Platypnea-orthodeoxia syndrome after failed percutaneous closure of secundum atrial septal defect.

abstract：OBJECTIVE:The aim of this study was to compare the effects of anesthesia by dexmedetomidine and propofol on the hemodynamics and oxygen balance in children with complex congenital heart disease who were undergoing cardiac surgery. METHODS:Fifty-seven children were randomized to receive either a continuous infusion of ...

journal_title：Congenital heart disease

authors： Cheng X,Zuo Y,Zhao Q,Gu E,Huang Y

更新日期：2015-05-01 00:00:00

abstract：BACKGROUND:Transient elastography (TE) offers a noninvasive correlate with the degree of hepatic fibrosis. However, factors other than fibrosis affect liver stiffness. We sought to determine whether hepatic congestion related to hemodynamics in Fontan circulation influences liver stiffness measurement (LSM) assessed by...

journal_title：Congenital heart disease

authors： Wu FM,Opotowsky AR,Raza R,Harney S,Ukomadu C,Landzberg MJ,Valente AM,Breitbart RE,Singh MN,Gauvreau K,Jonas MM

更新日期：2014-09-01 00:00:00

abstract：OBJECTIVE:The need for conduit replacement in the growing child remains a major problem after right ventricular outflow tract reconstruction. We compared two diverse surgical centers with considerable practice variation in Europe and the United States to identify modifiable risk factors that can increase conduit longev...

journal_title：Congenital heart disease

authors： Niemantsverdriet MB,Ottenkamp J,Gauvreau K,Del Nido PJ,Hazenkamp MG,Jenkins KJ

更新日期：2008-05-01 00:00:00

abstract：:The Fontan operation has gone through multiple incarnations since Fontan and Baudet's initial description in 1971. Through the medical dossier of a patient with a single ventricle, we plot the history of medical, surgical, and percutaneous interventions over the past 40 years, specifically focusing on the Fontan proce...

journal_title：Congenital heart disease

authors： AboulHosn JA,Shavelle DM,Castellon Y,Criley JM,Plunkett M,Pelikan P,Dinh H,Child JS

更新日期：2007-01-01 00:00:00

abstract：OBJECTIVE:Atrial septal defect (ASD) is the second most common congenital heart defect (CHD) and is observed in families as an autosomal dominant trait as well as in nonfamilial CHD. Mutations in the NKX2-5 gene, located on chromosome 5, are associated with ASD, often combined with conduction disturbances, cardiomyopat...

journal_title：Congenital heart disease

authors： Ellesøe SG,Johansen MM,Bjerre JV,Hjortdal VE,Brunak S,Larsen LA

更新日期：2016-05-01 00:00:00

abstract：:Brugada syndrome is an arrhythmogenic disease characterized by a pattern of ST segment elevation in the right precordial leads on an electrocardiogram with an increased risk of sudden cardiac death. It is primarily reported in adults with limited data about the prevalence, prognosis, and long-term management in childr...

journal_title：Congenital heart disease

authors： Zaidi AN

更新日期：2010-11-01 00:00:00

abstract：OBJECTIVE:We studied, as a physiological benchmark, acute effects of right ventricular (RV) apical, RV outflow, and left ventricular (LV) pacing in children with normal cardiac function on LV and RV function and ventricular-ventricular interactions. DESIGN:The design of the study was a prospective, acute intervention....

journal_title：Congenital heart disease

authors： Friedberg MK,Dubin AM,Van Hare GF,McDaniel G,Niksch A,Rosenthal DN

更新日期：2009-09-01 00:00:00

abstract：OBJECTIVES:To investigate functional health status among adults previously operated for aortic coarctation (CoA) compared with healthy subjects; to assess the influence of medication and exercise capacity on patients' functional health. DESIGN:Questionnaire-based investigation among 119 patients who underwent surgical...

journal_title：Congenital heart disease

authors： Pedersen TA,Røpcke DM,Hjortdal VE

更新日期：2011-11-01 00:00:00

abstract：OBJECTIVE:Enteral feeding is associated with decreased infection rates, decreased mechanical ventilation, decreased hospital length of stay, and improved wound healing. Enteral feeding difficulties are common in congenital heart disease. Our objective was to develop experience-based newborn feeding guidelines for the i...

journal_title：Congenital heart disease

authors： Simsic JM,Carpenito KR,Kirchner K,Peters S,Miller-Tate H,Joy B,Galantowicz M

更新日期：2017-05-01 00:00:00

abstract：:As physicians and caregivers of children with congenital heart disease, we are aware of the increasing need for procedures requiring anesthesia. While these procedures may be ideal for medical and cardiac surgical management, the risks and benefits must be assessed carefully. There are well known risks of cardiovascul...

journal_title：Congenital heart disease

authors： Char D,Ramamoorthy C,Wise-Faberowski L

更新日期：2016-05-01 00:00:00

abstract：INTRODUCTION:Perturbations in the CACNA1C-encoded L-type calcium channel α-subunit have been linked recently to heritable arrhythmia syndromes, including Timothy syndrome, Brugada syndrome, early repolarization syndrome, and long QT syndrome. These heritable arrhythmia syndromes may serve as a pathogenic basis for auto...

journal_title：Congenital heart disease

authors： Sutphin BS,Boczek NJ,Barajas-Martínez H,Hu D,Ye D,Tester DJ,Antzelevitch C,Ackerman MJ

更新日期：2016-12-01 00:00:00

abstract：:Protein-losing enteropathy (PLE) is a rare, but serious complication in single ventricle patients after Fontan palliation, and is associated with a 5-year mortality of 46%. We describe a patient with PLE after Fontan palliation who achieved remission with high-dose spironolactone (an aldosterone antagonist), but had t...

journal_title：Congenital heart disease

authors： Grattan MJ,McCrindle BW

更新日期：2010-03-01 00:00:00

abstract：BACKGROUND:Robust risk-adjustment algorithms are often necessary if data from clinical registries is to be used to compare rates of important clinical outcomes between participating centers. Although such algorithms have been successfully developed for surgical and catheter-based cardiac interventions in children, outc...

journal_title：Congenital heart disease

authors： Triedman JK,Pfeiffer P,Berman A,Blaufox AD,Cannon BC,Fish FA,Perry J,Pflaumer A,Seslar SP,Pediatric and Congenital Electrophysiology Society (PACES) MAP-IT Taskforce.

更新日期：2013-09-01 00:00:00

abstract：OBJECTIVE:Intraatrial Mustard baffle repair of dextro-transposition of the great arteries (d-TGA) is vulnerable to complications, typically obstruction and leaks. Because patients often require pacemakers or intracardiac electrophysiology studies (EPS)/ablation for arrhythmias, narrowed or obstructed baffles restrict c...

journal_title：Congenital heart disease

authors： Patel S,Shah D,Chintala K,Karpawich PP

更新日期：2011-09-01 00:00:00

abstract：OBJECTIVE:It is unclear whether neonates with interrupted aortic arch (IAA) and a smaller left ventricular outflow tract may have improved outcomes with a Yasui operation (ventricular outflow bypass procedure) over a primary complete repair. This study sought to identify preoperative echocardiographic parameters to dif...

journal_title：Congenital heart disease

authors： Abarbanell G,Border WL,Schlosser B,Morrow G,Kelleman M,Sachdeva R

更新日期：2018-05-01 00:00:00

abstract：OBJECTIVE:Intravascular stents are now routinely used to treat young patients with vascular stenoses. Future stent redilations are often necessary to account for somatic growth. The purpose of this study was to compile a database of characteristics for stents commonly used in the treatment of congenital heart disease p...

journal_title：Congenital heart disease

authors： Danon S,Gray RG,Crystal MA,Morgan G,Gruenstein DH,Goldstein BH,Gordon BM

更新日期：2016-12-01 00:00:00

abstract：OBJECTIVE:The study examined parent stress and health-related quality of life (HRQOL) among families of children with congenital heart disease (CHD) referred for psychological services. METHODS:Parents of 54 children (85% boys) aged 3 to 13 (Mage  = 7.48, SD = 2.38) completed measures to assess parenting stress (Paren...

journal_title：Congenital heart disease

authors： Kaugars A,Shields C,Brosig C

更新日期：2018-01-01 00:00:00

abstract：OBJECTIVES:To determine if patients evaluated using the pediatric chest pain standardized clinical assessment and management plan (SCAMP) in cardiology clinic were later diagnosed with unrecognized cardiac pathology, and to determine if other patients with cardiac pathology not enrolled in the SCAMP would have been ide...

journal_title：Congenital heart disease

authors： Kane DA,Friedman KG,Fulton DR,Geggel RL,Saleeb SF

更新日期：2016-09-01 00:00:00

abstract：:Down syndrome (DS) patients are prone to pulmonary hypertension (PHTN) due to various cardiopulmonary causes. However, the association of DS with pulmonary vein stenosis (PVS) is not adequately described. We illustrate three cases from our center and an additional 13 cases from an extensive review of the literature of...

journal_title：Congenital heart disease

authors： Gowda S,Bhat D,Feng Z,Chang CH,Ross RD

更新日期：2014-05-01 00:00:00

abstract：BACKGROUND:Left cardiac sympathetic denervation (LCSD) exerts significant antifibrillatory effects in patients with long QT syndrome (LQTS). Recently, electromechanical window (EMW) has emerged as a novel torsadogenic marker in LQTS, superior to QT interval (QTc) in distinguishing symptomatic from asymptomatic patients...

journal_title：Congenital heart disease

authors： Schneider AE,Bos JM,Ackerman MJ

更新日期：2016-09-01 00:00:00

abstract：BACKGROUND & AIMS:Fontan surgery for single ventricle congenital heart disease leads to Fontan-associated liver disease (FALD). Typical laboratory tests, imaging, and histopathology cannot predict clinical severity in FALD. HepQuant SHUNT is a proprietary serum test of hepatic function and physiology that has not yet b...

journal_title：Congenital heart disease

authors： Lemmer A,VanWagner L,Gasanova Z,Helmke S,Everson GT,Ganger D

更新日期：2019-11-01 00:00:00

abstract：INTRODUCTION:The right ventricle (RV) supports the systemic circulation in patients who have had an intraatrial repair of transposition of the great arteries or have congenitally corrected transposition. There is concern about the ability of a systemic RV to support the additional volume load of pregnancy, and previous...

journal_title：Congenital heart disease

authors： Bowater SE,Selman TJ,Hudsmith LE,Clift PF,Thompson PJ,Thorne SA

更新日期：2013-07-01 00:00:00

abstract：OBJECTIVE:  The objective of this study is to evaluate the safety and feasibility of the AZUR hydrogel-polymer coated platinum coil (hydrocoil) for vascular occlusion in patients with congenital cardiovascular disease (CCVD). DESIGN:  Retrospective case review. PATIENTS:  Eight patients with CCVD who underwent attemp...

journal_title：Congenital heart disease

authors： Goldstein BH,Aiyagari R,Bocks ML,Armstrong AK

更新日期：2012-05-01 00:00:00

abstract：:Pulmonary hypertension (PH) is a complex condition with a broad range of etiologies that result in a common outcome--elevated pulmonary arterial pressure. For the pediatric cardiologist, this entity provides a manifest demonstration of the interrelationship of cardiac and pulmonary physiology. A thoughtful approach mu...

journal_title：Congenital heart disease

authors： Kyle WB

更新日期：2012-11-01 00:00:00

abstract：:Transcatheter management of native coarctation of the aorta in 3 children with Turner syndrome is reported. Two children, 12 and 17 years of age, underwent stent implantation and 1 child, 3 years old, underwent balloon angioplasty alone. In all children the procedures were successful, both hemodynamically and angiogra...

journal_title：Congenital heart disease

authors： Kataoka K,Ozawa A,Inage A,Benson LN

更新日期：2006-11-01 00:00:00

abstract：:A 52-year-old male patient, with a medical history of surgically repaired double outlet right ventricle presented with severe aortic stenosis (AS) and hepatitis C with cirrhosis, presented with New York Heart Association Class IV heart failure. During evaluation for a liver transplant, he was deemed a poor surgical ca...

journal_title：Congenital heart disease

authors： Keswani A,Verma A,Dann K,Ventura L,Lucas V,Shah S,Ramee S

更新日期：2014-09-01 00:00:00

abstract：:Absence of the aortic valve is a rare congenital heart defect that is detectable in the prenatal period. In this condition, functional aortic valve leaflets are absent; in their place are rudimentary, immobile noncoapting plate-like structures at the level of the annulus resulting in severe aortic regurgitation. We re...

journal_title：Congenital heart disease

authors： Sabati AA,Wong PC,Randolph L,Pruetz JD

更新日期：2014-05-01 00:00:00

abstract：PURPOSE:The aim of this article was to assess the role of MRI in the diagnosis and management of a variety of complex aortic arch anomalies. MATERIALS AND METHODS:Imaging was performed on a 1.5T Philips Gyroscan Intera. We retrospectively reviewed all cardiac MR scans performed from November 2003 to February 2007 at o...

journal_title：Congenital heart disease

authors： Cantinotti M,Hegde S,Bell A,Razavi R

更新日期：2008-03-01 00:00:00

abstract：BACKGROUND:Congenital heart defects affect nearly 1% of all children born per year in the United States, and complete atrioventricular canal (CAVC) accounts for 2%-9%. While several patch materials have been used for septal defect closure during CAVC repair, clear superiority of one material over another has yet to be ...

journal_title：Congenital heart disease

authors： Al Haddad E,LaPar DJ,Dayton J,Stephens EH,Bacha E

更新日期：2018-11-01 00:00:00

abstract：:We report the case of a 30 year-old male with congenitally corrected transposition of the great arteries, atrial, and ventricular septal defects (VSD), and pulmonary stenosis. He previously underwent three palliative surgical procedures before undergoing intracardiac repair at age 20 with a left ventricular to pulmona...

journal_title：Congenital heart disease

authors： Aboulhosn J,Levi D,Sopher M,Johnson A,Child JS,Laks H

更新日期：2010-01-01 00:00:00