Abstract:
OBJECTIVE AND IMPORTANCE:Gorham-Stout disease is a rare entity characterized by vascular proliferation causing local destruction of bone tissue. Owing to its low incidence and variable clinical presentation, the diagnosis requires a high degree of awareness by the clinician. CLINICAL PRESENTATION:We present the case of a 2-year-old boy diagnosed of Gorham-Stout syndrome with involvement of the temporal bone and secondary cerebrospinal fluid (CSF) leakage. INTERVENTION:Because of the CSF leakage, the patient required two surgical interventions. The second intervention included mastectomy and placement of a patch and a lumbar drainage device during 50 days, after which the leakage ceased. CONCLUSION:Gorham-Stout disease is a rare condition that can affect the skull base and even present with CSF leakage.
journal_name
Pediatr Neurosurgjournal_title
Pediatric neurosurgeryauthors
Hernández-Marqués C,Serrano González A,Cordobés Ortega F,Alvarez-Coca J,Sirvent Cerda S,Carceller Lechón F,Azorín Cuadrillero Ddoi
10.1159/000336877subject
Has Abstractpub_date
2011-01-01 00:00:00pages
299-302issue
4eissn
1016-2291issn
1423-0305pii
000336877journal_volume
47pub_type
杂志文章abstract::Thirty-six cases of pilocytic astrocytomas treated at the Childrens Hospital of Los Angeles from 1984 through 1995 were reviewed. The mean age at initial presentation was 8 years (range 15 months to 14 years). These patients were followed for an average of 5.5 years. No patient was given chemotherapy or radiation ther...
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pub_type: 杂志文章,评审
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更新日期:2005-09-01 00:00:00
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