following hypoxia indicate severe function disturbances w...

journal_title：Klinische Padiatrie

authors： Karch D

更新日期：1984-11-01 00:00:00

abstract：BACKGROUND:The prevalence of asthma and overweight/obesity in children and adolescents is continuously increasing over the last decades. It remains unclear if overweight/obesity raises the risk of developing asthma or if an uncontrolled asthma increases the risk of developing overweight/obesity by restricting physical ...

journal_title：Klinische Padiatrie

authors： Schmauck-Gómez JS,Menrath I,Kaiser MM,Herz A,Kopp MV

更新日期：2016-07-01 00:00:00

abstract：:We identified betulinic acid (BetA) as a new cytotoxic agent active against neuroectodermal tumor cells including neuroblastoma, medulloblastoma, glioblastoma and Ewing's sarcoma cells representing the most common solid tumors of childhood. BetA induced apoptosis independent of wild-type p53 protein and accumulation o...

journal_title：Klinische Padiatrie

authors： Fulda S,Jeremias I,Pietsch T,Debatin KM

更新日期：1999-07-01 00:00:00

abstract：:Aim of this study was to describe the course of perinatal factors in neonates with meconium aspiration syndrome (MAS) from 1990 to 2010 and to determine risk factors for a severe course of the disease.All neonates with MAS hospitalized in our level III neonatal intensive care unit from 1990 to 2010.Retrospective analy...

journal_title：Klinische Padiatrie

authors： Hofer N,Jank K,Resch E,Urlesberger B,Reiterer F,Resch B

更新日期：2013-12-01 00:00:00