Scimitar syndrome associated with partial anomalous pulmonary venous draining into superior vena cava.

Abstract:

:Scimitar syndrome is a rare congenital cardiopulmonary malformation characterized by hypoplasia of the right lung and drainage of the right pulmonary veins into the vena cava inferior. It may also be associated with cardiac dextroversion and anomalies of the tracheobronchial system, cardiovascular system, and diaphragm. Some cases are asymptomatic with others diagnosed in early-childhood period with pulmonary hypoplasia and other associated malformations. We present here a patient whose venous return of the middle and lower lobes of the right lung is into the superior vena cava, which is a very unusual finding for this disorder.

journal_name

Eur J Pediatr

authors

Demir E,Aşkin M,Midyat L,Gülen F,Ulger Z,Tanaç R,Bayraktaroğlu S

doi

10.1007/s00431-010-1153-3

subject

Has Abstract

pub_date

2010-10-01 00:00:00

pages

1263-5

issue

10

eissn

0340-6199

issn

1432-1076

journal_volume

169

pub_type

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